A chang chuan doctor-in damdawi buaithlak deuh, kan hriat loh pawh a min pek hian kan hlauthawng deuh a, kan hlauthawng deuh thin a ni lawm ni? Zawhna tam tak "Hei hi eng damdawi nge ni? Hei hi eng nge thleng ang? Side effect a awm dawn em?" rilruah lo lang rawh. Vawiin hian Elapegademase vaccine chungchang kan sawi dawn a, mi tam takin an hriat ngai loh, mahse damdawi pawimawh tak a ni a, a awlsam zawngin i hrethiam thei ang.
Elapegademase hi eng nge ni?
A awlsam zawngin sawi ila, Elapegademase hi vaccine a ni a, chu chuan genetic condition hmuh tur awm lo tak a tidam thei a ni. Hetiang dinhmun hi Adenosine Deaminase (ADA Deficiency) an ti a. A hming hi a buaithlak deuh a, a awlsam zawkin han thlir ila.
Kan taksa hi factory lian tak niin han ngaihtuah teh. He factory-ah hian engkim a thawk tha tur chuan hnathawk chi hrang hrang a awm a ngai a ni. Enzyme te hi kan taksaa hnathawk te te an ni. Enzyme tin hian hna bik an nei vek a.
Chutiang enzyme bik pakhat chu Adenosine Deaminase a ni. A hna chu kan cell-a chemical duh loh (deoxyadenosine) lo awm chu tihchhiat a, taksa atanga paih chhuah a ni.
Tunah chuan mi thenkhat chu he enzyme adenosine deaminase an tih hi tlakchhamna neia piang an ni a, a nih loh leh an siam chhuah tlem hle. Chu chu ADA tlakchhamna kan tih chu a ni. He enzyme hi a bo chuan chu chemical duh loh chu taksaah a lo awm tan ta a ni. He thil hi kan immune system- a fighting cells (lymphocytes) te tan a toxic hle a ni . Chumi avang chuan chu cell te chu a chhe vek a, immune system chu a chak lo hle a ni.
He taksa hriselna chak lo tak hi Severe Combined Immunodeficiency (SCID) an ti a. Hetiang natna vei hi bacteria infection a vei awlsam hle.
Chuvangin, Elapegademase vaccine hian a tih chu taksa pawn lam atanga adenosine deaminase tih enzyme bo chu a pe a ni. Hei hi Enzyme Replacement Therapy an ti a . He vaccine hi pek a nih chuan taksaa thil tha lo awmkhawmte chu a chhe vek a, immune cells tihchhiatna chu a reh a, immune system chu a chak leh tan ta a ni. Hei hian taksain natna hrik a do theih phah a ni.
He damdawi hi i ei hmaa i doctor hnena i hrilh tur thilte
He damdawi hi i tan hma hian i hriselna dinhmun kimchang takin doctor hnenah i sawi hmasak phawt a pawimawh hle. A bik takin a hnuaia mite hi sawi tel tur a ni.
| Situation i report tur a ni | Engvângin nge chu chu a pawimawh? |
|---|---|
| Tuna hri kai theih dan (khawsik, khuh, khawsik ang chi) . | Damdawi ei tan hmain natna hrik awm tawhte chu control a pawimawh mai thei. |
| Platelet level a tlahniam | He damdawi hian thisen test a nghawng thei a, chuvangin doctor chuan natna awm tawh zawng zawng a hriat chian a ngai a ni. |
| Elapegamide emaw damdawi dang emaw, ei tur emaw, dye dang emaw allergy nei | Hei hi damdawi avanga allergy na tak awm theihna tur tehna atan a pawimawh hle. |
| Naupai emaw, nau pai tum emaw i nih chuan | Nausen pum chhunga naute chunga nghawng a neih theih dan tur chu i doctor nen in sawiho tur a ni. |
| Naute chu hnute pek a nih chuan | I doctor chuan damdawi chu nu hnute hmangin naute hnenah a kal em tih leh nghawng a nei dawn em tih te a hrilh ang che. |
He damdawi hi engtin nge dik taka i hman?
He damdawi hi intramuscular injection angin pek thin a ni . Hei hi damdawi in emaw clinic emaw-a medical team-in an pe tlangpui. Amaherawhchu, a then phei chuan damlo remchan zawk nan he injection hi in lamah pawh lak theih a ni bawk.
In lama vaccine lak a ngai a nih chuan...
Lungngai suh. Hospital-a trained nursing staff-te chuan chiang takin, step by step-in, in lama hetiang tih dan tur an kawhhmuh ang che.
- Damdawi buatsaih dan tur.
- Vaccine lakna hmun tha tak a ni.
- Vaccine lak dan tha tak a ni.
- Syringe leh needle hman tawhte him taka paih dan.
Pawimawh tak: Needle leh syringe hman tawhte chu bawlhhlawh bawlhhlawh pangngaiah paih ngai suh. Plastic bawm bik, thuk takah (sharps container)** dah tur a ni . I neih loh chuan i doctor emaw hospital emaw hnenah pakhat chungchang zawt la.
He damdawi hi naupangte hnenah i pe em?
Ni e, he damdawi hi naupangte hnenah pek a ni a, a chhan chu ADA tlakchhamna hi kum naupan lai atanga hmuhchhuah a nih fo vang a ni. Mahse, he damdawi hi naupang tê tête hnena pek dawnin ngaihtuah tur bik a awm avangin damdawi lam thupekte uluk taka zawm a pawimawh hle.
Damdawi i ei tam lutuk chuan engtin nge i tih ang?
Dose pek aia tam i ei nia i hriat chuan Colombo National Hospital-a National Poisons Information Center -ah call nghal la , a nih loh leh damdawi in hnai ber Emergency Department (ETU)-ah kal nghal rawh.
Damdawi dose i ei loh chuan engtin nge i tih ang?
- Damdawi in emaw, clinic emaw-ah i damdawi i ei a nih chuan: I appointment ruat lawk loh a pawimawh hle. Eng emaw chhan vanga i ni ruatah i kal thei lo a nih chuan damdawi inah call nghal la, hriattir rawh.
- In lama damdawi i ei a nih chuan: Dose i ei loh chuan i hriatreng veleh ei nghal tur a ni. Mahse, i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Double dose ei ngai suh.
He damdawi hian thil dang nen a inzawm em? (Inbiakpawhna) .
Damdawi dang, herbal product emaw, supplement emaw hian he damdawi nen hian engtin nge an inzawm tih hi nasa takin zirchian a la ni lo.
Chuvangin, i damdawi ei zawng zawng (condition dang damdawi, vitamin, herbal remedies, leh supplement te pawh tel) list kimchang tak i doctor hnenah pek a pawimawh hle. Tin, zu i in emaw, zu i in emaw a nih chuan doctor hrilh a pawimawh bawk.
Damdawi hman huna fimkhur tur thil
He enkawlna i dawn lai hian i doctor chuan a enfiah fo ang che.
- Scheded clinic-a kal: Hei hi damdawi hian i taksa a nghawng dan leh i natna lan chhuah dan a tlahniam em tih hriat nan a pawimawh hle.
- Thisen hnathawh: I doctor chuan i immune system hnathawh dan leh i damdawi hman tangkai dan tehna atan thisen test mumal turin a ti thei ang. Skip suh.
- Symptoms fimkhur rawh: I symptoms-ah danglamna a awm (a tha emaw a chhe emaw) a awm chuan doctor hnenah hrilh rawh.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a, mahse mi zawng zawngin an vei vek lo.
| Side effect chi hrang hrang | Ziarang |
|---|---|
| Heng symptoms te hi i neih chuan doctor hnenah hriattir nghal tur a ni. | |
| Allergy na tak a awm thei |
|
| A hnuaia symptoms, a awm fo, a awm reng emaw, a tibuai thei emaw i hmuh chuan i doctor hnenah hrilh rawh: | |
| Khuh | A thar persistent cough. |
| Luak chhuak | Damdawi ei hnua luak chhuak emaw, luak chhuak emaw. |
| Injection site-a thil thlengte | Injection na hmuna sen, na, emaw, a hring emaw. |
He list-ah hian side effect awm thei zawng zawng a tel lo. Heng bakah hian thil danglam bik i hmuh chuan i doctor nen sawiho rawh.
Damdawi hi engtin nge kan dahkhawm ang?
- Refrigerator-ah dah rawh: He damdawi hi refrigerator-a normal section-ah dah rawh. Freezer-ah dah ngai suh.
- Naupangte hmuh theih lohna hmunah dah: Naupang te leh ran vulhte thlen lohna hmunah dah rawh.
- Original packaging-ah dah rawh: Damdawi hi light laka ven nan a original packaging-ah dah a tha ber.
- Damdawi expired paih: Damdawi a expiry date hnuah hman loh tur. Damdawi expired emaw, mamawh tawh lo emaw him taka paih dan tur chungchangah doctor hnenah thurawn zawt rawh.
Take-Home Thuchah a ni
- Elapegademase hi enzyme replacement therapy a ni a, immune system a tichak a, chu chu genetic condition hmuh tur awm lo tak ADA deficiency an tih avangin a chak lo hle.
- He enkawlna hi i tan hmain i damdawi lam dinhmun zawng zawng, allergy leh damdawi dang i ei zawng zawngte chu i doctor hnenah hrilh kim vek ang che.
- Damdawi ei dan tur ruahman fel tak zawm rawh. Dose i miss a nih chuan vawi khatah dose hnih ei ngai suh.
- Allergy symptom na tak tak i neih chuan hmai emaw hmui emaw a hring, vun natna, thawk harsatna emaw i neih chuan doctor lam pan nghal rawh.
- Damdawi chu naupangte hmuh theih lohna hmunah refrigerator (freezer ni lo)-ah him takin dah la.
- He damdawi chungchangah hian zawhna emaw, ngaihtuahna emaw i neih chuan i doctor nen inbiakna neih hlau suh.











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