I fate hian hetiang thinlung lama harsatna hi a nei em? Endocardial Cushion Defect chungchang i zir dawn teh ang!

I naute a lo pian hian a chanchin engkim i ngaihtuah nasa hle a ni lawm ni? A châng chuan naupang tê tête hian pianpui thinlung lama harsatna an nei thei bawk. Chutiang, a buaithlak deuh nachungin, thinlung natna pakhat, hriat tur pawimawh tak chu Endocardial Cushion Defect (ECD) tih a ni. A hming hi a hlauhawm deuhin a lang thei a, mahse lungngai suh. Hemi chungchang hi awlsam takin, i hriatthiam theih tur angin han sawi ila, okay?

He Endocardial Cushion Defect hi eng nge ni?

A awlsam zawngin, hei hi kan naupang tête thinlunga chhiatna a ni a, chu chu pianpui , chu chu nu pum chhunga an la awm laia chhiatna a ni. Kan thinlung hi pindan pali nei in angin han ngaihtuah teh. Chhawng chung berah hian pindan pahnih (chu chu atria kan ti a), a hnuai lamah pindan pahnih (chu chu ventricles a ni) a awm bawk. Heng pindan te hi bang (septum) hmanga inthen a ni. Heng bangte avang hian thisen chu mumal takin a luang a, kawng khatah chauh a luang chhuak thin.

Tin, heng chamber inkarah hian gate ang chi valve a awm a, chu chuan thisen chu kawng khatah chauh a kal theih nan a pui bawk. A bik takin, upper chamber (atria) leh lower chamber (mitral chambers) inkar a awm tricuspid valve leh mitral valve te hi a famkim taka siam a ngai a ni.

Mahse, he endocardial cushion defect (ECD) nei nauteah hian thinlung hmun hrang hrang endocardial cushion an tih – heng bang leh valve siamtu tissue bulpui te hi an lo thang tha lo hle. Chumi avang chuan thinlung pindan inthenna bangte chu a lo thang tha lo thei a, a awm lo vek thei bawk. Valve pawimawh pahnih kan sawi tak (tricuspid leh mitral) te pawh hi a lo thang tha lo thei bawk.

Tunah chuan han ngaihtuah teh, thinlunga heng inthenna te, heng kulh te hian hna a thawk tha lo a, gate ang maia valve te pawh a thawk tha lo a nih chuan eng nge thleng thin? Thinlung chhunga thisen kal dan tur chu a tibuai a.

• Naute lungah thisen pangngai aia tam a luang lut a , chu chuan lung chhunga thisen kalna kawngah thisen sang (pulmonary high blood pressure) a thlen thin.
• Hetianga lungah hian pressure sang tak a awm avang hian thisen chu kawng dik lo lamah a luang tan ta a ni. Tichuan , oxygen tamna, thisen thianghlim leh oxygen tlachham, thisen bawlhhlawh chu a inzawm khawm tan ta a ni .
• He thisen kal dan tihbuai hmang hian thisen pump turin thinlung hian nasa takin hna a thawk a ngai a ni. Tlang lawn ang mai a ni. Hun a kal zel a, hei hian naute thinlung ruh a tichak lo thei a ni.

Endocardial cushion defect (ECD) chi hrang hrang a awm em?

Ni e, he natna hi chi hrang hrang a awm a, chu chu a chhiatna zau zawng a zirin a ni. Nausen thenkhat chuan thinlung pindan chunglam (atria) inkar wall-ah chauh harsatna an nei thei. Mi dangte chuan lower chamber (ventricles) inkar wall-ah harsatna an nei thei bawk. A châng chuan buaina pahnih hi a lo thleng dun thei bawk. Tin, mitral leh tricuspid valve-a chhiatna awmte pawh a inang lo thei bawk.

He natna hi endocardial cushion defect (ECD) tia koh a ni a, atrioventricular septal defect (AVSD) emaw atrioventricular canal defect emaw tia hriat a ni bawk.

Hetiang dinhmun hi a chang chuan pianpui thinlung natna dang nen pawh a inzawm thei bawk. Entir nan:

• Fallot-a tetralogy a ni
• Double outlet dinglam ventricle a ni
• Great arteries transposition (thisen kalna kawng lian pahnih hmun dik lovah transposition) .
• Patent ductus arteriosus hmanga siam a ni
• Ventricle pakhat (ventricle pakhat) 1.1.

Hetiang dinhmun hi engtiang chiahin nge a awm?

United States ang ram statistics i en chuan kum tin naute piang 1,800 zinga pakhat vel chuan he endocardial cushion defect (ECD) hi an nei thei a ni. Thil pawimawh dang chu Down syndrome vei zinga 20% velin he ECD natna hi an nei a ni.

Engtin nge ECD hian ka naute taksa a nghawng?

He ECD natna hi uluk taka enkawl a nih loh chuan a na zual sauh thei a, harsatna lian tak a thlen thei bawk.

• Lung chhiatna: A hmaa kan sawi tawh ang khan lungah thisen kal tam lutuk te, pressure sang lutuk te, leh hun kal zelah, lungpui tihchhiatna nghet tak a thlen thei a ni.
• Heart rhythm pangngai lo: Thinlung electrical activity a tibuai a, heartbeat pawh a mumal lo thei bawk.
• Congestive heart failure: Thinlung a chak lo a, taksaah thisen a pump tling thei lo.
• Eisenmenger syndrome: Hei hi natna khirh tak a ni. Lung chhunga pressure chu nasa takin a sang a, chu chuan thisen kal chu a tidanglam vek a, oxygen tlakchhamna thisen chu taksa pum puiah a kal kual ta a ni.

Thil na tak ṭhenkhatah chuan he natna hi nunna atana hlauhawm pawh a ni thei .

Tin, a chhiatna chu operation hmanga siam\hat a nih hnuah pawh i fa chu thinlung natna endocarditis , a vei theihna a hlauhawm thei bawk. Chuvangin, doctor-te chuan ha enkawlna thenkhat hmain antibiotics ei hmasak phawt a rawt mai thei.

Hetiang natna lan chhuah dan hi engte nge ni?

A chang chuan naute partial endocardial cushion defect nei te hian an naupan lai thlengin symptom an nei lo thei. Mahse, naute endocardial cushion defect (complete ECD) nei te chuan an pian atanga kar tlemte chhungin symptoms an nei thei a ni. Heng chhinchhiahnate hi en reng a pawimawh:

• Thinlung thawk chak tak
• Vun dum emaw, sen hring emaw:Blue discoloration zawng la, a bik takin hmui, lei leh kut zungtang te. Hei hi cyanosis an ti a.
• Ei leh in lama harsatna leh taksa rihna tihpun: I naute chu a buai em tih, hnute in hnuah a thawmhnaw a chhuak em tih emaw, a thau tha lo em tih emaw en rawh.
• Thahrui tlakchhamna: I naute chu a muhil reng a, inkhelh a ngaihven lo em ni?
• Thâwk rang emaw, thawk harsa emaw: Naute chu a rilru a thawm em tih te, a thawk chak em tih te, thawk chhuah laiin a rilru chhung lam a kal em tih enfiah rawh.
• Hri kai fo: Natna kai fo thin, a bik takin thawkna lam natna nei te fimkhur tur a ni.

Eng thilin nge he endocardial cushion defect hi a thlen?

Endocardial cushion defect (ECD) awm chhan dik tak hi hriat a la ni lo. Mahse, Down syndrome nen hian a inzawm tlat tih hmuhchhuah a ni. He defect hi naute pum chhunga naute lo thanglian tirh lamah a lo awm thin. Buaina ber chu a hmaa kan sawi tawh endocardial cushion an tih tissue hi a lo thang tha lo hle a ni. Hengte hi a hnua thinlung pindan hrang hrangte inthenna bang leh valve te an ni.

Engtin nge doctor-te hian he natna hi an hriat theih?

I naute doctor chuan i naute chu taksa enfiahna kimchang a pe hmasa ang . Tichuan, stethoscope hmanga thinlung ngaihthlak laiin aw pangngai lo (thinlung murmur) a hriat chuan he dinhmun hi a clue thei a ni.

Hei bakah hian test dang engemaw zat tih theih a ni bawk:

• Electrocardiogram (EKG/ECG): Hei hian thinlung electrical activity a test thin.
• Echocardiogram: Hei hi test pawimawh ber a ni. Sound wave hmangin thinlung thlalak a la thin. Thinlung pianzia atanga a bang khur leh valve hnathawh dan thlengin chiang takin a hmu thei a ni.
• Chest X-ray: Hei hian thinlung lian leh te leh lung dinhmun a enfiah thei a ni.
• Heart MRI: A chang chuan he test hi chipchiar zawka hriat a ngai a nih chuan tih thin a ni.
• Cardiac catheterization: Hetiang tih danah hian thisen kalna kawng (catheter) te tak te (catheter) chu thisen kaltlangin thinlung chhungah an lut a, chu chuan thinlung chhunga pressure teh a, thisen sample lak a ni. Hei hi operation hmain a ngai mai thei.

A pawimawh ber chu i naupai laia doctor pan chhunzawm a, ultrasound scan neih hi a ni.A dik taka hmuh theih. A chang chuan ECD hi naute pian hmain hriat theih a ni a, naute chu nausen pum chhunga a la awm laiin scan (fetal echocardiogram) hmanga hriat theih a ni. Hei hi hriat hmasak a nih chuan naute a pian veleh enkawlna tul tak tak tan nghal tur ruahmanna siam theih a ni.

Hei hi engtin nge enkawl a nih?

He endocardial cushion defect (ECD) enkawlna ber leh tha ber chu operation hi a ni. Amaherawhchu, zai a nih hma chuan naute chak lehzual tur leh a thau chhoh theih nan damdawi thenkhat pek theih a ni. Entirnan, taksaa tui tam lutuk tihtlemtu diuretics (‘water pills’ tia koh bawk) leh thinlung hnathawh thatna tura puitu digoxin (Cardoxin® emaw Lanoxin®) te.

Surgery hnuah eng nge thleng?

Surgery an neih chhung hian cardiac surgeon-te chuan thinlung chamber inkara thisen chhuak tur khur te chu an khar thin. Chutiang ti tur chuan patch bik an hmang thin. Tin, naute hian valve pakhat chauh a neih chuan chuta tang chuan mitral leh tricuspid valve hrang hrang pahnih an siam ang. A chang chuan naute mitral valve a leak chuan a tul chuan siamthat emaw thlak emaw theih a ni bawk.

He surgery hi naute thla 3 leh thla 6 inkar ah tih theih a ni tlangpui . Mahse, i naute hian endocardial cushion defect kimchang tak a neih chuan naute kum khat a tlin hmain operation tih hmasak a pawimawh . Hei chauh hi lung chhiatna awm reng tur venna kawng awmchhun a ni.

A châng chuan naute chu a na lutuk emaw, a thau lutuk emaw a, operation kimchang neih theih loh a ni thei bawk. Chutiang a nih chuan doctor-te chuan naute lung chhunga thisen kal zat tihtlem nan operation dang, awlsam zawk an ti hmasa ang. Hei hi pulmonary artery banding an ti a . Hei hian naute chu a chak lehzual a, a thau chhoh hma loh chuan symptoms control turin a pui thei a ni. Tichuan, a hun takah chuan a pum puia siam that theih a ni.

Enkawlnaah hian harsatna a awm em?

Surgery dang ang bawkin ECD surgery hnuah pawh harsatna engemaw zat a awm thei. Mahse, a tam zawkah chuan hengte hi enkawl theih a ni.

• Mitral valve a leak: A chang chuan operation hnuah mitral valve chu a khar tha lo thei a, thisen thenkhat chu hnunglam hawiin a leak thei bawk.
• Heart rhythm pangngai lo: Heartbeat-ah hian thil dik lo thenkhat a awm thei.

Heng harsatnate hi a chang chuan naupang chu a lo upa deuh deuh a, an tleirawl lai pawhin a lo awm thei a ni. Chuvang chuan regular medical checkup neih a pawimawh hle.

Hetiang dinhmun hi ven theih a ni em?

ECD thlen chhan dik tak hriat a nih loh avangin engtin nge a ven theih vek ang tih sawi a harsa hle. Mahse, i chhungkuaa mi tu emaw hian hetiang heart defect (ECD) emaw, genetic issue dang emaw a nei tawh a nih chuan naupai hmain genetic counselling lak hmasak phawt a tha mai thei.

Ka naute hian ECD a nei a nih chuan eng nge ka beisei ang?

Hei hi nu leh pa tam takin zawhna lian ber a ni. Thu lawmawm tak chu ECD siamthatna tura operation an neih hnuah naute tam zawk chu nun pangngai, hrisel takin an nung zel a ni. Mahse, naute hmalam hun hriselna chu an ECD nasat dan te, an lung a chhiat leh chhiat loh te, leh an hriselna zawng zawngah te a innghat a ni.

Statistics atanga a lan dan chuan operation hnu kum khatnaah damchhuah theihna chance chu 80% vel a ni. Kum 10 dang dam theihna chance chu 75% vel a ni a, kum 20 dang dam theihna chance chu 65% vel a ni.

Surgery an neih hnuah pawh naupang thenkhat chuan a hnuah harsatna an nei thei a ni. Buaina tlanglawn tak chu mitral valve a khar tha lo a, thisen a leak thin. Chutiang a nih chuan siamthat nan surgery dang tih leh theih a ni.

ECD status hi eng chen nge a awm?

Hei hi a pawimawh hle. Endocardial cushion defect (ECD) hi a takin a dam thei lo. Cardiac surgeon-in a chhiatna siam\hat nan operation a tih hma loh chuan buaina chu a awm reng ang. Surgery tel lo chuan nausen tam tak chu kum 2 emaw kum 3 aia rei an dam thei lovang. Chuvang chuan a hun taka surgery neih a pawimawh hle.

Engtin nge ka naute ka enkawl ang?

I naute chu ECD a vei tih hriat a nih hnuah, leh operation hnuah pawh, i naute chu cardiologist hnenah checkup neih fo a ngai dawn a ni . Heng follow-up appointment te hi kum khatah vawi khat emaw vawi hnih emaw a ni thei. Heng checkup te hi i fate naupan lai zawng zawng leh puitlin thlengin an chhunzawm zel ang. Hei hian doctor chuan i naute dinhmun a enfiah thei a, patch emaw valve emaw-ah harsatna a awm leh awm loh a en thei a, chu chu leak ang chi a ni a, a tul chuan a inrawlh hmasa thei bawk.

Engtikah nge ka naute hi doctor hnenah ka hruai ang?

I naute hian a hnuaia symptoms te hi a lan chhuah chuan doctor pan nghal rawh:

• Thâwk harsa tak tak
• Hun engemaw chen tlan leh khelh hnua thawhrimna tam tak tel lova hah
• Beisei angin a thang lo emaw, a thau lo emaw
• Vun rawng dum nei

Doctor hnenah eng zawhna nge ka zawh ang?

Ringhlelna i neih apiang tihfai a pawimawh hle. I doctor hnenah zawhna zawh hreh suh ang che:

• "Doctor, ka naute hian endocardial cushion defect kimchang emaw, a then emaw a nei em?"
• "Ka naute dinhmun atan hian eng treatment plan nge doctor in a rawt?"
• "Doctor, hetiang hian ECD surgery engzat nge i tih tawh?"
• "Surgery hnuah eng thil bik nge ka enkawl ngai?"

Hriat reng tur pawimawh ber berte (Take-Home Message) .

I fa tê tê tan surgery neih chu i mumang pawh a ni lo mai thei. Mahse, endocardial cushion defect (ECD) siamthatna kawng tha ber leh tangkai ber chu surgery hi a ni. He harsatna hi a mah chauhin a lo tha tawh dawn lo. Chuvangin, i hriatthiam loh thil a awm chuan i doctor hnenah hrilhfiah turin hrilh rawh.

A pawimawh ber chu nangmah chauh i ni lo. Doctor, nurse leh healthcare team zawng zawngte chu he zinkawngah hian tanpui tur leh tichak turin an awm reng a ni. Surgery zawhah pawh i naute clinic-ah kal lo la, doctor-in a tih angin a thupek zawm rawh. Chutiang chuan, nang leh i fate chuan nakin lawka harsatna lo awm thei apiang chu in hre thei ang a, hlawhtling takin in hmachhawn thei ang. Chak takin awm rawh!

` Endocardial Cushion Defect, AVSD, thinlung natna, piansualna, naupang lung natna, thinlung surgery, Down syndrome, pianpui thinlung natna, naupang cardiology