Nausen piang thar pum kan en hian a hrual em em a, a khat hlein kan hmu tlangpui a ni lawm ni? Mahse han ngaihtuah teh, a châng chuan, beisei loh takin, naute pum vun chu a hrual nasa hle tih kan hmu a, prune ang maiin. Hei hi i hmuh chuan nu emaw pa emaw angin i hlauthawng hle mai thei a, i mangang hle bawk. "Aw, ka naute kha eng thil nge thleng?" I ngaihtuah mai thei. Hei hi a takah chuan thil awm lo tak a ni. Vawiin hian hetianga thlen thei thil awm lo tak, Prune Belly Syndrome , kan sawi dawn a ni. Ngaihtuah buai suh, engkim hi awlsam tak leh chiang takin kan sawi dawn a ni.
A awlsam zawngin Prune Belly Syndrome hi eng nge ni?
Prune Belly Syndrome hi pianpui natna hmuh tur awm lo tak a ni. Naute pum vun chu prune ang maia a lan avangin a hming hi a pu a ni. Symptom lian pathum a nei a. Chuvang chuan a chang chuan ‘Triad Syndrome’ an ti thin. A hmuchhuaktu doctor te chawimawina atan ‘Eagle-Barrett Syndrome’ tia koh a ni bawk.
Heng thil pawimawh pathumte hi:
1. Pum ruh chak lo emaw awm lo emaw: Kan pum hian a pianzia vawng reng thei tur leh a chhunga taksa peng hrang hrang, intestines te venhimna tur muscle layer a nei a. He syndrome vei nauteah hian heng taksa peng hrang hrangte hi a thang tha lo hle. A châng chuan an insiam lo tak zet a ni. Chuvangin pum chhunga vun chu a hring leh a hring (wrinkled and saggy) angin a lang.
2. Undescended testicles: Nausen mipaah chuan a tlangpuiin taksa pawnah scrotum-ah a awm a. Mahse, he natna vei nauteah hian a pum chhungah a awm a ni. An la chhuk lo.
3. Urinary system lama harsatna: Hei hi a nasat ber a ni. Naute kal (kidney), bladder, leh a thlunzawm tube (ureters) te hi a lo thang kim lo. Hei hian zun kawngah harsatna lian tak a thlen thei a ni.
Heng symptom lian pathumte bakah hian nausen thenkhat chuan thinlung, lung, intestines, leh skeletal system-ah harsatna hrang hrang an nei thei bawk.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Hei hi thil awm lo tak a ni. Nau piang thar 30,000 atanga 40,000 zinga pakhat velin a vei a ni. What's special chu heng case zinga 95% hi mipa naupangah an report a ni . Chu chu a hmaa kan sawi tawh ang khan undescended testicle problem hian tlangval chauh a nghawng vang a ni.
I naute hian he natna hi a vei em tih hriat theihna tura pui thei tur chhinchhiahnate chu engte nge ni?
Prune Belly Syndrome hian symptom 50 chuang a nei nia sawi a ni. Mahse, heng symptoms te hi nausen hrang hrangah a inang lo thei. Nausen thenkhat chu nasa takin an tuar thei a, thenkhat erawh chu chutiang chuan a na lo thei bawk. I doctor chuan i naute chu a enfiah ang a, hei hi chiang taka finfiah turin test tul tak tak a ti ang.
A hnuaia table hi han en ila, a lan chhuah dan tlangpui chu engte nge ni.
| Symptom a ni | Hrilhfiahna awlsam tak |
|---|---|
| Pum chhunga vun hring (wrinkled skin) a awm | Abdominal muscle chak lo emaw awm lo emaw avang hian vun a tlahniam thei a, raisin ang maiin a hring thei bawk. |
| Pum lian tak nei | Pum chhungah taksa ruh a awm loh avangin a chhunga intestine ang chi thilte chu nawr chhuah ang maiin a lang. A châng chuan, vun hrual (twisted intestines) chu vun hring (thinth skin) atang hian hmuh theih a ni. |
| Testicles hnuai lam lo | Nausen mipaah chuan testicles pakhat emaw pahnih emaw chu scrotum chhungah a chhuk lovin pum chhungah a awm reng thin. |
| Urinary system lama harsatna awm thei | Harsatna lian tak tak, bladder leh kidney lian, urethra block, leh vesicoureteral reflux te. |
| Digestive system lama harsatna awm thei | Bowel problem leh condition hrang hrang, constipation ang chi te. |
| Skeletal system-a inthlak danglamna | Scoliosis emaw clubfoot emaw ang chi natna. |
| Lung lam harsatna a awm | Congenital heart disease emaw, thinlung insiam dan inthlak danglamna thenkhat emaw. |
Engvangin nge naute chungah hetiang hi a thlen?
Dik tak chuan doctor-te chuan hei hi a chhan dik tak an la hmu lo a , mahse theory engemaw zat a awm.
Doctor thenkhat chuan he natna hi nausen pum chhunga a lo seilian laia lo awm thin bladder-a thil danglam tak avanga lo awm niin an ngai. Chu chu zun kawng a inkhar chuan zun zawng zawng chu bladder-ah a khawlkhawm a, a hring nasa hle tihna a ni. Chutianga bladder a lo seilian chuan pum ruhte hmasawnna a tibuai a ni.
Mi dangte chuan he harsatna hi a tir lamah chuan pum ruh (abdominal muscles) a lo thanglian tha tawk loh vang niin an ngai. Mi dangte chuan genetic cause vang pawh a ni thei an ti bawk. Hetiang dinhmun hi unau zingah pawh hmuhchhuah a ni tawh bawk. Tin, naupang thenkhat chromosomal abnormalities `Trisomy 18 (Edwards Syndrome)` leh `Trisomy 21 (Down Syndrome)` te pawhin he Prune Belly Syndrome hi an nei ve bawk.
Hetiang dinhmun avang hian eng harsatna nge awm thei?
Prune Belly Syndrome nasat dan hi a kaihhnawih harsatna dangteah a innghat a, a bik takin zun kawng a tihchhiat nasat danah a innghat a ni.
Harsatna awm tam ber chu:
- Constipation: Pum ruh chak lo hian bawlhhlawh pass thei khawpa nawr nasat a ti harsa thin.
- Bone deformities: thil hip dislocation, kut, kut zungtang, ke ruh deformities ang chi.
- Urinary tract infection awm fo: Zun a chhuah that loh avangin awlsam takin infection a awm thei. Heng natna hrik te hian kal (kidney) a tichhe thei a ni.
- Nau pai theih lohna: Testicles a chhuk loh chuan nakin lawka fa neih theihna a nghawng thei a ni. Testicular cancer vei theihna a awm bawk.
- Pulmonary Hypoplasia: Pulmonary Hypoplasia: Nausen pum chhunga hmun a awm loh avangin lung a lo thang tha lo thei.
- Chronic Kidney Failure: Hei hi harsatna lian ber a ni. Urinary system lama harsatna awm chhunzawm zel chuan kal a tichhe zauh zauh thei a ni.
Engtin nge he natna hi hriat chhuah a nih?
A tam zawkah chuan he natna hi i naupai lai hian nausen ultrasound scan hmangin a hmain hriat theih a ni.Scan-a naute zun (bladder) a lian hle emaw, a kal (kidney) a hring emaw a nih chuan doctor-te chuan hei hi an ringhlel ang. Scan atang hian naute hian pum ruh a nei lo tih a lang thei bawk.
Naute a pian hnuah doctor chuan naute pawn lam lan dan, i.e. a pum hrual (wrinkled appearance) a zirin hei hi a ringhlel thei a ni. Tichuan, test hrang hrang hmangin natna a awm tih finfiah a, taksa peng hrang hrang a tihchhiat nasat zia hriat theih a ni.
Eng test nge tih thin?
- Thisen Test: Kal hnathawh dan zir rawh.
- Ultrasound Scan: Pum chhunga taksa peng hrang hrang, kal leh zunthlum te dinhmun enfiah thin ang che.
- X-ray: Skeletal system-a harsatna awm leh awm loh enfiah nan.
- CT Scan emaw MRI Scan: Organ hrang hrangte thlalak chiang zawk, chipchiar zawk hmu rawh.
- VCUG (Voiding Cystourethrogram): Hei hi X-ray test bik a ni. Hei hian bladder-ah tui bik inject a, naute zun laiin a chhunga tui luang chhuak en a huam a ni. Hei hian zun hnunglam (reflux) a luang em tih hriat nan a pui a ni.
Hei hi eng enkawlna nge ni?
Prune Belly Syndrome enkawl dan hi nausen hrang hrangah a inang lo. A chhan chu naute zawng zawng hi a nghawng dan inang vek an ni lo. A tlangpuiin, specialist team, naupang enkawltu, naupang urologist, leh nephrologist te chuan i naute enkawlna tur ruahmanna tha ber siam turin an thawk ho thin.
Enkawl dan tur thutlukna siam dawnin hengte hi ngaihtuah tel a ni:
- Naute hriselna zawng zawng.
- Naute kum zat.
- Natna nasat dan leh eng taksa peng nge tihchhiat.
- Naute hian zai leh enkawlna a tuar thiam dan.
- Nu leh pa kan nihna anga in ngaihdan leh duhdan te.
Naute thenkhat chuan an natna lan chhuah dan a nasat loh chuan zun kawng infection laka inven nan antibiotics an ei chhunzawm a ngai mai thei.
Mahse, naute tam tak chu vawi tam tak operation an neih a ngai dawn a ni. Heng surgery te hi pum chhunga bang tihchakna tur te, testicles tihhniam nan te, zun kawng lama harsatna awmte siamthatna tur te a ni.
Surgery tih hi chi hrang hrang lian tak tak a awm a:
- Vesicostomy: Hei hi surgery hmanga pum hnuai lam hawnna te tak te siam a ni a, chu chu bladder chhungah a lut a ni. Hei hian zun chu direct-in a chhuak thei a ni. Hei hian kal (kidney) chhiatna a ti tlem thei a ni.
- Orchiopexy: Hei hian pum chhunga awm testicles te chu surgery hmanga scrotum chhungah sawn a, siamthat a ni.
- Cystoplasty: Hei hi surgery buaithlak deuh a ni. Bladder siam thar vek a ngai a ni.
A nasat deuh deuhah chuan kal (kidney) a chhiat vek chuan, .Kidney transplant pawh a ngai thei bawk.
Chung naupangte hmalam hun chu eng ang nge ni ang?
Hei hi hriat a harsa deuh tih ka hria. Mahse thudik hriat a pawimawh. Heng naupangte dam rei zawng hi natna nasat danah a innghat a ni. Vanduaithlak takin naute 10% leh 25% inkar chu nausen pum chhungah an thi emaw, an pian tirh atanga kar hmasa berah harsatna avangin an thi emaw a ni.
Mahse, a êng lam a awm. Prune Belly Syndrome vei naupang 40% vel chuan an zun kawngah harsatna tenau nei mahse, kal hnathawh dan pangngai an vawng reng a, a tam zawk chu nun pangngai an hmang thin.
30% dang chuan an dam chhungin engtik lai pawhin kidney transplant an mamawh thei bawk. A pawimawh ber chu he natna nei apiang hi an dam chhung zawng damdawi lam enkawlna hnuaia awm a ngai a ni. Kidney tihchhiatna a awm loh nan urinary system enfiah fo a pawimawh hle.
I fa enkawl dan tur leh engtikah nge doctor i hmuh ang?
I fa chu Prune Belly Syndrome a vei tih hmuhchhuah a nih chuan a pawimawh ber chu doctor tawnhriat ngah tak, a natna chungchang hre chiang tak zawn hi a ni. Engkim a hrilhfiah ang che a, i fa enkawl dan tur a kaihruai ang che.
Heng naupangte tan hian Urinary Tract Infection (UTI) hi a hlauhawm hle. Chuvangin zun kawng infection chhinchhiahna tenau ber pawh i hriat chuan doctor ko nghal tur a ni.
| Urinary tract infection a awm chuan symptoms fimkhur tur | |
|---|---|
| Khawsik emaw, khawsik emaw | Zun chhuah a ngai fo thin |
| Zun hmanhmawhthlak tak a awm a, mahse tlemte chauh a chhuak. | Zun laiin kang emaw, na emaw |
| Pum hnuai lam emaw hnungzang emaw a na | Zun dum emaw, chhum emaw |
| Zun atanga rim na tak, duhawm lo tak a rawn chhuak | Zun chhungah thisen a awm |
Heng symptoms zinga pakhat tal i hriat chuan tihkhawtlai suh. Damdawi lam thurawn zawng nghal rawh. Tin, doctor-in a rawt angin hun ruat saah clinic-ah kal a, i fa chu enfiah tir a pawimawh bawk.
Take-Home Thuchah a ni
- Prune Belly Syndrome hi pianpui natna hmuh tur awm lo tak a ni a, pum ruh chak lo, testicles tla lo, leh zun lama harsatna a thlen thin.
- He hming hi naute pum vun chu raisin ang maia hrual ang maia lang a nih vang a ni.
- He natna hi naupai laiin scan hmangin a hmain hriat theih a ni fo.
- Naute dinhmun azirin enkawl dan a inang lo va, vawi tam tak zai a ngai fo bawk.
- Urinary tract infection hi heng naupangte tan hian a hlauhawm hle a ni. Infection chhinchhiahna tlemte pawh i hmuh chuan doctor pan nghal rawh.
- Heng naupangte hian dam chhung zawng enkawlna leh specialist doctor-te enkawlna an mamawh a ni. Inrelbawlna mumal tak a awm chuan naupang tam tak chuan nun tha tak an hmang thei a ni.
💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh