Cut tlemte pawhin thunun theih loh khawpin thisen a chhuah theihna dinhmunah i inhmu em? Hemophilia B ang chi thisen zam harsatna i nei mai thei. Vawiin hian hetiang thila kan taksa tanpui thei damdawi bik kan sawi dawn a ni. Vaccine Factor IX tih a ni. He thu i hriat hian hlau suh. Hemi chungchang hi awlsam takin i hrethiam vek ang u.
Factor IX chu eng nge ni?
A awlsam zawngin sawi ila, Factor IX hi protein a ni a, kan thisen a inzawm theih nan a pawimawh hle. A tlangpuiin mi pakhatin hliam a tuar chuan thisen chhuah a reh a, a chhan chu heng protein (clotting factors) te hian an thawk dun a ni. Mahse, Hemophilia B tih natna vei te tan chuan he protein Factor IX an tih hi a pianphung atanga siam a ni lo emaw, a tlem hle emaw a ni.
Chuvangin, he damdawi hian chu tlakchhamna chu siamthat tumin hna a thawk a ni. Factor IX hi vaccine anga pek a ni a, thisen zam a pui a, taksaa a luh dawna thisen chhuah a control bawk. Hemophilia B bakah hian doctor-te chuan thisen zam lohna tur natna dang thenkhat tan pawh he damdawi hi an pe thei bawk.
Damdawi ei hmaa doctor hnena i hrilh tur thilte
Okay, tunah chuan he damdawi hi i ei hmain doctor hnena i hrilh tur tlemte a awm. Heng thilte hi thup suh, i himna atan a pawimawh em em a ni.
- Natna dang i neihte chu:
- Liver natna
- Coagulation lama harsatna dang a awm bawk
- Thisen kalna kawng chhunga thisen zam (thrombosis) a lo awm dan (thrombosis) .
- Allergy: Damdawi, ei tur, dye, a nih loh leh preservative eng emaw zat allergy i nei tawh em? Hei hi sawi ngei ang che, a bik takin mihring emaw rannung emaw protein (e.g., mice, hamsters) allergy i neih chuan.
- Naupai leh nau hnute pek: Naupai, nau pai tum emaw, nau hnute pek emaw i nih chuan i doctor hnenah hrilh rawh.
He thu hi i doctor hnena a pek hian i tana enkawlna tha ber leh him ber tur chu a ruat thei ang.
He damdawi hi engtin nge i hman?
Hei hi vein chhunga injection (`(injection into a vein)`) a ni. Hospital emaw clinic emaw-a healthcare professional-in a pe tlangpui.
Mahse a chang chuan, he damdawi hi in lamah i hman a ngai mai thei. Chutiang a nih chuan damdawi inah a tul anga training pek i ni ang. Chu thupekte chu dik taka zawm a pawimawh hle.
In lama i hman chuan hengte hi hre reng ang che:
- Inbuatsaihna: Damdawi powder leh solution chu room temperature-ah lo thleng rawh.
- Mixing: A sawi angin uluk takin mix rawh. Foam siam turin chak takin vawt suh. Bottle chu a hmin theih nan swirl rawh.
- Hman dan: Dose pek zat, a hun ruatah, i doctor-in a tih angin ei thin ang che. A la awm zawng zawng chu paih vek rawh.
- Needle paih dan: Hei hi a pawimawh hle. Needle emaw syringe hman tawhte chu bawlhhlawh bawmah paih ngai suh. Sharps container bik ah dah tur a ni. I neih loh chuan i doctor hnenah pakhat dil rawh.
He damdawi hi naupangte hnenah pek theih a ni em?
Ni e, thlan bik thenkhatah chuan he damdawi hi naupangte hnenah pawh pek thin a ni. Mahse fimkhur bik a ngai a ni. Chuvangin, he damdawi hi i fa hnenah i pe dawn a nih chuan, i naupang enkawltu doctor nen hemi chungchang hi uluk takin sawipui rawh.
Damdawi i ei tam lutuk chuan engtin nge i tih ang?
He damdawi hi a dose pek aia tam i ei nia i hriat chuan Colombo National Hospital-a National Poisons Information Center ah call nghal rawh . A nih loh leh damdawi in hnai ber Emergency Department (ETU)-ah kal rawh. Tikhawtlai suh.
Damdawi nena inzawm thei thil dang
Damdawi thenkhat chu Factor IX nen an inzawm thei. Entir nan:
- Aminocaproic acid hmanga siam a ni
- Factor VIIa (factor VIIa) tih a ni.
- Tranexamic acid hmanga siam a ni
He list hi a kim lo. Chuvangin, i damdawi ei zawng zawng (doctor dangin an pek emaw, damdawi dawr atanga i lei emaw), vitamin, herbal product i hman te, leh zu i in emaw, zu i in emaw, damdawi dang i hman emaw te chu i doctor hnenah hrilh rawh
Damdawi hman huna fimkhur tur thil
- Virus hlauhawmna: Factor IX product thenkhat hi mihring thisen plasma atanga siam a ni. Chuvangin, virus ang chi thil kai theihna chance a tlem hle. Mahse, lungngai suh, hmanraw changkang ber berte hi he damdawi siam a nih hian heng virus leh bacteria tam zawk hi tihlum nan an hmang thin. Hemi chungchanga zawhna i neih chuan doctor nen inbia ang che. Hemophilia vei hmuhchhuah thar i nih chuan Hepatitis A leh B laka vaccine lak a pawimawh hle.
- ID: Hemophilia i vei chuan i details nen ID card keng reng tur a ni. Chutah chuan i hming, i damdawi ei tur hming leh a dose, i doctor hming leh phone number, leh emergency a thlen huna i biak tur mi details te a tel tur a ni. Hei hi nunna chhanhimtu a ni thei.
Damdawi avanga side effect awm thei te
Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a ni. Eng nge an nih i han thlir teh ang.
| Side effect hrang hrangte thliar hranna | |
|---|---|
| I doctor emaw Emergency Department (ETU) hnena report nghal tur thilte: | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui emaw lei emaw a hring. |
| Lung lam harsatna a awm | Chhuak na, thinlung thawk chak emaw, mumal lo emaw. |
| Thâwk lak harsat | Thâwk harsa, rilru atanga thawm ri chhuak. |
| Khawsik emaw, khawsik emaw | Chhan awm lovin khawsik emaw, khawsik emaw. |
| Injection na hmuna harsatna awm | A hmuna natna, sen, emaw, a hring emaw. |
| Thil pawi lo tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur: | |
| Flushing a ni | Hmai emaw taksaah sen leh lumna hriatna. |
| Lu na | Lu na tlangpui. |
| Nausea leh luak chhuak | Pum natna leh luak chhuak. |
| Chau lutuk | Chau tih hriatna. |
Take-Home Thuchah a ni
- Factor IX hi protein injection bik a ni a, hemophilia B ang natna vei te thisen zam a pui thin.
- He damdawi hi i ei hmain i doctor hnenah i damdawi lam dinhmun zawng zawng, allergy leh damdawi dang i ei zawng zawngte hrilh hmasa phawt ang che.
- In lama damdawi i ei a nih chuan a thupek ang chiah hian zawm tur a ni. Needle hman tawhte chu him takin paih vek tur a ni.
- I rilru natna, thawk harsa, allergy na tak ang chi symptom i neih chuan doctor lam pan nghal rawh.
- Hemophilia i vei chuan i details nen ID card keng reng tur a ni.
- He damdawi hi i tan chauh a ni. Midang hnenah share ngai suh.











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