I naute taksa sir khat chu a dang aiin a lian zawk em? (Hemihyperplasia) A chanchin hi i zir chiang ang u!

I fate taksa sir khat, kut emaw, ke emaw, an hmai sir khat emaw chu a dang aiin a lian deuh niin i hre ngai em? A châng chuan he inthlauhna hi a tlem lutuk a, a tir lamah chuan hriat theih loh a ni mai thei. Mahse naupang a lo puitlin chuan he danglamna hi a langsar zual zel a ni. Vawiin hian hetiang dinhmun hi kan sawi dawn a ni.

Hemihyperplasia hi eng nge ni? A awlsam zawngin i zawng chhuak ang u!

A awlsam zawngin sawi ila, hemihyperplasia chu kan taksa sir khat aiin a sir lehlamah a lo thang tam zawk hi a ni. Hei hi a then chuan overgrowth syndrome an ti a , a then chu hemihypertrophy an ti bawk . Hmai, kut leh ke a nghawng tam ber. Mahse a chang chuan pum chhunga taksa peng hrang hrangte pawh a nghawng thei bawk. Ke pakhat chu a dang aiin a sei deuh emaw, kut pakhat chu a thuk deuh emaw angin ngaihtuah rawh. A tirah chuan he inthlauhna hi a fiah lo hle mai thei a, mahse naupang a lo upat deuh deuh chuan a langsar zual zel a ni.

He natna hi tuin nge vei? Engtiang chiahin nge a hluar?

Hemihyperplasia hi naupangte zingah a awm thin a ni . Mipa leh hmeichhia inthlauhna a awm lo tihna a ni. It is a congenital condition , chu chu naupang chu he natna nen hian a piang tihna a ni. A châng chuan doctor-te chuan pian tirh lamah an hre chiang ṭhin. Mahse a chang chuan naupang chu a lo upa deuh hma loh chuan hriat theih loh a ni thei a, taksa sir lehlamah inthlauhna chiang taka a lan hma loh chuan.

Hei hi a awm lo hle a ni . Research atanga a lan dan chuan Beckwith-Wiedemann syndrome , hemihyperplasia subtype tlanglawn ber chu nau piang 11,000 zinga pakhat vel ah a awm thin. Chuvangin hei hi a tlem zia chu i ngaihtuah thei ang.

Engtin nge hemihyperplasia hian naupang a nghawng?

He natna hian naupang a nghawng dan ber chu taksa peng pahnih, a tlangpuiin inang vek tur, a lian zawng anga lang danglamna thlen hi a ni. Entirnan, hmai sir khat chu a sir dang aiin a lian zawkin a lang thei a, chu chu a lo thanglian zawkin a lang thei tihna a ni.

A pawimawh ber chu naupang hemihyperplasia vei te hi cancer vei theihna a sang zawk a ni . He hlauhawmna hi Wilms tumor, kal cancer chi khat leh naupang thin cancer chi khat hepatoblastoma te a ni ber. Heng cancer hlauhawmna sang tak hi taksa thanna lama he inthlauhna hian naupang chhungril lam a nghawng dan vang a ni.

I fain hemihyperplasia a neih chuan kum 7 tal cancer screening neih fo a ngai mai thei . Heng test-ah hian a tlangpuiin:

• Abdominal ultrasounds: Hengte hian tumor ang chi a lo thang lian leh awm loh an enfiah thin.
• Thisen test: Hei hian tumor marker alpha-fetoprotein tih a enfiah thin. Hei hian cancer a awm leh awm loh hriat theihna a pe thei a ni.

Heng test chungchang i hriat hian hlauhna i nei thei a, mahse heng thilte hi hriat lawk a, test dik taka tihsak hi i fa hriselna atana pawimawh ber a ni.

Hemihyperplasia natna lan chhuah dan chu engte nge ni?

Hetiang dinhmun chhinchhiahna ber leh langsar ber chu taksa sir khat chu a sir dang aiin a lian zawk a ni . A chang chuan he danglamna hi a fiah lo hle a, mahse hun kal zelah a langsar zual zel.

Symptom dang (a hmaa kan sawi tawh Beckwith-Wiedemann syndrome nena inzawm fo) te chu:

• Beng bulah a hring chhuak.
• Abdominal wall-a chhiatna thenkhat.
• Internal organs (liver, pancreas, kidney) tihpun.
• Lei lian tak.
• Thisen sugar level hniam (hypoglycemia) .

Heng symptoms pakhat emaw pahnih emaw a awm vang mai mai hian a natna chu a awm tihna a ni lo va, mahse i fain heng thilte hi a neih chuan doctor pan a tha ber.

Hemihyperplasia leh Hemiatrophy hi eng nge an danglamna?

Heng pahnih hian taksa lian leh te a tidanglam thin. Mahse, hemiatrophy hi taksa sir khata lo thanglian lo tihna a ni . Hemiatrophy hian taksa hmun khat chauh a nghawng tlangpui a, chu chu kutphah ang chi hi a ni. Hemihyperplasia hian a rualin taksa hmun hrang hrang a nghawng thei a ni.

Eng thilin nge hemihyperplasia hi a thlen?

Thil engemaw takah chuan hemihyperplasia hi Beckwith-Wiedemann syndrome tih hming pu genetic syndrome vang a ni thei. A dang erawh chuan he natna hi genetic disorder awm lovin a awm thei bawk. Chutiang hunah chuan Doctor-te chuan a chhan dik tak an hre lo. Chromosome abnormality nena inzawm lo a nih chuan sporadic condition a nih a rinawm a, chu chu a thleng mai mai tihna a ni.

Engtin nge hemihyperplasia hi an hriat theih?

Hemihyperplasia hriat theihna tur test bik a awm lo . I fa doctor chuan taksa peng hnih inkara ṭhanlenna inang lo a hmuh chuan, Beckwith-Wiedemann syndrome i vei em tih hriat nân taksa endikna leh genetic testing a nei thei a ni. Heng genetic test te hian i doctor hnenah he natna hi genetic condition avanga lo awm a nih leh nih loh a hriat theih nan a pui thei a ni.

Tin, naupang doctor chuan ultrasound hmangin a chhungril taksa peng hrang hranga thil danglam emaw, tumor emaw a awm leh awm loh a enfiah thei bawk.

Hei hi damdawi famkim a awm em? Enkawlnate chu engte nge ni?

Ni lo, Hemihyperplasia hi damdawi a awm lo . Mahse, lungngai suh. I fate medical team chuan an mamawh ang zela leh an natna lan chhuah dan azirin enkawlna tur ruahmanna an siam ang.

Naupang hemihyperplasia enkawl dan chu taksa sir lehlamah inthlauhna zau zawngah a innghat a ni. I fate medical team-ah hian specialist te pawh an tel thei a, chungte chu:

• Hepatologist: Liver nena inzawm harsatna nei tan.
• Orthopedist: Limb length ang chi thil atan.
• Nephrologist: Kidney nena inzawm harsatna nei tan.
• Neurologist: Nervous system nena inzawm.
• Naupang enkawltu: Naupang hriselna leh hmasawnna tlangpui enfiah thin.
• Plastic surgeon: A chang chuan hmel danglamna siamthat nan.

Heng specialist zawng zawng hian i fa enkawlna tur ruahmanna siamin, i fa pum chhunga taksa peng hrang hrangte chu an enfiah vek a ni. Hemihyperplasia hi cancer vei theihna a tipung a, doctor-te pawhin hepatoblastoma ang chi natna hi an ngaihven reng bawk.

Naupang hian operation a mamawh dawn em?

A châng chuan operation hian limb sei zawng inang lo chu a siam ṭha thei ṭhin . Hei atan hian surgery chi hrang hrang a awm a. I medical team-in operation an rawt chuan i fa tan eng surgery chi nge tha ber tih sawipui rawh. I fa chuan:

• Kut/ke tawi tih sei nan surgery a ni.
• Ke ruh lian/kut lian thang chakna tlem a control theihna surgery.

Enkawlna hian harsatna emaw, side effect emaw a nei em?

I fain operation a neih chuan a dam chhungin kar tlemte chhung chu a chau hle mai thei . An incision na hmunah pawh natna an nei thei bawk. I fate surgery bik avanga side effect dang awm thei chu i doctor zawt rawh.

Operation hnuah a dam leh theih nan eng chen nge a duh?

I fain operation a neih chi hrang hrang a zirin a dam leh hun chhung hi a inang lo. Operation hnu ni engemaw zat emaw, kar engemaw zat emaw chhung chu i hring chhuak thei a, i na a, i rilru a hah thei bawk. Hun kal zelah hmasawnna i hmuh loh chuan i fa doctor nen inbia ang che.

Hetiang dinhmun hi ven theih a ni em?

Hemihyperplasia, naupai laiin a lo awm mai mai thin chu ven theih a ni lo . Mahse, i naute hian Beckwith-Wiedemann syndrome a nei thei.Chuvangin hemihyperplasia i vei a, fa dang neih i beisei a nih chuan i doctor nen genetic testing chungchang sawipui rawh . Heng test te hian i fa dangte pawhin heng chromosomal abnormalities te hi an nei dawn em tih hriat nan a pui thei a ni.

Nangmah emaw, i kawppui emaw hian genetic disorders history i neih a, fa neih i ngaihtuah a nih chuan doctor nena inbiakna neih a tha. Preconception counseling pawh i ngaihtuah duh mai thei .

Ka fa hian hemihyperplasia a vei a nih chuan eng nge ka beisei ang?

Nangmah emaw i fa emaw hian hemihyperplasia i vei a nih chuan taksa peng hrang hrang lian tham lo chuan harsatna engemaw zat a thlen thei a ni . Entîr nân, thawmhnaw inkawp ṭha tak hmuh chu a harsa thei hle. Limb sei zawng inang lo hian a chang chuan crawling, walking, leh running ang chi thil a nghawng thei bawk.

Tin, hemihyperplasia hmuhchhuah a nih chuan i fa chu cancer enfiah fo a ngai dawn tihna a ni bawk . I fa kum 7 vel a tlin hma loh chuan thla engemaw zat danah heng test te hi tih thin beisei ang che.

Hemihyperplasia hi eng nge a hmalam hun?

Hemihyperplasia hi dam chhung zawnga natna a ni . Mahse, zirchianna chuan cancer hmuhchhuah hmasak leh screening neih fo hian hmalam hun chu nasa takin a tichangtlung thei tih a tarlang . Naupang screening neih fo chuan cancer a vei tak tak a nih pawhin, tumor te tak te leh natna hmasa ber a nih a rinawm zawk. Enkawlna an tan hma poh leh a hlawhtlin theihna a sang zawk.

Hemihyperplasia natna hi dam chhung pangngai neih theih a ni em?

Hemihyperplasia vei naupang tam zawk hi nun hrisel tak an hmang a , dam rei zawng pawh an nei tlangpui . Naupan laia cancer endik a pawimawh hle nachungin, naupangin tleirawl a thlen chuan he cancer vei theihna hi a tlahniam zauh zauh a ni.

Doctor hnenah eng zawhna nge ka zawh ang?

I fain hemihyperplasia a neih chuan zawhna tam tak i nei thei. Chûng zawhnate chhânna hriatna chuan rilru thlamuanna a pe ang che a, nakin hun atâna inbuatsaih tûrin a ṭanpui ang che. I fa doctor emaw nurse emaw hnenah zawhna zawt la:

• Ka fate hemihyperplasia natna hi genetic nge sporadic?
• Engvangin nge he enkawlna emaw, operation emaw hi i rawt?
• Ka naute chu operation hma leh operation zawhah a hahdam theih nan eng nge ka tih ang?
• Naupang chu damdawi inah eng chen nge a awm a ngaih ang?
• Eng ang cut nge awm, a awm a nih chuan?
• Naupang hian damdawi eng emaw a mamawh ang em?
• Naupang tan operation leh anesthesia te hian eng hlauhawmna nge a neih?
• Naute chu operation hnua a dam leh theih nan eng chen nge a mamawh ang?
• Ka fa hun rei tak hriselna chungchangah eng nge ka beisei ang?

Heng zawhnate bakah hian i rilru a i neih zawng zawng chu i doctor hnenah zawh hreh suh.

A tawp berah chuan take-home message

Hemihyperplasia, hemihypertrophy emaw overgrowth syndrome tia hriat bawk hi pianpui natna a ni a, taksa sir khat chu a sir dang aiin a thang tam zawk a ni. Heng than dan inang lote hi pian tirh lamah a lang lo mai thei. I fain an ke leh ke sei zawng emaw, an taksa lian zawng emaw a inthlauhna a neih chuan naupang enkawltu doctor nen inbia ang che. Hetiang dinhmun hian cancer vei theihna a tihpun avangin natna hi hriat hmasak a pawimawh . Hlauthawng lova, leh damdawi lam thurawn leh enkawlna tul tak tak i dawn hian i fa chu nun hrisel tak nei turin i pui thei ang.

` Hemihyperplasia, Beckwith-Wiedemann syndrome, overgrowth syndrome, Wilms tumor, hepatoblastoma, pianpui dinhmun, naupang hriselna