Aw, a chang chuan kan naute hian natna an tawrh theih dan ngaihtuah hian a buaithlak hle a ni lawm ni? A bik takin, naute pum chhunga a la awm laia kan hriat thin dinhmun thenkhat hi a buaithlak hle a, hriatthiam harsa tak a ni. Vawiin hian thluak natna khirh tak, a tlem em em, mahse hriat tur pawimawh tak chungchang kan sawi dawn a ni. Hei hi hydranencephaly an ti a.
Hydranencephaly hi eng nge ni tak tak?
A awlsam zawngin sawi ila, hydranencephaly hi nau piang laia thluak lam natna hmuh tur awm lo tak a ni. Hetiang dinhmunah hian naute thluak hmun pawimawh tak pahnih, cerebral hemispheres , an tih chu a lo piang lo. Ngaihtuah teh, kan thluak peng lian ber chu thluak (cerebrum) a ni. Chutah chuan heng hemisphere pahnih hi an awm a ni. Ngaihtuahna, hriatrengna leh hriatna te hi heng cerebral hemispheres te hian an thunun vek a ni.
Chuvangin, hydranencephaly vei naute lu-ah chuan, cerebral hemispheres awmna tur hmunah chuan, cerebrospinal fluid (CSF)-a khat bawm a awm a ni. He cerebrospinal fluid (CSF) hi a takah chuan kan thluak leh ruhro hualtu leh humhimtu tui a ni. Mahse hetiang dinhmunah hian thil danglam tak a thleng thin.
Hun a kal zel a, heng naute lu hi a lian chho tan a. Tin, symptom na tak dang a lo lang thei bawk. Lungchhiatthlâk takin, he dinhmun hian naute chu a pian hnu lawkah a thih phah fo va, nu pum chhungah awm lo mah se.
Hydranencephaly leh Hydrocephalus hi eng nge an danglamna?
Hydrocephalus tih natna pakhat i hre tawh mai thei. Heng pahnihah hian lu lian leh cerebrospinal fluid (CSF) a awm khawm a ni. Mahse heng dinhmun pahnih hi a danglam hle.
Hydrocephalus hi thluak chhunga tui, cerebrospinal fluid (CSF) an tih chu a lo pungkhawm a, chu chuan luruh chhungah pressure a tisang a ni. Hei hian thluak a tichhe thei a ni. Pian tirh lamah a awm thei a, accident emaw, natna emaw hnuah pawh a lo awm thei bawk. A châng chuan hydrocephalus hi hydranencephaly an tih natna lan chhuahna angin a awm thei bawk.
Mahse hydranencephaly-ah chuan nausen pum chhunga a la awm laiin thluak a thang tha lo. Chumi awmzia chu thluak peng tlem zawk a lo thang lian tihna a ni.
Heng dinhmun pahnih hi thliar hran a pawimawh a, enkawlna leh prognosis a inang lo hle a ni. Hydrocephalus vei naute tam tak chu uluk taka hmuhchhuah leh enkawl an nih chuan an dam thei a ni. Mahse, naute hydranencephaly vei te chuan an nei lo tlangpui.
Chuti a nih chuan hei leh holoprosencephaly hi eng nge a danglamna?
Hei hi thluak thanlenna nena inzawm thil danglam danglam tak a ni bawk.Holoprosencephaly-ah chuan naute thluak hmalam (forebrain), a hmaa kan sawi tawh cerebral hemispheres te chu a inthen lo. Chu chu hmun hnih ni lovin, pakhat angin a awm reng tihna a ni. Mahse, hydranencephaly-ah chuan chu hemisphere te chu a awm lo vek a ni.
A natna a nasat dan azirin holoprosencephaly vei naute thenkhat chu an pian hnuah an dam thei a ni.
He natna, Hydranencephaly hi engtiang chiahin nge a awm?
Hei hi thil awm lo tak a ni. Scientist-te chuan he natna hian naupai 10,000 zinga pakhat vel, a nih loh leh naupai 5,000 zinga pakhat a nghawng niin an chhut. Chu chu a hniam hle mai.
Engvangin nge hydranencephaly hi a lo awm? A chhante chu engte nge ni?
Dik tak chuan scientist-te chuan hydranencephaly hi eng nge a thlen tih chiang takin an la hre lo . Hrilhfiahna a ni thei a, mahse a thlen dan erawh hriatthiamna chiang tak a awm lo.
Mahse, ṭhenkhatah chuan he natna hi naupai laiin nuin toxin a tawrhna nen a inzawm tih hmuhchhuah a ni . Chuvangin naupai lai hian fimkhur hle tur a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
Hydranencephaly vei naute a pian chuan ni hmasa berah chuan naute pangngai ang maiin a lang thei. Chuvângin, hriat nghâl chu a harsa mai thei. A natna lan chhuah dan chu a dam chhung kar hmasa emaw, thla engemaw zat emaw chhungin a lang tan thin. A lan chhuah dan thenkhat chu hetiang hi a ni:
- Naute chu a lo thang lian thei lo tihna a ni .
- Muscle stiffness a pung emaw a tlahniam emaw thei a, chubakah muscle twitching .
- Lu chu a pangngai aia lian a ni.
- Hmuh leh hriat harsat .
- Ke ruh leh ke ruh (limbs) a nghet lo.
- Thâwk lak harsat .
Heng symptoms pakhat emaw a aia tam emaw i neih chuan doctor thurawn lak nghal a pawimawh hle.
Engtin nge Hydranencephaly hi hriat theih?
Hetiang dinhmun hi a châng chuan naute pian hmain hriat theih a ni a, chu chu ultrasound scan neih laiin a ni . I hriat angin ultrasound scan hian nu pum chhunga naute thlalak a siam a. Tichuan, naute thluak (cerebral hemispheres) te chu a bo tih hriat theih a ni.
Prenatal ultrasound-ah hydranencephaly a awm tih a hriat chuan doctor chuan MRI a ti thei a, chu chuan thlalak chiang zawk a hmu thei ang.
Mahse, a chang chuan naupai laiin hriat theih a ni lo va, naute pian hnuah pawh he natna hi a awm reng thei a ni. Chutiang a nih chuan, chu natna chu hriat theih nân kar tam tak emaw, thla tam tak emaw pawh a ngai thei a ni. A chhan chu, a hmaa kan sawi tawh ang khan, naute chu a tir lamah chuan a pangngai angin a lang thei a ni.
Doctor chuan naute natna lan chhuah dan leh thluak MRI hmangin a natna hi a finfiah thei a ni. MRI hian hydranencephaly hi natna dang, hydrocephalus leh holoprosencephaly, a hmaa kan sawi tawhte aiin a thliar hrang thei a ni.
Tin, test dang pawh tih theih a ni a, chungte chu:
- Angiography: Hei hi Dye bik hmanga thisen kalna kawng X-ray thlalak lak a ni.
- CT scan: Hei hi thluak thlalak lak dan dang a ni.
- Hydranencephaly ultrasound: Hetiang dinhmun hi enfiahna atana ultrasound test bik tih a ni.
- Transillumination: Hei hian luruh hnuai atanga thluak tissue kaltlangin êng a chhuah a, thil danglam a awm leh awm loh en a ni.
- Genetic testing: Hrilhfiahna atanga lo chhuak a nih leh nih loh en rawh.
Naute hydranencephaly vei te tan eng enkawlna nge awm?
Hei hi thil sensitive tak a ni. Nau neih hmaa test neih laiin hydranencephaly a awm tih finfiah a nih chuan chhungkaw ṭhenkhat chuan therapeutic abortion neih an rel a, chu chu damdawi lam thila naupai tihtawp a ni. Hei hi thutlukna harsa tak a ni a, mahse chutiang hunah chuan doctor leh counselor-te chuan a tul angin puihna an pe thin.
Naute hi hydranencephaly vei a piang a nih chuan a damdawi a awm lo. Enkawlna hian a natna lan chhuah dan tihtlem leh naute a nuam thei ang bera siam a tum ber a ni.
- Surgery hi thluaka tui tam lutuk lakchhuah a, thluaka pressure tihhniam nan shunt (tube te tak te) dah a ni. Hei hi hydrocephalus enkawlna tha tak a nih laiin, hydranencephaly tan chuan a tangkai lo hle.
- Endoscopic Choroid Plexus Coagulation (ECPC) tih damdawi hi a chang chuan thluak lian chak tak enkawlna atan hman theih a ni.
Chu bakah, doctor chuan hetiang hi a rawt thei bawk:
- Antiseizure damdawi hman tur.
- Nutritional support a ni.
- Physical therapy hmanga taksa ruh natna (muscle symptoms) tihziaawmna tur.
- Thluak lama harsatna a awm chuan tracheostomy (thlah surgery tenau) emaw, mechanical ventilation emaw a ngai thei.
Hetiang hydranencephaly natna hi ven theih a ni em?
Scientist-te chuan hetiang thil a thlen chhan hi an la hre chiang tawk lo a, chuvangin a ven dan tur chiang takin an sawi thei lo. Mahse, a hmaa kan sawi tawh ang khan case thenkhat chu naupai laiin toxins nena inzawmna nei an ni. Entirnan, ruihhlo cocaine, meizuk, leh seizure damdawi thenkhat sodium valproate te.
Chuvang chuan nu naupai tan chuan toxins an inhriat loh nan a pawimawh hle. Damdawi ei tur eng pawh an doctor nena inbiakna neih a pawimawh bawk.
Hydranencephaly vei naute dam rei zawng chu engzat nge ni ang?
Hei hi hriat a lungchhiatthlak hle. Hydranencephaly vei naupangte tan chuan outlook a tha vak lo. Nausen tam tak chu an pian hma emaw, kum khat an tlin hmain emaw an thi thin. A tlem hle a, intensive supportive care-ah chuan naupang hydranencephaly vei chu kum engemaw zat a dam thei a ni.
Hetiang dinhmun hi engtin nge i hmachhawn?
I fa hian hydranencephaly ang chi natna a nei tih hriat chu thil harsa tak a ni. Chu chu hriatthiam theih a ni.
- He natna hi a nasat zia hrethiam turin chhungkaw tinte zirtirna mamawh pek a pawimawh hle.
- Tin, counseling zawng leh dinhmun inang tawk chhungkaw dangte nena inzawmna siam theihna tur support group-a tel hi chakna nasa tak a ni thei bawk.
Hydranencephaly hi piansualna hmuh tur awm lo tak a ni a, thluak hmasawnna a tichhe thei a ni. Pian hma emaw, pian hnu rei vak lo emawa hriat chhuah a ni tlangpui. I naute hian he natna hi a neih chuan i medical team chuan nang leh i chhungte tanpuina, zirtirna leh counseling i mamawh zawng zawng an pe ang che. Nangmah chauh i ni lo tih hre reng ang che.
Take-Home Thuchah hnuhnung ber
Nu leh pa duh takte u, Hydranencephaly hi thinlung ti na tak leh harsa tak a ni tak zet a ni. Amaherawhchu, fimkhur a pawimawh hle.
- Hei hi thluak hmun thenkhat a lo thanglian tha lo a nih chuan a awm lo hle.
- Hei hi nau neih hmaa scan hmangin hriat theih a ni fo .
- Hei hi damdawi awm lo mah se, a natna lan chhuah dan control leh naute rilru hahdamna tur enkawlna a awm .
- A chhan dik tak hriat a nih loh avangin fimkhur taka hmalak a pawimawh a, chu chu naupai laia toxins ei loh te hi a ni.
- Hetiang dinhmun hmachhawn chhungkua te hian doctor te, counselor te, leh support group te hnen atangin chakna nasa tak an nei thei a ni .
Hemi chungchanga zawhna dang i neih chuan i doctor nen inbia ang che. I mamawh thu leh kaihhruaina zawng zawng an pe ang che.
` Hydranencephaly, thluak tha lo, nau piangsual, naute hriselna, cerebrospinal fluid, hydrocephalus, nau neih hmaa diagnosis











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