hATTR (hereditary transthyretin-mediated amyloidosis), genetic condition hmuh tur awm lo tak i nei em? I kut leh kea natna, rilru hahna, emaw, hriatna hloh reng rengte chu i chau tawh em? Chutiang a nih chuan i doctor chuan Inotersen tih hming pu vaccine chungchang a hrilh che a ni mai thei. Vawiin hian he damdawi hi eng nge a nih, eng nge a tih, leh a hman huna i fimkhur a ngaih thu te tawi te tein i sawi dawn nia.
Inotersen hi eng damdawi nge a nih?
A awlsam zawngin sawi ila, Inotersen hi hATTR tih natna vei te nerve lama harsatna nei te enkawlna atana pek thin vaccine a ni. He hATTR natnaah hian kan taksaa protein siam chhuah pakhat hian a tul aia tam a khawlkhawm a, nerve a tichhia a ni. He damdawi hian chu protein chu taksaa a khawlkhawm tihtlem nan hna a thawk a ni . Tichuan, i taksa peng hrang hranga natna, rilru hahna, leh hriatna hloh te ang chi natna lan chhuahna te chu zawi zawiin a tlahniam tan ta a ni. He damdawi hi `(Tegsedi)` tih hming puin bazarah hmuh theih a ni.
He damdawi hi i ei hmaa i doctor hnena i hrilh tur thilte
He damdawi hi i ei tan hmain doctor nen in sawiho ngei tur thil engemaw zat a awm. He information hi i himna atan a pawimawh hle.
- Kal natna i neih chuan: Kal lama harsatna i neih chuan min hrilh ang che.
- Thisen cell count tlem i neih chuan: Entîr nân, a hmaa thisen var, red blood cell, platelet hniam i neih nia hriat i nih chuan i doctor hnênah hrilh rawh.
- Allergy i neih chuan: Inotersen chauh ni lovin, damdawi dang, ei tur dang emaw, dye dang emaw i allergy i neih chuan min hrilh rawh.
- Naupai emaw, naupai tum emaw i nih chuan: Hemi chungchang hi i doctor hrilh a pawimawh a, he hun chhung hian damdawi chungchangah fimkhur bik a ngai a ni.
- Nu hnute petu i nih chuan: Nau hnute pek lai pawhin hei hi hriat reng a pawimawh.
Vaccine hi engtin nge hman ang?
Hei hi vun hnuaia injection a ni . Ngaihtuah buai suh, i doctor emaw nurse emaw chuan i inject dan tur dik tak a kawhhmuh ang che. Doctor-in a sawi ang chiah chiah, ni dik takah leh a zat dik takah injection hi ei a pawimawh hle. A tih loh tur a tih che hma loh chuan hmang chhunzawm zel ang che.
Pawimawh tak: Needle leh syringe hman tawhte chu bawlhhlawh bawmah paih ngai suh. Sharps container bik ah dah tur a ni. I neih loh chuan i doctor hnenah i neih dan tur zawt la.
He damdawi nen hian instruction leaflet bik ``(MedGuide)`` i dawng ang. A hun apiangah ngun takin chhiar thin tur a ni tih hre reng ang che.
Damdawi i ei tam lutuk chuan engtin nge i tih ang?
Damdawi i ei tam lutuk nia i hriat chuan damdawi in hnai ber Emergency Department (ETU) -ah kal nghal rawh . A nih loh leh Colombo National Hospital a National Poisons Information Center ah biak theih a ni bawk .
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
I hriatreng veleh missed dose kha ei nghal rawh. Mahse, i dose leh tur chu ni hnih aia rei lo a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Vawi khatah vawi hnih ei ngai suh, chu chu double dose tihna a ni.
He damdawi nena inzawm thei thil dang
He damdawi i ei lai hian damdawi dang i ei a nih chuan fimkhur hle tur a ni a, an inzawm thei a ni. Damdawi, vitamin leh herbal remedies i ei zawng zawngte chu i doctor hnenah hrilh rawh.
A hnuaia tarlan te hi he damdawi nena inzawm thei damdawi thenkhat an ni.
| Ruihhlo chi hrang hrang | Entirnan |
|---|---|
| Thisen tithianghlimtu | Warfarin, Enoxaparin, Aspirin, Clopidogrel, Apixaban, Rivaroxaban te pawh a awm bawk |
| Natna tidamtu (NSAIDs) . | Damdawi Ibuprofen leh Naproxen ang chi te |
| Infection thenkhat tan antibiotics leh damdawi dangte | Acyclovir, Gentamicin, Vancomycin, Amphotericin B. te hi a tha hle a, a rilru a hah lutuk chuan a rilru a buai em em bawk a |
| Diuretics te pawh a awm | Furosemide ang chi damdawi te |
| Damdawi dang | Cisplatin, Cyclosporine, Zoledronic acid, Pamidronate te a awm bawk |
He list hi a kimchang lo hle a, chuvangin i ei zawng zawng doctor hnenah hrilh vek a tha ber.
Damdawi ei huna fimkhur tur thil
- Doctor hmu fo rawh: I doctor hnenah i awm dan leh damdawi a thawk tha em tih hriat nan i check fo thin. I symptoms a na zual em tih hrilh rawh.
- Vitamin A lakah fimkhur rawh: I doctor chuan he damdawi i ei lai hian vitamin A supplement ei turin a hrilh mai thei che. Hei hi a chhan chu he damdawi hian taksaa vitamin A level a tihhniam theih vang a ni. I doctor-in a hrilh angin vitamin A supplement ei thin ang che. Tin, i ei leh in chungchang pawh sawipui bawk ang che.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a ni. Ṭhenkhat chu a serious a, a then chu a common. Hengte hi hriat chian a pawimawh.
| Side effect a awm thei | Hrilhfiahna |
|---|---|
| I doctor hnena hrilh nghal tur thil | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui, lei emaw kawr emaw a hring. |
| Kidney hliam a awm | Zun chhuah tlem, ke ruh, kut leh ke ruh hring. |
| Liver hliam a awm | Pum dinglam a na, chaw ei chak lohna, luak chhuak, vun emaw mit emaw a sen, zun dum/brown. |
| Thisen chhuah emaw, hliam emaw danglam tak | Vun awlsam taka hliam, hnar thisen chhuak, leh hmui thisen chhuak. |
| Thai | Hmai, kut leh ke sir khatah rang taka rilru hah/thawlh, tawng harsa, kal harsa, lu na nasa tak. |
| A awm reng emaw, a buaithlak emaw chuan doctor hnenah hrilh rawh. | |
| Injection na hmuna natna leh sen hring | Injection hmuna thil thleng (reaction). |
| Lu na | |
| Luhai | |
| Khawsik | |
| Chau | |
Engtin nge damdawi chu i dahkhawm thin?
He damdawi hi uluk taka dahkhawm a pawimawh hle.
- A tha ber: Refrigerator-ah dah tur a ni. Mahse, freeze ngai suh. Hman theih a nih hma chu original packaging-ah dah tur a ni.
- Thil tih dan dang: He damdawi hi room temperature (20-25 Celsius inkar) ah kar 6 thleng dah theih a ni. Mahse, i tih chuan eng leh lum lakah i venghim tur a ni. Kar 6 hnuah a la awm zawng zawng chu paih vek tur a ni.
- Naupang leh ran vulhte hmuh theih lohna hmunah dah ngei ang che.
Damdawi hun kal tawh emaw, hman loh emaw chu bawlhhlawh bawmah emaw, toilet hnuaiah emaw paih ngai suh. I doctor hnenah him taka paih dan tur zawt rawh.A tih dan tur tha ber a hrilh ang che.
Take-Home Thuchah a ni
- Inotersen hi hATTR an tih natna avanga thluak lam harsatna vaccine a ni.
- Damdawi i ei tan hmain i doctor hnenah natna dang i neih leh i damdawi ei zawng zawngte hrilh hmasa phawt ang che.
- Vaccine dik taka inject dan zir rawh. Needle hman tawhte chu him takin paih vek tur a ni.
- Side effect na tak tak, allergy, kidney emaw liver lama harsatna emaw, paralysis emaw i neih chuan doctor hnenah hrilh nghal rawh.
- Damdawi chu refrigerator-ah emaw, doctor-in a tih angin emaw dah la.
- He damdawi chungchanga zawhna i neih chuan i doctor zawh hreh ngai suh.











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