I fa hian vun rawng leh taksa listless tak a nei em? Juvenile Dermatomyositis (JDM) chungchang hi i zir dawn nia.

I fa chu a hma aia a chau zawkin a inhria em, a tlan kual vel emaw, stairs a chhoh lai emaw pawhin? A nih loh leh, a hmaiah emaw, a kutah emaw, a sen/purple spot a nei em? Heng symptoms te hi i neih chuan a pangngai angin hnawl suh. Hei hi naupangte zingah chuan a awm fo thei a, mahse mi tam tak chuan an hre lo. Ngaihtuah buai suh, chiang takin kan sawi dawn nia.

Juvenile Dermatomyositis (JDM) hi eng nge ni?

A awlsam zawngin, Juvenile Dermatomyositis (JDM) hi kan taksa peng hrang hrang (immune system)-a chhiatna awmin kan vun, taksa ruh leh thisen kalna kawngte a rawn bei a ni. Chutiang natna chu autoimmune disease kan ti a. Hemiah hian taksaah inflammation a awm a. Hei hian vun natna leh taksa ruh chak lohna a thlen ber a ni . "Juvenile" tih awmzia chu kum naupan lai, chu chu naupan lai atanga intan a nih vang a ni.

He natna hian naupang tan tho, tlan, stairs lawn, leh nitin hna, kut chawi leh sam hrual te pawh a ti harsa thei a ni. Nu leh pa kan nih angin naupang hetiang taka a beih lai hmuh hi a lungchhiatthlak hle thei a ni. Mahse a pawimawh ber chu enkawl dan dik a nih chuan heng symptoms te hi a control tha thei a, naupang chuan nunphung tha tak a nei thei bawk .

He natna hi tuin nge vei tam ber?

JDM hi naupang kum 5 leh 10 inkar atanga tan a ni tlangpui a, mipa aiin hmeichhiaah a tam zawk. Naupang tu pawh a nghawng thei a, mahse naupang var zingah a tam zawk.

Puitling pawhin heng symptoms te hi an nei thei bawk. Mahse kum 40 leh 50 chho velah a lang tlangpui. Dermatomyositis an ti a. An pahnih hian condition group khatah an awm ve ve a ni.

JDM natna lan chhuah dan ber berte chu engte nge ni?

Naupang hian he natna hi a hriat hma pawhin a hmaa chhinchhiahna engemaw zat a lantir thei a ni. He natna lan chhuah dan ber chu vun inthlak danglam leh taksa ruh chak lohna te a ni. Hengte hi a hranin han thlir ila.

Natna khirh tak takah pawh a awm thei symptoms

Hengte hi a tlem ber tlangpui. Mahse, JDM a nasat chuan naupang thawk leh ei leh in ruhte pawh a nghawng thei bawk . Heng symptoms te hi a hnuaia mi ang hian a ni thei:

• Chaw ei hi a ei hian a tlakbuak fo thin.
• Aw a inthlak a, a chak lo.
• Thâwk harsa (Dyspnea).

Enkawl loh chuan eng harsatna nge a awm?

Hei hian hlauthawng suh. Hei hi enkawlna i hmuh loh chuan eng nge thleng thei tih chungchang a ni. Tunlaia enkawlna changkang tak tak hmang hian heng thil tam tak hi ven theih a ni.

• Calcium deposits: Vun hnuaiah hian lung ang chi hnah khauh tak tak a lo awm thei. Chungte chuan taksa ruhte tiharh a harsat phah thei a ni.
• Muscle contractures: Muscle a tight a, ruh a ben lai pawhin a awm thei.
• Ulcers: Ulcers hi vunah emaw, intestines-ah emaw a awm thei .
• Chak lohna nasa tak: I chak lo lutuk a, thawk i la thei lo va, i ei thei lo bawk.

Engvangin nge he JDM hi a lo awm? Eng nge a chhan?

Hetiang hian han ngaihtuah teh: kan taksa hi kulhpui ang a ni. A chhungah hian sipai pakhat, immune system an tih chu a awm a. An hna chu hnam dang hmelma virus leh bacteria ang chi te bei a, min venhim hi a ni. JDM ang autoimmune natna ah chuan he sipai hian kan cell tha (vun, thau) te chu a rawn bei sual tan thin.

He immune system malfunction chhan dik tak hi hriat a la ni lo a, mahse doctor-te chuan genetic component leh environmental factors (entir nan, virus infection) inzawmkhawm vang a ni thei niin an ngai.

Engtin nge doctor hian he natna hi dik taka a hriat theih ang?

I fa chu doctor hnena i hruai dawn chuan uluk takin naupang chu a enfiah hmasa ang a, vun natna leh taksa ruh chakna ang chi thilte a enfiah hmasa ang. Hei bakah hian test eng emaw zat tih theih a ni a, chu chu a natna hmuhchhuah a nih thu finfiah theih a ni.

• Thisen test: Hengte hian thisen a inflammation level leh muscle a chhiat huna muscle enzyme siam chhuah level a enfiah thei a ni. JDM-a hmuh theih protein bik (autoantibodies) an zawng thei bawk.
• Electromyography (EMG): Hei hian needle ang chi electrode te tak te tak te chu taksa ruh chhungah dahin an electrical activity tehna a ni.
• MRI (Magnetic Resonance Imaging): He test hian magnet lian tak hmangin taksa chhunga inflammation leh swelling te chiang takin a hmu thei a, a bik takin taksa ruh chhunga inflammation leh swelling te chu a chiang hle.
• Muscle biopsy: Hei hi surgery tenau tak, muscle tissue te tak te tak te lakchhuah a, microscope hmanga enfiah a ni. Hei hi JDM nge taksa natna dang (e.g. muscular dystrophy) a nih leh nih loh finfiah nan a pawimawh hle.
• Nailfold capillaroscopy: Naupang nail hnuaia thisen kalna kawng te tak te (capillaries) te chu a hring em tih enfiah nan hmanraw bik hman a ni. Heng thisen kalna kawngte hian JDM vei naupangteah hian danglamna bik a nei tih hmuh theih a ni.

JDM enkawl dan tur chu engte nge ni?

JDM enkawlna tum ber chu taksaa inflammation tihziaawm te, symptoms control te, naupang nun tha tak nei tura tanpui te hi a ni. Enkawlna hian natna lan chhuah dan a bo hunah remission hun engemaw chen a thlen thei.

Damdawi chi hrang hrang

• Corticosteroids te hi a hnuaia mi ang hian a ni.Hengte hi damdawi chi hrang hrang pek hmasak ber a ni. Hengte hian inflammation a tihziaawm thuai thin. A tir lamah chuan dose sang takin pek an ni a, chutah chuan symptoms a reh deuh deuh chuan dose chu tihhniam zauh zauh a ni.
• Methotrexate: Damdawi pawimawh dang, corticosteroids nen emaw, ei hnu emawa pek thin a ni. Immune system hnathawh a control a ni.
• Hydroxychloroquine: He damdawi hian vun rawng titawp turin a pui hle.
• Intravenous immunoglobulin (IVIG): Hei hian thisen kaltlangin taksaah antibody thianghlim tak tak pek a huam a ni. Hei hian kan taksa tichhe mek antibodies te chu a block thei a ni.
• Damdawi dang: A natna a nasat emaw, damdawi dang a chhan loh emaw chuan doctor chuan damdawi dang cyclosporine leh rituximab te a pe thei a ni.

Nunphung thlak danglam leh enkawl dan dang

Damdawi bakah hian heng thilte hi a pawimawh hle bawk.

• Physical therapy: Physical therapist chuan taksa ruh tichak turin exercise a zirtir a, ruh nghet tihziaawmna tur leh flexibility tihpun nan a zirtir thin.
• Ni laka invenna: Hei hi a pawimawh hle. Ni chhuahna hian vun rawng a ti na zual thei. Chuvangin, SPF 30 aia sang sunscreen hman fo tur a ni. Hat leh sunglass vuah rawh. Zing dar 10 leh tlai dar 4 inkarah ni êng chak tak lakah pumpelh tur a ni.
• Ei leh in tha: Thlai, thei, protein tha lo, leh buh chi hrang hrang tamna ei leh in hian taksaa inflammation tihziaawmna kawngah a pui thei a ni.
• Speech therapy: Speech therapist chuan ei leh in lama harsatna nei naupangte chu ei leh in him dan leh exercise te a zirtir thin.

Nakin hun chungchâng eng nge kan ngaihtuah ang?

JDM damdawi a awm lo. Mahse, hlauthawng suh. Thu lawmawm tak chu enkawlna hmang hian naupang tam tak chu hlawhtling takin, active takin an nung thei a ni.

Naupang tam zawk chu enkawl tan atanga kum hnih chhungin remission-ah an kal ang. Chutih lai chuan damdawi ei kha i chawlhsan thei mai thei. Amaherawhchu, natna lanchhuahna a lo kir leh loh nan ei leh in tha, exercise leh ni laka invenna tha tak i neih chhunzawm zel tur a ni.

Naupang thenkhat chuan he natna hi rei tak an nei thei a, a nih loh leh a lan chhuah dan a bo a, a lo lang leh thei bawk. Mahse, JDM hi nunna atana hlauhawm a ni lo. Damdawi lam enkawlna mumal a awm chuan he natna hi uluk taka enkawl theih a ni a, naupangte pawhin naupang dang ang bawkin nun pangngaiin an hmang thei bawk.