I kal (kidney) te hi sponge ang mai a ni em? Vawiin hian Medullary Sponge Kidney chungchang kan sawi dawn!

‘Medullary Sponge Kidney’ tih hi i la hre lo mai thei. Sawifiah harsa deuh niin a lang a, mahse a takah chuan kal (kidney) nena inzawm congenital condition a ni. A awlsam zawngin, i kal chhungah, a bik takin kal lai tak (medulla)-ah tui bubble te tak te, cyst an tih te a lo awm na hmun a ni. Vawiin hian he thu hi chipchiar takin sawi ila, kan sawi dawn em ni?

Medullary Sponge Kidney hi eng nge ni tak tak?

Kidney hi eng nge a nih a, engtin nge a hnathawh tih hi han en hmasa ila. I hriat angin kal (kidney) hi kan taksaa zun (Urinary system) pawimawh tak a ni. Kidney tin hian middle part an nei a, chu chu medulla kan ti a. He medulla hian channel te tak te tak te, tiny tubules an tih te a nei a. Heng channel te hian thisen atanga bawlhhlawh filtered te chu an khawlkhawm a, zun an siam thin. Tichuan heng channel te hi an inzawm khawm a, channel lian deuh deuh, collecting ducts an tih te nen an inzawm khawm a ni. Chung atang chuan zun chu kal lai takah a khawlkhawmna hmunpui ber, renal pelvis-ah a kal a ni. Chuta tang chuan zun chu ureter kaltlangin bladder thlengin a kal a, chuta tang chuan urethra kaltlangin taksa a chhuahsan leh thin.

Okay, tunah chuan `Medullary Sponge Kidney` nei mi pakhat chunga thil thleng chu ka sawi tawh collecting ducts te hian cyst te te an siam a, chu duct te chu an lo hring chhuak a, an lian chho ta zel a ni. Sponge ang maiin an lang. Chuvang chuan `Sponge Kidney` tih a ni. Hetiang dinhmun hian kal pahnih a nghawng tlangpui a, mahse a chang chuan kal pakhat chauh a nghawng thei bawk.

Engtin nge he medullary sponge kidney condition hi a lo awm?

Tunah chuan heng cyst te hi an lo awm hian eng nge thleng tih zawhna i nei ta. Heng cyst te hi a lo awm chuan chu fine channel (tubules) te chuan hna a thawk tha thei lo. Tichuan, heng channel chhungah hian calcium ang chi thil a awm tan ta a ni. Hei hi (nephrocalcinosis) kan ti a. Calcium chauh ni lovin thil dang phosphate leh oxalate te pawh hetiang hian a pungkhawm thei a ni. Hun a kal zel a, heng thil khawlkhawmte hi an inzawm khawm a, kal lung (kidney stone) an siam a ni .

Heng cyst leh lungte hian zun kawng kal tlanga zun kalna tur a tikhawlo bawk a, chu chuan zun kawng infection (UTIs) vei theihna a tipung a ni.

Hei leh Polycystic Kidney Disease hi eng nge a danglamna?

Polycystic Kidney Disease (PKD) tih hi i hre tawh mai thei. Tin, kal (kidney)-a cyst (cyst) lo awm thin natna a ni bawk. Chuti a nih chuan eng nge an danglamna?

Polycystic kidney disease (PKD) hi genetic natna a ni a, a tlangpuiin rochun a ni. Kidney a ti lian a, taksa pum puiah cyst tam tak a lo awm thin. PKD hian a chang chuan harsatna lian tak a thlen thei bawk.Nun chhung zawng harsatna a thlen thei a ni. PKD vei tam tak chuan kal (kidney failure) an nei a, an thisen tihthianghlim nan dialysis an mamawh a ni.

Mahse, medullary sponge kidney (MSK) vei te tan chuan kal (kidney failure) hi a tlem hle . Chu chu a danglamna ber chu a ni.

He natna hian tute nge a nghawng ber? Engtiang chiahin nge a hluar?

Tunah hian he ``medullary sponge kidney (MSK)'' natna hi random takin a thleng niin an ngai. Chu chu chhan bik nei lo tihna a ni. Amaherawhchu, chhungkaw \henkhatah a lo lan avangin rochan theihna eng emaw zat a awm thei a ni. Mahse, a tan hian genetic pattern chiang tak hmuh tur a la awm lo.

Mi tam zawk chuan natna lanchhuahna a lan hnuah chauh an nei tih an hrechhuak a, a tlangpuiin kum 20 vel an ni. Hmeichhia pawh mipa aiin an hlauhawm zawk niin an sawi bawk .

A hluar hle a, a vaiin mi 5,000 zinga pakhatin MSK an vei a ni. Mahse, kal (kidney stone) nei tan chuan a tam zawk hle. Chumi awmzia chu chutiang mi 12% leh 20% inkar chuan MSK an nei thei tihna a ni.

Medullary sponge kidney hian hypertension a thlen em?

Mi thenkhat chuan he ``MSK'' hian hypertension emaw pressure emaw a thlen em tih an ngaihtuah mai thei. Tuna zirchianna atanga a lan dan chuan ``medullary sponge kidney'' hian hypertension a thlen tih finfiahna a awm lo .

Eng thilin nge medullary sponge kidney hi a thlen?

Doctor-te chuan mi thenkhatin he natna hi an neih chhan chiang takin an la hre lo. Nausen stage-a kal (kidney development) lama harsatna awm vang nia ngaih a ni a, chutih lai chuan naute chu a pum chhungah a la awm a ni .

He natna lan chhuah dan engte nge ni?

Mak tak maiin Medullary Sponge Kidney (MSK) vei tam tak chuan symptoms an nei lo . Chumi awmzia chu natna an vei tih pawh hre lovin an khawsa tihna a ni. Za zela tlemte chauh, 10% vel chauhvin symptoms an nei thin.

Chutiang symptoms a awm chuan urinary tract infection (UTIs) leh kidney stones nen a inzawm tlangpui. Hengte hi a lan chhuah dan berte chu an ni:

• Zun chhunga thisen (hematuria): Hei hian zun chu a sen thei tihna a ni a, a chang chuan tea tui rawng a ni.
• Flank pain: I hnungzang sir lehlamah, i rib cage hnuai lama natna awm.
• Zun laia na (dysuria): Zun laiin kang leh na a awm thei.
• Kidney stones: Hei hi mi tam takin an lo tawn tawh a ni. Back pain na tak nen a lo thleng thei bawk.
• Urinary tract infection: Zun tam leh khawsik ang chi natna lanchhuahna a awm thei.

Engtin nge medullary sponge kidney hi hmuhchhuah a nih?

Heng symptoms te hi i neih chuan i doctor chuan physical exam a ti hmasa ang. I medical history, chhungkaw history leh symptom i neih apiang an zawt ang.

I doctor-in kal natna i neih a rinhlelh chuan thisen leh zun test vawi tam tak a ti mai thei . Hengte hian hetiang hi an en ang:

• Zun ah thisen a awm em?
• Engtin nge kal (kidney) hian hna a thawh?
• Urinary tract infection a awm em?

Chu bakah, special imaging test pawh tih theih a ni a, chu chu ka sawi tawh cyst te chu kidney-ah a awm leh awm loh enfiah theih a ni. Scan chi hrang hrang hman tlanglawn ber chu:

• CT scan: Hei hian X-ray hmangin kal (kidney) chu three-dimensional (3D) image a siam a.
• Intravenous Pyelogram (IVP): Hei hian i vein-ah dye bik inject a ni. Tichuan, X-ray thlalak eng emaw zat lak a ni. Dye hi kal atanga thisen kal tlangin zun chhungah a filter lut a, chuvangin X-ray thlalak atang hian zun kalna kawng chu chiang takin a lang. Hei hian cyst leh zun a block na hmun zawng turin a pui thei a ni.
• Ultrasound scan: Hei hian sound wave hmangin kal (kidney) thlalak a la thin.

Engtin nge medullary sponge kidney hi enkawl a nih?

Tunah hian medullary sponge kidney (MSK) tia hriat natna hi enkawlna bik a la awm lo . Enkawlna hian zun kawng (UTI) leh kal lung (kidney stone) te control leh enkawl a tum ber a ni.

Urinary tract infection enkawlna ber chu antibiotics a ni .

Kidney stone enkawl dan chu lung lian leh te a zirin a ni. Lung te te te hi zun kaltlangin anmahni chauhin an kal tlang tlangpui. I doctor chuan lung chu a kal chak zawk theih nan tui tam zawk in turin a hrilh mai thei che. I ureter-a taksa ruhte tih hahdamna tur painkiller leh damdawi an pe thei bawk.

Lung lian zawk chu tlem a enkawl a ngai mai thei. Entirna tlemte chu hetiang hi a ni:

• Shock Wave Lithotripsy: Hei hi non-invasive treatment a ni a, high-energy shock wave hmangin kidney lungte chu a tichhia a ni. Chumi hnuah chuan a chhe tawhte chu taksa atangin zun chhungah an kal chhuak leh thin.
• Ureteroscopy: Hei hian lung awmna hmun en nan ureteroscope an tih tube sei tak, te tak te hman a ni. He hmanraw hmang hian lung te tak te te lakchhuah theih a ni a, a nih loh leh laser hmangin lung lian zawk te chu a tikehsawm thei bawk.
• Percutaneous Nephrolithotomy hmanga tihchhuah a ni:Doctor-te chuan hmanraw dang a hlawhtlin loh hunah chauh an hmang thin. Hei hian a hnungzangah incision te tak te siam a, chuta tang chuan kidney lung chu tihkeh a, lakchhuah a huam a ni. Hei pawh hi minimally invasive surgery a ni bawk.

Medullary sponge kidney hi a veng thei ang em?

Medullary sponge kidney (MSK) hi pianpui natna a ni a, a chhan hriat loh a nih avangin ven theih a ni lo . Mahse, chuta chhuak thei zun kawng (UTI) leh kal (kidney stone) te ven nan hma i la thei a ni.

I doctor chuan hetiang damdawi hi a pe thei ang:

• Urinary tract infection lo awm leh tur venna atana antibiotics dose tlem .
• Damdawi potassium citrate emaw thiazide (tui pill tia hriat bawk) te hian zun a calcium level a tihniam bakah kal lung (kidney stone) siam a veng thei bawk.

I ei leh in thlak danglam hian zun kawng infection leh kidney stones te pawh a veng thei bawk:

• Calcium: I ei leh in atanga calcium tling tak i hmuh hian kal (kidney stone) awm theihna a ti tlem thei a ni. (Mi thenkhat chuan calcium ei tam lutuk hian lung a tipung ang tih an ring mai thei, mahse hei hi chu a ni lo. A tlem berah i ei tur a ni. Doctor rawn rawh.)
• Fluids: Tui tam tak in hi a pawimawh hle. Hei hian zun a ti dilute a, lung siam theihna a ti tlem bawk. Tin, kal atanga bacteria te chu a paih chhuak thei bawk. Ni khatah tui litre 2-3 tal in tum ang che.
• Protein tamna ei tur: Sa, sangha, leh artui ang chi protein tamna ei tur tihtlem hian kal (kidney stone) a veng thei a ni.
• Chi: I ei leh in a chi (salt) tihtlem hi a pawimawh hle bawk. Chi ei tam lutuk hian kal (kidney stone) a tipung a ni. Chuvangin i chaw eiah chi i dah zat hi fimkhur rawh. Canned food leh instant noodles ang chi thilah hian chi a tam hle.

Pawimawh: I ei leh in lama inthlak danglamna i siam hmain i doctor emaw dietitian emaw rawn hmasa phawt ang che .

Medullary sponge kidney nei mi pakhat hmalam hun chu eng nge ni?

Mi tam tak chuan he thu hi an hriat chuan an hlau mai thei a, mahse Medullary Sponge Kidney (MSK) vei tam zawk chuan an dam chhungin kidney function tha tak an nei thei a ni .

Mahse, mi za zela tlemte, 10% vel chuan kal (kidney failure) an nei thei a ni. A chhan ber chu urinary tract infection (UTI) awm fo, lo awm leh thin leh kal (kidney stone) te hi a ni.

Chronic pain hi complication hmuh tur awm lo dang a ni a, chu chu kidney stone nei fo thinte zingah a ni. Hetiang dinhmun hi kal (kidney stone) venna atana hmalakna hmanga control theih a ni.

Medullary sponge kidney (MSK) hian thisenah calcium a ti hniam thei a. Hei hian ruh a tichak lo thei a ni . Hei hian ruh kaihhnawih natna vei theihna a tipung a ni. Entir nan:

• Osteoporosis (ruh a hring leh a chhe thei natna) .
• Secondary hyperparathyroidism (parathyroid glands atanga hormone chhuak tam lutuk) .

Hetiang hian hun rei tak chhung ruh chhiatna a thlen loh nan i doctor chuan potassium citrate ang chi damdawi a pe thei ang.

Engtin nge medullary sponge kidney hi kan nunpui ang?

I doctor chuan i kal hnathawh dan a enfiah fo ang a, a tul angin supportive care a pe bawk ang. I damdawi ei tur chu a tih ang chiaha ei a pawimawh a, i ei leh in zawm a pawimawh a, i follow-up appointment te pawh zawm reng a pawimawh bawk . Heng thilte hian zun kawng infection leh kal (kidney stone) te a veng thei a ni.

Medullary Sponge Kidney (MSK) hi damdawi a la awm lo. Mahse ka sawi tawh ang khan he natna vei tam tak hian symptom an nei lo a, thenkhat chuan an nei tih pawh an hre lo. Symptoms a awm tak tak chuan urinary tract infection emaw kidney stone emaw avanga lo awm a ni tlangpui. Heng pahnih hi enkawl theih tak an ni . I ei leh in leh nunphung tihdanglamna hmangin zun kawng infection leh kidney stone te pawh i veng thei bawk. Zawhna emaw, ngaihtuahna emaw i neih chuan i doctor nen inbiakna neih hreh suh .

Take-Home Thuchah a ni

Okay, chuvangin tunah chuan kan sawi tawh `Medullary Sponge Kidney` kha i hrethiam tawh ngei ka beisei. Thu pawimawh ber berte hi i inhriat nawn tir leh ang u:

• Hei hi pianpui natna a ni a, kal (medulla) lai takah cyst te te a lo awm thin.
• Mi tam zawk chuan symptom an nei lo . An tih chuan zun kawng (UTI) emaw, kal (kidney stone) vang a ni.
• Hemi atan hian enkawlna bik a awm lo a , mahse a symptom leh complication te chu uluk taka enkawl theih a ni.
• Kidney stone leh urinary tract infection laka inven nan a pawimawh hle . Chutiang ti tur chuan tui tam tak in la, i ei leh inah fimkhur la, doctor thupek zawm rawh.
• Mi tam zawk chuan an dam chhungin kidney function tha tak an nei thei . Kidney failure hi a tlem hle.
• Hemi chungchanga zawhna i neih chuan doctor pan ngei ang che .

Ngaihtuah buai suh, mi tam tak chu he natna nen hian nun pangngai, hrisel takin an nung thei!

`Medullary Sponge Kidney, Cacchi-Ricci Disease, kal natna, kal lung, zun kawng natna, kal cyst, pianpui kal natna, kal cyst, nephrocalcinosis, hematuria, kal hriselna Sinhala