Nu leh pa ka nih angin i doctor-in i naute piang thar hian thinlung natna Hypoplastic Left Heart Syndrome (HLHS) tih a nei tih a hrilh che hian i rit leh hlauthawng hle ngei ang tih ka hrethiam. I khawvel pum pui chu a rawn tla nghal vek ang maiin a lang ngei ang. Mahse, lungngai suh. Tunah chuan medical science hian hma a sawn nasa hle. Norwood Procedure hi chutiang naute nunna pekna atana hmalakna hmasa ber pawimawh tak a ni. Vawiin hian he thu hi i hriatthiam theih tur awlsam takin kan sawi dawn a, chutiang chuan i hlauhthawnna i tihziaawm theih nan.
Norwood Procedure chu eng nge ni?
A awlsam zawngin sawi ila, Norwood procedure hi naute pianpui (born with) heart condition Hypoplastic Left Heart Syndrome (HLHS) -a nei te tan heart surgery bik a ni.
In te tak te, pindan pali nei ang maiin han ngaihtuah teh. A then hnih a nei a, a dinglam leh a veilam a ni. A tlangpuiin thinlung veilam hian thisen thianghlim, oxygen tamna taksa pum puiah a pump chhuak thin. A dinglam chuan taksa atanga thisen deoxygenated chu lungah a pump kir leh a, oxygen pek a ni.
Mahse, HLHS vei naute thinlung veilam chu a lo thang tha lo . Chumi awmzia chu chu lam chu a te hle a, a chak lo hle tihna a ni. Chuvangin chu lam chuan taksaah thisen a pump thei lo. Hei hi buaina lian ber a ni.
Norwood procedure hian thil mak tak a ti a ni. Doctor-te chuan thinlunga thisen kalna tur kawng thar an siam a. Chu chu, thinlung veilam thil tih tur hna chu dinglam lamah an redirect tihna a ni a, chu chu a thawk tha hle a ni . Surgery zawhah naute ventricle dinglam chuan oxygenated blood chu taksa pum puiah a pump tan a, chubakah lungah thisen a thawn chhuak bawk.
Hei hi damdawi kim a ni lo. Mahse, naute nunna chhanhimna atana hmalakna hmasa pawimawh tak a ni. Hei hian naute cell-in oxygen mamawh zat an dawn theih nan thisen kal dan a tidanglam thei a ni.
He surgery hi tute nge mamawh?
He surgery hi naute Hypoplastic Left Heart Syndrome (HLHS) vei tan a ngai ber a ni. An pian tirh atanga kar hnih chhungin he surgery hi an neih a ngai a ni.
Naute pian tirh hian thinlung chhunga thisen kalna kawng lian pahnih (aorta leh pulmonary artery) inzawmna te tak te an nei vek a. Hei hi `patent ductus arteriosus` an ti a. Hei hian HLHS vei naute chu ni hmasa berah an taksaah thisen engemaw zat a lut thei a ni. Mahse, he inzawmna hi ni engemaw zat hnuah chuan a pianphungah a khar dawn a ni. Hetiang a nih chuan naute hian an taksaah thisen a thlen theihna tur kawng a nei tawh lovang a, chu chu a hlauhawm hle a ni.
Chuvangin Doctor ten an tih hmasak ber chu thisen kalna kawng khar loh nan damdawi bik (`Prostaglandin` an tih) pek hi a ni. Mahse chu chu rei lo te chauh a ni. Norwood operation hi permanent solution angin an ti a ni.
A châng chuan, naute piang hma, nau piang rit lo emaw, harsatna dang nei emaw tan he surgery hi tih theih a ni lo mai thei. Chutiang hunah chuan doctor-te chuan hmanraw dang, pulmonary artery bands te hi an hmang thin.
Surgery neih chhung leh operation zawhah eng nge thleng?
Surgery hma leh operation neih laiin
Surgery neih hma hian naute hi intensive care unit (ICU)-ah a awm a. Sawi tawh angin thisen kalna kawng bik hawn reng turin damdawi an pe chhunzawm zel dawn a ni. Tin, thinlung chunglam chamber pahnih inkar khur chu tihzauh a ngai thei bawk (a `septostomy`).
Norwood procedure hi a buaithlak hle a, darkar tam tak chhung (a tlangpuiin darkar 8-10 vel) a ni. Doctor team hian uluk takin a hnuaia mite hi an ti thin:
- Thinlung chunglam (atria) pahnih inkarah hian thisen a kal theih nan khur siam a ni.
- Aorta te tak te chu pulmonary artery lian tak nen an inzawm a, aorta thar, lian zawk siam turin patch bik an dah a ni.
- He aorta thar hi working right ventricle nen a inzawm a ni.
- A dawtah chuan ‘shunt’ , artificial tube te tak te chu lungah thisen thawn turin an dah a. Hei hi aorta atanga lung (Blalock-Taussig shunt) emaw, right ventricle atanga lung (Sano shunt) thleng pawh a ni thei.
He surgery chhung zawng hian naute chu cardiopulmonary bypass machine nen an inzawm a ni . Chumi awmzia chu naute thinlung leh lungte chu he machine hmang hian hun eng emaw chen a thawk tihna a ni.
Operation hnuah
Surgery zawhah naute chu intensive care unit (ICU)-ah hruai kir leh a ni. Naute en tura i kal chuan tube, wire leh machine tam tak i hmu ang. Anmahni i hmuh hian hlau suh. Naute ṭhatna tûrin an awm vek a, naute ṭanpui tûrin an awm vek a ni . I rilru lai takah surgical wound khuh tu bandage i hmu ang.
Hetianga operation an neih hnu pawh hian naute vun chu blue tint (cyanosis) tlem a nei thei a ni. Hei hi a chhan chu thisen deoxygenated leh oxygenated blood thenkhat chu thinlung chhungah an la inhmeh hle a ni. Hei hi tun dinhmunah chuan thil pangngai a ni.
Intensive care unit-a kar khat vel a awm hnuah naute chu regular ward-ah sawn a ni ang. I dam kim theih nan kar 2-3 vel damdawi inah i awm a ngai dawn a ni. In i haw hnuah doctor leh nurse te chuan naute enkawl dan tur te, damdawi pek dan tur te, a oxygen level enfiah dan tur te chipchiar takin an hrilh ang che.
HLHS tan surgery series neih a ni
HLHS hi surgery vawi khat chauh a tawp lo. Stage thum chhunga surgery neih a ni . Norwood hi stage hmasa ber chauh a ni.
| Dawhsan | Surgery neihna hmun hming | Kum khata tih thin a ni |
|---|---|---|
| Surgery hmasa ber a ni | Norwood kalphung | Pian atanga kar 2 chhungin |
| Surgery vawi hnihna a ni | Glenn-a kalphung | Thla 4 - 8 inkar |
| Surgery vawi thumna a ni | Fontan tih dan tur | Kum 1.5 - 5 inkar a ni |
Eng nge a hlawkna leh a hlauhawmna?
A thatna te
Hei hi a thatna lian ber leh awmchhun chu naute hian dam khawchhuah theihna hun a nei a ni . Kum 1980 chho hma khan HLHS vei nausen piangte tan enkawlna tur a awm lo. Mahse Norwood procedure an siam chhuah atang khan heng naute te hian naupan lai leh tleirawl thlengin an dam khawchhuah theihna hun an nei ta a ni.
Risk leh Complication awm thei te
Surgery lian dang ang bawkin, a hlauhawmna a awm bawk. Hengte hi hriat chian a pawimawh.
- Shunt blockage emaw dysfunction: Lung chhunga thisen phurtu tube te tak te chu a block thei.
- Thisen kalna kawng a zim (Stenosis): Surgery hmanga lakchhuah aorta emaw, lung lam panna thisen kalna kawng emaw chu a zim thei.
- Heartbeat abnormalities (Arrhythmia): Heartbeat rhythm a mumal lo thei.
- Lung hnathawh chak lohna: Ventricle dinglam hian rit zawk a phur a ngaih avangin a hnathawh a chak lo thei.
- Neurodevelopmental delays: Thluak leh nervous system hmasawnna tikhawtlai thenkhat a awm thei. Chuvângin, naute ṭhenkhat chuan thusawi leh kea kal ang chi thila ṭanpuina bîk an mamawh thei a ni.
Norwood procedure hnua damdawi ina damchhuah zat hi 90% vel a ni. Mahse, naute thenkhat chu operation vawi hnihnaah an thleng thei lo.
Engtikah nge doctor i hmuh ang?
In i thlen hnuah i naute chu ngun takin i ngaihven tur a ni. Thil ngaihtuah tur i neih chuan doctor ko nghal rawh.A bik takin heng thilte hi fimkhur hle ang che:
- In lama naute enkawl dan tur zawhna i neih chuan.
- Naute chu a thau tha lo a nih chuan.
- Doctor-in beisei aia naute oxygen level a hniam chuan.
- Naute hian damdawi a pek chu a chhang tha lo a nih chuan.
- Naute chu a tlangpui aia mut a tam emaw, bawnghnute ei tlem emaw a nih chuan.
He naute hian a dam chhung zawngin cardiologist enkawlna leh enkawlna a mamawh dawn tih hre reng ang che.
Take-Home Thuchah a ni
- Hypoplastic Left Heart Syndrome (HLHS) hi natna khirh tak a ni. Mahse, Norwood procedure hi naute nunna chhanhim thei tur step hmasa ber leh pawimawh ber a ni.
- Hei hi damdawi kim a ni lo. Hemi hnu hian operation pahnih (Glenn leh Fontan) neih a ngai dawn a ni.
- Surgery hi a buaithlak a, risk a nei a, mahse damchhuah theihna chance erawh a phu hle.
- Naute damna atan chuan in lama haw hnua doctor thupek dik taka zawm leh ni ruat saah clinic-a kal a pawimawh hle.
- Nu leh pa kan nih angin hlauhna leh lungkhamna kan neih hi thil pangngai a ni. Zawhna emaw, ngaihtuahna emaw i neih chuan i doctor zawh pawh hlau ngai suh. Nangmah chauh i ni lo.











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