I kekawr ipteah hian tuar theih loh khawpin natna i nei nghal em? Ni engemaw zat hnuah, kar tlemte hnuah pawh a natna chu a reh deuh a, mahse chutah chuan i kut chu a hlim lo va, a chak lo hle tih i hria em? Tichuan, i tana pawimawh tak ni thei tur thil kan sawi dawn a ni. Hei hi thil awm lo tak a ni a, mi tam tak a ti hlauhawm hle. Parsonage-Turner Syndrome kan ti a. Vawiin hian i hriatthiam theih tur awlsam takin kan sawi dawn a ni.
A awlsam zawngin, Parsonage-Turner Syndrome (PTS) hi eng nge ni?
Parsonage-Turner Syndrome (PTS), a then chuan ``brachial neuritis'' an ti bawk a, hei hi nervous system inrawlhna a ni. I kephah leh i kut chunglam natna nasa tak, a chhan hriat loha lo thleng nghal mai ang maia lang a ni. He natna hi ni tam tak atanga kar tam tak chhung a awm thei. Tichuan harsatna dangte chu a intan ta a ni. Natna a reh deuh deuh chuan i ke ruh, i kut, i kut hmawr, a nih loh leh i kut ruhte chu a chak lo tan ta a ni. He chak lohna hi thla tam tak, a nih loh leh kum tam tak chhung pawh a daih thei.
Kan kawr atanga kan kutphah thlenga kal chhuak nerve network kan nei ang tih han ngaihtuah teh. Kan in chhunga main switchboard-ah hian room tinah wire a kal ang bawkin, he nerve network hian kan kut peng tinah signal a thawn bawk. He nerve network hi `(brachial plexus)` kan ti a. Parsonage-Turner Syndrome-ah hian he `(brachial plexus)` network of nerve hi a chhe thin. A bik takin movement control tu nerve te hi a chhe ber thin. Chuvang chuan, a na hnuah chuan kutphah ah hian rilru hah leh chak lohna a awm thin.
Hetiang dinhmun hi a tlem avangin doctor-te chuan a chang chuan natna tlanglawn dang nen an inzawm lo thei a ni. Entirnan, a natna lan chhuah dan a inang vek avangin cervical radiculopathy emaw cervical spondylosis emaw tia hriat sual theih a ni.
He natna hi stage thum a awm a.
Hetiang dinhmun hi a tlangpuiin stage thum-ah a lo awm thin. Hetiang hian mi zawng zawngin an nei vek dawn lo a, mahse hei hi mi tam zawkin an hmuh thin pattern chu a ni.
Stage 1: Natna nasa tak Phase
Hei hi a hmasa ber a ni. Vawikhatmah natna nasa tak a intan a, a tam zawkah chuan kekawr bul pakhatah. He natna hi ni engemaw zat atanga kar tlemte thleng a awm thei. He hun hrehawm tak hi a rei poh leh a dam kim theih nan a rei zawk dawn niin an sawi tlangpui.
Stage 2: Taksa chak lohna
Zawi zawiin natna a reh hnuah stage hnihna chu a intan leh ta a ni. Hei hi ke ruh leh kut ruhte a chak lo tanna hmun a ni. Kut chawi emaw, thil rit tak tak chawi emaw chu a harsa ta hle. Hun a kal zel a, hman loh avangin taksa ruhte chu a atrophy thei a ni. He stage hi thla ruk atanga thla 18 chhung a ni thei a, a then chuan a rei thei bawk.
Stage 3: Dam lehna
Hei hi recovery phase a ni. Hun engemaw chen hnuah chuan i taksa ruhte chu zawi zawiin chakna an nei leh tan ang. I kut chu zawi zawiin a hnathawh dan pangngaiah a kir leh ang.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Parsonage-Turner Syndrome hi a takah chuan a awm lo hle . Statistics atanga a lan dan chuan kum tin mi sang za zinga mi pathum vel chauhvin he natna hi an vei thin. Chuvangin i kekawrte a na apiangin ngaihtuah buai a ngai lo.
Kum eng pawhah a lo awm thei a, mahse mipaah a tam zawk . Kum 40-45 inkar velah hmuh tur a awm tlangpui.
Eng chiah nge a symptoms te chu?
A lan chhuah dan ber pahnih chu natna nasa tak, a hnua taksa ruh chak lohna a ni. Heng symptoms te hian i kephah, i kut chunglam, i kut hmawr leh i kut khawi hmunah pawh a nghawng thei a ni.
A pawimawh ber chu 80% velin kut pakhat (unilateral) chauh a nghawng a ni. Tin, chu chu i hman tam ber arm (dominant arm) a ni fo bawk. Mi tlemte, 20% velah chuan kut pahnih a nghawng thei a ni.
Symptoms a lan dan tlangpui hi han en ila.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Vawikhatmah, natna nasa tak | Natna na tak, tuar theih loh, chemte kah ang mai. He natna hi zan lamah a na zual thei hle. He natna nasa tak hi darkar tlemte atanga kar li vel thleng a ni thei. |
| Muscle chak lohna | Natna a reh hnuah chuan kutphah chakna chu a bo ta a ni. Hei hi kephah leh kut chunglam ah a lang tam ber. A châng chuan rilru emaw, diaphragm emaw ruhte pawh a nghawng thei bawk. |
| Thil dang pawh a awm | Heng main features bakah hian thil dang hmuh tur a awm bawk.
|
Engvangin nge hetiang hi a lo awm? Hei hi eng nge a chhan?
Dik tak chuan zirchiangtute chuan he thil thleng chhan dik tak hi an la hre chiang lo . Mahse a ngaihdan ber chu kan taksaa immune-mediated response pangngai lo vang a ni.
A awlsam zawngin, hrik, virus emaw, bacteria emaw ang chi, kan taksaa a luh chuan kan taksa hriselna (immune system) chuan a do let thin. Mahse a chang chuan he indonaah hian kan immune system hian tihsual a nei a, chu ai chuan kan taksa peng hrisel tak, chu chu ``brachial plexus`` nerve network a ni. Chutah chuan heng nerve te hi a chhiat a, symptoms a lo lang thin.
Vawi tam tak chu he natna hi tun hnaia virus infection hma hian a awm thin. Entir nan:
- Coxsackie B virus a ni
- HIV (Mihring taksa chak lohna hrik) .
- Natna pangana (parvovirus B19) .
- Mumps a awm
Mahse, a châng chuan chhan hriat lohvin a lo ṭhang chho thei a ni. A tlem hle a, hei hi genetic condition, hereditary neuralgic amyotrophy an tih vang pawh a ni thei.
Hetiang natna vei theihna tipungtu thilte
Thil thleng thenkhat emaw, damdawi lam dinhmun emaw hian Parsonage-Turner Syndrome vei theihna a tipung deuh thei tih hmuhchhuah a ni.
- Tun hnaia operation emaw anesthesia emaw hmanga tih a ni
- Connective tissue natna - e.g. Ehlers-Danlos natna a ni
- Autoimmune dinhmun - e.g. lupus tih hi a ni
- Accident pakhat chu a kekawr ipteah a ni
- Exercise tih hian kekawrteah harsatna nasa tak a siam thin
- Vaccine chi hrang hrang
- Naupai leh nau neih lai
- Radiation hmanga enkawlna a ni
- Lumbar puncture test a ni
Engtin nge doctor hian hei hi a hmuh theih?
Heng symptoms te hi i neih chuan doctor rawn hmasa phawt tur a ni. I natna lan chhuah dan leh i damdawi lam chanchin a zawt ang che. Tichuan, i kut ruh, i hriatna leh i reflexes te enfiah turin taksa enfiahna an nei ang. Neurologist, nerve lama harsatna nei doctor hnenah an refer mai thei che a ni.
Hei hi Parsonage-Turner Syndrome a nih leh nih loh finfiah nan i doctor chuan test bik electromyography (EMG) tih a rawt thei ang.
EMG test hi i taksa ruh leh a thununtu nerve-te hnena electrical signal te tak te tak tak thawn chhuakin, chu nerve leh taksa ruhte chu engtiang chiahin nge hna an thawh tih hriat nan test a ni. Hei hian nerve chhiatna a awm leh awm loh leh a chhiatna chu khawiah nge a awm tih hriat theih nan a pui thei a ni.
Chu bakah, hetiang imaging test hi tih theih a ni bawk a, chu chuan natna dang a awm loh nan leh a natna hmuhchhuah chu a nemnghet thei a ni:
- MRI (Magnetic Resonance Imaging) hmanga tihchhuah a ni
- Nerve ultrasound hmanga enfiah a ni
- CT (Computed Tomography) hmanga enfiah a ni
Enkawlna a awm em? Eng nge tih theih ang?
Hei hi enkawlna leh damdawi chiang tak a la awm lo. A tha ber chu he dinhmun hi hun kal zelah a mah chauhin a reh tlangpui thin. Mahse, a hmaa hriatchhuah leh symptoms control nan supportive treatment chuan damna a ti chak thei a, result tha zawk a nei thei bawk.
I doctor chuan i natna lan chhuah dan tur enkawl nan enkawlna hrang hrang a rawn rawt ang che.
Acute phase chhung hian
- Painkillers: Common painkillers (NSAIDs) ang chi thil te.
- Oral Corticosteroids: Nerve inflammation leh immune system hnathawh control nana damdawi chi khat a ni.
- Arm immobilization: I kut chu chawlh tir la, shoulder stabilizer ang chi thil hmang mai thei.
- TENS (Transcutaneous Electrical Nerve Stimulation): Vun kaltlanga electric signal te te thawn chhuah hmanga natna control dan a ni.
- Acupuncture: Mi thenkhat chuan hei atang hian natna tihziaawmna an hmu bawk.
A natna a reh hnuah
- Physical Therapy: Hei hi a pawimawh hle a ni . Physical therapist chuan exercise leh stretch te a zirtir ang che, chu chuan taksa ruh chhia te a tichak ang a, ruh a tichak lo ang a, i kut a hnathawh leh theih nan a pui ang che.
- Nerve natna damdawi bik: Mi thenkhat chuan natna reh tawh mahse nerve inflammation ang chi natna an nei thei. Chutiang hunah chuan i doctor chuan damdawi bik, gabapentin, carbamazepine, emaw amitriptyline emaw a pe thei a ni.
A nasat em em, enkawlna dang a hlawhtlin loh chuan operation (nerve grafting emaw tendon transfer emaw) tih ngaihtuah theih a ni. Mahse, hei hi a tlem hle.
Hetiang dinhmun nen hian hmalam hun eng nge awm ang? (Prognosis) tih a ni.
Hetiang dinhmun hi mi hrang hrangah a kal dan a inang lo thei. Mi thenkhat tan chuan an nunah vawi khat chauh a thleng a, an dam leh vek thin. Mi dangte tân chuan eng emaw chen chu chak lohna emaw, hrehawmna emaw an nei chhunzawm thei a ni. Mi tlemte tan chuan a lo thleng leh thei a ni.
Research atanga a lan dan chuan an natna lan chhuah dan enkawltu leh physical therapy dik tak dawngtu zinga 89% vel chu kum thum chhungin an dam kim vek ang. Chumi zinga 75% chu kum hnih chhungin an dam leh ang a, 36% chu kum khatna chhungin an dam leh ang.
Chumi awmzia chu, he thil atanga dam leh tur hian hun a duh viau nachungin, mi tam zawk chu an dam leh thin tihna a ni. A pawimawh ber chu dawhthei taka enkawl a, enkawl laia doctor thupek zawm hi a ni.
Take-Home Thuchah a ni
- Parsonage-Turner Syndrome (PTS) hi thluak lam natna hmuh tur awm lo tak a ni a, ke ruh leh kut natna nasa tak a thlen a, chu chu taksa ruh chak lohna a thlen leh a ni.
- Hei hi a chhan dik tak hriat chhuah ni lo mah se, taksa hriselna (immune system) hnathawh dan dik lo vang nia ngaih a ni.
- I kekawrte na na tak i neih thut chuan ngaihthah suh la , doctor pan nghal rawh. Diagnosis rang tak neih a pawimawh hle.
- Hei hi damdawi chiang tak awm lo mah se, natna lan chhuah dan chu natna tihdamna leh taksa lam enkawlna ang chi, puihna hmanga enkawl theih a ni.
- Dam nan hun a duh thei. Thla tam tak atanga kum tam tak a daih thei. Chuvangin i enkawl danah dawhthei leh positive taka i awm a pawimawh. Mi tam zawk chuan hun kal zelah an dam leh vek thin.











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