I kut leh keah natna, rilru hahna, a nih loh leh tingling i nei reng em? A châng chuan heng thilte hi kan taksaa damdawi lam dinhmun bik avanga lo awm a ni. Chuvangin vawiin hian Patisiran vaccine chungchang kan sawi dawn a, chu chu hetiang dinhmun enkawlna atana pek a ni. Hei hi damdawi bik deuh a nih avangin hei hi i hriat chian a pawimawh hle.
He Patisiran hi eng nge ni? Eng nge a awmzia?
A awlsam zawngin, Patisiran hi damdawi a ni a, a hming rei deuh , hereditary transthyretin-mediated amyloidosis (hATTR) tia koh natna nei tan a ni. A tawi zawngin hATTR kan ti ang.
Okay, chuti a nih chuan hATTR chu eng nge ni? Hei hi genetic condition a ni a, thlah kal zelah a kal zel a ni. Kan thin (liver) hian protein pakhat TTR tih a siam chhuak a. A tlangpuiin hei hi a buaithlak lo. Mahse hATTR nei mi pakhatah chuan he TTR protein hi a fold dik lo va, a inzawm khawm a, taksa hmun hrang hrangah a insiam a, a bik takin nerve chhehvelah a insiam chhuak thin. Tui pipe chhunga bawlhhlawh lo awm ang mai a ni. Hei hi amyloid deposit kan ti a.
He protein hi nerve vel a lo awm khawm chuan a tichhe thin. Chuvang chuan a hmaa kan sawi tak symptoms te, ke ruh natna, rilru hahna, leh taksa peng hrang hranga hriatna hloh te hi a lo lang thin.
Chuvangin Patisiran tih chu chu TTR protein dik lo siam chhuah tihtawp a puih hi a ni. Buaina chu a bul tanna hmun ngeia tihtawp ang mai a ni. Tichuan protein deposit tharte chu a tlahniam a, zawi zawiin a natna lan chhuah dan chu a thunun tan ta a ni.
He damdawi hi i ei hmaa i doctor hnena i hrilh tur thilte
I doctor-in he damdawi hi pek che a tum hma hian thil tlemte i hrilh ngei ngei tur a awm. Hengte hi thup suh, i himna atan a pawimawh em em a ni.
- I allergy chungchang: I allergy i neih chuan, he Patisiran damdawi chauh ni lovin, damdawi dang, ei tur, preservative, emaw colouring emaw pawh hi, allergy i neih chuan min hrilh ngei ang che.
- Naupai emaw, naupai tum emaw i nih chuan: Naupai tawh emaw, nau pai tum emaw, naupai theih rinhlelhna i neih chuan he damdawi hi i tan hmain doctor hnenah hrilh hmasa phawt ang che.
- Nu hnute pe i nih chuan: Naute i hnute i pe a nih chuan chu chu i doctor hnenah pawh hrilh bawk ang che.
He thu hi dik taka i doctor hnena pek hian him taka enkawlna tha ber pe turin nasa takin a pui ang che.
Engtin nge he damdawi hi ka pek theih ang che?
Patisiran hi pill in lama i hruai tur a ni lo. HeiA thisen kal tlanga infusion a ni. Hei hian damdawi chu i vein pakhatah zawi zawiin tube hmangin i inject tihna a ni a, chu chu saline nen a inang a ni.
He enkawlna hi damdawi in emaw clinic emaw ah chauh tih thin a ni . Doctor trained emaw nursing staff emaw chuan a pe ang che. Chuvangin ngaihtuahawm tur a awm lo.
I overdose a nih chuan engtin nge i tih ang?
Hei hi damdawi in hmuna pek a nih avangin hetiang thil thleng theihna chance hi a tlem hle. Mahse, he damdawi hi i ei tam lutuk nia i hriat chuan damdawi in pakhat Emergency Unit (ETU)-ah kal nghal rawh. A nih loh leh, Colombo National Hospital-a National Poisons Information Center-ah thurawn dil turin phone la.
Damdawi ka ei tur ni kha ka miss a nih chuan engtin nge ni ang?
He damdawi hi a hun taka ei a pawimawh hle . Chuvangin i tan ni ruat saah damdawi inah kal ngei ngei tur a ni. Eng thil vang pawha i kal thei lo a nih chuan i doctor emaw clinic emaw ko nghal la, hriattir nghal rawh.
Damdawi ei huna fimkhur tur thil bik
He damdawi i ei lai hian fimkhur ngai tlem a awm a.
1. Infusion avanga thil thleng
Hei hi a pawimawh ber a ni. Mi thenkhat chuan he damdawi hi thisenah emaw, pek a nih hnu rei vak loah emaw pek a nih hian reaction engemaw zat an nei thei. Hengte hi infusion reaction kan ti a ni . Chûng zîngah chuan:
- A rilru a na
- Thâwk harsa
- Spinning (vertigo) ang maia inhriatna .
- Hot tih hriatna
Hetiang hlauhawmna tihziaawm nan hian i doctor chuan he vaccine hi a pek hma darkar khat vel khan damdawi dang (allergy damdawi emaw paracetamol emaw ang chi) a pe thei che a ni. Chuvangin i doctor thupek ang chiah kha zawm rawh. Damdawi pek a nih chhung hian medical staff ten uluk takin i dinhmun an enfiah ang.
2. Mit hmuh dan inthlak danglam
I mit hmuh danah danglamna i hmu a, a bik takin zan lamah emaw, i mit a vawt tih i hriat chuan doctor hnenah hrilh nghal rawh.
3. Vitamin A ei tur a awm
He damdawi ei hian i vitamin A level a tihniam thei a ni. Vitamin A hi kan mit leh vun hriselna atan a pawimawh hle. Chuvangin, i doctor chuan nitin ei tur vitamin A supplement a pe thei che a ni. I doctor-in ei tur a tih ang chiah kha ei rawh. Tin, vitamin A tamna ei tur (carrot, sweet potato, spinach ang chi) ei hi a tha hle bawk. Hemi chungchang hi i doctor nen sawiho rawh.
Damdawi avanga side effect lo awm thei
Damdawi dang ang bawkin Patisiran hian side effect engemaw zat a nei thei a ni. Mi zawng zawngin an hmu vek lo. Mahse, anmahni fimkhur a pawimawh. Hriatthiam awlsam tak takah kan then ang.
| Side effect a awm thei | Description leh tih tur |
|---|---|
| Side effect na tak tak, doctor hnena hriattir nghal tur | |
| Allergic Reaction na tak tak a awm thei | Vun vun rawng, hnim hring, hmai, hmui, lei emaw kawr emaw a hring, thawk harsa. Chung zinga pakhat tal a lo awm chuan doctor thurawn la nghal rawh. |
| Infusion avanga thil thleng | Chhung na, thawk harsa, thawk hah, muhil, luak chhuak. Damdawi i ei laiin heng symptoms te hi i neih chuan doctor emaw nurse emaw hnenah hrilh nghal rawh. |
| Vitamin A tlakchhamna chhinchhiahna | Mit a inthlak danglam (a bik takin zan lama mit a tlahniam), mit a vawt, vun a vawt, natna hrik kai fo thin. Chungte chu i doctor hnenah report rawh. |
| Thil hlauhawm lo tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur a ni | |
| Joint natna | Joint natna. |
| Muscle spasms a awm thin | A taksa ruhte chu a inthlak danglam nghal tih hriatna. |
| Hrawk thip | Hrawk thip. |
| Pum natna (upset stomach) a awm | Pum na leh rilru hahna ang chi natna. |
He list-ah hian side effect zawng zawng a tel lo mai thei. Thil danglam tak i hmuh chuan i doctor nen sawiho rawh.
Damdawi dangah harsatna a awm thei em?
Tun thlenga zirchiannaah chuan Patisiran hian damdawi dang chungchangah harsatna lian tham a thlen lo tih hmuhchhuah a ni. Mahse, i damdawi ei zawng zawng (vitamin leh herbal remedies te pawh tel) doctor hnenah hrilh la a tha ber.
Take-Home Thuchah a ni
- Patisiran hi hATTR an tih gene atanga lo chhuak neurological condition enkawlna bik a ni.
- He damdawi hi i ei tan hmain i doctor hnenah allergy i neih leh neih loh leh naupai emaw, naupai emaw i nih leh nih loh hrilh hmasa phawt ang che.
- Damdawi thisen kal tlanga i dawn laiin i rilru a na emaw, thawk harsatna emaw i neih chuan medical staff te hriattir nghal tur a ni. Hei hi infusion reaction a ni thei.
- I mit hmuh danah danglamna i hmuh chuan doctor hnenah hrilh rawh. Vitamin A supplement hi doctor-in a tih ang chiah khan ei thin ang che.
- I damdawi ei tura ruahman ni te chu skip suh. Harsatna i neih chuan clinic-ah hriattir hmasak phawt tur a ni.
- He damdawi chungchangah hian zawhna emaw rinhlelhna emaw i neih chuan doctor zawt hreh ngai suh.











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