Mi thenkhatin an rilru lai takah hollow an nei tih i hmu ngai em? Nang emaw i fa emaw hian hetiang hi i nei mai thei. T-shirt i bun hian a nuam lo hle thei a, a zahthlak hle thei bawk a, a bik takin swimming pool-a i kal hian. Tin, i tlan kual vel leh inkhelh hian thawk harsa zawk leh hah chak zawk angin i inhria em? Damdawi lamah chuan he dinhmun hi Pectus Excavatum kan ti thin. Chuvangin vawiin hian kan sawi vek dawn a, awlsam takin, in hriatthiam theih tur angin.
A awlsam zawngin, Pectus Excavatum chu eng nge ni?
A awlsam khawp mai. Kan rilru lai takah ruh flat (flat bone) hi sternum an ti a. Chu chu i khawih huna i hriat theih chu i rilru lai takah ruh chak tak a ni. Pectus Excavatum an tih dinhmunah chuan he hnute ruh hi pawn lamah a chhuak lo va, chu ai chuan a rilruah a lo thang lian zawk a ni. Funnel ang maiin a rilruah a pil lut a. Hei vang hian mi thenkhat chuan "funnel chest" an ti thin.
Sternum chu chhung lam hawia a pil chuan a bula rib pali emaw panga emaw chu a sir lehlamah chhung lam hawiin an hruai lut thin. Hei hian rilru chhunga hmun a tihtlem phah a ni. Hei hian kan thinlung leh lungte zalen taka hnathawh theihna tur hmun a tihtlem thei a ni.
Hei hi pianpui (congenital condition) a ni. Chu chu mi chu hetiang dinhmun neia piang a ni tihna a ni. Amaherawhchu, pian tirh lamah chuan hriat theih a ni lo. Vawi tam tak chu he rilru natna hi naupang a lo upa deuh deuh chuan a langsar zawk a, a bik takin kum 12-14 vel a nih chuan taksa a lo thang chak hle a ni.
A tam zia thlir chuan naupang 1,000 zinga pakhat atanga pariat vel a nghawng a ni. Hmeichhia aiin mipaah a tam zawk bawk.
Hetiang natna lan chhuah dan hi engte nge ni?
Pectus Excavatum natna lan chhuah dan hi chi hnih ah then theih a ni. Pakhat chu taksa lama harsatna a ni a, pakhat chu rilru lam nghawng a ni. Heng pahnih hian mi nunah nghawng lian tak a nei thei a ni.
| Mihring ziarang chi khat | Hrilhfiahna leh entirnan |
|---|---|
| Taksa lama natna lan chhuah dan |
|
| Rilru lam natna lan chhuah dan |
|
A pawimawh ber chu, hetiang hian i awm a nih chuan i rilruah dah suh. I sualna a ni lo. Hemi atan hian enkawlna tha tak tak a awm.
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Mi tam takah Pectus Excavatum awm chhan dik tak hi hmuhchhuah a la ni lo. Chumi awmzia chu chhan awm lovin a thleng mai thei tihna a ni.
Mahse, a then phei chuan damdawi lam thil dang, a bik takin taksa inzawmkhawmna (connective tissue) tichhe thei natna te nen a inzawm tih hmuhchhuah a ni. Entir nan:
- Marfan syndrome a ni
- Ehlers-Danlos natna a ni
Hengte hi genetic diseases an ni. Chuvangin he natna chi hi i neih chuan Pectus Excavatum vei theihna i nei a ni.
Hei hi thlah kal zel atanga lo chhuak thil a ni em?
Researcher-te chuan Pectus Excavatum thlentu gene bik an la hmuchhuak lo. Mahse, genetic a ni mai thei niin an ring. Pectus Excavatum vei zinga 40% leh 53% inkar chuan chhungkaw member (pa emaw unaupa emaw ang chi) he natna vei an nei a ni. Chuvangin i chhungkuaa mi pakhatin a neih chuan nang pawhin i neih theihna chance a sang zawk.
Engtin nge doctor hian hei hi a hriat chian?
Diagnose chu chutiang chuan a harsa lo tlangpui. Doctor hmu tura i kal chuan taksa enfiahna awlsam tak hmangin an hre thei ang . Doctor chuan i rilru a enfiah hunah he dimple hi a hmu thei ang.
Mahse, he natna hian i thinlung leh lung a nghawng dan chiang taka hriat theih nan doctor chuan test eng emaw zat tih belh leh turin a rawt ang.
Chu test-te chu engte nge ni?
- Chest CT scan (Computed Tomography) emaw MRI scan (Magnetic Resonance Imaging): Heng scan te hian rilru chhung lam chu three-dimensional image a la thei a ni. Chumi hnuah chuan sternum chu engzat nge a pil tawh tih leh thinlung leh lungte chu engzat nge a compress tih dik takin a teh thei a ni.
- Cardiopulmonary exercise testing: Hei hian treadmill-a tlan tir che a, exercise nena i thinlung leh lung hnathawh dan en a huam a ni.
- Electrocardiogram (EKG): Hei hian thinlung electrical activity a test a, heartbeat-ah thil dik lo a awm em tih a enfiah thin.
- Echocardiogram: Hei hi thinlung scan a ni. Thinlung hnathawh dan leh valve (mitral valve prolapse ang chi) dinhmun hriat nan a pui thin.
- Pulmonary Function Tests (PFTs): Hengte hian i lungin boruak a luh leh chhuah theih zat a teh a, chu chuan i lungin hna a thawh that dan tur ngaihtuahna a pe a ni.
Heng test zawng zawng hi i tih zawh hnuah doctor chuan operation i mamawh leh mamawh loh chu a rel ang.
Enkawlnate chu engte nge ni? Dam theih loh a ni em?
A theih ngei ang! Hemi atan hian enkawlna tha tak tak a awm a. Surgery hman dan tlangpui pahnih a awm a. Heng surgery te hi inverted sternum chu a awmna dik takah, chu chu pawn lam hawia hruai kir leh nan an hmang thin.
Heng surgery pahnih hmang hian:
- I thinlung leh lungte chunga harsatna awm chu a tihziaawm a, chu chuan hna a thawk tha zawk thei a ni.
- I rilru hmel a siam tha leh thin.
Taksa lama symptoms (thâwk harsa, rilru na), emaw, i hmel lan dan avanga lungngaihna nasa tak i neih chuan operation hi a solution tha ber a ni thei.
He surgery tih theihna tur kum tha ber chu kum 10 leh 14 inkar anga ngaih a ni a, hei hi a chhan chu chutiang kum chuan rilru ruh leh ruh (cartilage) te chu a la inthlak danglam thei a ni. Chuvangin surgery hi tih a awlsam a, a result pawh a hlawhtling hle.
Tunah chuan heng surgical procedure pahnih hi eng nge ni tih i lo en ang u.
| Surgery tih dan tur | Engtin nge kan tih ang |
|---|---|
| Nuss tih dan tur (Minimally invasive surgery tih a ni) . | Hei hi tunlai khawvela hmanraw hman lar ber a ni. Incision lian tham a awm lo.
|
| Ravitch kalphung a ni (Open surgery tih a ni) . | Hei hi traditional open surgery a ni.
|
I surgeon chuan a enfiah ang che a, eng surgery nge i tan a tha ber tih a rel ang.
Operation hnuah a dam leh theih nan eng chen nge a duh? A na hi a na em?
Hei hi mi tam takin an hlauh em em a ni. Mahse thu lawmawm ber chu tunlai natna enkawl dan avang hian operation hnua natna hi a tlem hle a, dam leh hun pawh a tawi zawk hle.
Tuna hmanraw hlawhtling ber pakhat chu cryoablation hi a ni .
A awlsam zawngin, hei hian operation hmaa rilru (ribs inkar) thlenga natna thlentu nerve te chu hun engemaw chen a vawt tir a ni. Ha lakchhuah hmaa i hmui i numbing ang mai a ni. Hei hian operation hnu ni engemaw zat chhung chu natna tam tak i nei lovang tihna a ni.
Hetiang tih dan avang hian:
- Tun hma angin ni 5-7 chhung damdawi inah i awm a ngai tawh lovang. Operation hnu ni khatah i haw thei fo.
- I tih thin angin natna tidamtu (opioids) chak tak i rinchhan a ngai tawh lovang.
- Tun hma chuan sikul kal thei naupang chu sikul chawlh laiin he surgery hi tih a ngai a, a chhan chu a dam theih nan thla khat vel a ngai a ni. Mahse tunah chuan kar hnih atanga kar thum chhungin sikul an kal leh thei ta.
Chuvangin, surgery tih hlauhna tur a awm lo.
Ṭhenkhat chuan zawhna an zawt fo ṭhin
Surgery ka neih loh chuan ka upat deuh deuh chuan he natna hi a zual zel dawn em ni?
Kan tar chhoh zel chuan rilru tightness hi a na zual lo. Mahse, kan tar chhoh zel chuan kan taksa hnathawh dan pangngai a tlahniam zel a, kan thinlung leh lung kan tihbuai avanga natna lanchhuahna (thâwk hahna, hahna) kan nei tam tan thei a ni.
Surgery ka neih loh chuan ka dam rei zawng hi a tawi dawn em ni? Ka thinlung leh ka lungah chhiatna nghet tak a awm dawn em ni?
No. Pectus Excavatum hian mi dam rei zawng a ti tawi emaw, hun kal zelah thinlung emaw lung emaw a tichhe vek tih finfiahna a awm lo. Mahse, enkawl loh chuan a natna lan chhuah dan chu nunpui a harsa zual thei a ni.
Hei hi ven dan tur a awm lo em ni?
Hei hi a chhan dik tak hriat a nih loh avangin a lo thlen lohna tur kawng a awm lo.
Engtikah nge operation hnuah hnathawh pangngaiah ka kir leh theih ang?
Operation hnuah rei vak lo chawlh hahdam a ngai dawn a ni. A natna a reh tawh chuan kea kal leh tlan tlem i tan thei tawh ang. Mahse, i surgeon chuan engtikah nge rit phurh leh infiamna i khelh leh theih ang tih a rel ang. A tlangpuiin sikul kal thei naupang chu kar 2-3 chhungin sikul a kal leh thei.
A pawimawh ber chu i taksa lem chungchangah lungngai lo tur a ni. Miin cosmetic issue mai mai a nih thu a hrilh che chuan pawm suh. Taksa leh rilru lama harsatna i neih hi a tak tak a ni. Chuvângin, chu mi chungchâng chu doctor hnênah inhawng takin sawi la, i mamawh ṭanpuina chu la rawh.
Take-Home Thuchah a ni
- Pectus Excavatum hi rilru ruh lai tak (sternum) chu chhung lam hawia a pil thinna a ni. Hei hi pianpui (congenital condition) a ni.
- Hei hian taksa lama symptoms, thawk hah leh hahna te a thlen thei a, chubakah hmel lan dan nena inzawm mualphona leh rilru hahna a thlen thei bawk.
- Doctor chuan hei hi enfiahna awlsam tak hmangin a hre thei a ni. He natna hi CT emaw MRI scan ang chi test hmanga finfiah belh theih a ni.
- He dinhmun hi surgery (Nuss emaw Ravitch procedure) hmangin hlawhtling takin siamthat theih a ni.
- Tunlai natna enkawl dan (Cryoablation ang chi) avang hian tunah chuan operation hi a hrehawm lo hle a, dam leh hun pawh a tawi tawh hle.
- Nangmah emaw, i fa emaw hian hetiang dinhmun hi i nei a nih chuan hlau lo la, zak suh. Doctor thiam tak hnenah thurawn pe rawh.











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