I pum a na lo va, i taksa a khat tih i hriat a, i chaw ei kham reng i nei ngai em? A chang chuan hengte hi thil pangngaiah kan ngai a, mahse a tlem berah chuan heng natna lan chhuahna chhan dang a awm thei bawk. Vawiin hian cancer natna hmuh tur awm lo tak, mahse pawimawh tak mai kan sawi dawn a ni. Chu chu `Pseudomyxoma Peritonei` an tih condition a ni a, chu chu a tawi zawngin `(PMP)` kan ti bawk.
Pseudomyxoma Peritonei (PMP) hi eng nge ni?
A awlsam zawngin sawi ila, `Pseudomyxoma Peritonei` hi cancer chi khat hmuh tur awm lo tak a ni. Hemi kawngah hian thil thleng chu i pum chhungril, chu chu pum leh a chhehvel (`(peritoneal cavity)`) chu cancer cell-in a khat a ni. Heng cancer cell te hian jelly ang chi, slimy substance ``mucin`` tih chu tam tak an siam chhuak thin. Ngaihtuah teh, i pum chhung lam chu jelly-in a khat ang mai a ni! Hei vang hian mi thenkhat chuan he natna hi ``jelly belly.`` an ti bawk
"Pseudomyxoma Peritonei" tih hming hian "peritoneal cavity-a mucinous tumor dik lo" tih ang chi a kawk a ni. Doctor-te chuan hei hi "false tumor" an ti a, a chhan chu cancer dang hmun khata intan a, darh zel ang a nih loh vang a ni. A takah chuan i appendix, appendix -a lo awm ``polyp'' an tih lump te tak te atanga tan a ni.
He polyp hi appendix atanga a chhuah chuan chu jelly ang chi ka sawi tak thil siamtu cancer cell te chu pum chhung zawngah a darh tan ta a ni. Hun a kal zel a, hei hian i chaw ei leh in (digestive system) a nghawng thei a ni.
PMP kan neih hian eng symptoms nge kan neih?
PMP symptoms hi a lo lang nghal vat fo thin. A tir lamah chuan i hre lo mai thei a, thil pangngai, constipation emaw indigestion emaw ang chi niin i ngai mai thei bawk. Mahse heng symptoms te hi a awm reng emaw, a na zual emaw chuan i ngaihtuah tur a ni.
A lan chhuah dan tlangpui thenkhat chu hetiang hi a ni:
- Abdominal distension: Pum chu a hring leh a lian tih hriat theihin a lang.
- Pum natna: He jelly ang chi hi pum chhunga thil awm hi general discomfort emaw pain emaw ang maiin a awm thei.
- Constipation: Bloating hian intestine lian tak a block thei a, stool pass a ti harsa thei bawk.
- Naupai harsatna: A bik takin hmeichhia tan chuan he jelly-a khat uterus avanga pressure emaw, reproductive organs inflammation emaw avang hian nau pai a harsa thei hle.
- Hernias: Pum chhunga pressure sang chuan i taksa peng pakhat chu taksa ruh hmangin a rawn nawr chhuak thei a ni. Mipaah chuan inguinal hernia hi PMP chhinchhiahna tlanglawn tak a ni.
- Chaw chu a thlum lo.
- Luhai.
A châng chuan, doctor chuan kum tin i check-up lai emaw, natna dang i test lai emaw pawhin he `PMP` natna hi a lo man hmasa thei a ni. Mahse mi tam zawk chuan an pum harsatna a awm reng a, a zual zel chuan an hre thei chauh a ni.
Engvangin nge he PMP hi a lo awm? Eng nge a chhan?
Dik tak chuan mithiamte chuan eng chain of events nge PMP thlen tih chiang takin an la hre lo. Mahse, appendix-a polyp an tih, a lo ṭhan lian lo tak aṭanga ṭan a ni tih an hria. Chuta tang chuan mucin siamtu cancer cell te chu pum chhungah an kal lut ta a ni.
`PMP` hi natna hmuh tur awm lo tak a ni tih hre reng ang che . Kum khatah mi maktaduai khatah mi pakhat atanga pali vel a nghawng thin. Chuvangin he thu hi hriatin a tul lovah hlau suh.
Doctor ten PMP an neih leh neih loh engtin nge an hriat?
Doctor i pan hunah i symptoms te an zawt ang che. Eng chen nge i neih tawh a, an na zual zel em? Tichuan physical exam an ti leh ang. Thisen test leh imaging test pawh an order dawn bawk.
Thisen test a ni
I doctor chuan thisen chhiar kimchang (CBC) a ti thei ang. Tumor marker zawng turin thisen test pawh an ti thei bawk. Hengte hi i taksaah cancer i nei tih tilang thei thilte an ni.
Imaging test te pawh a awm
I pum chhunga taksa peng hrang hrangte chu a lian em, tui (ascites)-in a khat em tih emaw, "jelly belly" ang chi mucin a lo awm em tih enfiah theih a ni:
- Pum chhunga ultrasound hmanga tih a ni.
- CT scan a ni.
- MRI scan a ni.
Chu bâkah, doctor chuan needle biopsy a ti thei a, chu chu i pum chhûng aṭanga tui emaw, tissue emaw sample tê tê a laksak a ni. Medical pathologist chuan microscope (cytology) hmangin sample chu a enfiah ang. A chang chuan laparoscopy hmangin i pum chhung enin tissue sample lak theih a ni bawk.
PMP enkawl dan tur chu engte nge ni? Dam theih a ni em?
Enkawlna chu thil tam takah a innghat a, chutah chuan i dinhmun leh i hriselna zawng zawng pawh a tel. A then phei chuan doctor te hian Pseudomyxoma Peritonei hi an enkawl thei a, an tidam thei hial a ni .
A tam zawkah chuan he enkawlna hi operation a ni. Hei hian cancer cell awmna taksa peng zawng zawng paih chhuah a huam a ni. Surgery neih chhung hian chemotherapy (intraperitoneal chemotherapy) pek i ni thei bawk. Mahse surgeon chuan hetiang hi a ti ang, surgery hian cancer emaw mucin emaw zawng zawng emaw, a tam zawk emaw a paih chhuah theih phawt chuan. Chu thutlukna chu operation neih laiin siam a ni.
PMP enkawl nan hian surgery chi hrang hrang a awm a.
Entirnan, i intestine te emaw, large intestine emaw ah mucin i neih chuan i doctor chuan bowel resection a ti ang . Surgery chi dang pawh a awm a, chu chuan taksa peng hrang hrang a paih chhuak thin:
- Cholecystectomy: I gallbladder lakchhuah.
- Hysterectomy with bilateral salpingo-oophorectomy : I fallopian tube, ovary leh uterus te lakchhuah.
- Liver capsulectomy: I liver chunglam thenkhat lakchhuah .
- Omenectomy: Pum hmaa thau awm chu paih chhuah .
- Peritonectomy : I pum chhung leh i pelvis (peritoneum) line-a awm membrane lakchhuah.
- Splenectomy : I rilru a buai em em a.
Surgery neih chhung hian eng harsatna nge thleng thei?
I taksa peng hrang hrang lakchhuahna tur operation i neih hian thisen chhuah tam lutuk , natna hrik kai, emaw anastomotic leak ang chi harsatna a awm fo thin. Surgery lian tham tak tak hian nunna atana hlauhawm tak tak a thlen thei bawk. Damlo zaa khat atanga zaa hnih (1-2%) vel chu operation lian tham an tih hnuah an thi niin an sawi. Chuvangin heng zawng zawng hi doctor nen sawiho a pawimawh hle.
Surgery tel lo enkawlna dang a awm em?
A châng chuan i doctor chuan operation ni lo enkawlna dang a rawt thei a, chu chu:
- Active surveillance : PMP i neih hmasak ber a nih chuan, emaw, a nasat em em a nih chuan, leh operation neih theihna chu natna hlauhawmna aiin a tam zawk a nih chuan, i doctor chuan active surveillance a rawt thei ang. Hei hian i doctor-in i hriselna a enfiah reng a ngai a ni. PMP hi a darh zel em tih hriat nan imaging test leh thisen test an nei thei bawk.
- Palliative care : Operation i tih theih loh chuan i doctor chuan PMP condition control thei leh symptoms tihziaawm thei tur chemotherapy emaw radiation therapy emaw ang chi enkawlna a rawt thei ang.
Tunah hian doctor-te pawhin small bowel transplantation hi small intestine-a PMP vei te enkawlna atan an zirchiang mek bawk.
PMP neitu hian eng ang hmalam hun nge a beisei theih ang?
Thil engemaw takah chuan, pum chhunga cancer cell zawng zawng paih chhuah vek tura operation tih hian natna chu hun rei tak chhung thunun theih a ni . Enkawlna dangte chuan he natna nen hian hun rei zawk dam turin a pui thei che a ni.
``Survival rate`` chungchang kan sawi hian hriat reng tur pawimawh tak chu hei hi natna hmuh tur awm lo tak a ni. Chumi awmzia chu mi tlemte chauhvin an nei tihna a ni. Zirchiangtute chuan a chungchanga an hriatte chu mi tlemte tak tak hnen atangin an zir chhuak mek a ni. He natna hi i neih chuan i doctor hnenah he ``survival rate`` research chungchang leh i dinhmun a nghawng dan hi zawt la a tha ber.
Engtin nge ka in enkawl ang? (Mahni inenkawlna) .
Cancer cell lakchhuah emaw, taksa peng thenkhat lakchhuah emaw tura operation i neih tawh chuan i taksain a dam theih nan hun leh chawlh a mamawh tih hriat reng a pawimawh. Entirnan, i spleen lakchhuahna tur surgery i neih chuan i doctor chuan hei hian engtin nge a nghawng dawn tih a hrilhfiah ang che.
Palliative care i thlan chuan i dam chhung zawng cancer enkawlna chemotherapy leh radiation therapy te i neih a ngai mai thei. Chak taka awm reng a, doctor thupek uluk taka zawm a pawimawh.
Engtik hunah nge Doctor ka hmuh ang?
`PMP` i neih chuan a hnuaia thil thlengah hian i doctor hnenah i hriattir ngei tur a ni:
- Enkawlna hnua harsatna a awm chuan. Entirnan, operation hnua thisen chhuak tam lutuk a awm chuan, a nih loh leh surgery hliamah natna hrik kai chhinchhiahna a awm chuan.
- Enkawlna avanga side effects i beisei aia na zawk a nih chuan.
- Operation hnua `Pseudomyxoma Peritonei` lo lang leh tur symptoms a awm chuan.
A tawp berah chuan thuchah pawimawh ber (Take-Home Message) .
Pseudomyxoma Peritonei (PMP) hi natna hlauhawm tak leh harsa tak a ni. Mithiamte chuan engvanga lo thanglian nge tih chiang takin an la hre lo. Hun rei tak i nei a, i taksaah danglamna lian tham i hmu lo thei bawk. Symptoms a lan tak tak chuan constipation emaw bloating emaw ang maia awlsam a ni thei.
Chuvangin, i symptoms te hi chutiang natna hmuh tur awm lo tak avanga lo awm a ni tih i hriat chuan thil mak tak a ni thei. Enkawlna chu i pum chhunga taksa peng pakhat emaw, a aia tam emaw paih chhuah nan operation a ngai dawn tih hrilh chu a buaithlak thei hle. Heng zawng zawng hi vawi khata hriatthiam a harsa thei hle.
Mahse, lungngai suh. I doctor-te chuan zawhna tam tak i nei thei tih an hrethiam a – zawhna inang pawh vawi tam tak i nei mai thei. I enkawl dan tur i hriat a, i hmalakna tur i ngaihtuah rual hian i rilru a awm zawng zawng chu hriat an duh vek a ni. Chu chu i dikna a ni. Rilru dinhmun tha taka awm hian enkawlna kawngah pawh nasa takin a pui bawk.
` Pseudomyxoma Peritonei, PMP, cancer, pum chhunga awm, mucin, jelly belly, appendix, surgery tih te











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