Restrictive Cardiomyopathy: natna hmuh tur awm lo tak, thinlung ruh a tichak lo tih hi i zir dawn a ni.

A châng chuan i chau a, thawk i hah a, i ke a hring emaw i nei em? Heng symptoms te hi kan theihnghilh fo thin a, chu chu hahdamna pangngai emaw, kan thawhrimna avanga thil thleng mai emaw ang maiin kan ngai thin. Mahse a chang chuan heng symptoms hnung hian thinlung natna hmuh tur awm lo leh awm lo tak a awm thei bawk. Chu chu vawiin a kan sawi tur natna pakhat a ni a, chu chu Restrictive Cardiomyopathy (RCM) . Ngaihtuah buai suh, he thu hi awlsam tak leh i hriatthiam theih tur angin kan sawi dawn a ni.

A awlsam zawngin, Restrictive Cardiomyopathy chu eng nge ni?

He hming hi a buaithlak deuhin a lang thei a, mahse a awlsam zawngin han then ila, i hrethiam ang u.

Kan thinlung hi taksa peng mak tak a ni. Chamber lian pali a nei a. A chung lam chamber pahnih chu atria an ti a, a hnuai lama chamber lian leh chak tak pahnih chu ventricles an ti bawk. Chamber hnuai lam pahnih hian kan taksa pum puiah thisen pump hna an thawk ber a ni. He hna hi a thawk tha tur chuan chamber chhunga ruhte chu nghet taka inzawm a ngai a, thisenin a khat a, chutah chuan thisen chu hmalam pan turin chak takin a inzawm khawm a ngai a ni.

Rubber ball thar tak mai chu han mitthla teh. Engtiang chiahin nge a flexible? Chutiang chuan thinlung hrisel cell te chu a awm tur a ni. Thisen a luh chuan an hring tha tur a ni a, thisen chu an la lut tur a ni a, pump chhuah a ngaih hunah an inzawm tha tur a ni.

Natna pakhat Restrictive Cardiomyopathy an tih ah chuan heng cell te taksa ruh ( muscle walls ) te hi a nghet lo hle a . Rubber hlui, ni-a vawt ang maiin. Hetianga a khauh avang hian cell te chu an inzawm tha thei lo va, thisenin an khat thei lo. Chumi awmzia chu thinlunga thisen lo lut chu an la lut tling thei lo tihna a ni. Thinlung chhunga thisen lut zat a tlem chuan taksaa thisen pump chhuah zat pawh a tlahniam bawk. Hei hi he natna bulpui ber a ni.

He natna hi thinlung ruh natna pawl Cardiomyopathy an tih zingah a tel a ni . Mahse, an zingah chuan chi tlem ber nia ngaih a ni. Cardiomyopathy vei zawng zawng zinga 5% vel chauhvin he natna hi an vei a ni.

He natna hian engtin nge a tiharh che? (Natna)

He natna hi a tir lamah chuan symptoms i nei lo mai thei. Mahse hun a kal zel a, thinlunga thisen kalna a tlahniam chuan thinlung chak lohna chhinchhiahna a lo lang tan ta a ni. Chûngte chu pakhat khatin emaw, vawi khatah engemaw zât emaw a lo lang thei a ni.

Chu symptoms chu eng nge ni tih a hnuaia table-ah hian i en ang u.

Engvangin nge hetiang hi a lo awm? (A chhan) .

A tam zawkah chuan Restrictive Cardiomyopathy hi damdawi lam thil dang avanga side effect angin a lo awm thin. Chu chu natna dangin thinlung ruh a tichhe a, a tikhauh phah tihna a ni. A châng chuan, a chhan chiang tak hmuh tur a awm lo.

Hengte hi a chhan lian ber thenkhat chu a ni:

• Amyloidosis: Hei hi taksain protein a siam danglam (amyloid) chu taksa peng hrang hrangah a awm a, chu chu thinlungah a awm a ni. He protein hi thinlungah a awm chuan thinlung ruh bangte chu a thim a, a nghet lo hle.
• Sarcoidosis: Hei hi taksa peng hrang hranga inflammatory cells (granulomas) te te te lo awm thin a ni. Chungte chu thinlungah a lo awm chuan thinlung ruh a tichhe thei a, a tikhauh thei bawk.
• Hemochromatosis: Hei hi taksain iron a khawlkhawm tam lutuk a, chu chu thinlung ang chi taksa peng hrang hrangah a khawlkhawm thei a ni. Hei hian thinlung a tichhe thei bawk.
• Connective tissue natna: Scleroderma ang chi natna hian thinlung ruh a ti nghet thei bawk.
• Cancer enkawl dan thenkhat: Cancer dona damdawi thenkhat (chemotherapy) leh radiation therapy te hian side effect angin heart muscle a tichhia thei bawk.

Engtin nge doctor hian hei hi a hmuh theih?

Doctor hnenah i natna lan chhuah dan i hrilh hian a tih hmasak ber tur chu uluk taka a enfiah che hi a ni. I thinlung thu an ngaithla ang a, i thisen sang an teh ang a, i ke a hring em tih an enfiah ang.

Tichuan, a natna dik tak hriat chian nan leh a chhan hriat chian nan test eng emaw zat neih a tha.

Hei hi eng enkawlna nge ni?

Restrictive Cardiomyopathy hi enkawlna bik a awm lo. Enkawlnaah hian thil tum lian tak pahnih a awm a, chungte chu:

1. Hetiang dinhmun thlentu natna hnuaia awm enkawl.

2. Symptom awmsa control a, nun awlsam zawk siam.

Entir nan:

• Hetiang dinhmun hi sarcoidosis vang a nih chuan a damdawi corticosteroids te pawh pek theih a ni.
• Hemochromatosis (iron overload) vang a nih chuan taksa atanga iron tam lutuk paih chhuah nan thisen engemaw zat lakchhuah nan therapeutic phlebotomy an tih damdawi an ti thin.
• Tunah chuan amyloidosis chi thenkhat tan damdawi thar a awm ta .

Chu bâkah, i doctor chuan heart failure symptoms enkawl nân a hnuaia mite hi a rawt thei bawk ang:

• Diuretics: Hengte hi ‘tui pills’ an ti tlangpui. Taksain zun hmanga tui tam lutuk a paih chhuah theih nan an pui a, hei hian ke ruh natna leh thawk hahna tihziaawmna kawngah a pui thei a ni.
• Heart rate control damdawi: I heartbeat a mumal lo a nih chuan a control nan damdawi beta-blocker emaw calcium channel blocker emaw pek theih a ni.
• Thisen sang damdawi.

Natna nasa tak nei damlo thenkhat chuan heart transplant an mamawh mai thei . Doctor-te chuan palliative care , damlo chu a rilru hahdam zawk nan a pui a, a natna lan chhuah dan avanga hrehawmna a tihziaawm bawk.

Hetiang dinhmun hi engtin nge kan hrisel theih ang?

He natna hi i vei tih i hriat veleh hlauhna i neih hi thil pangngai tak a ni. Amaherawhchu, Damdawi inenkawlna dik tak leh i nunphung tihdanglamna tenau te i neih chuan i thinlunga phurrit chu i tihziaawm thei a, nun tha zawk i hmang thei a ni.

Nunphung a inthlak danglam thin

• Salt control: I chaw eiah chi i dah zat tihtlem. Chi (salt) hian taksaah tui a tipung thei a, chu chuan a hring a, thawk harsatna a thlen thei a ni. Canned food, dawr atanga lei sauce leh sausage te hian chi a pai tam hle.
• Ei leh in hrisel: Thlai thar, thei leh fiber tamna ei tam zawk rawh. Ran thau, thil thlum leh chhangphut atanga siam te tihtlem.
• Exercise: I doctor hnenah eng exercise nge i tan a tha tih zawt rawh. Exercise hahthlak hi a dik lo mai thei a, mahse kea kal ang chi exercise light tak hi a tha fo thin.
• Stress tihziaawm: Stress hi thinlung tan a tha lo. I rilru chu ngaihtuahna, thawk chhuahna exercise, leh i hobby nuam tak tih ang chi thil hmangin ti hahdam rawh.

Engtikah nge doctor pan vat a ngaih?

Restrictive Cardiomyopathy i neih chuan a bik takin i hriat tur symptom thenkhat a awm. Chûngte chu emergency a ni thei.

A hnuaia symptoms te hi i neih chuan damdawi in hnai ber Emergency Department (ETU) ah kal nghal rawh:

• A rilru a na lutuk emaw, a rang lutuk emaw
• Thâwk lak harsat thut, nasa tak
• Fainting emaw, hriatna hloh emaw

Chûngte chu thinlunga lungkhamna nasa tak thlentu chhinchhiahna a ni thei a, chuvângin hun khawhral lova enkawlna zawn chu nunna chhanhimna a ni thei a ni.