I naute thinlung thisen kalna kawng lian tak takte chu transpose a ni tawh em? (Transposition of the Great Arteries) - Hemi chungchang hi han sawi ila!

I naute piang thar hian thinlung natna a nei tih i hriat hian i hlauhthawn leh lungngaihna chu thuin sawi chhuah a harsa khawp mai, a dik em? Mahse, lungngai suh. A châng chuan naute hi an pian hunah an thinlunga thisen kalna kawng lian ber pahnih chu an inthlak thei ṭhin. Vawiin hian chutiang dinhmun pakhat kan sawi dawn a, chu chu `(Transposition of the Great Arteries)` tih a ni. Hei hi a buaithlak deuhin a lang thei a, mahse a awlsam zawngin i dah ang u.

Transposition of the Great Arteries chu eng nge ni?

A awlsam zawngin sawi ila, hei hi naute pian tirh atanga lo awm ``congenital`` condition a ni. Chu chu, he harsatna hi naute nu pum chhunga a la awm laiin a lo awm tihna a ni. Kan thinlung atanga kan taksa peng dang thlenga thisen phurtu thisen kalna kawng lian pahnih kan nei a. Pakhat chu pulmonary artery a ni a, chu chuan lungah thisen a phur a , pakhat chu aorta a ni a, chu chuan kan taksa dang zawng zawngah thisen a phur a ni . Hetiang dinhmunah hian thil thleng chu heng thisen kalna kawng lian pahnih hi hmun dik takah ni lovin hmun dik lovah thinlung nen an inzawm tlat a ni. Tui tank pahnih pan tur pipe te chu switch ang mai a ni.

Engtin nge thisen hi a tlangpuiin a kal? Hetiang dinhmunah hian eng thil nge thleng?

A tlangpuiin hetiang hi a thleng thin: taksaa oxygen tlachham (blue blood) chu thinlungah a kal a, chuta tang chuan lungah oxygen la turin a kal thin. Tichuan thisen thar, oxygen tamna (thisen sen) chu thinlungah a kal leh a, chuta tang chuan thisen kalna kawng lian tak tak kaltlangin taksa pum puiah a kal leh ta a ni. Mahse he ``Transposition of the Great Arteries'' dinhmunah hian thisen kalna kawng pahnih a inthlak avangin oxygen tlachham thisen chu lungah kal lovin taksaah a kal leh ta zawk a ni. Chutiang bawkin lung atanga oxygen tamna thisen lo chhuak chu taksaah kal lovin lungah a kal leh thin. Hei hian naute taksa peng hrang hrangah oxygen a thlen tlemzia hi han ngaihtuah teh.

Hei hi chi hrang hrang a awm em?

Ni e, hei hi chi hnih a awm a, chungte chu: 1. Levo-transposition (Levo-transposition emaw l-TGA): Hetiang a nih chuan naute aorta chu pulmonary artery veilam lamah a awm a. Chutiang a nih chuan thisen kalna kawng pahnih chauh ni lovin, thinlung hnuai lam pindan pawh a inthlak a ni. Mahse, he type-ah hian deoxygenated thisen chu lungah a kal a, oxygenated thisen chu taksaah a kal bawk a, chuvangin harsatna lian tham a thlen lo. Hei hi a tlem deuh a ni. 2. Dextro-transposition (Dextro-transposition or d-TGA): Hetiang a nih chuan naute aorta chu pulmonary artery dinglamah a awm a. Hei hi a tam ber chi a ni a, ngaihven zual ngai chi pawh a ni. He `(d-TGA)` chungchang hi he thuziak ah hian kan sawi belh dawn a ni.

Engvangin nge he natna hi d-TGA an tih hi naute tan a hlauhawm?

A hmaa ka sawi tawh ang khan `(d-TGA)` chungchangah chuan naute taksa chu oxygen tlachham thisenin a khat a ni. Chumi awmzia chu naute taksa peng pawimawh zawng zawng, thluak, kal leh thin te hian oxygen mamawh zat an dawng lo tihna a ni. Hei hi naute nunna atan a hlauhawm hle. A châng chuan heng naute hi an lo pian hian thinlung pindan chunglam `(Atrial Septal Defect emaw ASD)` emaw, thinlung pindan hnuai lam inkar `(Ventricular Septal Defect emaw VSD)` emaw inkarah khur a awm thei bawk. Heng khur te hi thil danglam tak ni mahse, chutiang hunah chuan heng khur te hian tanpuina tlemte chauh a nei thei a ni. Chu chu heng khur te hian oxygen tamna thisen thenkhat chu oxygen nei lo thisen nen a inhmeh tir thei tihna a ni. Mahse, oxygen kan dawn zat hi a tawk lo tak zet a ni. Chuvangin naute hian enkawlna a mamawh tak zet a ni.

Ngaihtuah buai suh, he natna hi surgery a awm bawk. Doctor-te hian kum tam tak chhung chu heng surgery te hi hlawhtling takin an lo ti tawh a ni.

I naute hian he natna hi a vei a nih chuan eng chhinchhiahna leh lanchhuahna nge a neih? (Natna)

`(d-TGA)` vei nau piang tharte hian oxygen tlakchham vangin vun rawng blue/gray a ni thin `(cyanosis),` tih natna an nei thei a ni. Thinlung chak lo an nei thei bawk. A lan chhuah dan ber chu:

• Thâwk lak harsat .
• Pulse a chak lo hle.
• Bawnghnute in duh lohna leh harsatna a lantir.
• Ka thinlung chu a na lutuk ang maiin ka hria a, a na lutuk ang maiin ka hria.
• Mit vun leh var chu blue (nausen vun dum neiah) emaw, grey (nausen vun dum neiah) emaw a lang thei.

Engtikah nge heng symptoms te hi a intan?

Naute `(d-TGA)` vei chuan a pian tirh atangin heng symptoms te hi a lantir tan ang. Mahse, a chang chuan `(ASD)` ang chi thil avang hian naute thinlunga khur te te hian oxygen tamna thisen engemaw zat taksaah a thlen thei a, chuvangin a natna lanchhuahna chu a lang tlem thei hle. Tin, `(patent ductus arteriosus)`, nausen pum chhunga a awm laia a hman thin thisen kalna kawng chu a pian hnuah ni engemaw zat a inhawng thei a, chu chuan thisen a ti pawlh thei a ni. Mahse, heng temporary holes leh tubes te hi vawi khat an khar chuan a symptoms chu a pung nghal thei a ni. Chutiang a nih chuan naute chuan damdawi lam pan vat a ngai a ni.

Engvangin nge hetiang hi a lo awm? (A chhan) .

Doctor-te chuan Transposition of the Great Arteries hi eng nge a thlen tih chiang takin an la hre lo. Congenital heart disease dang ang bawkin naupai laiin genetic mutation emaw toxins nena inzawmna emaw avanga lo awm nia ngaih a ni. He natna thlen thei thil thenkhat chu:

• Naupai laiin gestational diabetes i nei a nih chuan .
• Naupai laiin rubella ang natna i neih chuan.
• Pesticide emaw herbicide emaw thenkhat i hman tawh chuan.
• Epilepsy damdawi thenkhat i ei tawh chuan.

Heng thilte hian hlauthawng suh. Hetiang thil pakhat pawh nei tawh zawng zawng hian hetiang hi an tawng vek lovang.

Engtin nge doctor-te hian hei hi an hriat chian? (Diagnosis) tih a ni.

A châng chuan, doctor-te chuan naupai lai hian he natna hi an hmu thei a ni. Hei hi nau neih hmaa test hmanga tih a ni. I doctor chuan i naute ultrasound scan laiin thil dik lo a rinhlelh chuan fetal echocardiogram tihsak turin a ti thei che a ni. Hei hi ultrasound nen a inang a, mahse naute thinlung chu chipchiar takin a en a ni. Hei hian d-TGA i neih leh neih loh a nemnghet thei. Naupai laia hmuh chhuah a nih loh chuan nau pian hnu kar khatna chhungin hmuhchhuah a ni tlangpui.

Hei atan hian eng test nge tih thin?

He natna hi doctor-te’n test an hman thinte chu:

• Echocardiogram (Echo): Hei hi thinlung ultrasound scan a ni bawk.
• Electrocardiogram (EKG): Thinlung electric hnathawh dan enfiahna test a ni.
• Nau piang thar pulse oximetry screening: Hei hi nau piang thar zawng zawngah tih a ni fo.
• Chest X-ray test neih a ni.
• Cardiac catheterization: Hei hi test buaithlak zawk a ni. Tube te tak te ( catheter ) chu ke emaw kut emaw hmangin thinlung chhungah dah a ni. Hei hi test dang a chiang lo a nih chuan tih a ni.
• CT scan hi test a ni.

Hei hi engtin nge kan enkawl ang? I naute hian tanpuina a mamawh thuai!

Nausen `(d-TGA)` neia piang chu a dam theih nan surgery a neih a ngai a ni. A tam zawkah chuan he surgery hi nau piang kar hmasa berah tih a ni. He surgery hi arterial switch procedure an ti a . A awlsam zawngin, hei hian thisen kalna kawng pahnih (aorta leh pulmonary artery) chu an awmna tur dik takah inzawm leh a huam a ni. Hei hian thisen a luang tha thei a ni. I naute hian an thinlungah khur, `(VSD)` ang chi a neih chuan chu pawh chu he surgery neih chhung hian siamthat a ni ang.

Surgery hmaa tih tur hun eng emaw chen

Doctor-te chuan naute dinhmun tihngheh nan hian hun eng emaw chen enkawlna eng emaw zat an hmang a, chu chu major surgery tih theih a nih hma loh chuan a ni. Chung zingah chuan:

• Prostaglandin: He damdawi hi nausen pum chhunga thisen kalna kawng (ductus arteriosus) hawn nan hman a ni a, naute hian a pian hnuah a khar thin. Hei hi hawn a nih veleh oxygen nei thisen thenkhat chu taksaah a luang lut tan ta a ni.
• Balloon atrial septostomy tih hming pu procedure chu:Hetah hian thin tube (catheter) te tak te hmangin thinlung chunglam chamber pahnih inkar natural opening chu tihzauh a ni. Hei hian oxygenated leh deoxygenated thisen a inhmeh tir a, taksaah oxygen engemaw zat a pe a ni.

Hetiang dinhmun hi ven theih a ni em?

Transposition of the Great Arteries tih loh dan tur hriat a ni lo. Amaherawhchu, i naupai lai hian hriselna kawng tha zawm a pawimawh. I shot zawng zawng chu a hun takah la la, i multivitamin chu ei la, doctor appointment pawh vawng reng rawh. I chhungkuaa tu pawhin pianpui thinlung natna nei tawh an awm chuan i doctor nen sawiho rawh. Genetic counseling a rawt thei bawk.

Operation hnuah eng nge thleng? TGA nena khawsak dan tur

Surgery hian natna hi "tidam" kim lo mah se, `(d-TGA)` vei tam tak chu nun famkim, hrisel takin an hmang a ni. Mahse, he `(congenital)` natna vei te hian dam chhung zawng damdawi lam enkawlna an mamawh a ni. Cardiologist chuan i fa dinhmun a enfiah fo ang a, thurawn tul apiang a pe ang. `(arterial switch)` surgery hnua damchhuah zat chu 95% aia tam a ni. Kum 25 hnuah pawh he rate hi a la awm reng niin an sawi.

I fa hi TGA nen hian a nung tha thei ang em?

Ni e, a dik tak zet. `(Transposition of the Great Arteries)` natna enkawl hnuah i fa chu nun pangngaiin a nung thei ang. Amaherawhchu, thinlung hi dam chhung zawnga enkawl a ngai a ni. Chumi awmzia chu:

• Hetiang chi hrang hranga specialist cardiologist nen hian inzawmna nei reng tur a ni.
• Damdawi pek tur dik tak i ei a ngai a ni.
• Thinlung hnathawh dan enfiahna test, `(EKG), `(Holter monitor), `(exercise stress test), leh `(echocardiogram),' te hi tih fo a ngai dawn a ni.

Cardiologist tam tak chuan `(d-TGA)` surgery hnuah competitive sports khelh hi an rawt lo. Chuvangin, nang leh i fa, i naupang enkawltu doctor leh i cardiologist te hian i fa hriselna atana thutlukna tha ber siam turin i thawk ho tur a ni. Hmeichhia tam tak `(d-TGA)` surgery nei tawhte chuan hlawhtling takin nau an pai ta a ni. Mahse, naupai hmain doctor leh cardiologist te nen in inbia ngei tur a ni.

Nakin lawkah chuan heart surgery tam zawk neih a ngai dawn em?

Ni e, a hnuah operation tam zawk neih a ngai mai thei. A tam zawkah chuan heart rhythm problem siamthat nan emaw, heart valve siamthat nan emaw an ni.

Endocarditis vei theihna a awm em?

Endocarditis hi bacteria infection thinlunga a luh chuan a lo awm thin a ni. TGA ang heart condition nei te hian hetiang hi an vei tam zawk. Chuvangin, transposition surgery nei tawhte chuan ha enkawl hmain antibiotics an ei a ngai mai thei.

Thluak hmasawnna a nghawng thei ang em?

Naupang thenkhat arterial switch nei tawhte chuan ADHD (attention deficit hyperactivity disorder) an nei thei bawk. A nih loh leh, sikul hnathawhnaah ṭanpuina bîk an mamawh mai thei bawk. Hei pawh hi hre reng ang che.

Engtikah nge Doctor ka hmuh ang?

I naute hian heng symptoms te hi a neih chuan...

• Thâwk harsa i tih nia i hriat chuan.
• Pulse a chak lo hle a nih chuan.
• Kawngkhar vel vun chu a sen/var a lo ni tawh a nih chuan.

Hetiang thil i hmuh chuan Doctor pan nghal rawh.

Naupan lai khan he surgery hi i nei a nih chuan...

I dam chhungin medical checkup leh monitoring neih reng a ngai dawn a ni. Puitling (congenital) heart disease lama tawnhriat nei cardiologist hmu rawh.

Doctor hnenah eng zawhna nge i zawh tur?

I naute hian Transposition of the Great Arteries a neih chuan doctor hnenah heng zawhnate hi i zawt thei ang:

• Ka naute hian operation a mamawh thuai dawn em?
• Enkawlna tha ber chu eng nge ni?
• Ka naute hian eng ang follow-up care nge a mamawh?
• Surgery dang a neih leh a ngai dawn em ni?
• A thiltih danah khapna a awm em?
• Ka naute hi operation hnuah engtin nge ka enkawl ang?

Naupang i nih laiin he natna hi operation i neih chuan i doctor hnenah hetiang hian i zawt thei ang:

• Surgery dang ka mamawh dawn em ni?
• Eng ang medical supervision nge ka mamawh?
• Ka thiltih danah khapna a awm em?
• Fa ka nei thei ang em?

A tawp berah chuan a pawimawh ber (Take-Home Message) .

I nau piang thar hian pianpui thinlung natna a nei tih hriat chu nu leh pa tu pawhin an beisei a ni lo. Thinlung tichhe thei tak a ni. Mahse, nangmah chauh i ni lo. I naute doctor-te chuan he zinkawngah hian an pui thei che a, thutlukna i siamnaah pawh an kaihruai thei bawk che a ni.

Doctor-te hian kum tam tak chhung TGA hmanga naute an enkawl tawh tih hre reng ang che, a result pawh a hlawhtling hle. I fa tan chak takin awm rawh. I hriatthiam loh emaw, i hriat chian loh emaw chu i doctor hnenah zawhna zawh hreh suh. I hriatna hi i fate hmalam hun hrisel tak neih theihna tura chakna lian ber a ni.

Cardiac shunting, pianpui thinlung natna, arterial switch surgery, cyanosis, nausen thinlung natna, d-TGA, thinlung surgery te a awm bawk