Nausen piang thar i en hian nu leh pa anga i hlimna chu sawifiah theih loh a ni. Mahse, a châng chuan, doctor-in naute a enfiah a, a taksaah thil dik lo a awm tih a hrilh che chuan, tlem chuan i hlauthawng a, i lungngai deuh mai thei. Vawiin hian piansualna hmuh tur awm lo tak, mahse pawimawh tak kan sawi a ni. Hei hi Urogenital Sinus an ti a.
He Urogenital Sinus hi eng nge ni?
A awlsam zawngin, hei hi pianpui chhiatna a ni a, hmeichhe naupangte chauh a nghawng . Ngaihtuah teh, hmeichhe naupang pakhat hian a taksa hnuai lamah hawnna pathum a nei tlangpui.
1. Zun kawng (urethra) hawnna, zun chhuahna.
2. Vaginal hawn (vagina).
3. Rectum (anus)-a bawlhhlawh chhuahna kawngkhar.
Mahse, naupang Urogenital Sinus nei chuan hawnna pahnih a nei a. Pakhat chu bawlhhlawh chhuahna tur a ni. A hawnna dang chu urethra leh vagina inzawmna avanga hawnna tlangpui a ni. Hei hian urethra leh vagina pahnih hi he opening khatah hian an inzawm tihna a ni .
Engvangin nge hetiang hi a lo awm?
Hei hi hrethiam tur chuan nausen pum chhunga naute lo thanglian chhoh tirh lam kan pan leh a ngai a ni. Naute chu nausen angin a lo thanglian chhoh chuan kan sawi tak system pathum (intestinal system, urinary system, leh reproductive system) te hi a tir lamah chuan an inzawm khawm a, common chamber-ah an inhawng thin. Hei hi ``cloaca'' an ti a. Naute chu pum chhunga a lo seilian chhoh zel chuan heng system pathumte hi zawi zawiin an inthen a, hawnna hrang hrang pathum an siam a ni. Mahse a chang chuan eng emaw chhan vangin zun leh serh hi a inthen tha lo. Chutah chuan an inzawm khawm a, ``Urogenital Sinus'' tih hming pu condition an siam ta a ni.
Urogenital Sinus chi hrang hrang lian ber ber a awm em?
Ni e, he natna hi chi hnih ah then theih a ni a, chu chu common pathway chu eng chen nge a sei tih leh taksa chhunga khawiah nge a inzawm tih a zirin a ni.
| Lampang | Hrilhfiahna awlsam tak |
|---|---|
| Low-joined / inzawmna hniam tak nei | Hetiang chi ah hian urethra leh vagina te hi taksa pawn lam hawnna hnaih takah an inzawm khawm thin. Chuvangin, common passage hi a tawi hle a ni . Urethra leh vagina hi a lian leh a awmna pangngai a ni thei. Hei hi a nasat loh deuh a ni. |
| High-joined / confluence sang tak nei | Hetah hian kawng pahnih hi taksa chhungah, pawn lam hawnna atanga hla takah an inzawm khawm a ni. Chuvangin, common path chu a rei zawk hle . Hei hi natna khirh zawka ngaih a ni . A chhan chu harsatna dang thlen theihna sang zawk nen a inzawm tlat a ni. |
Hei hi thil awm lo tak a ni. Nau piang 10,000 zinga pakhat aia tlem lovah a awm tlangpui. Chuvangin he thuthang hian hlauthawng suh.
Hei hi eng symptoms nge ni?
Natna nasat dan azirin symptoms a inang lo thei. Hengte hi nausen pian hnua doctor-in a enfiah hian hmuh tur a awm fo.
- A langsar ber chu, kan sawi tawh ang khan , hawnna pahnih chauh a awm : pakhat chu bawlhhlawh tan a ni a, pakhat chu urethra leh vagina tan hawnna tlangpui angin.
- Vagina chhungah zun a khawlkhawm a, chu chuan vagina chu a ti hring chhuak thin. Hei hi damdawi lam chuan ``hydrocolpos`` an ti a.
- A chang chuan vagina hi a lo thang kim lo thei bawk.
- Tin, chhungril lam taksa peng hrang hrang, nausen pum, ovary emaw, fallopian tube emaw te pawh a lo thanglian lo vek tih i hmu thei bawk.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
A chhan bik hriat chian a harsa fo a, mahse doctor-te’n an hriat chhuah chhan lian ber tlemte a awm.
- Congenital Adrenal Hyperplasia (CAH): Hei hi thlahtute atanga lo chhuak a ni. Hetiang dinhmunah hian naute adrenal glands te hian hormone siam chhuahna atana mamawh enzyme an siam chhuak lo. Hei hian hormone imbalances leh genitals hmasawnna dik lo a thlen thei a, a bik takin hmeichhe naupangah chuan.
- Virilization: A awlsam zawngin, hmeichhe nausen chhunga mipa hormone (androgens) tam lutuk hi a ni. Hei hian mipat hmeichhiatna lama hmasawnna a nghawng thei bawk.
Engtin nge doctor-te hian he natna hi an hriat theih?
He natna hi dik taka hriatchhuah hi enkawl dan tur ruahmanna siam nan a pawimawh hle. A châng chuan nau neih hmaa ultrasound scan-ah pawh hriat theih a ni. Mahse a tam zawkah chuan doctor chuan naute pian hnua taksa enfiahna hmasa berah he inthlak danglamna hi a hmu thin . Tichuan, a natna hriat chian nan leh a nasat dan hriat nan test eng emaw zat tih belh leh tura tih a ni.
| Fiahna | A awlsam zawngin, engtin nge i tih? |
|---|---|
| Ultrasound hmanga Scan a ni | Hei hian naute chhungril peng hrang hrang, kal, bladder, vagina leh rectum te dinhmun a hriat theih nan a pui a ni. Hydrocolpos (vagina hring) a awm leh awm loh a enfiah thei bawk. |
| Retrograde Genitogram tih a ni | Hei hi X-ray test bik a ni. Doctor chuan common opening kaltlangin dye bik a dah a, X-ray thlalak a la thin. Hei hian a chhunga taksa peng hrang hrangte pianzia, a lian leh te, a awmna hmun chu chiang takin a hmu thei a ni. |
| MRI Scan a ni | Hei hian taksa chhung lam thlalak chiang tak, chipchiar tak tak a siam thei a ni. Urogenital Sinus awmna dik tak leh harsatna dang awm thei, a chhehvel ruhro ang chi te pawh a tarlang thei bawk. |
| Endoscopy hmanga enfiah a ni | Hetiang method hian common orifice kaltlanga dah tur leh a chhung lam chu screen-a direct-a en theih tur camera leh light hmanga thuam thin tube (endoscope) te tak te a hmang a ni. |
Engtin nge enkawl a nih?
He natna enkawl dan awmchhun chu vagina leh urethra surgery hmanga then hran hi a ni .
Hei hi thutlukna buaithlak tak a ni. Surgery neih hma hian i fa medical team te nen rei tak sawihona hun i nei ang. He team-ah hian urinary leh reproductive system lama tui doctor (`Urologist`) leh hormone lama tui doctor (`Endocrinologist`) te an tel tlangpui.
He surgery hi naupang dam kum khatna chhunga tih thin a ni tlangpui . Surgery tih chi chu a dinhmun chu `low-joined` emaw `high-joined` emaw a nih danah a innghat a, chu chu a hmain kan sawi tawh a ni.
- Low-joined status atan chuan:Surgical procedure `flap vaginoplasty` an tih hi an ti fo thin. Hetiang tihnaah hian surgeon chuan common opening thenkhat hmangin vagina leh urethra tan opening hrang hrang pahnih a siam thin.
- Joined sang tak nei tan chuan: Surgery buaithlak zawk, `pull-through vaginoplasty` ang chi hi a ngai a ni. Hetah hian vagina chu common passage a\angin a in\hen a, a tan hawnna hran siam a ni.
Naupang thenkhat chu an clitoris emaw labia emaw pianzia chu a pangngaia awm leh turin operation an neih a ngai thei bawk a, chu chu `clitoroplasty` emaw `labiaplasty` emaw a ni thei bawk.
Hei hian ka fa hmalam hun a nghawng dawn em ni?
Hei hi nu leh pa tin tan zawhna lian tak a ni. Surgery tum ber chu naupang taksa hnathawh dan pangngai a tih theih nan leh serh pengte hmel pangngaia siam leh a ni.
- Zun: Operation hnuah naupang tam zawk chu harsatna awm lovin an zun pangngaiin an zun thei .
- Menstrual cycle: Hei hian naupang a lo puitlin hnua thlasik hun pangngai a nghawng dawn lo.
- Sex life: A châng chuan naute a lo seilian deuh deuh chuan a vagina chu a zim deuh emaw, a tawi deuh emaw a ni thei (vaginal stenosis). Hei hian nakin lawkah mipat hmeichhiatna hman laiin harsatna engemaw zat a thlen thei a ni. Hemi chungchang hi i doctor nen inbiain a tul anga enkawlna i zawng thei bawk.
- Naupai: Hetiang dinhmun a neih hian nakin lawkah nau a pai thei dawn lo tihna a ni lo. Mahse, surgery hi a buaithlak em em a nih chuan doctor-te chuan naute pian hunah cesarean section (C-section) neih a rawt thei a ni.
Heng thilte hi i fa dinhmun azirin a danglam thei a, chuvangin i doctor nen zalen taka sawiho a tha ber.
Doctor hnena zawhna zawh tur
I zawhna leh hlauh zawng zawng doctor hnenah zawt rawh. Entirnan, hetiang zawhna hi i zawt thei ang:
- Ka fa hian eng ang Urogenital Sinus nge a neih?
- Eng ang surgery nge i rawt? Kum engzat nge tih tir chu a tha ber?
- Tunah hian ka fa hi a na em?
- Naupang a lo puitlin chuan operation tam zawk neih a ngai dawn em?
- Hei hian naupang thlasik hun chhung a nghawng dawn em?
- Hei hian nakin lawkah fa enkawl danah nghawng a nei dawn em?
Take-Home Thuchah a ni
- Urogenital sinus hi hmeichhe naupangte piansualna hmuh tur awm lo tak a ni a, chutah chuan urethra leh vagina chu common opening pakhatah an inzawm a ni.
- He natna hi naute pian hnu lawka doctor-in a enfiahnaah hmuhchhuah a ni fo thin.
- Hei hi enkawlna awm chhun chu surgery hmanga kawng pahnih hi then hran hi a ni. Hei hi nu leh pa leh medical team te thawhhona pawimawh tak a ni.
- Surgery mumal tak an neih hnuah naupang tam zawk chuan nun pangngai an nei thei a ni. An zun dan pangngaiin an zun thei a ni.
- I fa doctor nen rinhlelhna emaw, hlauhna emaw i neih apiang chu zalen takin sawipui rawh. Anni chuan kaihhruaina tha ber ber an pe ang che.











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