Kan taksa chhunga thisen awm hi tui ang ni lovin, liquid, viscosity engemaw chen nei a ni tih kan hre vek. Mahse, han ngaihtuah teh, he thisen hi a pangngai aia nasa zawk, leilung thim tak ang maia a lo thim chuan eng nge thleng ang? He thisen thuk tak hi kan taksa pum puia thisen kalna kawng tha tak takte kal tlanga kal a harsa ta hle a ni. Pipe chhunga leilung thim tak a tlakbuak ang mai a ni. Chutiang chuan thisen chu coconut milk ang maiin a thim a, taksaa thisen kal dan a tichhe a, chu chu damdawi lamah Hyperviscosity Syndrome kan tih chu a ni. Hei hi thil tenawm tak mai a ni lo va, a chang chuan hlauhawm tak, nunna atana hlauhawm tak a ni. Hemi chungchang hi awlsam takin, i hriatthiam theih dan tur angin sawi ila.
Engvangin nge thisen chu a thim thut mai?
Hriatthiam hmasak tur chu Hyperviscosity Syndrome hi a takin natna a ni lo. A hnuaia awm dinhmun dang chhinchhiahna a ni. Khuh hi khawsik emaw pneumonia emaw chhinchhiahna a nih ang bawkin. Thisen thickening hi thisen chhunga cell chi hrang hrang emaw protein chi hrang hrang tam lutuk vang a ni ber.
A awlsam zawngin, thisenah hian thisenah thisen sen (red blood cells), thisen var, platelet, a nih loh leh serum proteins awm zat chu a pangngai lo taka a pun chuan thisen chu a thim a ni.
A hnuaia table-ah hian he natna thlen thei damdawi lam thil pawimawh thenkhat tarlan a ni.
| Thisen zam thei dinhmun | A sawifiahna awlsam tak |
|---|---|
| Waldenström-a natna hrik (Macroglobulinemia) (WB) a ni. | Hei hi hyperviscosity thlentu ber a ni. Hei hi thisen cancer chi khat a ni a, ruhro leh lymphatic tissue-ah a awm a ni. Protein pangngai lo a siam chhuah tam lutuk vang a ni a, chu chuan thisen a ti thim a ni. |
| Multiple Myeloma natna a awm | Hei hi cancer chi khat a ni bawk a, plasma cells a nghawng a ni. Cancer cell-te siam protein pangngai lo tak takte hian thisen chu a ti thim a ni. |
| A rilru a hah lutuk chuan a rilru a buai em em a. Rubra Vera | Hei hi ruhro natna a ni. Hetiang dinhmunah hian thisen sen (red blood cells) chu thunun theih lohvin a siam chhuak thin. Thisen sen (red blood cells) a pun zel chuan thisen viscosity pawh nasa takin a pung bawk. |
| Leukemia natna (Leukemia) a ni | Thisen cancer, leukemia-ah chuan thisen var (white blood cells) a tam lutuk a. Heng cell te hi a pianphung pangngai lo tak tak an ni thei. Hei hian thisen kalna kawng a tikhawlo thei a, thisen a ti thim thei bawk. |
| Connective tissue lama harsatna awm thei | Thisen zam hi a chang chuan natna chi hrang hrang, rheumatoid arthritis-ah a awm thei a, mahse hei hi a tlem hle. |
| A chhan dang hmuh tur awm lo | A chhan dang pawh a awm thei a, chu chu cryoglobulinaemia (thisen kalna kawng tichhe thei natna), chronic hypoxia (oxygen tlakchhamna rei tak), leh cancer enkawlna thenkhat (Retinoic acid therapy) te hi a ni. |
I thisen a thim chuan engtin nge i awm? Eng nge a lan chhuah dan?
Ngaihtuah teh, kan taksa peng tinreng, thluak atanga kan kut zungtang hrual thlengin thisenin a phur a, oxygen leh nutrients a keng tel vek a ni. Chuvangin he thisen kal dan hi tihkhawtlai a nih chuan chu taksa peng hrang hrangte chuan an mamawh chu an hmu lo. Chuvang chuan symptoms a lo lang thin. Heng symptoms te hi mi hrang hrangah a inang lo thei a, thisen tizautu natna bulpui a zirin a danglam thei bawk.
Hengte hi a lan chhuah dan tlangpui thenkhat chu an ni:
Thluak leh nervous system tichhe thei symptoms
Thluak hi thisen kal that loh vangin a nghawng nasa ber thei.
- Lu na na tak leh luak chhuak
- Mit lama harsatna: mit a fiah lo, mit pahnih, a chang chuan mit a hloh nghal
- Hriatna lama harsatna: hriatna tlahniam emaw, hriatna hloh emaw
- Convulsions a awm thin
- Chauhna nasa tak leh mut theih lohna (Lethargy) .
Thisen chhuahna nena inzawm symptoms
Thisen a thim chuan thisen kal dan control nalh tak chu a tibuai a, chu chuan beisei loh takin thisen a chhuah thei a ni.
- Bruising awlsam tak
- Mucosal bleeding (hnar thisen, hmui) .
- Thisen chhuahna dang danglam tak (e.g., bawlhhlawh chhunga thisen) .
Symptom na tak dang a awm bawk
Chungte chuan taksa peng lian ber berte a chhiat phah tih a tilang a ni.
- Thisen sang (Hypertension) 1.1.
- Heart failure: rilru na, thawk hah
- Kidney tha lo a awm
- Thisen zam (Thrombosis) .
- Hri kai na tak (Sepsis) .
Nangmah emaw, i hriat miin emaw heng symptoms pakhat emaw a aia tam emaw an neih chuan tihkhawtlai lova doctor pan nghal a pawimawh hle.
He dinhmun hlauhawm tak hi engtin nge kan enkawl ang?
Hyperviscosity Syndrome hi medical emergency a ni a, a chhan chu enkawl loh chuan taksa peng pawimawh tak tak, thluak, thinlung leh kal te chu oxygen riltam takin a riltam thei a, chu chuan a tichhe vek thei a, a tichhe thei hial a ni. Chuvangin, rang taka enkawl hi a pawimawh hle.
Treatment plan hi level hnih a awm tlangpui.
1. Inenkawl nghal, hun rei lote chhunga enkawl
A hmasa ber chu a symptoms control a, rang taka thisen viscosity tihhniam hi a ni. Hei hi enkawlna atana hman tlanglawn ber pakhat chu Plasmapheresis a ni .
Plasmapheresis hi thisen tihthianghlimna ang chiah a ni. I thisen tlemte chu i taksa atangin lakchhuah a ni a, machine bik kaltlangin, plasma, i thisen zam tirtu proteins tam tak awmna chu a inthen a, lakchhuah a ni. Chumi hnuah chuan thisen sen leh var hrisel tak takte chu a thlakna tur tui nen an pawlh a, i taksaah an rawn kir leh thin.
Hei hian thisen zam a tihziaawm thuai thei a, taksa peng hrang hrang chhiatna a titawp thei bawk. Mahse, he enkawlna hi mi zawng zawng tan a tha em tih leh a tul em tih chu i medical team-te kutah a awm a ni.
2. Hun rei tak enkawl (natna hnuaia awm enkawlna) .
Thisen viscosity tihhniam hnuah a dawt leh pawimawh ber chu a thlentu natna bulpui enkawl hi a ni. A chhan chu chu natna chu enkawl a nih loh chuan thisen chu a thim leh thei a ni.
- A chhan chu cancer Multiple Myeloma emaw Leukemia emaw a nih chuan cancer dona damdawi, chemotherapy ang chi te pek thin a ni.
- A chhan chu polycythaemia a nih chuan thisen sen tam zawk paih chhuah emaw, an siam chhuah tihtlem emaw nan enkawlna pek thin a ni.
- Damdawi lam thil dang a nih chuan doctor-te chuan a enkawlna tur bik an rawt ang.
Chumi atan chuan doctor team, hematologist, oncologist, leh nephrologist te chu an rawn inkhawm ang a, i tan enkawlna tur ruahmanna tha ber an siam ang.
Take-Home Thuchah a ni
- Hyperviscosity Syndrome hi thisen chu coconut oil ang maia a thim a, taksaa thisen kal dan a tikhawlo a ni.
- Hei hi natna hran a ni lo. Natna khirh tak dang, thisen cancer ang chi chhinchhiahna a ni .
- Lu na nasa tak, mit hmuh dan danglam, thisen chhuak danglam tak, hah lutuk ang chi symptoms te chu ngaihthah suh.
- Hei hi medical emergency a ni a . Symptoms i hriat veleh doctor rawn rawh. A tul chuan damdawi in pakhata Emergency Treatment Unit (ETU) pan nghal tur a ni.
- Enkawlnaah hian thisen tihthianghlim nghal (plasmapheresis ang chi) leh natna hnuaia awm enkawlna te pawh a tel a ni.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh