I naute pum vun a hrual em? Prune Belly Syndrome chungchang hi han sawi ila

I naute piang thar pum chu i en a, a vun chu a hrual nasa hle tih i hmu ngai em, thei hring ang maiin? Nge a chak lo hle a, tisa nei lovin a inhria em? Hetiang thil i hmuh hian nu anga i hlauhthawn hi thil pangngai tak a ni. Mahse hei hi nau piangsualna awm lo tak, mahse na tak, Prune Belly Syndrome an tih chhinchhiahna a ni thei. Vawiin hian he thu hi i hriatthiam theih tur awlsam takin kan sawi dawn a ni.

Prune Belly Syndrome hi eng nge ni?

A awlsam zawngin sawi ila, Prune Belly Syndrome hi pian tirh atanga lo awm thin a ni. Eagle-Barrett syndrome an ti bawk. "Prune" tih hi grape hring emaw plum emaw ang maia lang thei a ni. A hming hi heng naupangte hian an pum chhungah a hring (wrinkled appearance) an neih vang a ni.

He natna hian symptom lian pathum a nei a, chuvang chuan "triad syndrome" tia sawi a ni bawk.

1. Pum ruh awm loh emaw, chak lo lutuk emaw: Hei hi pawn lam chhinchhiahna ber a ni. Abdominal muscles te hi a lo thang tha lo a, chu chuan pum chhunga vun chu a saggy leh wrinkled angin a lang thin.

2. Undescended testicles: He natna hian mipa naupang a nghawng ber. An testicles chu scrotum chhungah a chhuk ai chuan, pum chhungah a awm reng a ni.

3. An abnormally large bladder leh urinary system lama harsatna: Hei hi he natna harsatna lian ber a ni. Bladder chu a lian hle a, zun kawngah harsatna lian tak a thlen thin.

Heng urinary system lama harsatna te hian naupang chu a bladder, kidney leh kidney atanga bladder (ureters) thlenga zun phurtu tube te chu a ti hring vek thei lo.

Prune Belly Syndrome hian piansualna dang a thlen thei bawk. Chung zingah chuan lung, thinlung, intestines, leh skeletal system-a chhiatna awmte pawh a tel. He natna hian hmeichhe naupang a nghawng tlem hle nachungin, 95% chu mipaah ​​an awm tih hmuhchhuah a ni.

Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?

Dik tak chuan doctor-te chuan Prune Belly Syndrome hi a chhan chiang tak an la hmu lo a, mahse a chhan ni thei tur theory engemaw zat a awm.

• Ngaihdan hmasa ber:Naute chu pum chhunga a lo seilian chhoh zel chuan bladder emaw urethra emaw-ah blockage a awm nia ngaih a ni. Hei hian zun taksa atanga a chhuah loh nan a veng a, chu chuan bladder, ureters leh kidney te a ti lian a ni. Bladder a lian lutuk chuan pressure a siam chuan pum ruh te chu a thang lian thei lo va, testicles te pawh a tlahniam thei lo bawk.
• Ngaihdan pahnihna: Pum ruhte a lo thang tha lo a, naupang tan zun a harsa thin. Hei hian zun kawng a ti na a, infection leh harsatna a thlen thin.
• Ngaihdan pathumna: He taksa chak lohna leh zun kawng lama harsatna te hian thil inang an nei mai thei a, a chhan pawh kan la hriat loh (entir nan, nervous system-a chhiatna) a awm thei bawk.

Chhungkaw khata unau zingah he natna hi a thleng tih report eng emaw zat a awm tawh avangin, hei hi genetic link a awm em tih hriat tumin zirchianna neih mek a ni bawk.

Hetiang natna lan chhuah dan hi engte nge ni?

Prune Belly Syndrome vei naupang hrang hrangah natna lan chhuah dan leh a nasat dan a inang lo thei. Mahse, a lan chhuah dan tlangpui thenkhat a awm. A hnuaia table hi en rawh.

Chu bâkah, naupang ṭhenkhat chuan clubfoot, ke chu chhung lam hawia piang, leh spina bifida , piansualna, ruhro nerve-te ṭha taka ṭhan lohna an nei thei bawk.

Engtin nge he dinhmun hi kan hriat theih ang?

A tam zawkah chuan doctor-te chuan i naupai laiin ultrasound scan hmangin he natna hi an hmu thei a ni. A nih loh chuan naute pian hnua medical check-up hmasa berah heng symptoms te hi chiang takin a lang ang.

I doctor chuan test eng emaw zat a nei thei a, chu chuan i natna a hriat chian theih nan leh i natna a nasat dan dik tak a hriat theih nan a hmang thei a ni.

• Ultrasound Scan: Hei hian kal leh zun kawng peng dangte dinhmun a hriat theih nan a pui a ni.
• X-ray test: X-ray chi hnih a awm a, taksaa dye bik hmanga inject tur a ni. Pakhat chu intravenous pyelogram (IVP) a ni a, pakhat chu voiding cystourethrogram (VCUG) a ni. Hengte hian urinary system-a blockage leh harsatna awmte chu chiang takin a lantir thei a ni.
• Thisen test: Heng test te hian i fa kal (kidney) a thawk tha em tih hriat nan a pui thin.

Enkawlnate chu engte nge ni?

Prune Belly Syndrome natna lan chhuah dan leh a nasat dan a inang lo avangin enkawlna kawng hrang hrang a awm a. Doctor chuan naupang dinhmun a zirin enkawl dan tur dik ber a ruat ang. Vawi tam tak chu operation tam tak neih a ngai thin.

Naupang hmalam hun chu eng ang nge ni ang? (Prognosis) tih a ni.

He zawhna hi chhanna pakhat chauh pek a har a, a chhan chu naupang hmalam hun chu natna nasat dan te, naupang kum leh an hriselna zawng zawngah a innghat a ni.

Mahse, enkawl a nih pawhin naupang ṭhenkhat chuan kal (kidney failure) an nei thei a ni . Kidney failure chu kal hian a hnathawh 85-90% vel a hloh a, chu chu a thawk tha thei tawh lo tihna a ni. Tichuan, bawlhhlawh leh tui tam zawk taksaah a pungkhawm a, naupang chu a na hle. A lan chhuah dan chu hah, chaw ei chak lohna, ke na leh ke hring te a ni.

Kidney a chhiat chuan enkawlna chu dialysis emaw kidney transplant emaw a ni .

A tawp berah chuan, i naute hian heng natna lan chhuah dan hi a lantir tih rinhlelhna tlemte pawh i neih chuan doctor pan nghal rawh . A hmaa hriatchhuah leh enkawlna dik tak tan chuan i naute tan result tha zawk a thlen thei a ni.