He toto toto tiketike tōu, he toto toto tiketike rānei? Tērā pea e rua, e toru rānei ngā rongoā e tangohia ana e koe i tohua e tō tākuta. Engari he uaua tonu te whakahaere i tō toto toto? Kei te ngenge hoki koe, kei te ngoikore, ā, he maha ngā wā ka maroke te wai? Mēnā koinā, ko te take pea o tō mate he mea kē atu i te toto toto noa. I tēnei rā ka kōrero tātou mō tēnei mate. Ko te Aldosteronism Tuatahi, ko te Conn's Syndrome rānei.
He aha te Aldosteronism Tuatahi?
He mea tēnei e hiahia ana kia whakamāramahia. I roto i tō tātou tinana, e rua ngā repe iti kei runga ake i ngā whatukuhu. Ka kiia ēnei e tātou ko ngā repe adrenal, i te reo Pākehā rānei, ko ngā repe adrenal . Ka whakaputahia e ēnei repe ētahi momo homoni e tika ana mō tō tātou tinana.
He homoni steroid te Aldosterone e hangaia ana e ēnei repe. Ko te mahi matua o tēnei homoni he whakahaere i ngā taumata o te konutai (tote) me te pāhare pāporo i roto i ō tātou toto. Mā tēnei, ka āwhina hoki tēnei homoni ki te whakahaere i te taurite wai o tō tātou tinana me te toto toto.
Nō reira, ko te Aldosteronism Tuatahi ko te wā e nui rawa ai te homoni aldosterone e whakaputaina ana e ō repe adrenal mō tētahi take. Ina piki ake ngā taumata aldosterone, ka piki ake te nui o te konutai (tote) i roto i tō tinana, ā, ka heke te nui o te pāhare pāporo. Ka hua ake tēnei i te toto toto tiketike e kore e taea te whakahaere me ngā taumata pāhare pāporo iti i roto i te toto (hypokalemia).
I mua i whakaarohia tēnei he mate tino onge, engari kua kitea ināianei kei waenganui i te 5% me te 10% o ngā pakeke he toto toto tiketike ka pāngia pea e tēnei mate.
He aha ngā tohu matua o tēnei mate?
Ehara i te mea ka pāngia te katoa e tēnei mate e ngā tohumate ōrite. Engari koinei ngā tohumate e tino kitea ana. Me titiro tātou ki ēnei i roto i tētahi ripanga.
| Tohu | He whakamārama māmā |
|---|---|
| Te toto toto tiketike (hypertension) | Koinei te tohu matua, inā koa te toto toto tiketike e uaua ana ki te whakahaere ahakoa he maha ngā rongoā e tangohia ana. |
| Te iti o te pāhare pāporo i roto i te toto (Hypokalemia) | Tērā pea ka kitea he iti ngā taumata pāhare pāporo i roto i te whakamātautau toto. Ka taea e tēnei te whakakorikori i ngā uaua me te ngoikore o te tinana. |
| Ngenge auau | Te ngenge me te kore ora i ngā wā katoa, kāore he take. |
| Ānini | Ngā mamae o te upoko i ngā wā katoa. |
| Te matewai nui me te mimi pinepine | Nui atu te matewai i tō te tikanga, ā, me mimi pinepine atu. |
| Te ngoikore o te uaua me te māuiui o ngā uaua | Te āhua nei kei te hurihuri ngā uaua o ngā waewae me ngā ringa, inā koa nā te iti o te pāhare pāporo. |
| Te tirohanga pōuri | I ētahi wā ka pōuriuri te tirohanga. |
He aha i pēnei ai te pikinga o te homoni aldosterone?
Tērā pea he maha ngā take mō tēnei.
- Ngā pukupuku pai o ngā repe adrenal: Koinei te take o tēnei āhuatanga i roto i te nuinga o te tangata. Ka puta he pukupuku iti, ehara i te matepukupuku (adenoma) i roto i tētahi, i ngā repe adrenal e rua rānei, e whakaputa nui rawa ana i te homoni aldosterone.
- Te hyperplasia adrenal rua-taha: I ētahi wā, ki te kore he pukupuku, ka kaha rawa te mahi a ngā pūtau i roto i ngā repe adrenal e rua, ā, ka nui rawa te homoni e whakaputaina ana.
- Ngā take tuku iho: Ka taea te tuku iho i tēnei āhuatanga i roto i ētahi whānau. Hei tauira ko te `(Congenital Adrenal Hyperplasia)`.
- Matepukupuku repeure: He tino onge tēnei take.
Te rerekētanga i waenga i te Aldosteronism Tuatahi me te Tuarua
Tērā tētahi atu mea nui me mōhio koe. Ko te Aldosteronism Tuatahi, i kōrerohia e tātou, he raruraru e puta ana i roto i te repe adrenal tonu, e hua ai te pikinga o te homoni.
Engari i ētahi wā, ka piki ake ngā taumata aldosterone nā ētahi atu āhuatanga hauora o te tinana. Hei tauira, ka piki ake anō hoki tēnei homoni i roto i ngā āhuatanga pēnei i te ngoikore o te ngākau, te mate ate, te stenosis rānei o te uaua whatukuhu. Ka kiia tēnei ko te Aldosteronism Tuarua . Ka wehewehe tika te tākuta i waenga i ēnei āhuatanga e rua.
Me pēhea te mōhio ki tēnei?
Mena kei a koe ngā tohu kua whakahuatia ake nei, ka tirohia tuatahitia e tō tākuta tō toto toto. Kātahi, ki te mea he ruarua mō tēnei mate, ka tukuna koe e ia ki ētahi whakamātautau toto motuhake.
- Ngā taumata homoni toto: Ko te nuinga o tēnei ka ine i ngā taumata o ngā homoni aldosterone me te renin. I roto i te aldosteronism tuatahi, he teitei ngā taumata aldosterone, he iti ngā taumata renin.
- Whakamātautau Taumata Irahiko: Ka whakamātauhia e tēnei te taumata o te konutai me te pāhare pāporo i roto i tō toto.
He mea nui: Mena kei te tango koe i ngā rongoā mō te toto toto tiketike, ka pā pea ētahi o aua rongoā ki ngā hua o ēnei whakamātautau toto. Nō reira, kia tika ai te tautuhi i te mate, ka tohutohu pea tō tākuta kia huri, kia mutu rānei tō rongoā mō tētahi wā.
Mena ka whakaūtia tēnei āhuatanga e ngā whakamātautau toto, ko te mahi e whai ake nei ko te tirotiro i ngā repe adrenal kia kitea ai te pūtake. Ko te tikanga ka mahia tēnei mā te matawai CT (Computed Tomography) te matawai MRI rānei (Magnetic Resonance Imaging) .
He aha ngā maimoatanga mō tēnei?
Ko te rongoā mō tēnei mate ka whakawhirinaki ki te pūtake. E rua ngā tikanga rongoā matua.
1. Te rongoā
Mena he nui rawa te mahi a ngā repe adrenal e rua (hyperplasia), kāore e mahia he pokanga. Engari, ka hoatu he rongoā hei aukati i te mahi a te homoni aldosterone. Ko ngā rongoā e whakamahia whānuitia ana ko te spironolactone me te eplerenone . Ka taea e ēnei rongoā te whakahaere i te toto toto me te whakahoki mai i ngā taumata pāhare pāporo.
2. Te maimoatanga mā te pokanga
Mena ka whakaūtia e te matawai CT, MRI rānei he pukupuku (adenoma) kei roto i te repe adrenal kotahi anake, ko te maimoatanga pai ko te tango i taua repe mā te pokanga. Ka kiia tēnei pokanga he adrenalectomy . He tikanga tēnei hei pokanga kī (pokanga laparoscopic) kia tere ake ai te ora.
I muri i te pokanga, ka hoki te toto toto o te nuinga o te tangata ki te noho noa, ka taea rānei te whakahaere mā te iti noa o te rongoā.
Ka aha mēnā ka kore e rongoatia?
Ki te kore tēnei āhuatanga e rongoatia, ka puta pea ngā raruraru nui nā te toto toto tiketike me te kore taurite o ngā electrolytes mō te wā roa.
- Te whakaeke ngakau, te ngoikore rānei o te ngakau
- Whiu
- Te ngoikore o te whatukuhu
- Te pā o te manawa kāore i te tika (Arrhythmia)
- Pararutiki rangitahi
Nō reira, ki te puta ngā tohu, he mea nui kia tere tonu te toro atu ki te tākuta me te rapu maimoatanga.
Karere Tangohia ki te Kāinga
- Ko te aldosteronism tuatahi he āhuatanga e hua mai ana i te nui rawa o te hanga o te homoni aldosterone e ngā repe adrenal.
- Ko ngā tohu matua ko te toto toto tiketike me te iti o te pāhare pāporo i roto i te toto, he uaua ki te whakahaere ahakoa te whakamahi i ētahi rongoā.
- Tērā pea ka puta ngā tohu pēnei i te ngenge pinepine, te ānini, te matewai nui, me te wiri o ngā uaua.
- Ka taea e ngā whakamātautau toto me ngā karapa te tautuhi tika i tēnei mate me tōna pūtake.
- I runga i te pūtake, ka taea te whakahaere angitu i tēnei āhuatanga mā te rongoā, te pokanga rānei.
- Mena kei a koe ēnei tohu, inā koa he uaua ki a koe te whakahaere i tō toto toto, me kōrero koe ki tō tākuta mō tēnei mea.











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