Kei te ngoikore haere ō uaua? Tērā pea ko te Primary Lateral Sclerosis (PLS) tēnei?

Kei te ahua taumaha ō waewae i ētahi wā, me te mea he kōhatu? Kei te ahua rānei kei te ngaro tō taurite i a koe e hikoi ana, kei te memeha haere rānei te kaha o ō peka? Ki te kore ēnei tohu e puta ohorere mai, engari ka piki haere, ka piki haere, he mea nui pea kia mōhio koe ki tēnei āhuatanga e kiia nei ko te Primary Lateral Sclerosis (PLS). Kaua e manukanuka, ka kōrerohia e tātou ngā mea katoa i roto i ngā kupu māmā noa iho.

He aha te tikanga o te primary lateral sclerosis (PLS)?

Ko te Primary Lateral Sclerosis, arā, ko te PLS , he mate e pā ana ki ō tātou io me ō tātou uaua. Ka ngoikore haere, ka mārō haere rānei ō tātou uaua.

He maha ngā wā ka tīmata ēnei tohu i ō waewae. I roto i te wā, ka horapa pea tēnei ngoikore me te pakari ki ētahi atu uaua o tō tinana. He mate ahu whakamua tēnei, arā, ka kino haere ngā tohu i roto i te wā.

Kāore he rongoā motuhake mō tēnei mate (PLS), nō reira ko te whāinga matua o te maimoatanga ko te whakahaere i ngā tohu me te āwhina i a koe ki te mahi i ngā mahi o ia rā kia māmā ake. Hei tauira, mā te whakamahi i tētahi taputapu āwhina pērā i te tokotoko, i te taputapu hikoi rānei.

He tino onge tēnei mate, arā, kāore e kitea whānuitia ana i roto i te hapori.

He aha te rerekētanga i waenga i te PLS me te ALS?

Kua rongo pea koe i tētahi mate e kiia nei ko te Amyotrophic Lateral Sclerosis (ALS) . Ahakoa e pā ana ēnei mate ki ngā io me ngā uaua, he mārama ngā rerekētanga i waenganui i ngā mea e rua. Hei mārama ki tēnei, me titiro tuatahi tātou ki te whakahaere a ō tātou tinana i te nekehanga.

He momo pūtau io motuhake tēnei e kawe ana i ngā karere mai i tō tātou roro ki ō tātou uaua, e kiia ana ēnei he neuron motuka . E rua ngā momo o ēnei:

1. Ngā Neuron Motika o Runga (UMN): Koinei ngā 'waea matua' e kawe ana i ngā karere mai i te roro ki te taurakira.

2. Ngā Neuron Pūkaha o Raro (LMN): Koinei ngā 'neuron iti' e kawe ana i ngā karere tika mai i te taurakira ki ngā uaua.

He mea tino nui inaianei kia mārama ki tēnei rerekētanga.

He tino ōrite ngā tohu tōmua o te ALS ki ērā o te PLS. Nō reira, i ētahi wā ka tātaritatia koe e te tākuta ki te PLS, kātahi ka huri ki te ALS ina puta ngā tohu e pā ana ki te LMN. Mō tēnei take, hei whakaū i te PLS, me tirotiro ngā tohu mō te toru ki te whā tau pea te roa.

He aha ngā tohu o te PLS?

Ka tino pōturi te puta mai o ngā tohu o te PLS. Anei ētahi o ngā tohu tuatahi ka kitea pea e koe:

• Te pakari o ngā uaua o ngā waewae.
• Te ngoikore o ngā uaua o ngā waewae.
• He uaua ki te hikoi , he uaua rānei ki te pupuri i te taurite.
• Te wiri o te uaua, te mamae rānei o ngā uaua, ngā kōroke rānei.

I te whanaketanga o te mate, ka puta pea ētahi atu tohu:

• Te pakari me te ngoikore o ngā uaua o ngā maihao, ngā ringa, me ngā ringaringa.
• Te uaua ki te whakahaere i te mimi(Te hiahia nui ki te mimi me te turuturu o te mimi).
• Te mamae o te tuara me te kaki.

I ētahi wā tino onge, ka pāngia hoki ngā uaua o te arero. I tēnei wā, ka kitea pea e koe ngā tohu pēnei i:

• Te kōrero pōturi (Dysarthria).
• Te uaua ki te horomi kai (Dysphagia).

He aha ngā take o te PLS?

Ina hoki, kāore anō kia mōhiotia te tino take o te PLS i roto i ngā pakeke. I te nuinga o te wā, ka puta noa mai, kāore he take e kitea ana.

Heoi anō, he momo PLS tino onge e pā ana ki ngā tamariki me ngā taiohi. Ka puta mai i te whakarerekētanga ira (te panoni o te DNA).

Ko te mea nui , ehara te PLS i te mate tuku iho. Ko te tikanga ka taea e koe te pāngia e tēnei mate ahakoa kāore anō kia pāngia e tētahi o tō whānau.

Ko wai te mea tino mōrearea?

Ka taea e te tangata katoa te pāngia e te PLS. Heoi, ko te tikanga ka kitea te mate i te hunga e 50 tau te pakeke. Heoi, ka taea hoki te pāngia e te hunga taitamariki, pakeke ake rānei. He nui ake te kitea o tēnei mate i roto i ngā tāne i ngā wāhine .

Me pēhea te tautuhi i tēnei mate?

I muri i te mōhio ki ō tohumate, ka whakahaerehia e tō tākuta he whakamātautau tinana me te whakamātautau io. Tērā pea ka whakahaerehia hoki e rātou he whakamātautau hei whakakore i ētahi atu mate e rite ana ngā tohumate ki te PLS, pērā i te ALS, te multiple sclerosis rānei. Ko ētahi o ēnei whakamātautau ko:

• Ngā whakamātautau toto: Tirohia mēnā he take kē atu.
• Ngā whakamātautau tātaritanga hiko: Ka ine tēnei i te pai o te mahi a ō io me ō uaua.
• Matawai MRI: Tangohia he whakaahua taipitopito o te roro me te taurakira hei tirotiro mēnā he raruraru kē atu.
• Wero i te tuaiwi (te pokanga tuaiwi): Ko te tikanga tēnei he tango i tētahi wai iti mai i tō tuaiwi, ka tirotirohia mēnā he rerekē.

He aha ngā maimoatanga?

E ai ki tā mātou i kōrero ai i mua, kāore he rongoā motuhake mō te PLS. Ko te whāinga o te maimoatanga he whakahaere i ngā tohu me te āwhina i a koe kia noho motuhake.

• Ngā Rongoā: Ka hoatu ngā rongoā hei whakaiti i te pakari o te uaua, te kopa, me te uaua ki te horomi (hei tauira, Baclofen, Tizanidine, Quinine, Diazepam).
• Whakaora tinana: E taunakihia ana te whakakori tinana hei whakaiti i te ngoikore o te uaua, hei whakanui ake i te ngāwari, me te pupuri i te nekenekehanga pai o ngā hononga.
• Ngā taputapu āwhina: Ka whakamahia ngā taputapu pēnei i te tokotoko, te kaiārahi hikoi , te tūru wīra rānei hei āwhina i a koe ki te neke takitahi.
• Whakaora kōrero: Mena he uaua ki a koe te kōrero, ka taea e ia te āwhina.

Āhea koe me toro atu ki te tākuta?

Ki te mea kei te piki haere te pakari, te ngoikore rānei o ō uaua, me toro atu ki tō tākuta.

Waihoki, ki te mea kua tākutatia kētia koe kei te pāngia koe e te PLS, ā, kei te kino haere ngā tohumate, kei te pāngia rānei koe e ngā pānga taha o te rongoā e tangohia ana e koe, me kōrero anō hoki ki tō tākuta.

Ki te whara koe i te hinganga ohorere, i te aituā rānei, haere tonu ki te Wāhanga Maimoatanga Ohotata (ETU) o te hōhipera.

He mea noa te pouri i te mea ka heke haere te kaha o ō uaua, ā, kāore e taea e koe te mahi i ngā mea i mahia e koe i mua. Mena kei te pāngia koe e te ahotea mō ēnei huringa tinana, he pai te kōrero ki tētahi kaitohutohu hauora hinengaro .