ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯣꯡ ꯑꯗꯨ ꯁꯣꯟꯊꯕꯥ, ꯆꯦꯌꯥꯔꯗꯒꯤ ꯊꯣꯔꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯃꯥꯌꯣꯛꯅꯔꯤ, ꯈꯣꯡꯗꯥ ꯆꯦꯅꯁꯤꯜꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯑꯣꯕ꯭ꯔꯥ? ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯃꯤꯠ ꯇꯥꯡꯕꯥ, ꯃꯤꯠ ꯁꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯗꯕꯜ ꯚꯤꯖꯟꯒꯨꯝꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯋꯥꯈꯜ ꯇꯥꯗꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ? ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯁꯨꯞꯅꯒꯤ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯈꯛꯇꯃꯛ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯑꯗꯣꯝꯅꯥ ꯇꯥꯕꯤꯔꯝꯂꯔꯣꯏꯗꯕꯥ, ꯑꯗꯨꯕꯨ ꯌꯥꯝꯅꯥ ꯈꯉꯅꯔꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯒꯅꯤ, ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯣꯟ ꯃꯥꯏꯌꯥꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ, ꯅꯠꯔꯒꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯊꯣꯏꯗꯣꯛꯅꯥ ꯀꯧꯔꯤꯕꯥ ``(LEMS)``꯫
ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯟ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ (LEMS) ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯟ ꯃꯥꯏꯌꯥꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ (LEMS) ꯑꯁꯤ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯗꯤꯁꯑꯣꯔꯗꯔ ꯑꯃꯅꯤ꯫ ꯍꯧꯖꯤꯛꯇꯤ ꯑꯗꯣꯝꯅꯥ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯗꯤꯁꯑꯣꯔꯗꯔ ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ ꯍꯥꯌꯅꯥ ꯈꯅꯕꯤꯔꯃꯒꯅꯤ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯃꯥ ꯂꯩ꯫ ꯃꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯕꯨ ꯃꯄꯥꯟꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯂꯥꯌꯅꯥ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯔꯃꯁꯤꯡ ꯊꯦꯡꯅꯗꯨꯅꯥ ꯉꯥꯀꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯂꯩꯕꯥꯛ ꯑꯁꯤꯗꯥ ꯂꯩꯔꯤꯕꯥ ꯑꯥꯔꯃꯤꯒꯨꯝꯕꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯁꯤ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯃꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯏꯁꯥꯒꯤ ꯍꯀꯆꯥꯡ ꯐꯕꯥ ꯁꯦꯂꯁꯤꯡꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯕꯥ ꯍꯧꯏ꯫ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯇꯥ ꯊꯣꯛꯂꯤꯕꯥ ꯑꯁꯤꯃꯀꯅꯤ꯫
ꯃꯁꯤꯒꯤ `(LEMS)` ꯑꯁꯤꯗꯥ, ꯑꯩꯈꯣꯌꯒꯤ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯃꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯃꯣꯇꯣꯔ ꯅꯔꯚꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯀꯅꯦꯛꯁꯟ ꯑꯗꯨꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯏ . ꯆꯨꯝꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯀꯅꯦꯛꯁꯟ ꯑꯁꯤꯕꯨ `ꯅ꯭ꯌꯨꯔꯣꯃꯁꯀꯨꯂꯥꯔ ꯖꯉ꯭ꯀꯁꯟ` ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯖꯉ꯭ꯀꯁꯟ ꯑꯁꯤꯅꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯅꯔꯚꯁꯤꯡꯗꯒꯤ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯄꯥꯎꯖꯦꯂꯁꯤꯡ ꯇ꯭ꯔꯥꯟꯁꯃꯤꯁꯟ ꯇꯧꯕꯗꯥ ꯑꯀꯥꯌꯕꯥ ꯄꯤ꯫ ꯃꯁꯤ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯃꯇꯃꯗꯥ ꯑꯣꯏ꯫
ꯃꯁꯤꯒꯤ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯊꯛ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ ꯍꯧꯏ , ꯑꯗꯨꯕꯨ ꯃꯁꯤ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠꯁꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ, ꯈꯣꯡ ꯍꯥꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥ ꯉꯥꯡꯕꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯌꯥꯏ꯫
ꯃꯁꯤꯒꯤ `(LEMS)` ꯑꯁꯤ ꯀꯅꯥꯅꯥ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯈꯠꯂꯀꯄꯒꯦ?
`(LEMS)` ꯁꯦꯝꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯀꯥꯡꯂꯨꯞ ꯑꯅꯤ ꯂꯩ꯫
1. ꯀꯦꯟꯁꯔꯒꯥ ꯃꯔꯤ ꯂꯩꯅꯕꯥ: LEMS ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 60% ꯗꯤ ꯃꯈꯜ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯀꯦꯟꯁꯔ ꯂꯩ꯫ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯁꯤ ꯁ꯭ꯃꯣꯜ ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔꯅꯤ . ꯑꯉꯀꯄꯥ ꯑꯣꯏꯅꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯂꯥꯛꯠꯔꯤꯉꯩ ꯃꯃꯥꯡꯗꯥ ꯊꯥ ꯀꯌꯥ ꯅꯠꯠꯔꯒꯥ ꯆꯍꯤ ꯀꯌꯥ ꯐꯥꯎꯕꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ ꯶꯰ꯒꯤ ꯃꯊꯛꯇꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯤ, ꯅꯨꯄꯥꯁꯤꯡꯅꯤ ꯑꯃꯁꯨꯡ ꯇꯝꯕꯥ ꯉꯃꯗꯕꯥ ꯄꯣꯠꯂꯃꯁꯤꯡ ꯁꯤꯖꯤꯟꯅꯈ꯭ꯔꯦ꯫
2. ꯀꯦꯟꯁꯔ ꯂꯩꯇꯦ: ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯑꯇꯣꯞꯄꯥ ꯴꯰% ꯗꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯠꯇꯥ ꯊꯦꯡꯅꯗꯦ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 35ꯗꯥ ꯑꯃꯁꯨꯡ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 60ꯗꯥ ꯂꯥꯌꯦꯡꯏ꯫
LEMS ꯑꯁꯤ ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫
ꯃꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯁ꯭ꯃꯣꯜ ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔ (LEMS) ꯈꯛꯇꯃꯛ ꯃꯔꯤ ꯂꯩꯅꯕꯔꯥ?
ꯅꯠꯇꯦ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ ꯄ꯭ꯔꯣꯁ꯭ꯇꯦꯠ ꯀꯦꯟꯁꯔ, ꯊꯥꯏꯃꯣꯃꯥ, ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯣꯞꯔꯣꯂꯤꯐꯦꯔꯦꯇꯤꯚ ꯗꯤꯁꯑꯣꯔꯗꯔꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯎꯏ꯫ ꯃꯔꯃꯗꯤ ꯀꯦꯟꯁꯔꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯛꯠꯔꯤꯉꯩ ꯃꯃꯥꯡꯗꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯀꯄꯨ LEMS ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯈꯪꯂꯕꯗꯤ ꯀꯦꯟꯁꯔ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯑꯆꯨꯝꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯇꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
LEMS ꯑꯁꯤ ꯖꯦꯅꯦꯇꯤꯛ ꯑꯣꯏꯕꯥ ꯑꯍꯣꯡꯕꯁꯤꯡꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯊꯣꯀꯍꯅꯕꯔꯥ?
ꯁꯥꯏꯟꯇꯤꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯊꯥꯖꯩ ꯃꯗꯨꯗꯤ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯂꯥꯌꯅꯥꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯂꯤꯉ꯭ꯛ ꯈꯔꯥ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯁꯨ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤꯅꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯏꯅꯐ꯭ꯂꯨꯑꯦꯟꯁ ꯑꯃꯁꯨ ꯂꯩꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯁꯤ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯈꯉꯕꯥ ꯉꯃꯗ꯭ꯔꯤ꯫
`(LEMS)` ꯑꯁꯤ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯒꯦ?
ꯂꯦꯃꯁ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ . ꯃꯁꯤꯒꯤ ꯐꯤꯚꯝ ꯑꯁꯤꯅꯥ ꯃꯥꯂꯦꯝ ꯁꯤꯅꯕꯥ ꯊꯨꯡꯅꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯃꯤꯑꯣꯏ ꯃꯤꯂꯤꯌꯟ 2.8ꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ ꯍꯥꯌꯅꯥ ꯄꯥꯅꯔꯤ꯫ ꯌꯨꯅꯥꯏꯇꯦꯗ ꯁ꯭ꯇꯦꯇꯁꯇꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯀꯦꯁꯁꯤꯡ ꯑꯁꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 400 ꯔꯣꯝ ꯔꯤꯄꯣꯔꯠ ꯇꯧꯔꯀꯈꯤ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯂꯩꯕꯥꯛ ꯑꯁꯤꯗꯥ ꯃꯤꯑꯣꯏ ꯀꯌꯥ ꯂꯩꯕꯒꯦ ꯍꯥꯌꯕꯒꯤ ꯑꯆꯨꯝꯕꯥ ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯛ ꯂꯩꯇꯕꯁꯨ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯁꯤ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫
`(LEMS)`ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?
`(LEMS)`ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯌꯦꯡꯁꯤ꯫ ꯂꯥꯏꯑꯣꯡ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯃꯤꯄꯨꯝ ꯈꯨꯗꯤꯡꯃꯛꯇꯥ ꯃꯇꯝ ꯑꯃꯗꯥ ꯊꯣꯛꯇꯦ, ꯂꯥꯏꯑꯣꯡ ꯈꯔꯗꯤ ꯉꯟꯅꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ, ꯈꯔꯗꯤ ꯇꯨꯡꯗꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫
- ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯆꯔꯥꯡꯅꯕꯥ: ꯃꯔꯨꯑꯣꯏꯅꯥ ꯃꯊꯛꯀꯤ ꯈꯣꯡꯗꯥ꯫
- ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ: ꯊꯣꯡꯅꯥꯎ ꯍꯥꯡꯗꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ꯆꯦꯌꯥꯔꯗꯒꯤ ꯊꯣꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
- ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯣꯟꯊꯕꯥ꯫
- ꯂꯤꯝꯐꯇꯥ ꯁꯣꯟꯊꯕꯥ ꯐꯥꯎꯕꯥ꯫
- ꯃꯤꯠ ꯎꯗꯕꯥ (ptosis) : ꯃꯁꯤ ꯇꯨꯝꯕꯥ ꯌꯥꯗꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯎꯕꯥ ꯐꯪꯏ꯫
- ꯋꯥꯐꯝ ꯑꯅꯤ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯎꯕꯥ (ꯗꯤꯞꯂꯣꯄꯤꯌꯥ)꯫
- ꯃꯤꯠ ꯑꯃꯁꯨꯡ ꯃꯤꯠ ꯁꯣꯀꯄꯥ (xerostomia): ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯄꯥ, ꯃꯃꯤꯠꯇꯥ ꯏꯁꯤꯡ ꯊꯨꯃꯖꯤꯅꯕꯥ ꯍꯟꯊꯔꯀꯄꯥ꯫
- ꯈꯣꯉ ꯍꯥꯝꯕ ꯌꯥꯗꯕ.
- ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯍꯟꯊꯕꯥ꯫
- ꯑꯔꯨꯝꯕꯥ ꯍꯟꯊꯕꯥ꯫
- ꯌꯨꯔꯤꯟ ꯇꯧꯕꯗꯥ ꯑꯋꯥꯕꯥ꯫
- ꯅꯨꯄꯥꯁꯤꯡꯗꯥ ꯏꯔꯦꯛꯇꯤꯚ ꯗꯤꯁꯐꯉ꯭ꯀꯁꯟ ꯂꯩꯕꯥ꯫
- ꯋꯥ ꯉꯥꯡꯕꯗꯥ ꯑꯋꯥꯕꯥ (dysarthria) ꯑꯃꯁꯨꯡ ꯂꯧꯅꯒꯅꯕꯥ ꯑꯋꯥꯕꯥ (dysphagia): ꯃꯍꯧꯁꯥꯅꯥ ꯃꯁꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯂꯥꯀꯄꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ꯫
- ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (dyspnea) ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ: ꯃꯁꯤꯁꯨ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯑꯔꯣꯏꯕꯥ ꯁ꯭ꯇꯦꯖꯁꯤꯡꯗꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ, ꯁꯥꯊꯤꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯅꯤ꯫
ꯃꯔꯨꯑꯣꯏꯕꯥ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯃꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯁꯤ LEMSꯅꯤ ꯍꯥꯌꯅꯥ ꯂꯧꯒꯅꯨ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯂꯧꯁꯤꯡꯅꯤ꯫
ꯃꯍꯧꯁꯥꯅꯥ LEMS ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯊꯣꯛꯀꯗꯒꯦ ꯑꯃꯁꯨꯡ ꯀꯔꯝꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯇꯧꯕꯒꯦ?
ꯃꯍꯧꯁꯥꯅꯥ ꯂꯦꯃꯁꯅꯥ ꯑꯍꯥꯅꯕꯗꯥ ꯈꯣꯡꯒꯤ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ . ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯃꯁꯤꯅꯥ ꯈꯨꯎꯒꯤ ꯃꯁꯂꯁꯤꯡ, ꯈꯨꯠ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯒꯤ ꯃꯁꯂꯁꯤꯡ, ꯋꯥ ꯉꯥꯡꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯧꯊꯣꯀꯄꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯂꯤꯕꯥ ꯃꯁꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯃꯤꯠꯀꯤ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯅꯍꯥꯛꯅꯥ ꯆꯦꯌꯥꯔꯗꯒꯤ ꯊꯣꯔꯀꯄꯥ, ꯁ꯭ꯇꯦꯖ ꯅꯠꯠꯔꯒꯥ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯆꯦꯅꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡ-ꯈꯨꯠ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯑꯀꯅꯕꯥ ꯊꯕꯛ ꯇꯧꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯃꯥꯌꯣꯛꯅꯔꯀꯄꯥ ꯌꯥꯏ꯫
ꯃꯍꯧꯁꯥꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯂꯥꯀꯏ, ꯅꯨꯃꯤꯠ ꯈꯔꯅꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ . ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯀꯦꯟꯁꯔꯒꯥ ꯂꯣꯌꯅꯅꯥ LEMS ꯂꯩꯔꯕꯗꯤ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯊꯨꯅꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫
LEMS ꯑꯁꯤ ꯀꯔꯤꯅꯥ ꯊꯣꯀꯍꯅꯕꯒꯦ?
ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯈꯟꯅꯈꯤꯕꯒꯨꯝꯅꯥ, ꯂꯦꯃꯁ ꯑꯁꯤ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ . ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯃꯁꯥꯒꯤ ꯑꯣꯏꯕꯥ ꯗꯤꯐꯦꯟꯁꯁꯤꯡ (ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ)ꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯁꯥꯒꯤ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯇꯤꯁꯨꯁꯤꯡꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯏ꯫ LEMSꯇꯥ, ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯅꯔꯚ ꯁꯦꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯐꯤꯕꯔꯁꯤꯡꯅꯥ ꯊꯦꯡꯅꯔꯤꯕꯥ ꯃꯐꯝ ꯑꯗꯨꯗꯥ, ꯅ꯭ꯌꯨꯔꯣꯃꯁꯀꯨꯂꯥꯔ ꯖꯉ꯭ꯀꯁꯅꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯏ꯫ ꯃꯔꯨꯑꯣꯏꯅꯥ, ꯃꯈꯣꯌꯅꯥ ꯃꯐꯃꯗꯨꯗꯥ ꯂꯩꯕꯥ ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯏ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯅꯔꯚ ꯃꯦꯁꯦꯖꯁꯤꯡ ꯊꯥꯗꯣꯀꯄꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
ꯃꯁꯤ ꯗꯣꯃꯤꯅꯣꯒꯤ ꯂꯝꯕꯤ ꯑꯃꯒꯨꯝ ꯈꯅꯕꯤꯌꯨ꯫ ꯃꯁꯤꯒꯤ ꯑꯦꯇꯦꯛꯇ ꯑꯁꯤꯅꯥ ꯊꯧꯗꯣꯀꯁꯤꯡꯒꯤ ꯆꯦꯟ ꯑꯃꯥ ꯊꯣꯀꯍꯜꯂꯤ:
1. ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯅꯔꯚ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯑꯔꯣꯏꯕꯗꯥ ꯂꯩꯕꯥ ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡꯗꯥ ꯆꯦꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯕꯨ ꯕ꯭ꯂꯣꯛ ꯇꯧꯏ꯫
2. ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡ ꯍꯟꯊꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯅ꯭ꯌꯨꯔꯣꯠꯔꯥꯟꯁꯃꯤꯇꯔ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯅꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯏ꯫ ꯃꯁꯤꯒꯤ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯟ ꯑꯁꯤ ꯃꯁꯜ ꯐꯉ꯭ꯀꯁꯅꯒꯤꯗꯃꯛꯇꯥ ꯇꯉꯥꯏꯐꯗꯕꯥ ꯀꯦꯃꯤꯀꯦꯜ ꯑꯃꯅꯤ꯫
3. ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯟ ꯃꯔꯥꯡ ꯀꯥꯌꯅꯥ ꯊꯥꯗꯣꯀꯄꯥ ꯉꯃꯗꯕꯥ ꯃꯇꯃꯗꯥ, ꯃꯁꯜ ꯐꯤꯕꯔꯁꯤꯡꯗꯥ ꯄꯤꯔꯤꯕꯥ "ꯃꯦꯁꯦꯖꯁꯤꯡ" ꯑꯁꯤ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯆꯠꯄꯥ ꯉꯃꯗꯦ꯫ ꯑꯗꯨꯗꯒꯤ ꯅꯍꯥꯛꯀꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯉꯃꯗꯦ꯫
4. ꯃꯁꯤꯒꯤ ꯃꯍꯩ ꯑꯣꯏꯅꯥ ꯃꯁꯂꯁꯤꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯅꯥ ꯊꯕꯛ ꯇꯧꯗꯦ, ꯃꯗꯨꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫
ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯑꯁꯤ ꯁ꯭ꯃꯣꯜ-ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯀꯔꯝꯅꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯕꯤꯌꯨ: ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯀꯦꯟꯁꯔ ꯂꯩꯕꯥ ꯃꯇꯃꯗꯥ, ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡꯅꯥ "ꯂꯥꯅꯗꯥ ꯆꯠꯂꯨ" ꯍꯥꯌꯕꯒꯤ ꯁꯤꯒꯅꯦꯜ ꯑꯃꯥ ꯐꯪꯏ꯫ ꯑꯗꯨꯕꯨ ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯗꯥ (ꯃꯔꯨꯑꯣꯏꯅꯥ, ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯃꯊꯛꯇꯥ ꯂꯩꯕꯥ ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡꯗꯥ) ꯑꯦꯇꯦꯛ ꯇꯧꯕꯒꯤ ꯃꯍꯨꯠꯇꯥ, ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯑꯔꯥꯅꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯅꯔꯚ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯃꯊꯛꯇꯥ ꯂꯩꯕꯥ ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯂꯁꯤꯡꯗꯥ ꯑꯦꯇꯦꯛ ꯇꯧꯏ꯫ ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯆꯞ ꯃꯥꯟꯅꯕꯥ ꯊꯧꯗꯣꯀꯁꯤꯡꯒꯤ ꯆꯦꯟ ꯑꯗꯨ ꯊꯣꯀꯏ꯫
ꯁꯥꯏꯟꯇꯤꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯊꯥꯖꯩ ꯃꯗꯨꯗꯤ ꯂꯪꯁ ꯀꯦꯟꯁꯔ ꯂꯩꯇꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯀꯤ ꯃꯔꯝ ꯑꯁꯤ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯃꯒꯤ ꯑꯁꯣꯏ-ꯑꯉꯥꯝ ꯊꯣꯀꯄꯈꯛꯇꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯃꯁꯤ ꯀꯔꯤꯒꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ ꯍꯥꯌꯕꯁꯤ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯗ꯭ꯔꯤ꯫
`(LEMS)` ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯉꯗꯣꯛꯀꯅꯤ?
LEMS ꯈꯪꯗꯣꯛꯅꯕꯒꯤ ꯑꯍꯥꯅꯕꯥ ꯈꯣꯡꯊꯥꯡꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯀꯄꯨ ꯆꯦꯀꯁꯤꯟꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯅꯤ꯫ ꯃꯁꯤꯗꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯅ꯭ꯌꯨꯔꯣꯂꯣꯖꯤꯁ꯭ꯠ ꯑꯃꯥ, ꯅꯠꯠꯔꯒꯥ ꯅꯔꯚ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡꯗꯥ ꯑꯈꯟꯅꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯃꯥ ꯌꯥꯑꯣꯒꯅꯤ꯫ ꯊꯧꯑꯣꯡ ꯑꯁꯤꯒꯤ ꯁꯔꯨꯛ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ, ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯍꯤꯁ꯭ꯇꯔꯤ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯂꯧꯔꯤꯕꯥ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯍꯪꯕꯁꯤ ꯌꯥꯎꯏ꯫ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ ꯑꯃꯁꯨꯡ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯈꯨꯗꯃꯁꯤꯡ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯑꯀꯨꯞꯄꯥ ꯅ꯭ꯌꯨꯔꯣꯂꯣꯖꯤꯀꯦꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯀꯏ꯫
ꯃꯊꯪꯒꯤ ꯈꯣꯡꯊꯥꯡꯗꯤ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯅꯤ꯫ `(LEMS)`ꯒꯤ ꯇꯦꯁ꯭ꯇꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡꯁꯤ ꯌꯥꯎꯏ:
- ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯗꯥ ꯑꯦꯟꯇꯤ-ꯀꯦꯂꯁꯤꯌꯝ ꯆꯦꯅꯦꯜ ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯆꯦꯛ ꯇꯧꯕꯥ ꯌꯥꯏ꯫ LEMSꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 85%ꯗꯤ ꯃꯈꯣꯌꯒꯤ ꯏꯗꯥ ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯎꯏ꯫
- ꯏꯂꯦꯛꯠꯔꯣꯃꯥꯌꯣꯒ꯭ꯔꯥꯐꯤ (EMG): ꯇꯦꯁ꯭ꯠ ꯑꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯅꯔꯚꯁꯤꯡꯅꯥ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯐꯖꯅꯥ ꯄꯨꯟꯅꯥ ꯊꯕꯛ ꯇꯧꯃꯤꯟꯅꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯇꯥ ꯏ.ꯑꯦꯝ.ꯖꯤ.ꯒꯤ ꯇꯦꯁ꯭ꯠ ꯑꯁꯤꯅꯥ ꯌꯥꯝꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯐꯂꯁꯤꯡ ꯂꯩ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤꯅꯥ ꯗꯥꯏꯒ꯭ꯅꯣꯁꯤꯁ ꯀꯅꯐꯔꯝ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯃꯒꯅꯤ꯫
- ꯂꯪꯁꯀꯤ ꯑꯦꯛꯁ-ꯔꯦ `(ꯑꯦꯛꯁ-ꯔꯦ)` ꯅꯠꯠꯔꯒꯥ ꯁꯤ.ꯇꯤ.ꯁ꯭ꯀꯦꯟ `(ꯁꯤ.ꯇꯤ. ꯁ꯭ꯀꯦꯟ)` ꯅꯠꯠꯔꯒꯥ ꯑꯦꯝ.ꯑꯥꯔ.ꯑꯥꯏ.
LEMSꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯂꯥꯀꯄꯒꯤ ꯃꯃꯥꯡꯗꯥ ꯊꯥ ꯑꯃꯗꯒꯤ ꯆꯍꯤ 6 ꯐꯥꯎꯕꯥ ꯍꯧꯕꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯪꯗꯣꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯆꯍꯤ ꯑꯅꯤꯒꯤ ꯑꯣꯏꯅꯥ ꯊꯥ ꯑꯍꯨꯃꯗꯒꯤ 6 ꯐꯥꯎꯕꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯀꯦꯟꯁꯔ ꯁ꯭ꯛꯔꯤꯅꯤꯡ ꯇꯧꯒꯗꯕꯅꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯆꯨꯅꯕꯥ ꯁ꯭ꯛꯔꯤꯅꯤꯡ ꯁꯦꯗ꯭ꯌꯨꯜ ꯑꯃꯥ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯒꯅꯤ꯫
LEMS ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯒꯦ?
ꯂꯦꯃꯁꯀꯤ ꯂꯥꯏꯌꯦꯡ ꯀꯌꯥ ꯂꯩ꯫
- ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯀꯦꯟꯁꯔ ꯑꯗꯨ ꯂꯥꯏꯌꯦꯡꯕꯥ: ꯀꯔꯤꯒꯨꯝꯕꯥ LEMS ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯒꯥ ꯃꯔꯤ ꯂꯩꯅꯔꯕꯗꯤ, ꯍꯥꯌꯕꯗꯤ ꯁ꯭ꯃꯣꯜ ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔ ꯑꯁꯤ ꯂꯥꯏꯌꯦꯡꯕꯅꯥ LEMSꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯁꯨ ꯍꯟꯊꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯀꯦꯟꯁꯔ ꯂꯥꯌꯦꯡꯕꯗꯥ ꯀꯦꯃꯣꯊꯦꯔꯥꯄꯤ, ꯔꯦꯗꯤꯑꯦꯁꯟ ꯊꯦꯔꯥꯄꯤ, ꯑꯃꯁꯨꯡ/ꯅꯠꯠꯔꯒꯥ ꯁꯔꯖꯔꯤ ꯌꯥꯎꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯀꯦꯟꯁꯔꯒꯤ ꯃꯈꯜ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯤ ꯔꯤꯀꯃꯦꯟꯗꯦꯁꯅꯁꯤꯡꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫
- (LEMS)ꯒꯤ ꯑꯀꯛꯅꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ: ꯃꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯁꯤꯅꯕꯥ ꯉꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯝ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯎꯏ꯫
ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯒꯤ ꯂꯥꯏꯌꯦꯡ꯫
- ꯑꯦꯃꯤꯐꯥꯝꯞꯔꯤꯗꯤꯟ (Firdapse®), ꯒꯨꯌꯥꯅꯤꯗꯤꯟ: ꯗ꯭ꯔꯒꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯁꯂꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫ ꯃꯈꯣꯌꯅꯥ ꯅ꯭ꯌꯨꯔꯣꯃꯁꯀꯨꯂꯥꯔ ꯖꯉ꯭ꯀꯁꯟꯗꯥ ꯅ꯭ꯌꯨꯔꯣꯠꯔꯥꯟꯁꯃꯤꯇꯔ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯟ ꯊꯥꯗꯣꯀꯄꯥ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ, ꯃꯁꯤꯅꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯤꯒꯅꯦꯂꯁꯤꯡ ꯐꯒꯠꯍꯜꯂꯤ꯫
- ꯄꯥꯏꯔꯤꯗꯣꯁ꯭ꯇꯤꯒꯃꯤꯟ (Pyridostigmine - Mestinon®): ꯄꯥꯏꯔꯤꯗꯣꯁ꯭ꯇꯤꯒꯃꯥꯏꯅꯅꯥ ꯅ꯭ꯌꯨꯔꯣꯃꯁꯀꯨꯂꯥꯔ ꯖꯉ꯭ꯀꯁꯟꯗꯥ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯅꯒꯤ ꯕ꯭ꯔꯦꯀꯗꯥꯎꯟ ꯊꯤꯡꯗꯨꯅꯥ ꯊꯕꯛ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯟ ꯁꯤꯒꯅꯦꯂꯤꯡꯁꯨ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯐꯒꯠꯍꯜꯂꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯄꯥꯏꯔꯤꯗꯣꯁ꯭ꯇꯤꯒꯃꯤꯟ ꯑꯁꯤ ꯑꯦꯃꯤꯐꯥꯝꯞꯔꯤꯗꯤꯅꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯄꯤꯗꯨꯅꯥ ꯃꯁꯂꯒꯤ ꯐꯉ꯭ꯀꯁꯟ ꯐꯒꯠꯍꯟꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯤꯠ ꯁꯣꯀꯄꯥ, ꯃꯤꯠ ꯁꯣꯀꯄꯥ, ꯈꯣꯡ ꯍꯥꯝꯕꯥ, ꯁꯦꯛꯁꯨꯑꯦꯜ ꯗꯤꯁꯐꯉ꯭ꯀꯁꯟ, ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯍꯟꯊꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯂꯦꯃꯁꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯌꯦꯡꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯀꯤꯗꯃꯛꯇꯥ ꯄꯥꯏꯔꯤꯗꯣꯁ꯭ꯇꯤꯒꯃꯤꯟ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯑꯁꯤ ꯑꯣꯐ-ꯂꯦꯕꯦꯜ ꯁꯤꯖꯤꯟꯅꯕꯅꯤ, ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯌꯨ.ꯑꯦꯁ.ꯀꯤ ꯐꯨꯗ ꯑꯃꯁꯨꯡ ꯗ꯭ꯔꯒ ꯑꯦꯗꯃꯤꯅꯤꯁ꯭ꯠꯔꯦꯁꯟ (ꯑꯦꯐ.ꯗꯤ.ꯑꯦ.)ꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯒꯤꯗꯃꯛꯇꯥ ꯗ꯭ꯔꯒ ꯑꯁꯤ ꯑꯌꯥꯕꯥ ꯄꯤꯈꯤꯗ꯭ꯔꯤ꯫
ꯏꯝꯝꯌꯨꯟ-ꯃꯣꯗ꯭ꯌꯨꯂꯦꯇꯤꯡ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇ꯫
- ꯏꯝꯝꯌꯨꯅꯣꯁꯞꯔꯦꯁꯦꯟꯇꯁꯤꯡ: ꯱.ꯗ꯭ꯔꯒꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯃꯒꯤ "ꯗꯤꯐꯦꯟꯁ" ꯐꯉ꯭ꯀꯁꯟ ꯑꯗꯨ ꯊꯤꯡꯕꯗꯥ ꯅꯠꯠꯔꯒꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯇꯩ ꯗ꯭ꯔꯒꯁꯤꯡꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗ꯭ꯔꯕꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯗ꯭ꯔꯒꯁꯤꯡ ꯑꯁꯤ ꯄꯤꯕꯥ ꯌꯥꯏ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ, ꯄ꯭ꯔꯦꯗꯅꯤꯁꯟ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯥ ꯑꯖꯥꯊꯤꯑꯣꯞꯔꯤꯟ ꯅꯠꯠꯔꯒꯥ ꯁꯥꯏꯛꯂꯣꯁ꯭ꯄꯣꯔꯤꯅꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯅꯠꯠꯔꯒꯥ ꯌꯥꯎꯗꯅꯥ ꯄꯤꯕꯥ ꯌꯥꯏ꯫
- ꯄ꯭ꯂꯥꯖꯃꯥ ꯑꯦꯛꯁꯆꯦꯟꯖ: ꯄ꯭ꯔꯣꯁꯤꯗ꯭ꯌꯨꯑꯣꯔ ꯑꯁꯤꯗꯥ, ꯃꯦꯁꯤꯟ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯒꯤ ꯂꯤꯛꯌꯨꯏꯗ ꯑꯣꯏꯕꯥ ꯁꯔꯨꯛ (ꯄ꯭ꯂꯥꯖꯃꯥ) ꯑꯗꯨ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯗꯒꯤ ꯇꯣꯈꯥꯌꯍꯜꯂꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯑꯦꯟꯇꯤꯕꯣꯗꯤꯁꯤꯡ ꯑꯗꯨ ꯄ꯭ꯂꯥꯖꯃꯥ ꯑꯁꯤꯗꯥ ꯂꯩ꯫ ꯇꯣꯈꯥꯌꯅꯥ ꯂꯩꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯏ ꯑꯗꯨ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯆꯪꯁꯤꯜꯂꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯛꯀꯤ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯃꯊꯧ ꯇꯥꯔꯕꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯈꯟꯅꯔꯀꯄꯥ ꯌꯥꯏ꯫
- ꯏꯝꯝꯌꯨꯅꯣꯒ꯭ꯂꯣꯕꯨꯂꯤꯅꯁꯤꯡ: ꯃꯤꯑꯣꯏ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯍꯥꯏ-ꯗꯣꯖ ꯏꯝꯝꯌꯨꯅꯣꯒ꯭ꯂꯣꯕꯨꯂꯤꯟ ꯂꯥꯌꯦꯡꯕꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯇꯕꯥ ꯊꯤꯡꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
LEMS ꯊꯤꯡꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?
ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯀꯤ ꯑꯆꯨꯝꯕꯥ ꯃꯔꯝ ꯑꯁꯤ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯈꯉꯕꯥ ꯉꯃꯗ꯭ꯔꯤ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯥꯀꯁꯤꯟꯅꯕꯥ ꯄꯥꯝꯕꯩ ꯂꯩꯕꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯈꯉꯕꯥ ꯉꯃꯗ꯭ꯔꯤ꯫
ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯪꯁ ꯀꯦꯟꯁꯔ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ LEMS ꯂꯥꯀꯄꯥ ꯌꯥꯏ ꯃꯔꯝ ꯑꯗꯨꯅꯥ, ꯅꯍꯥꯛꯅꯥ ꯂꯪꯁꯀꯤ ꯀꯦꯟꯁꯔ ꯂꯥꯀꯁꯤꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯌꯥꯏ:
- ꯃꯩꯈꯨ ꯊꯥꯗꯣꯛꯂꯣꯏꯗꯕꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯇꯝꯕꯥ ꯉꯃꯗꯕꯥ ꯄꯣꯠꯁꯀꯁꯤꯡ ꯁꯤꯖꯤꯟꯅꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯍꯥꯌꯌꯨ꯫
- ꯁꯦꯀꯦꯟꯗ-ꯍꯦꯟꯗ ꯃꯩꯈꯨ ꯁꯤꯖꯤꯟꯅꯔꯣꯏꯗꯕꯅꯤ꯫
- ꯅꯍꯥꯛꯀꯤ ꯌꯨꯃꯗꯥ ꯔꯦꯗꯟ ꯒ꯭ꯌꯥꯁ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯆꯦꯛ ꯇꯧ꯫ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯔꯦꯗꯟ ꯒ꯭ꯌꯥꯁꯇꯥ ꯑꯦꯛꯁꯄꯣꯖ ꯇꯧꯕꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁ ꯀꯦꯟꯁꯔꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯅꯍꯥꯛꯅꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯃꯥ ꯊꯝꯅꯕꯒꯤꯗꯃꯛ ꯈꯣꯡꯊꯥꯡꯁꯤꯡꯁꯨ ꯂꯧꯈꯠꯄꯥ ꯌꯥꯏ:
- ꯃꯅꯥ-ꯃꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯎꯍꯩ-ꯋꯥꯍꯩꯁꯤꯡ ꯍꯦꯟꯅꯥ ꯆꯥꯒꯗꯕꯅꯤ꯫ ꯃꯦꯗꯤꯇꯦꯔꯦꯅꯤꯌꯟ ꯅꯠꯠꯔꯒꯥ DASH ꯗꯥꯏꯠ ꯏꯅꯒꯗꯕꯅꯤ꯫
- ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯑꯔꯨꯝꯕꯥ ꯑꯃꯥ ꯊꯝꯕꯥ꯫
- ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯄꯥꯎꯇꯥꯛ ꯄꯤꯔꯀꯄꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯇꯧ꯫
- ꯃꯇꯤꯛ ꯆꯥꯅꯥ ꯇꯨꯝꯕꯥ - ꯃꯍꯧꯁꯥꯅꯥ ꯄꯨꯡ 7ꯗꯒꯤ 9 ꯐꯥꯎꯕꯥ꯫
- ꯅꯍꯥꯛꯀꯤ ꯁ꯭ꯠꯔꯦꯁ ꯑꯗꯨ ꯍꯟꯊꯍꯅꯒꯗꯕꯅꯤ꯫ ꯁ꯭ꯠꯔꯦꯁꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯇꯕꯥ ꯌꯥꯏ꯫
- ꯑꯁꯥꯕꯥ ꯏꯁꯤꯡꯗꯥ ꯂꯨꯄꯊꯣꯛꯀꯗꯕꯅꯤ꯫ ꯅꯨꯡꯁꯤꯠꯅꯥ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯇꯕꯥ ꯌꯥꯏ꯫
- ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ, ꯑꯃꯁꯨꯡ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯁꯦꯜ ꯍꯣꯡꯂꯛꯂꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ ꯃꯈꯣꯌꯗꯥ ꯈꯨꯗꯛꯇꯥ ꯈꯪꯍꯅꯕꯤꯌꯨ꯫
LEMS ꯃꯄꯨꯡꯐꯥꯅꯥ ꯂꯥꯌꯦꯡꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?
ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯀꯤ ꯂꯥꯌꯦꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯂꯦꯃꯁꯀꯥ ꯃꯔꯤ ꯂꯩꯅꯕꯥ ꯑꯟꯗꯔꯂꯥꯏꯟ ꯀꯦꯟꯁꯔ ꯂꯥꯌꯦꯡꯕꯅꯥ ꯂꯦꯃꯁꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯃꯤ ꯍꯥꯌꯕꯥ ꯎꯠꯂꯦ꯫ ꯏꯝꯝꯌꯨꯅꯣꯁꯞꯔꯦꯁꯤꯕ ꯗ꯭ꯔꯒꯁꯤꯡꯅꯥ ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯑꯦꯇꯦꯛ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯃꯤ, ꯑꯃꯁꯨꯡ ꯅꯔꯚ ꯑꯦꯟꯗꯁꯤꯡꯗꯥ ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯅꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯍꯟꯗꯨꯅꯥ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯐꯒꯠꯍꯟꯗꯨꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯁꯤꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡꯁꯨ ꯂꯩꯔꯤ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯀꯦꯟꯁꯔ ꯌꯥꯎꯗꯅꯥ LEMS ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯅꯥ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯕꯥ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯃꯥ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ LEMS ꯑꯃꯁꯨꯡ ꯀꯦꯟꯁꯔ ꯂꯩꯔꯕꯗꯤ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯀꯦꯟꯁꯔ ꯑꯗꯨ ꯇꯣꯏꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯦꯅꯦꯖ ꯇꯧꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯐꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ (ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯂꯩꯇꯕꯁꯨ)꯫
ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ ꯑꯗꯨꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯩꯅꯥ `(LEMS)` ꯂꯩꯔꯕꯗꯤ ꯑꯩꯒꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯀꯗꯥꯏꯗꯥ ꯀꯟꯇꯦꯛꯇ ꯇꯧꯒꯗꯒꯦ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯁꯦꯂꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯇꯥꯔꯕꯗꯤ, ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯂꯕꯗꯤ, ꯃꯇꯝ ꯑꯃꯠꯇꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯄꯥꯎ ꯐꯥꯎꯅꯕꯤꯌꯨ . ꯂꯥꯡꯇꯛꯅꯒꯅꯨ, ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯑꯣꯒꯅꯨ꯫ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯑꯗꯣꯃꯒꯤ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯂꯩꯔꯤ꯫
`(LEMS)` ꯑꯃꯁꯨꯡ `(Myasthenia Gravis - MG)`ꯒꯤ ꯃꯔꯛꯇꯥ ꯀꯔꯤ ꯈꯦꯠꯅꯕꯥ ꯂꯩꯕꯒꯦ?
ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯟ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ (LEMS) ꯑꯃꯁꯨꯡ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯌꯥ ꯒ꯭ꯔꯦꯚꯤꯁ (MG) ꯑꯁꯤꯅꯥ ꯃꯥꯟꯅꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯈꯔꯗꯤ ꯌꯥꯎꯏ꯫ ꯑꯅꯤꯃꯛꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫
ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯌꯥ ꯒ꯭ꯔꯦꯚꯤꯁ (MG)ꯅꯥ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯍꯥꯅꯕꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯤꯠꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯂꯩꯕꯥ ꯃꯁꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯂꯧꯊꯣꯀꯄꯗꯥ ꯁꯤꯖꯤꯟꯅꯔꯤꯕꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯃꯇꯨꯡ ꯇꯥꯔꯀꯄꯗꯥ, ꯃꯁꯤꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯀꯤ ꯃꯁꯂꯁꯤꯡ ꯌꯥꯎꯅꯥ ꯍꯦꯟꯅꯥ ꯖꯦꯅꯦꯔꯦꯜ ꯑꯣꯏꯕꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯃꯍꯧꯁꯥꯅꯥ LEMS ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯃꯊꯛ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ ꯁꯣꯟꯊꯔꯀꯄꯗꯒꯤ ꯍꯧꯏ, ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠꯁꯥꯗꯥ ꯆꯪꯁꯤꯜꯂꯤ꯫ LEMSꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯤꯠꯀꯤ ꯃꯁꯂꯁꯤꯡꯗꯁꯨ ꯁꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯁꯤ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯌꯥ ꯒ꯭ꯔꯦꯚꯤꯁ (MG)ꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯂꯨꯝꯃꯤ꯫
ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯌꯥ ꯒ꯭ꯔꯦꯚꯤꯁ (MG)ꯗꯥ, ꯔꯦꯁ꯭ꯄꯤꯔꯦꯇꯔꯤ ꯃꯁꯂꯁꯤꯡ (ꯅꯍꯥꯛꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯂꯤꯕꯥ ꯃꯁꯂꯁꯤꯡ) ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯅꯥ ꯁꯣꯀꯍꯜꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯑꯦꯜ.ꯏ.ꯑꯦꯝ.ꯑꯦꯁ.ꯇꯥ ꯌꯥꯝꯅꯥ ꯊꯦꯡꯅꯩ꯫
ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯌꯥ ꯒ꯭ꯔꯦꯚꯤꯁ (MG)ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯣꯇꯣꯅꯣꯃꯤꯛ ꯅꯔꯚꯁ ꯁꯤꯁ꯭ꯇꯦꯝ ꯗꯤꯁꯐꯉ꯭ꯀꯁꯅꯒꯤ ꯂꯥꯏꯑꯣꯡ ꯀꯌꯥ (ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ, ꯃꯤꯠ ꯁꯣꯀꯄꯥ, ꯃꯤꯠ ꯁꯣꯀꯄꯥ, ꯈꯣꯡ ꯍꯥꯝꯕꯥ, ꯈꯣꯡ ꯍꯥꯝꯕꯥ ꯍꯟꯊꯕꯥ, ꯁꯦꯛꯁꯨꯑꯦꯜ ꯗꯤꯁꯐꯉ꯭ꯀꯁꯟ) ꯎꯕꯥ ꯐꯪꯗꯦ꯫ ꯃꯁꯤꯒꯤ ꯑꯣꯟꯅ-ꯇꯩꯅꯕꯗꯥ, ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯀꯃꯞꯂꯦꯟꯇꯁꯤꯡ ꯑꯁꯤ ꯊꯦꯡꯅꯩ, ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯅꯤ ꯑꯁꯤ ꯈꯦꯠꯅꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
ꯑꯔꯣꯏꯕꯗꯥ, ꯅꯤꯡꯁꯤꯡꯒꯗꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ (ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ)
ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯈꯉꯂꯃꯒꯅꯤ ꯃꯗꯨꯗꯤ ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯣꯟ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ (LEMS) ꯑꯁꯤ ꯑꯣꯚꯔꯑꯦꯛꯇꯤꯚ ꯏꯝꯝꯌꯨꯟ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯅꯔꯚ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯁꯜ ꯐꯤꯕꯔꯁꯤꯡꯗꯥ "ꯀꯟꯠꯔꯦꯛꯇ" ꯇꯧꯅꯕꯥ ꯄꯥꯎꯖꯦꯜ ꯃꯇꯤꯛ ꯆꯥꯅꯥ ꯊꯥꯗꯦ꯫ ꯃꯁꯤꯒꯤ ꯃꯍꯩ ꯑꯣꯏꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯊꯣꯀꯏ꯫
ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, LEMSꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 60%ꯗꯤ ꯁ꯭ꯃꯣꯜ-ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔ ꯂꯩ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ LEMS ꯂꯩꯔꯕꯁꯨ ꯀꯦꯟꯁꯔ ꯂꯩꯠꯔꯕꯗꯤ, ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯊꯥ ꯈꯔꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯆꯍꯤ ꯑꯅꯤꯒꯤ ꯑꯣꯏꯅꯥ ꯀꯦꯟꯁꯔ ꯁ꯭ꯛꯔꯤꯅꯤꯡ ꯇꯧꯕꯥ ꯁꯣꯌꯗꯅꯥ ꯇꯧꯕꯤꯌꯨ꯫
ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯑꯣꯡ ꯂꯩ꯫ ꯃꯁꯤꯗꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯀꯦꯟꯁꯔ ꯂꯩꯔꯕꯗꯤ ꯂꯥꯌꯦꯡꯕꯥ, ꯂꯣꯌꯅꯅꯥ ꯅꯔꯚ ꯁꯦꯜ-ꯃꯁꯜ ꯐꯥꯏꯕꯔ ꯀꯝꯝꯌꯨꯅꯤꯀꯦꯁꯟ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯗ꯭ꯔꯒꯁꯤꯡ ꯂꯧꯕꯥ ꯌꯥꯑꯣꯔꯤ꯫ ꯀꯝꯝꯌꯨꯅꯤꯀꯦꯁꯟ ꯐꯒꯠꯍꯅꯕꯅꯥ ꯃꯁꯂꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫
ꯏꯅꯐꯣꯔꯃꯦꯁꯟ ꯑꯁꯤ ꯑꯗꯣꯃꯒꯤꯗꯃꯛ ꯀꯥꯟꯅꯕꯥ ꯑꯣꯏꯒꯅꯤ ꯍꯥꯌꯅꯥ ꯑꯩꯅꯥ ꯊꯥꯖꯩ꯫ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯍꯀꯁꯦꯂꯒꯤ ꯑꯋꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯗꯨꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯪꯖꯤꯅꯒꯗꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯃꯒꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯩ꯫
` ꯂꯃꯕꯦꯔꯠ-ꯏꯇꯣꯟ ꯃꯥꯏꯁ꯭ꯇꯦꯅꯤꯛ ꯁꯤꯟꯗꯣꯝ, ꯂꯦꯃꯁ, ꯑꯣꯇꯣꯏꯝꯌꯨꯟ ꯂꯥꯌꯅꯥ, ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ, ꯑꯄꯤꯀꯄꯥ ꯁꯦꯜ ꯂꯪꯁ ꯀꯦꯟꯁꯔ, ꯅ꯭ꯌꯨꯔꯣꯃꯁꯀꯨꯂꯥꯔ ꯖꯉ꯭ꯀꯁꯟ, ꯑꯦꯁꯤꯇꯤꯂꯀꯣꯂꯤꯟ꯫











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