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ꯑꯩꯈꯣꯌꯅꯥ LAM (Lymphangioleiomyomatosis) ꯀꯧꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ?

ꯑꯩꯈꯣꯌꯅꯥ LAM (Lymphangioleiomyomatosis) ꯀꯧꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ?

ꯃꯃꯤꯡ ꯑꯁꯤ ꯈꯔꯥ ꯄꯥꯕꯥ ꯌꯥꯝꯅꯥ ꯂꯨꯏ, ꯅꯠꯇꯦ? "ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ"꯫ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ, ꯃꯁꯤꯕꯨ ꯂꯝ ꯍꯥꯌꯅꯥ ꯀꯧꯔꯁꯤ . ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯤ ꯑꯌꯥꯝꯕꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯃꯤꯡ ꯑꯃꯥ ꯇꯥꯕꯗꯥ ꯂꯥꯡꯇꯛꯅꯕꯥ ꯄꯣꯀꯄꯥ ꯑꯁꯤ ꯂꯧꯁꯤꯅꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯑꯥꯔꯇꯤꯀꯜ ꯑꯁꯤꯗꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯁꯨꯞꯅꯒꯤ ꯀꯔꯤ ꯍꯥꯌꯔꯤꯕꯒꯦ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, LAM ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯃꯅꯨꯡꯗꯥ ꯂꯩꯕꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯍꯧꯔꯀꯄꯥ ꯃꯇꯃꯅꯤ꯫ ꯑꯄꯤꯀꯄꯥ ꯇꯤꯎꯃꯔꯁꯤꯡꯒꯨꯝꯅꯥ꯫ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯄꯨꯟꯅꯥ ꯀꯨꯄꯁꯤꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯀꯧꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯕꯨꯕꯂꯒꯨꯝꯕꯥ ꯁ꯭ꯠꯔꯀꯆꯔꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯇꯤꯎꯃꯔꯁꯤꯡ ꯑꯁꯤ ꯍꯦꯅꯒꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯃꯈꯣꯌꯅꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯂꯪꯁꯀꯤ ꯇꯤꯁꯨꯁꯤꯡꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫

ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯪꯁ ꯈꯛꯇꯗꯥ ꯂꯤꯃꯤꯠ ꯂꯩꯇꯦ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯇꯤꯎꯃꯔꯁꯤꯡ ꯑꯁꯤ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯁꯨ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯔꯤꯕꯥ ꯖꯤꯅꯁꯤꯡꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯊꯣꯀꯄꯅꯤ꯫

ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯤꯡꯁꯤꯡꯕꯥ ꯃꯊꯧ ꯇꯥꯏ ꯃꯗꯨꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯆꯍꯤ 20ꯗꯒꯤ 40 ꯐꯥꯎꯕꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯃꯤꯔꯣꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯍꯣꯔꯃꯣꯟ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯒꯥ ꯃꯔꯤ ꯂꯩꯅꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯥ ꯂꯩ ꯍꯥꯌꯅꯥ ꯂꯧꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯁꯤꯡꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤ ꯂꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤꯗꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯌꯥꯏ, ꯑꯅꯤꯁꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯔꯥ ꯈꯦꯠꯅꯕꯥ ꯂꯩ꯫

ꯂꯝ ꯃꯈꯜ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯃꯁꯛ ꯇꯥꯀꯄꯥ꯫
ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.-ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ ꯀꯧꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯊꯣꯀꯄꯥ LAM ꯃꯈꯜ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯃꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯒꯤ ꯁꯔꯨꯛ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯏ꯫
ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝꯃꯁꯤꯒꯤ ꯃꯈꯜ ꯑꯁꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯔꯦꯟꯗꯝ ꯖꯦꯅꯦꯇꯤꯛ ꯆꯦꯟꯖ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤ ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯅꯠꯇꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯁꯤꯒꯤ ꯃꯈꯜ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯁꯟꯗꯣꯔꯀꯄꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯃꯊꯧ ꯇꯥꯗꯦ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯩ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ, ꯍꯥꯌꯕꯗꯤ ꯑꯦꯖꯃꯥꯒꯥ ꯌꯥꯝꯅꯥ ꯃꯥꯟꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯁꯤ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯃꯇꯝ ꯈꯔꯥ ꯆꯪꯂꯝꯕꯥ ꯌꯥꯏ꯫ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ꯫

  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ (dyspnea): ꯑꯍꯥꯅꯕꯗꯥ ꯎꯕꯥ ꯐꯪꯗ꯭ꯔꯕꯁꯨ, ꯑꯁꯣꯛ-ꯑꯄꯟ ꯑꯁꯤ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯇꯦꯅꯕꯥ ꯂꯝꯕꯤꯗꯥ ꯆꯠꯄꯥ ꯃꯇꯃꯗꯁꯨ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ, ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯗꯥ ꯆꯠꯄꯥ ꯃꯇꯃꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯁꯤ ꯌꯥꯎꯕꯥ ꯌꯥꯏ꯫
  • ꯍꯨꯏ-ꯍꯧꯗꯣꯡ (wheezing): ꯈꯣꯡꯒꯤ ꯃꯅꯨꯡꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯇꯔꯨ-ꯇꯅꯥꯅꯕꯥ ꯈꯣꯟꯖꯦꯜ ꯑꯃꯅꯤ꯫
  • ꯈꯣꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ (chest pain): ꯈꯪꯍꯧꯗꯅꯥ, ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ (chest pain) ꯂꯩꯕꯥ ꯌꯥꯏ꯫
  • ꯀꯣꯛ ꯆꯤꯀꯄꯥ: ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ (persistent dry cough)꯫
  • ꯏ ꯁꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ‘ꯆꯥꯏꯜ’ (chail) : ꯆꯥꯏꯜ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯗꯥꯏꯖꯦꯁ꯭ꯇꯤꯚ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯃ꯭ꯌꯨꯀꯁ ꯐ꯭ꯂꯨꯏꯗ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯃꯆꯨ ꯁꯉ꯭ꯒꯣꯝ ꯑꯣꯏ꯫

ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯂꯝ ꯑꯁꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯀꯔꯤꯅꯣ?

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ ꯃꯁꯤ ꯖꯤꯅꯁꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯣꯏꯔꯤ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯱ ꯑꯃꯁꯨꯡ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯲ ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯂꯩ꯫ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯔꯤꯕꯥ ‘ꯒꯥꯔꯗꯤꯌꯟ’ꯒꯨꯝꯅꯥ ꯑꯣꯏꯔꯤ꯫ ꯃꯈꯣꯌꯕꯨ ‘ꯇꯤꯎꯃꯔ ꯁꯞꯞꯔꯦꯁꯔ’ ꯖꯤꯅꯁꯤꯡ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯍꯥꯌꯕꯗꯤ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯊꯕꯛ ꯑꯁꯤ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯇꯤꯎꯃꯔ ꯁꯦꯝꯕꯥ ꯊꯤꯡꯕꯅꯤ꯫

LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯗꯥ, TSC1 ꯅꯠꯠꯔꯒꯥ TSC2ꯗꯥ ꯑꯁꯣꯌꯕꯥ ꯑꯃꯥ, ꯅꯠꯠꯔꯒꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯥ ꯂꯩ꯫ ꯑꯗꯨꯗꯒꯤ ꯑꯗꯨꯒꯨꯝꯕꯥ ‘ꯒꯥꯔꯗꯁꯤꯡ’ ꯑꯗꯨꯅꯥ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯗꯦ꯫ ꯃꯁꯤꯒꯤ ꯃꯍꯩ ꯑꯣꯏꯅꯥ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯍꯧꯔꯀꯏ, ꯃꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯈꯤꯕꯥ ꯇꯤꯎꯃꯔ ꯃꯈꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯦꯃꯒꯠꯂꯤ꯫

  • ꯂꯪꯁꯀꯤ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ꯫
  • ꯀꯤꯗꯅꯤꯒꯤ ꯇꯤꯎꯃꯔꯁꯤꯡ (ꯑꯦꯟꯖꯤꯑꯣꯃꯥꯌꯣꯂꯤꯄꯣꯃꯥꯁ) .
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯒꯤ ꯇꯤꯎꯃꯔꯁꯤꯡ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯑꯣꯏꯊꯣꯀꯄꯥ ꯌꯥꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯀꯔꯤꯅꯣ?

LAMꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯁꯤ ꯂꯪꯁ (neumothorax) . ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯕꯕꯂꯒꯨꯝꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯃꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ, ꯃꯗꯨ ꯈꯪꯍꯧꯗꯅꯥ ꯊꯨꯒꯥꯌꯗꯨꯅꯥ, ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯆꯦꯁ꯭ꯠ ꯋꯥꯂꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯃꯐꯝ ꯑꯗꯨꯗꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯌꯥꯍꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯂꯪꯁ ꯑꯗꯨ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯦꯡꯅꯒꯅꯤ꯫ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ, LAM ꯑꯁꯤ ꯑꯍꯥꯅꯕꯥ ꯑꯣꯏꯅꯥ ꯂꯪꯁ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯈꯪꯗꯣꯀꯏ꯫

ꯑꯇꯩ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯁꯨ ꯂꯩꯕꯥ ꯌꯥꯏ:

  • ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ‘ꯆꯥꯏꯂꯣꯁ’ ꯐ꯭ꯂꯨꯏꯗ (chylothorax) ꯊꯨꯒꯥꯌꯕꯥ (chylothorax)
  • ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗ ꯑꯦꯛꯌꯨꯃꯨꯂꯦꯁꯟ (ꯄ꯭ꯂꯤꯎꯔꯦꯜ ꯏꯐ꯭ꯌꯨꯁꯟ)
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯑꯀꯥꯌꯕꯥ ꯄꯤꯕꯥ꯫

ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯃꯇꯧ ꯀꯔꯝꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯇꯥꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯀꯄꯨ ꯌꯦꯡꯁꯤꯜꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯍꯥꯛꯅꯥ ꯃꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯑꯃꯥ ꯇꯧꯅꯕꯥ ꯑꯣꯔꯗꯔ ꯇꯧꯒꯅꯤ꯫

ꯆꯥꯡꯌꯦꯡ ꯃꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯑꯗꯣꯝꯅꯥ ꯀꯔꯤ ꯇꯧꯔꯤꯕꯒꯦ?
ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯁꯤꯡ ꯑꯗꯨ ꯀꯌꯥꯝ ꯐꯖꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯀꯄꯥ ꯌꯥꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯂꯦꯄꯊꯣꯀꯏ꯫
ꯄꯂꯁ ꯑꯣꯛꯁꯤꯃꯦꯠꯔꯤ ꯇꯧꯕꯥ꯫ ꯃꯈꯣꯌꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠꯁꯥꯗꯥ ꯀ꯭ꯂꯤꯄꯒꯨꯝꯕꯥ ꯄꯣꯠꯁꯛ ꯑꯃꯥ ꯊꯥꯗꯣꯀꯏ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫
ꯏꯃꯦꯖꯤꯡ (ꯁ꯭ꯀꯦꯅꯁꯤꯡ) ꯴. ꯁꯤ.ꯇꯤ.ꯁ꯭ꯀꯦꯟ ꯑꯃꯅꯥ , ꯃꯔꯨꯑꯣꯏꯅꯥ HRCT (ꯍꯥꯏ-ꯔꯤꯖꯣꯂꯨꯁꯟ ꯁꯤ.ꯇꯤ.) ꯁ꯭ꯀꯦꯟ ꯑꯃꯅꯥ ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯑꯗꯨ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫
ꯚꯤ.ꯏ.ꯖꯤ.ꯑꯦꯐ.-ꯗꯤ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ꯫ ꯚꯤ.ꯏ.ꯖꯤ.ꯑꯦꯐ.-ꯗꯤ.ꯅꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯅꯤ꯫ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯏꯗꯥ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
ꯂꯪꯁꯀꯤ ꯕꯥꯏꯑꯣꯞꯁꯤ ꯇꯧꯕꯥ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯇꯣꯞꯄꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯑꯗꯨ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯗꯤ, ꯂꯪꯁꯇꯒꯤ ꯇꯤꯁ꯭ꯌꯨꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯁꯔꯨꯛ ꯑꯃꯥ ꯂꯧꯊꯣꯀꯏ ꯑꯃꯁꯨꯡ ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫ ꯃꯁꯤ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯁ꯭ꯀꯣꯄꯤ ꯅꯠꯠꯔꯒꯥ ꯚꯤ.ꯑꯦ.ꯇꯤ.ꯑꯦꯁ .

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?

ꯑꯍꯥꯅꯕꯗꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯍꯤꯗꯥꯛ ꯂꯥꯡꯊꯛ ꯑꯃꯠꯇꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯐꯪꯗ꯭ꯔꯤ꯫ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯍꯧꯖꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯕꯥ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯂꯍꯟꯗꯅꯕꯥ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯂꯩꯔꯦ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ . ꯃꯁꯤꯕꯨ ꯔꯦꯄꯥꯃꯥꯏꯁꯤꯟ ꯍꯥꯌꯅꯥꯁꯨ ꯀꯧꯏ꯫ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯊꯤꯡꯗꯨꯅꯥ ꯊꯕꯛ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯊꯝꯕꯥ ꯉꯝꯃꯤ ꯑꯃꯁꯨꯡ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯂꯩꯕꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯅꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯍꯥꯌꯕꯗꯤ:

  • ꯑꯣꯛꯁꯤꯖꯦꯟ ꯊꯦꯔꯥꯄꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯝꯅꯥ ꯂꯩꯔꯕꯗꯤ꯫
  • ꯏꯅꯍꯦꯜ ꯇꯧꯔꯕꯥ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯗꯤꯂꯦꯇꯔꯁꯤꯡ: ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯍꯟꯊꯍꯅꯕꯥ꯫
  • ꯄꯂꯃꯣꯅꯥꯔꯤ ꯔꯤꯍꯦꯕꯤꯂꯤꯇꯦꯁꯟ: ꯂꯪꯁꯀꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯈꯠꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯐꯁ꯭ꯇꯥꯏꯂꯒꯤ ꯄꯥꯎꯇꯥꯀꯁꯤꯡ꯫
  • ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ: ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯁ꯭ꯠ ꯔꯤꯁꯣꯔꯠ ꯑꯣꯄꯁꯟ ꯑꯃꯅꯤ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ: ꯁꯤꯔꯣꯂꯤꯃꯁꯅꯥ ꯀꯤꯗꯅꯤꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏꯅꯐꯦꯛꯁꯅꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯍꯧꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤꯒꯤ ꯀꯥꯟꯅꯕꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯀꯥꯟꯅꯕꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯩꯃꯤꯟꯅꯕꯗꯥ ꯈꯉꯒꯗꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯂꯩꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯂꯃꯣꯅꯣꯂꯣꯖꯤꯁ꯭ꯠ ꯑꯗꯨꯒꯥ ꯅꯛꯅꯅꯥ ꯊꯕꯛ ꯇꯧꯃꯤꯟꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ (progression) ꯍꯥꯌꯕꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯀꯤ ꯈꯣꯡꯖꯦꯜ ꯑꯁꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯒꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯈꯦꯠꯅꯩ꯫ ꯃꯁꯤ ꯐꯦꯛꯇꯔ ꯀꯌꯥꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ:

  • ꯃꯁꯤ ꯅꯍꯥꯛꯅꯥ ꯀꯔꯤ ꯃꯈꯂꯒꯤ LAM ꯂꯩꯕꯒꯦ ꯍꯥꯌꯕꯗꯨꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯆꯍꯤ (ꯃꯤꯑꯣꯏ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯆꯤꯜꯂꯀꯄꯥ ꯂꯦꯄꯈꯤ)꯫
  • ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯗꯥ ꯀꯔꯝꯅꯥ ꯔꯦꯁꯄꯣꯟꯁ ꯇꯧꯕꯒꯦ꯫

ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯗꯥ ꯀꯤꯒꯅꯨ꯫ ꯑꯌꯥꯝꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡ (ꯆꯥꯎꯔꯥꯛꯅꯥ 64%)ꯗꯤ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 20 ꯅꯠꯠꯔꯒꯥ ꯃꯁꯤꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯐꯥꯎꯕꯗꯥ ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯒꯤ ꯃꯊꯧ ꯇꯥꯔꯣꯏ꯫ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯜꯂꯦ꯫ ꯃꯤꯑꯣꯏ 90%ꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯂꯥꯏꯑꯣꯡ ꯈꯪꯗꯣꯛꯂꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 10ꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯤꯡꯂꯤ꯫

ꯀꯗꯥꯏꯗꯥ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯒꯗꯒꯦ꯫

ꯑꯁꯤꯒꯨꯝꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯕꯨ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ:

  • ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯂꯩꯕꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
  • ꯂꯦꯡ-ꯑꯣꯠꯄꯥ ꯉꯃꯗꯕꯥ ꯀꯣꯛ ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫
  • ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯗꯨꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ ꯈꯨꯗꯛꯇꯥ ꯏ.ꯇꯤ.ꯌꯨ.(ꯏꯃꯔꯖꯦꯟꯁꯤ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇ ꯌꯨꯅꯤꯠ)ꯗꯥ ꯆꯠꯂꯨ:

  • ꯈꯪꯍꯧꯗꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯅꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ꯫
  • ꯏ ꯊꯣꯀꯄꯥ꯫
  • ꯈꯣꯡ, ꯂꯤꯞ ꯅꯠꯠꯔꯒꯥ ꯅꯥꯀꯣꯡꯗꯥ ꯕ꯭ꯂꯨ ꯗꯤꯁꯀꯂꯔ ꯑꯣꯏꯕꯥ (cyanosis)꯫

ꯂꯝ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯔꯥ?

ꯃꯁꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯒꯤ ꯈꯨꯗꯣꯡꯆꯥꯗꯕꯥ ꯑꯃꯅꯤ꯫ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯕꯨ ꯀꯦꯟꯁꯔ ꯍꯥꯌꯅꯥ ꯂꯧꯅꯗꯦ . ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ ꯃꯁꯤꯗꯥ ꯀꯦꯟꯁꯔꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯃꯒꯨꯟ ꯈꯔꯥ ꯂꯩ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ, ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯒꯤ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯀꯤꯗꯅꯤꯗꯥ ꯁꯟꯗꯣꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯕꯗꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯒꯨꯝꯅꯥ ꯎꯕꯥ ꯐꯪꯗꯦ, ꯑꯗꯨꯕꯨ ꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡꯒꯨꯝꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯂꯤꯚꯔ ꯅꯠꯠꯔꯒꯥ ꯕ꯭ꯔꯦꯅꯒꯨꯝꯕꯥ ꯑꯣꯔꯒꯥꯅꯁꯤꯡꯗꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯉꯃꯗꯦ꯫

ꯅꯍꯥꯛꯅꯥ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯕꯥ ꯈꯉꯕꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯈꯥꯗꯒꯤ ꯂꯩꯃꯥꯌ ꯑꯗꯨ ꯆꯦꯟꯊꯔꯀꯄꯒꯨꯝ ꯐꯥꯑꯣꯕꯁꯤ ꯅꯣꯔꯃꯦꯂꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯉꯗꯤ ꯅꯉꯅꯥ ꯅꯠꯇꯦ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔ, ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯃꯔꯨꯞ-ꯃꯄꯥꯡꯁꯤꯡꯒꯤ ꯃꯇꯦꯡꯅꯥ ꯅꯍꯥꯛꯅꯥ ꯐꯤꯚꯝ ꯑꯁꯤ ꯊꯦꯡꯅꯕꯥ ꯉꯃꯒꯅꯤ꯫

ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫

  • LAM ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯤ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯍꯦꯟꯅꯥ ꯊꯣꯀꯏ꯫
  • ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯤ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯀꯣꯛ ꯆꯤꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯈꯣꯡ ꯍꯥꯝꯕꯥ ꯑꯁꯤꯅꯤ꯫
  • ꯃꯁꯤ ꯖꯤꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯣꯏꯔꯤ, ꯅꯍꯥꯛꯀꯤ ꯑꯁꯣꯌꯕꯥ ꯅꯠꯇꯦ꯫
  • ꯃꯄꯨꯡꯐꯥꯅꯥ ꯂꯥꯌꯦꯡꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯁꯨ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯌꯥꯝꯅꯥ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯔꯦꯁ꯭ꯄꯤꯔꯦꯇꯔꯤ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯗꯨꯒꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯀꯟꯇꯦꯛꯇ ꯇꯧ꯫
  • ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯑꯦꯃꯔꯖꯦꯟꯁꯤꯁꯤꯡꯗꯥ ꯈꯨꯗꯛꯇꯥ ꯏ.ꯇꯤ.ꯌꯨ.

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ., ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ, ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯅꯨꯄꯤꯒꯤ ꯂꯥꯌꯅꯥ, ꯁꯤꯔꯣꯂꯤꯃꯁ, ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯂꯥꯌꯅꯥ꯫
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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ꯑꯩꯈꯣꯌꯅꯥ LAM (Lymphangioleiomyomatosis) ꯀꯧꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ?
ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ꯫জুলাই ৭, ২০২৬

ꯑꯩꯈꯣꯌꯅꯥ LAM (Lymphangioleiomyomatosis) ꯀꯧꯕꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯒꯗ꯭ꯔꯥ?

ꯃꯃꯤꯡ ꯑꯁꯤ ꯈꯔꯥ ꯄꯥꯕꯥ ꯌꯥꯝꯅꯥ ꯂꯨꯏ, ꯅꯠꯇꯦ? "ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ"꯫ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ, ꯃꯁꯤꯕꯨ ꯂꯝ ꯍꯥꯌꯅꯥ ꯀꯧꯔꯁꯤ . ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯤ ꯑꯌꯥꯝꯕꯅꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯃꯤꯡ ꯑꯃꯥ ꯇꯥꯕꯗꯥ ꯂꯥꯡꯇꯛꯅꯕꯥ ꯄꯣꯀꯄꯥ ꯑꯁꯤ ꯂꯧꯁꯤꯅꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯑꯥꯔꯇꯤꯀꯜ ꯑꯁꯤꯗꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯁꯨꯞꯅꯒꯤ ꯀꯔꯤ ꯍꯥꯌꯔꯤꯕꯒꯦ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, LAM ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯀꯤ ꯃꯅꯨꯡꯗꯥ ꯂꯩꯕꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯍꯧꯔꯀꯄꯥ ꯃꯇꯃꯅꯤ꯫ ꯑꯄꯤꯀꯄꯥ ꯇꯤꯎꯃꯔꯁꯤꯡꯒꯨꯝꯅꯥ꯫ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯄꯨꯟꯅꯥ ꯀꯨꯄꯁꯤꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯇꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯀꯧꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯕꯨꯕꯂꯒꯨꯝꯕꯥ ꯁ꯭ꯠꯔꯀꯆꯔꯁꯤꯡ ꯁꯦꯝꯃꯤ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯇꯤꯎꯃꯔꯁꯤꯡ ꯑꯁꯤ ꯍꯦꯅꯒꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯃꯈꯣꯌꯅꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯂꯪꯁꯀꯤ ꯇꯤꯁꯨꯁꯤꯡꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫

ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯪꯁ ꯈꯛꯇꯗꯥ ꯂꯤꯃꯤꯠ ꯂꯩꯇꯦ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯇꯤꯎꯃꯔꯁꯤꯡ ꯑꯁꯤ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯁꯨ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯔꯤꯕꯥ ꯖꯤꯅꯁꯤꯡꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯊꯣꯀꯄꯅꯤ꯫

ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯤꯡꯁꯤꯡꯕꯥ ꯃꯊꯧ ꯇꯥꯏ ꯃꯗꯨꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯆꯍꯤ 20ꯗꯒꯤ 40 ꯐꯥꯎꯕꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯃꯤꯔꯣꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯍꯣꯔꯃꯣꯟ ꯏꯁ꯭ꯠꯔꯣꯖꯦꯅꯒꯥ ꯃꯔꯤ ꯂꯩꯅꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯥ ꯂꯩ ꯍꯥꯌꯅꯥ ꯂꯧꯏ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯁꯤꯡꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤ ꯂꯩ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯈꯜ ꯑꯅꯤꯗꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯌꯥꯏ, ꯑꯅꯤꯁꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯔꯥ ꯈꯦꯠꯅꯕꯥ ꯂꯩ꯫

ꯂꯝ ꯃꯈꯜ꯫ ꯏꯆꯝ ꯆꯝꯕꯥ ꯃꯁꯛ ꯇꯥꯀꯄꯥ꯫
ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.-ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ ꯃꯁꯤ ꯇꯤꯎꯕꯔꯁ ꯁ꯭ꯛꯂꯦꯔꯣꯁꯤꯁ ꯀꯧꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯊꯣꯀꯄꯥ LAM ꯃꯈꯜ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯃꯁꯤ ꯑꯇꯣꯞꯄꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯒꯤ ꯁꯔꯨꯛ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯏ꯫
ꯁ꯭ꯄꯣꯔꯦꯗꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝꯃꯁꯤꯒꯤ ꯃꯈꯜ ꯑꯁꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯔꯦꯟꯗꯝ ꯖꯦꯅꯦꯇꯤꯛ ꯆꯦꯟꯖ (ꯃ꯭ꯌꯨꯇꯦꯁꯟ) ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯃꯁꯤ ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯅꯠꯇꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯁꯤꯒꯤ ꯃꯈꯜ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯁꯟꯗꯣꯔꯀꯄꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯃꯊꯧ ꯇꯥꯗꯦ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯌꯅꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯑꯇꯩ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ, ꯍꯥꯌꯕꯗꯤ ꯑꯦꯖꯃꯥꯒꯥ ꯌꯥꯝꯅꯥ ꯃꯥꯟꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯁꯤ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯃꯇꯝ ꯈꯔꯥ ꯆꯪꯂꯝꯕꯥ ꯌꯥꯏ꯫ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯅꯤ꯫

  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ (dyspnea): ꯑꯍꯥꯅꯕꯗꯥ ꯎꯕꯥ ꯐꯪꯗ꯭ꯔꯕꯁꯨ, ꯑꯁꯣꯛ-ꯑꯄꯟ ꯑꯁꯤ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯇꯦꯅꯕꯥ ꯂꯝꯕꯤꯗꯥ ꯆꯠꯄꯥ ꯃꯇꯃꯗꯁꯨ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ, ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯗꯥ ꯆꯠꯄꯥ ꯃꯇꯃꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯁꯤ ꯌꯥꯎꯕꯥ ꯌꯥꯏ꯫
  • ꯍꯨꯏ-ꯍꯧꯗꯣꯡ (wheezing): ꯈꯣꯡꯒꯤ ꯃꯅꯨꯡꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯇꯔꯨ-ꯇꯅꯥꯅꯕꯥ ꯈꯣꯟꯖꯦꯜ ꯑꯃꯅꯤ꯫
  • ꯈꯣꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ (chest pain): ꯈꯪꯍꯧꯗꯅꯥ, ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ (chest pain) ꯂꯩꯕꯥ ꯌꯥꯏ꯫
  • ꯀꯣꯛ ꯆꯤꯀꯄꯥ: ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ (persistent dry cough)꯫
  • ꯏ ꯁꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ‘ꯆꯥꯏꯜ’ (chail) : ꯆꯥꯏꯜ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯗꯥꯏꯖꯦꯁ꯭ꯇꯤꯚ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯃ꯭ꯌꯨꯀꯁ ꯐ꯭ꯂꯨꯏꯗ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯃꯆꯨ ꯁꯉ꯭ꯒꯣꯝ ꯑꯣꯏ꯫

ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯂꯝ ꯑꯁꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯀꯔꯤꯅꯣ?

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ ꯃꯁꯤ ꯖꯤꯅꯁꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯣꯏꯔꯤ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯱ ꯑꯃꯁꯨꯡ ꯇꯤ.ꯑꯦꯁ.ꯁꯤ.꯲ ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯅꯤ ꯂꯩ꯫ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯔꯤꯕꯥ ‘ꯒꯥꯔꯗꯤꯌꯟ’ꯒꯨꯝꯅꯥ ꯑꯣꯏꯔꯤ꯫ ꯃꯈꯣꯌꯕꯨ ‘ꯇꯤꯎꯃꯔ ꯁꯞꯞꯔꯦꯁꯔ’ ꯖꯤꯅꯁꯤꯡ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯍꯥꯌꯕꯗꯤ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯊꯕꯛ ꯑꯁꯤ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯃꯊꯧ ꯇꯥꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯇꯤꯎꯃꯔ ꯁꯦꯝꯕꯥ ꯊꯤꯡꯕꯅꯤ꯫

LAM ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯖꯤꯅꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯗꯥ, TSC1 ꯅꯠꯠꯔꯒꯥ TSC2ꯗꯥ ꯑꯁꯣꯌꯕꯥ ꯑꯃꯥ, ꯅꯠꯠꯔꯒꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯥ ꯂꯩ꯫ ꯑꯗꯨꯗꯒꯤ ꯑꯗꯨꯒꯨꯝꯕꯥ ‘ꯒꯥꯔꯗꯁꯤꯡ’ ꯑꯗꯨꯅꯥ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯗꯦ꯫ ꯃꯁꯤꯒꯤ ꯃꯍꯩ ꯑꯣꯏꯅꯥ ꯁ꯭ꯃꯨꯗ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯈꯥꯌꯗꯣꯀꯄꯥ ꯍꯧꯔꯀꯏ, ꯃꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯈꯤꯕꯥ ꯇꯤꯎꯃꯔ ꯃꯈꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯦꯃꯒꯠꯂꯤ꯫

  • ꯂꯪꯁꯀꯤ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ꯫
  • ꯀꯤꯗꯅꯤꯒꯤ ꯇꯤꯎꯃꯔꯁꯤꯡ (ꯑꯦꯟꯖꯤꯑꯣꯃꯥꯌꯣꯂꯤꯄꯣꯃꯥꯁ) .
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯒꯤ ꯇꯤꯎꯃꯔꯁꯤꯡ꯫

ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯑꯣꯏꯊꯣꯀꯄꯥ ꯌꯥꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯀꯔꯤꯅꯣ?

LAMꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯑꯁꯤ ꯂꯪꯁ (neumothorax) . ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯕꯕꯂꯒꯨꯝꯕꯥ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯃꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ, ꯃꯗꯨ ꯈꯪꯍꯧꯗꯅꯥ ꯊꯨꯒꯥꯌꯗꯨꯅꯥ, ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯆꯦꯁ꯭ꯠ ꯋꯥꯂꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯃꯐꯝ ꯑꯗꯨꯗꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯌꯥꯍꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯂꯪꯁ ꯑꯗꯨ ꯁꯣꯀꯍꯜꯂꯤ꯫ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤꯁꯤꯡꯒꯤ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯦꯡꯅꯒꯅꯤ꯫ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ, LAM ꯑꯁꯤ ꯑꯍꯥꯅꯕꯥ ꯑꯣꯏꯅꯥ ꯂꯪꯁ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯈꯪꯗꯣꯀꯏ꯫

ꯑꯇꯩ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯁꯨ ꯂꯩꯕꯥ ꯌꯥꯏ:

  • ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ‘ꯆꯥꯏꯂꯣꯁ’ ꯐ꯭ꯂꯨꯏꯗ (chylothorax) ꯊꯨꯒꯥꯌꯕꯥ (chylothorax)
  • ꯂꯪꯁꯀꯤ ꯑꯀꯣꯌꯕꯗꯥ ꯑꯇꯩ ꯐ꯭ꯂꯨꯏꯗ ꯑꯦꯛꯌꯨꯃꯨꯂꯦꯁꯟ (ꯄ꯭ꯂꯤꯎꯔꯦꯜ ꯏꯐ꯭ꯌꯨꯁꯟ)
  • ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯑꯀꯥꯌꯕꯥ ꯄꯤꯕꯥ꯫

ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯃꯇꯧ ꯀꯔꯝꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.

ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯇꯥꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯀꯄꯨ ꯌꯦꯡꯁꯤꯜꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯍꯥꯛꯅꯥ ꯃꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯑꯃꯥ ꯇꯧꯅꯕꯥ ꯑꯣꯔꯗꯔ ꯇꯧꯒꯅꯤ꯫

ꯆꯥꯡꯌꯦꯡ ꯃꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯑꯗꯣꯝꯅꯥ ꯀꯔꯤ ꯇꯧꯔꯤꯕꯒꯦ?
ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯪꯁꯁꯤꯡ ꯑꯗꯨ ꯀꯌꯥꯝ ꯐꯖꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯅꯨꯡꯁꯤꯠ ꯁꯤꯠꯄꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯀꯄꯥ ꯌꯥꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯂꯦꯄꯊꯣꯀꯏ꯫
ꯄꯂꯁ ꯑꯣꯛꯁꯤꯃꯦꯠꯔꯤ ꯇꯧꯕꯥ꯫ ꯃꯈꯣꯌꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠꯁꯥꯗꯥ ꯀ꯭ꯂꯤꯄꯒꯨꯝꯕꯥ ꯄꯣꯠꯁꯛ ꯑꯃꯥ ꯊꯥꯗꯣꯀꯏ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫
ꯏꯃꯦꯖꯤꯡ (ꯁ꯭ꯀꯦꯅꯁꯤꯡ) ꯴. ꯁꯤ.ꯇꯤ.ꯁ꯭ꯀꯦꯟ ꯑꯃꯅꯥ , ꯃꯔꯨꯑꯣꯏꯅꯥ HRCT (ꯍꯥꯏ-ꯔꯤꯖꯣꯂꯨꯁꯟ ꯁꯤ.ꯇꯤ.) ꯁ꯭ꯀꯦꯟ ꯑꯃꯅꯥ ꯂꯪꯁꯇꯥ ꯂꯩꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯁꯤꯁ꯭ꯇꯦꯃꯁꯤꯡ ꯑꯗꯨ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫
ꯚꯤ.ꯏ.ꯖꯤ.ꯑꯦꯐ.-ꯗꯤ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ꯫ ꯚꯤ.ꯏ.ꯖꯤ.ꯑꯦꯐ.-ꯗꯤ.ꯅꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯅꯤ꯫ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯏꯗꯥ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯪꯗꯣꯀꯄꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
ꯂꯪꯁꯀꯤ ꯕꯥꯏꯑꯣꯞꯁꯤ ꯇꯧꯕꯥ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯇꯣꯞꯄꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯑꯗꯨ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯗꯤ, ꯂꯪꯁꯇꯒꯤ ꯇꯤꯁ꯭ꯌꯨꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯁꯔꯨꯛ ꯑꯃꯥ ꯂꯧꯊꯣꯀꯏ ꯑꯃꯁꯨꯡ ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫ ꯃꯁꯤ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯁ꯭ꯀꯣꯄꯤ ꯅꯠꯠꯔꯒꯥ ꯚꯤ.ꯑꯦ.ꯇꯤ.ꯑꯦꯁ .

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?

ꯑꯍꯥꯅꯕꯗꯥ, ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯤ ꯍꯤꯗꯥꯛ ꯂꯥꯡꯊꯛ ꯑꯃꯠꯇꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯐꯪꯗ꯭ꯔꯤ꯫ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯍꯧꯖꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯕꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯕꯥ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯂꯍꯟꯗꯅꯕꯥ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯂꯩꯔꯦ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ . ꯃꯁꯤꯕꯨ ꯔꯦꯄꯥꯃꯥꯏꯁꯤꯟ ꯍꯥꯌꯅꯥꯁꯨ ꯀꯧꯏ꯫ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯃꯁꯜ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯒ꯭ꯔꯣꯊ ꯊꯤꯡꯗꯨꯅꯥ ꯊꯕꯛ ꯇꯧꯏ꯫ ꯃꯁꯤꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯊꯝꯕꯥ ꯉꯝꯃꯤ ꯑꯃꯁꯨꯡ ꯀꯤꯗꯅꯤ ꯑꯃꯁꯨꯡ ꯂꯤꯝꯐꯦꯇꯤꯛ ꯁꯤꯁ꯭ꯇꯦꯃꯗꯥ ꯂꯩꯕꯥ ꯇꯤꯎꯃꯔꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯅꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯍꯥꯌꯕꯗꯤ:

  • ꯑꯣꯛꯁꯤꯖꯦꯟ ꯊꯦꯔꯥꯄꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯝꯅꯥ ꯂꯩꯔꯕꯗꯤ꯫
  • ꯏꯅꯍꯦꯜ ꯇꯧꯔꯕꯥ ꯕ꯭ꯔꯣꯉ꯭ꯀꯣꯗꯤꯂꯦꯇꯔꯁꯤꯡ: ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯍꯟꯊꯍꯅꯕꯥ꯫
  • ꯄꯂꯃꯣꯅꯥꯔꯤ ꯔꯤꯍꯦꯕꯤꯂꯤꯇꯦꯁꯟ: ꯂꯪꯁꯀꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯈꯠꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯐꯁ꯭ꯇꯥꯏꯂꯒꯤ ꯄꯥꯎꯇꯥꯀꯁꯤꯡ꯫
  • ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ: ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯁꯤꯡꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯃꯗꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯁ꯭ꯠ ꯔꯤꯁꯣꯔꯠ ꯑꯣꯄꯁꯟ ꯑꯃꯅꯤ꯫

ꯃꯔꯨꯑꯣꯏꯕꯥ: ꯁꯤꯔꯣꯂꯤꯃꯁꯅꯥ ꯀꯤꯗꯅꯤꯗꯥ ꯑꯃꯥꯡ-ꯑꯇꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏꯅꯐꯦꯛꯁꯅꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯍꯧꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤꯒꯤ ꯀꯥꯟꯅꯕꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯀꯥꯟꯅꯕꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯩꯃꯤꯟꯅꯕꯗꯥ ꯈꯉꯒꯗꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ꯫

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯂꯩꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯂꯃꯣꯅꯣꯂꯣꯖꯤꯁ꯭ꯠ ꯑꯗꯨꯒꯥ ꯅꯛꯅꯅꯥ ꯊꯕꯛ ꯇꯧꯃꯤꯟꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ (progression) ꯍꯥꯌꯕꯗꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯀꯤ ꯈꯣꯡꯖꯦꯜ ꯑꯁꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯒꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯈꯦꯠꯅꯩ꯫ ꯃꯁꯤ ꯐꯦꯛꯇꯔ ꯀꯌꯥꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ:

  • ꯃꯁꯤ ꯅꯍꯥꯛꯅꯥ ꯀꯔꯤ ꯃꯈꯂꯒꯤ LAM ꯂꯩꯕꯒꯦ ꯍꯥꯌꯕꯗꯨꯒꯤ ꯃꯈꯥ ꯄꯣꯜꯂꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯆꯍꯤ (ꯃꯤꯑꯣꯏ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯦꯅꯣꯄꯣꯖꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯆꯤꯜꯂꯀꯄꯥ ꯂꯦꯄꯈꯤ)꯫
  • ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯗꯥ ꯀꯔꯝꯅꯥ ꯔꯦꯁꯄꯣꯟꯁ ꯇꯧꯕꯒꯦ꯫

ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯗꯥ ꯀꯤꯒꯅꯨ꯫ ꯑꯌꯥꯝꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡ (ꯆꯥꯎꯔꯥꯛꯅꯥ 64%)ꯗꯤ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 20 ꯅꯠꯠꯔꯒꯥ ꯃꯁꯤꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯐꯥꯎꯕꯗꯥ ꯂꯪꯁ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯒꯤ ꯃꯊꯧ ꯇꯥꯔꯣꯏ꯫ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯜꯂꯦ꯫ ꯃꯤꯑꯣꯏ 90%ꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯂꯥꯏꯑꯣꯡ ꯈꯪꯗꯣꯛꯂꯕꯥ ꯃꯇꯨꯡ ꯆꯍꯤ 10ꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯤꯡꯂꯤ꯫

ꯀꯗꯥꯏꯗꯥ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯒꯗꯒꯦ꯫

ꯑꯁꯤꯒꯨꯝꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯕꯨ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ:

  • ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯂꯩꯕꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
  • ꯂꯦꯡ-ꯑꯣꯠꯄꯥ ꯉꯃꯗꯕꯥ ꯀꯣꯛ ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ꯫
  • ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯗꯨꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ ꯈꯨꯗꯛꯇꯥ ꯏ.ꯇꯤ.ꯌꯨ.(ꯏꯃꯔꯖꯦꯟꯁꯤ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇ ꯌꯨꯅꯤꯠ)ꯗꯥ ꯆꯠꯂꯨ:

  • ꯈꯪꯍꯧꯗꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯅꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ꯫
  • ꯏ ꯊꯣꯀꯄꯥ꯫
  • ꯈꯣꯡ, ꯂꯤꯞ ꯅꯠꯠꯔꯒꯥ ꯅꯥꯀꯣꯡꯗꯥ ꯕ꯭ꯂꯨ ꯗꯤꯁꯀꯂꯔ ꯑꯣꯏꯕꯥ (cyanosis)꯫

ꯂꯝ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯔꯥ?

ꯃꯁꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯒꯤ ꯈꯨꯗꯣꯡꯆꯥꯗꯕꯥ ꯑꯃꯅꯤ꯫ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ.ꯕꯨ ꯀꯦꯟꯁꯔ ꯍꯥꯌꯅꯥ ꯂꯧꯅꯗꯦ . ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ ꯃꯁꯤꯗꯥ ꯀꯦꯟꯁꯔꯒꯥ ꯃꯥꯟꯅꯕꯥ ꯃꯒꯨꯟ ꯈꯔꯥ ꯂꯩ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ, ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯒꯤ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯀꯤꯗꯅꯤꯗꯥ ꯁꯟꯗꯣꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯕꯗꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯁꯦꯂꯁꯤꯡꯒꯨꯝꯅꯥ ꯎꯕꯥ ꯐꯪꯗꯦ, ꯑꯗꯨꯕꯨ ꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡꯒꯨꯝꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯂꯤꯚꯔ ꯅꯠꯠꯔꯒꯥ ꯕ꯭ꯔꯦꯅꯒꯨꯝꯕꯥ ꯑꯣꯔꯒꯥꯅꯁꯤꯡꯗꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯉꯃꯗꯦ꯫

ꯅꯍꯥꯛꯅꯥ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯕꯥ ꯈꯉꯕꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯈꯥꯗꯒꯤ ꯂꯩꯃꯥꯌ ꯑꯗꯨ ꯆꯦꯟꯊꯔꯀꯄꯒꯨꯝ ꯐꯥꯑꯣꯕꯁꯤ ꯅꯣꯔꯃꯦꯂꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯉꯗꯤ ꯅꯉꯅꯥ ꯅꯠꯇꯦ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔ, ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯃꯔꯨꯞ-ꯃꯄꯥꯡꯁꯤꯡꯒꯤ ꯃꯇꯦꯡꯅꯥ ꯅꯍꯥꯛꯅꯥ ꯐꯤꯚꯝ ꯑꯁꯤ ꯊꯦꯡꯅꯕꯥ ꯉꯃꯒꯅꯤ꯫

ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫

  • LAM ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯤ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ ꯍꯦꯟꯅꯥ ꯊꯣꯀꯏ꯫
  • ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯤ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯀꯣꯛ ꯆꯤꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯈꯣꯡ ꯍꯥꯝꯕꯥ ꯑꯁꯤꯅꯤ꯫
  • ꯃꯁꯤ ꯖꯤꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯣꯏꯔꯤ, ꯅꯍꯥꯛꯀꯤ ꯑꯁꯣꯌꯕꯥ ꯅꯠꯇꯦ꯫
  • ꯃꯄꯨꯡꯐꯥꯅꯥ ꯂꯥꯌꯦꯡꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯁꯨ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯁꯤꯔꯣꯂꯤꯃꯁꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯌꯥꯝꯅꯥ ꯐꯖꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯅꯍꯥꯛꯀꯤ ꯔꯦꯁ꯭ꯄꯤꯔꯦꯇꯔꯤ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯗꯨꯒꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯀꯟꯇꯦꯛꯇ ꯇꯧ꯫
  • ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯆꯦꯛꯁꯤꯟ-ꯊꯧꯔꯥꯡ ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯑꯦꯃꯔꯖꯦꯟꯁꯤꯁꯤꯡꯗꯥ ꯈꯨꯗꯛꯇꯥ ꯏ.ꯇꯤ.ꯌꯨ.

ꯑꯦꯜ.ꯑꯦ.ꯑꯦꯝ., ꯂꯤꯝꯐꯦꯟꯖꯤꯑꯣꯂꯦꯏꯑꯣꯃꯥꯏꯑꯣꯃꯦꯇꯣꯁꯤꯁ, ꯂꯪꯁꯀꯤ ꯂꯥꯌꯅꯥ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ, ꯅꯨꯄꯤꯒꯤ ꯂꯥꯌꯅꯥ, ꯁꯤꯔꯣꯂꯤꯃꯁ, ꯅ꯭ꯌꯨꯃꯣꯊꯣꯔꯦꯛꯁ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯒꯤ ꯂꯥꯌꯅꯥ꯫
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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