Kodi mukuda nkhawa ndi mawonekedwe a nkhope ya mwana wanu? Tiyeni tikambirane za Binder Syndrome!

Pamene mwana wanu anabadwa, kodi munaona kusintha pang'ono pa mawonekedwe a nkhope yake? Nthawi zina mphuno yake ingawoneke yopyapyala pang'ono, kapena mlomo wake wapamwamba sungakhale pamalo oyenera. Ndizachilendo kuti mayi kapena bambo achite mantha pang'ono akaona chinthu chonga ichi. Koma musadandaule, lero tikambirana za vuto lomwe limasonyeza zizindikiro zofanana, koma si lofala kwambiri, lotchedwa Binder Syndrome.

Kodi Binder Syndrome ndi chiyani? Mwachidule...

Matenda a Binder ndi matenda obadwa nawo osowa omwe amachitika munthu akangobadwa. Amadziwika ndi mafupa pakati pa nkhope, makamaka mphuno ndi nsagwada yapamwamba, osakula bwino. Amafanana ndi momwe makoma ena a nyumba samangidwira bwino. Izi zingapangitse kuti nkhope ya mwana iwoneke mosiyana pang'ono.

Taganizirani izi, mphuno yathu ndi milomo yathu yapamwamba zimapangika chifukwa cha mafupa omwe ali pansi pake. Chifukwa chake mafupa amenewo akasiya kukula, mawonekedwe awo amasintha. Ana ena amatha kupuma movutikira chifukwa cha vutoli, ndipo amathanso kukhala ndi mavuto pakudya, makamaka poyamwitsa . Koma nkhani yabwino ndi yakuti, pali mankhwala a izi. Nthawi zambiri, mwanayo akakula pang'ono, ndiko kuti, akafika msinkhu waunyamata (nthawi zambiri pakati pa zaka 15-19), mafupawa amatha kusinthidwa ndipo mawonekedwe a nkhope amatha kubwezeretsedwanso kudzera mu opaleshoni ya nkhope ndi nsagwada (`maxillofacial surgery`) .

Kodi pali mayina ena a Binder Syndrome?

Inde, nthawi zina madokotala amagwiritsa ntchito mayina ena pa vutoli. Ndi bwino kudziwa chifukwa mungamvenso mayina awa:

• Binder phenotype - Ili ndi dzina lina la Binder syndrome.
• Binder mtundu wa nasomaxillary dysplasia
• Kusokonezeka kwa mphuno ya m'mphuno (Maxillonasal dysplasia)
• Kuchepa kwa mpweya m'mitsempha ya nasomaxillary

Ngakhale mayina awa angawoneke ovuta pang'ono, onse amatanthauza chinthu chimodzi.

Kodi vuto limeneli lotchedwa Binder Syndrome ndi lofala bwanji?

Izi ndi zachilendo kwambiri . Malinga ndi malipoti ena, vutoli limapezeka mwa ana ochepera m'modzi mwa ana 10,000 obadwa kumene. Choncho musachite mantha ndi izi. Koma, ngakhale kuti sizichitika kawirikawiri, ndikofunikira kudziwa za izi.

Kodi zizindikiro za Binder Syndrome ndi ziti?

Chizindikiro chachikulu cha vutoli ndi kusakula bwino pakati pa nkhope . Chifukwa cha zimenezi, nkhope ya mwana ikhoza kusonyeza kusintha kumeneku:

• Mphuno imakhala yathyathyathya, ndipo mlomo wapamwamba umakhala wathyathyathya . Zingawoneke ngati mphuno yalowa mkati.
• Nsagwada yapansi imatuluka patsogolo.Zikuoneka motere. Kuoneka kumeneku kumachitika chifukwa nsagwada yapamwamba imalowa mkati ndipo nsagwada yapansi imatulukira patsogolo.
• Mano apamwamba ndi apansi sagwirizana bwino (malocclusion) . Izi zingayambitse mavuto pakudya ndi kulankhula.
• Mphuno zimakhala ndi mawonekedwe a triangle kapena crescent .

Izi ndi zizindikiro zodziwika kwambiri. Komabe, kuwonjezera apo, mutha kuwonanso zizindikiro zotsatirazi nthawi zina :

• Mkamwa wosweka .
• Zilema za mtima zobadwa nazo .
• Mavuto a kumva .
• Kulephera kwa nzeru .
• Kusokonekera kwa msana .
• Maso opingasa kapena opingasa .

Si ana onse omwe ali ndi zizindikiro zonsezi. Ana ena angakhale ndi zizindikiro zoyambira zokha.

N’chifukwa chiyani matenda a Binder amachitika? Kodi zimayambitsa chiyani?

Kunena zoona, akatswiri sanadziwebe chomwe chimayambitsa izi . Nthawi zambiri, ana amakhala ndi vutoli popanda chifukwa chomveka.

Komabe, popeza ana angapo m'mabanja ena ali ndi vutoli, akukayikiridwa kuti pakhoza kukhala zinthu zina zokhudzana ndi majini, zomwe ndi zotsatira za majini . Komabe, izi sizinatsimikizidwebe mokwanira.

Kuphatikiza apo, ofufuza amakhulupirira kuti zinthu zingapo zachilengedwe zingathandizenso. Zinthu zimenezi ndi monga:

• Kugwiritsa ntchito mowa kwa amayi panthawi ya mimba.
• Kumwa mankhwala ena panthawi ya mimba. Zitsanzo zake ndi monga mankhwala oletsa khunyu otchedwa phenytoin (Dilantin®, Phenytek®) ndi mankhwala ochepetsa magazi otchedwa warfarin (Coumadin®, Jantoven®). (Mankhwalawa ayenera kumwedwa moyang'aniridwa ndi dokotala ngati pakufunika kutero, koma chisamaliro chapadera chiyenera kutengedwa panthawi ya mimba.)
• Kusowa kwa Vitamini K panthawi ya mimba.
• Kuvulala mutu kapena nkhope panthawi yobereka.

Izi ndi zinthu zomwe zikudziwika kuti ndi zoopsa.

Kodi madokotala amazindikira bwanji Binder Syndrome?

Madokotala amayamba kukayikira vutoli poyang'ana mawonekedwe a nkhope ya mwana . Kenako, kuti atsimikizire kapena kuchotsa kukayikirako, amachita mayeso apadera omwe amatha kuwona bwino kapangidwe ka mafupa a nkhope . Awa amatchedwa:

• Kujambula kwa CT
• Kujambula kwa MRI (`MRI`)
• Kujambula kwa Ultrasound (`ultrasound`)

Kudzera mu ma scan amenewa, titha kuzindikira molondola kuti mafupa a nkhope sakukula bwino.

Kodi mankhwala a Binder Syndrome ndi ati?

Chithandizo cha izi chimasiyana malinga ndi mwana, komanso chimadalira kuopsa kwa zizindikiro.Zimasiyana. Pali njira ziwiri zazikulu zochizira:

1. Chisamaliro cha mano:

• Izi zimaphatikizapo kuyika mawaya (`braces`) mkamwa kuti nsagwada ndi mano zigwirizane bwino .
• Nthawi zina, ngati zizindikiro sizili zazikulu kwambiri, chithandizo cha mano ichi chokha chingakhale chokwanira.
• Nthawi zina, chithandizochi chingafunike kuchitidwa opaleshoni isanayambe kapena itatha.

2. Opaleshoni:

• Iyi ndiyo njira yaikulu yochiritsira. Dokotala wochita opaleshoni ya mutu ndi nkhope (dokotala yemwe ndi katswiri pa chigaza ndi nkhope) ndiye amachita opaleshoni imeneyi.
• Pankhaniyi, mawonekedwe a mphuno amasinthidwa pogwiritsa ntchito mafupa, cartilage, kapena zinthu zopangidwa kuchokera m'thupi la mwana . Izi zimatchedwanso rhinoplasty .
• Komanso, opaleshoni yotchedwa Le Fort I kapena II osteotomy ingathe kuchitidwa kuti nsagwada yapamwamba ikhale pamalo oyenera. Izi ndi opaleshoni zovuta pang'ono, koma madokotala odziwa bwino ntchito amatha kuchita bwino.
• Madokotala nthawi zambiri amalimbikitsa kudikira mpaka mafupa a nkhope ya mwana atasiya kukula asanayambe opaleshoniyi, yomwe nthawi zambiri imakhala yapakati pa zaka 15 ndi 19. Izi zili choncho chifukwa ngati itachitika isanafike nthawi imeneyo, mavuto amatha kubwereranso pamene mafupawo akupitirira kukula.

Chofunika: Si ana onse omwe angafunike chithandizo chonsechi. Ana ena angafunike chithandizo chimodzi chokha. Izi zidzatsimikiziridwa ndi gulu lachipatala atatha kumufufuza mwanayo.

Kodi vuto ili lotchedwa Binder Syndrome lingapewedwe?

Popeza chifukwa chenicheni cha izi sichikudziwika, sizingatheke kutsimikizira kuti zitha kupewedwa kotheratu .

Komabe, ngati muli ndi pakati, mungachepetse chiopsezo chanu chokhala ndi vutoli pang'ono pochepetsa kukhudzana ndi zinthu zina zachilengedwe zomwe takambirana kale. Mutha kulankhula ndi dokotala wanu za izi:

• Chitetezo cha mankhwala panthawi ya mimba , makamaka phenytoin ndi warfarin (musamwe mankhwala aliwonse pokhapokha ngati dokotala wakupatsani, ndipo ngati mwakupatsani, lankhulani ndi dokotala wanu za izi).
• Za kusowa kwa mavitamini, makamaka kusowa kwa vitamini K. Ndikofunikira kwambiri kupeza zakudya zoyenera panthawi ya mimba.

Kodi chiyembekezo cha mwana yemwe ali ndi Binder Syndrome ndi chotani?

Iyi ndi nkhani yabwino kwambiri. Pali chiyembekezo chabwino pa nkhaniyi .

Ana ambiri safunikira chithandizo china chilichonse pambuyo pa opaleshoni ya rhinoplasty. Amatha kupuma bwino, kudya bwino, ndipo nkhope zawo zimaoneka bwino akachitidwa opaleshoni.N'zotheka. Choncho palibe chodetsa nkhawa, koma chofunika kwambiri ndikupempha upangiri wa dokotala mwamsanga.

Ndi mafunso ati omwe ndiyenera kufunsa dokotala wanga?

Ngati mwapeza kuti inu kapena mwana wanu ali ndi Binder Syndrome, mutha kufunsa dokotala wanu mafunso ngati awa. Mafunso awa adzakuthandizani kumvetsetsa vutoli:

• "Dokotala, kodi n’chiyani chomwe chingakhale chifukwa chachikulu cha vuto la mwana wanga? "
• " Ndi mayeso ati omwe amachitidwa kuti adziwe molondola vuto la Binder Syndrome? "
• " Ndi njira ziti zochiritsira izi? Ndi chiyani chomwe chili chabwino kwa mwana wanga?"
• " Kodi pali mwayi wotani woti mungafunikenso chithandizo mtsogolo? "
• "Ngati ndili ndi mwana wina, kodi pali mwayi wotani woti nayenso akhale ndi vutoli? "

Kuwonjezera pa mafunso awa, funsani dokotala wanu chilichonse chomwe muli nacho m'maganizo mwanu.

Ndi matenda ena ati omwe ali ndi zizindikiro zofanana ndi za Binder Syndrome?

Palinso matenda ena angapo omwe amakhudza kukula kwa mafupa a nkhope ndipo amafanana ndi matenda a Binder. Madokotala nawonso akuda nkhawa ndi izi. Zitsanzo zina ndi izi:

• Acrodysostosis
• Matenda a Apert
• Chondrodysplasia punctata, mtundu wa rhizomelic (CDPR)
• Matenda a warfarin a fetal (matenda omwe amayamba chifukwa chogwiritsa ntchito warfarin panthawi ya mimba)
• Matenda a Keutel
• Matenda a Stickler

Ingodziwani mayina awa. Madokotala ndi omwe adzadziwe matenda enieni a mwana wanu.

Pomaliza, zinthu zoti muzikumbukira (Uthenga Wopita Nawo Kunyumba)

Chabwino, tiyeni tifotokoze mwachidule zomwe takambirana:

• Binder Syndrome ndi vuto lobadwa nalo losowa kwambiri .
• Izi zimapangitsa kuti mafupa achepe pakati pa nkhope, makamaka mphuno ndi nsagwada yapamwamba . Izi zimapangitsa kuti pakhale mphuno yathyathyathya komanso nsagwada yapansi yomwe ikutuluka.
• Chifukwa chenicheni cha izi sichikudziwika , koma majini ndi zinthu zachilengedwe zitha kukhala ndi gawo.
• Vutoli lingathe kuchiritsidwa bwino ndi chithandizo cha orthodontic ndi/kapena opaleshoni .
• Ana ambiri amapeza zotsatira zabwino kwambiri akalandira chithandizo ndipo amatha kukhala ndi moyo wabwinobwino.

Ngati muli ndi nkhawa kapena nkhawa zokhudza maonekedwe a nkhope ya mwana wanu, chonde pitani kwa dokotala woyenerera mwamsanga . Chofunika kwambiri si kuchita mantha, koma kupeza chidziwitso ndi chitsogozo choyenera. Madokotala alipo kuti akuthandizeni.

Ndikukhulupirira kuti izi zikuthandizani. Ndikufunirani inu ndi banja lanu thanzi labwino!

Matenda a Binder , Matenda a Binder, kufooka kwa nkhope, matenda obadwa nawo, thanzi la ana, opaleshoni ya maxillofacial, opaleshoni ya craniofacial