Ngaba kukho umntu omdala kusapho lwakho, mhlawumbi umama, utata, okanye utatomkhulu noomakhulu, osoloko elibaleka aze abonakale exhalabile kancinci? Ngaba kubonakala ngathi imilenze yakhe irhuqa phantsi xa ehamba, kwaye umzimba wakhe ubonakala uqinile? Ngaba ngamanye amaxesha ukhe uve izinto ezinje, "Ngubani lo uhleli esitulweni?" xa kungekho mntu ungomnye egumbini? Xa ubona izinto ezinje, mhlawumbi uziva usoyika. Usenokuzibuza ukuba esi sisifo se-Alzheimer, okanye enye into. Namhlanje sithetha ngemeko eza nezi mpawu kunye, kodwa engathethwa kangako kuluntu. Leyo yiLewy Body Dementia.
Ngamafutshane, yintoni iLewy Body Dementia (LBD)?
Kulungile, masiyibeke ngokulula. Sinezigidi zeeseli engqondweni yethu. Ezi seli ziyanxibelelana ukulawula yonke into esiyicingayo, esiyenzayo, nesiyenzayo. Kwimeko ebizwa ngokuba yiLewy body dementia (LBD), uhlobo olungaqhelekanga lweproteni ebizwa ngokuba yiLewy bodies luqala ukuqokelelana ngaphakathi kweeseli zengqondo. Cinga ngayo njengenqwaba yenkunkuma endlwini yethu. Oku kuqokelelana kweeproteni ezingafunekiyo konakalisa iiseli zengqondo kwaye kuzithintele ekusebenzeni kakuhle. Oku kuchaphazela inkumbulo, ukucinga, iintshukumo zomzimba, kunye nokuziphatha.
Esi sisifo esiqhubekayo . Oko kukuthi, iimpawu aziveli ngequbuliso. Ziqala kancinci kancinci kwaye zisiba mandundu ngokuhamba kwexesha. I-LBD lolona hlobo lwesibini oluxhaphakileyo lwe-dementia kubantu abadala, emva kwesifo se-Alzheimer.
Into ebalulekileyo kukuba, oku akupheleli nje ekwaluphaleni okuqhelekileyo. Le yimeko yezonyango enokunyangeka kwaye ilawulwe. Ngoko ke kubalulekile ukukwazi oku.
Kukho iintlobo ezimbini eziphambili zale LBD.
Ewe, kukho iintlobo ezimbini eziphambili ze-LBD. Iimpawu zazo zombini ziyafana kakhulu. Kodwa umahluko ophambili kukuba zeziphi iimpawu eziqala kuqala. Abanye abantu baqala ngeengxaki zenkumbulo, ngelixa abanye beqala ngezinto ezifana nobunzima bokuhamba kuqala.
Makhe sibone ukuba zeziphi ezi ntlobo zimbini.
| Uhlobo lwe-LBD | Uphawu oluPhambili |
|---|---|
| Isifo sengqondo esixhalabisayo esinemizimba kaLewy (DLB) | Kolu hlobo, iingxaki zokucinga kunye nenkumbulo ziqala kuqala, njengesifo sika-Alzheimer. Iingxaki zokunyakaza, ezifana nokuqina kunye nokungcangcazela, ziqala kamva, okanye zisenokuqala ngexesha elinye neengxaki zenkumbulo. |
| Isifo sikaParkinson sengqondo esixhalabisayo | Kolu hlobo, iingxaki zokuhamba komzimba ziqala kuqala. Zifana nesifo sikaParkinson. Izinto ezifana nokuxhawula izandla, ubunzima bokuhamba, kunye nokuqina komzimba ziza kuqala. Iingxaki zenkumbulo kunye nokucinga ziza kamva, ngamanye amaxesha emva konyaka. |
Zingaba yintoni iimpawu zesi sifo?
I-LBD inokubakho ngeempawu ezahlukeneyo. Ezi mpawu azibonakali ngendlela efanayo kuye wonke umntu. Zinokwahluka kumntu nomntu. Ezinye iimpawu zinokubakho ngenye imini zize ziphele ngolandelayo. Yiyo loo nto isifo sibonakala.
Masizihlube ezi mpawu zibe ziinxalenye.
| Uhlobo oluneempawu | Izinto onokuzibona |
|---|---|
| Iimpawu zokuqonda | |
| Ukubona izinto ezingekhoyo (Iimbono ezingabonakaliyo) | Olu luphawu oluqhelekileyo lwe-LBD. Lukwenza uzive ngathi ubona abantu, izilwanyana, okanye iimilo ezingekhoyo. |
| Ukuguquguquka kwengqwalasela kunye nokuqonda | Ngomzuzu omnye, usenokuba uphaphile kakhulu kwaye uthetha kakhulu, kwaye ngomzuzu olandelayo, usenokuba ulele kakhulu kwaye uphazamisekile. Ezi meko zinokutshintsha kwanangexesha elifanayo lemini. |
| Ukukhubazeka kwenkumbulo kunye nokwenza izigqibo | Ukulibala izinto, ukuba nobunzima bokwenza izigqibo, nokungakwazi ukuthetha. |
| Iimpawu zeNtshukumo | |
| Ukuqina komzimba | Izihlunu ziyaqina, nto leyo eyenza kube nzima ukugoba okanye ukolula amalungu omzimba. |
| Iingxolo | Izandla ezingcangcazelayo, ingakumbi xa uphumle. |
| Ukucotha kokuhamba | Ukuhamba ngesantya esicothayo, ukurhuqa iinyawo, ukuwa rhoqo kunye nokulahlekelwa yibhalansi. Ukungabikho kwembonakalo yobuso. |
| Iingxaki Zokulala | |
| Ingxaki Yokuziphatha Kokulala Kwe-REM | Olu luphawu olubaluleke kakhulu kwasekuqaleni. Izinto ezifana nokukhwaza ulele, ukujika iingalo nemilenze, nokuwa ebhedini. |
| Ukulala kakhulu emini | Ukuziva ulele kakhulu emini, nangona ulala kakuhle ebusuku. |
| Iimpawu zeMood kunye nokuziphatha | |
| Uxinzelelo | Ukulahlekelwa ngumdla kuyo nayiphi na into, uhlala uziva ulusizi kwaye uphoxekile. |
| Ixhala kunye nokungazoli | Ukuziva usoyika kwaye uxhalabile ngaphandle kwesizathu. |
| Iingcamango eziphosakeleyo | Ukukholelwa kakhulu kwizinto ezingeyonyani. Umzekelo, umntu uzama ngasese ukukutyhefa okanye ukuba imali yakho. |
Kutheni esi sifo senzeka? Zithini izinto ezibangela umngcipheko?
Enyanisweni, oogqirha abasazi isizathu esichanekileyo sokuba abanye abantu bavelise imizimba kaLewy ebuchotsheni babo kanti abanye abasazi. Nangona kunjalo, bachonge ezinye izinto ezinokubangela umngcipheko wokufumana esi sifo.
- Ubudala: Esi sifo sidla ngokubonakala kubantu abangaphezu kweminyaka engama-50 ubudala.
- Imbali yosapho: Ukuba isalamane esisondeleyo kusapho lwakho sikhe saba nesifo se-LBD okanye i-Parkinson's, usenokuba nomngcipheko okhulayo wokufumana esi sifo.
- Iijini: Iijini ezithile, ezifana ne-`(APOE)` kunye ne-`(GBA)`, zifunyenwe zinyusa umngcipheko wokufumana esi sifo. Nangona kunjalo, oku akuthethi ukuba wonke umntu onezo jini uza kuba ne-LBD.
Ugqirha uluchonga njani ngokuchanekileyo olu sifo?
Le yingxaki abantu abaninzi abanayo. Akukho vavanyo lunye olunokuxilonga ngokuchanekileyo i-LBD. Ke ngoko, ugqirha uya kudibanisa izinto ezahlukeneyo, asuse ezinye izifo, aze afikelele kwisigqibo esichanekileyo. Oku kunokubandakanya iqela leengcali ezisebenzisanayo.
Inkqubo yokuxilonga idla ngokuba ngolu hlobo.
1. Ukuthetha ngembali yakho yezonyango: Ukubuza ngeempawu zakho, ukuba zaqala nini, kunye nokuba kukho nabani na kusapho lwakho okhe waba nezigulo ezifanayo.
2. Uvavanyo lomzimba nolwemithambo-luvo: Oku kuya kujonga inkumbulo yakho, amandla okucinga, ukulinganisela, kunye namandla emisipha.
3. Iimvavanyo ezahlukeneyo ziya-odolwa:
- Uvavanyo lwegazi: Jonga ukuba ezi mpawu zibangelwa zezinye iimeko zempilo (umz. ukunqongophala kweevithamini, iingxaki ze-thyroid).
- Iiskeni zobuchopho: Iskeni ye-CT okanye ye-MRI isetyenziselwa ukujonga ezinye iingxaki, ezifana nomhlaza wobuchopho okanye isifo sohlangothi. Ezinye iintlobo ezikhethekileyo zeskeni (i-SPECT, i-PET) zinokubonelela ngolwazi malunga nokusebenza kobuchopho.
- Ukufunda ngokulala: Oku kunokunceda ukuqinisekisa ukuba kukho naziphi na iimpawu zokuhamba ulele.
4. Ukufuna uncedo koogqirha abaziingcali:Ukufuna uncedo kwingcali yezifo zengqondo, ugqirha wengqondo, okanye ugqirha wezifo zabantu abadala.
Ngokudibanisa lonke olu lwazi, oogqirha banokugqiba kwelokuba oku "kunokwenzeka ukuba yi-LBD."
Ngaba ikhona indlela yokunyanga oku? Ndingazilawula njani iimpawu?
Nangona oku kusenokuvakala kubuhlungu, inyaniso kukuba akukho nyango lwe-LBD okwangoku, kwaye akukho ndlela yokuthintela ukuba ikhule.
Kodwa musa ukuvumela oko kukutyhafise! Kukho iindlela ezininzi zonyango ezisebenzayo kunye neendlela zokulawula ezinokulawula iimpawu kwaye zenze ubomi bube lula kakhulu kwisigulana nakwintsapho yaso.
Isicwangciso sonyango senziwe ngokusekelwe kwiimpawu zesigulana kunye nenqanaba lesi sifo.
Amayeza
Ugqirha angakunika amayeza ahlukeneyo okulawula iimpawu ezahlukeneyo.
- Phucula inkumbulo nokucinga: Amayeza abizwa ngokuba yi-`(Cholinesterase inhibitors)` (umz. `rivastigmine`, `donepezil`) anceda abanye abantu.
- Kwiingxaki zokuhamba: I-Carbidopa-levodopa, iyeza elisetyenziselwa ukunyanga isifo sikaParkinson, linokunceda ekuqineni nasekungcangcazeleni.
- Ukulawula ukubona izinto ezingekhoyo: Ngamanye amaxesha kusetyenziswa amayeza okulwa nezifo zengqondo. Nangona kunjalo, ngenxa yokuba la mayeza anokuba nemiphumo emibi kubantu abane-LBD, oogqirha bawanika ngononophelo olukhulu.
- Kwingxaki yokudakumba: Amayeza okudakumba.
- Kwiingxaki zokulala: Amayeza afana ne-`(Clonazepam)` kunye ne-`(melatonin)`.
Unyango kunye neNkxaso
Njengamayeza, olu nyango lukwanceda ekwenzeni ubomi bube lula.
- Unyango lomsebenzi: Lukunceda ukuba wenze imisebenzi yemihla ngemihla (ukutya, ukunxiba) ngokuzimela nangokukhuselekileyo.
- Unyango lomzimba: Lunceda ukuphucula amandla omzimba kunye nokulinganisela, lwenza ukuhamba kube lula, kwaye lunciphise ukuwa.
- Unyango lokuthetha: Lunceda kwiingxaki zokuthetha nokuginya.
Ukongeza kuko konke oku, kubaluleke kakhulu ukugcina inkqubo ezolileyo neqhubekayo . Oku kunokunciphisa ixhala kunye nokungazoli kwesigulana.
Kunini apho kungcono ukubona ugqirha?
Ukuba wena okanye umntu okwintsapho yakho, ingakumbi umntu omdala, uqala ukubona izinto ezingekhoyo (iimbono eziphosakeleyo), kunye naluphi na utshintsho kwinkumbulo, indlela ohamba ngayo, okanye indlela oziphatha ngayo, nceda ungakutyesheli oko. Qiniseka ukuba ubona ugqirha uze uthethe ngako.
Ukuba sele uyazi ukuba une-LBD, kubalulekile ukubona ugqirha wakho rhoqo ukuze ahlolwe. Ukuba ubona naluphi na utshintsho kwiimpawu zakho okanye iimpawu ezintsha, kufuneka uxelele ugqirha wakho.
Izinto ekufuneka uzazi malunga nokuphila nesi sifo
Ngenxa yokuba esi sifo siyaqhubeka, ngokuhamba kwexesha, kunokuba nzima kwisigulana ukuzenzela izigqibo ngokwaso nokwenza imisebenzi yemihla ngemihla. Kungoko ke, kubaluleke kakhulu ukuthetha nokuceba ikamva ngelixa isigulana sisaphaphile engqondweni.
Ngokomndilili, umntu one-LBD kuthiwa uphila phakathi kweminyaka emi-5 ne-8 emva kokuba efunyenwe ene-LBD, kodwa oku kuyahluka kakhulu kumntu nomntu. Abanye abantu baphila ixesha elide kakhulu kunoko.
Ukuphila nesi sifo ngumceli mngeni kumguli nakwintsapho emkhathalelayo. Kodwa khumbula, awuwedwa. Ngonyango olufanelekileyo, inkxaso, kunye nokwazi, olu hambo lunokwenziwa lube lula.
Umyalezo Wokuya Ekhaya
- I-Lewy Body Dementia (LBD) ayipheleli nje ekulibaleni izinto. Yimeko enzima echaphazela yonke into ukususela kwinkumbulo, intshukumo, ukulala, kunye nokuziphatha.
- Ukuphupha izinto ezingekhoyo kunye nokudlala amaphupha kunokuba zezona mpawu ziphambili nezisekuqaleni kwesi sifo.
- Nangona esi sifo singenakunyangwa ngokupheleleyo, kukho amayeza amaninzi kunye nonyango olunokulawula iimpawu kwaye lwenze ubomi bube lula.
- Ukuba wena okanye umntu omthandayo unezi mpawu, musani ukoyika niye kubona ugqirha ngokukhawuleza. Okukhona isifo sifunyanwa ngokukhawuleza, kokukhona kulula ukusilawula.
- Inkxaso kumguli nakubanakekeli ibaluleke kakhulu. Ukugcina indawo ezolileyo kunye nenkqubo eqhubekayo kunokunceda kakhulu ekulawuleni iimpawu.











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