Momma yensua fifiri sɔhwɛ no ho ade nhwɛ sɛ wowɔ cystic fibrosis anaa.

So ɛtɔ mmere bi a ɛyɛ den ma wo ba kumaa no sɛ ɔbɛhome, anaasɛ ɔhaw bi wɔ hɔ a ɛne sɛ ne mu duru renkɔ soro? Anaasɛ wuhu biribi te sɛ ɔfe a ɛba bere nyinaa anaa nnyigyei a ɛyɛ hu wɔ wo koko mu? Ɛtɔ da bi a, saa nneɛma yi akyi no, ebia yare bi wɔ hɔ a yɛntee ho asɛm pii, nanso ɛho hia paa sɛ yɛma yɛn ani da hɔ. Ɛno na yɛrebɛka ho asɛm nnɛ. Wɔfrɛ eyi Cystic Fibrosis , na ɛtɔ mmere bi a wɔtwa no tiaa sɛ (CF) . Momma yɛnhwɛ nea ɛyɛ, sɛnea wohu, ne titiriw no, nsɛm bi a ɛfa ‘Fifiri Sɔhwɛ’ a wɔyɛ ma eyi ho.

Dɛn ankasa ne Cystic Fibrosis?

Sɛ yɛbɛka no tiawa a, cystic fibrosis yɛ yare a wonya fi awo mu . Ɛne sɛ, ɛyɛ biribi a wobetumi de afi awofo hɔ akɔ mmofra nkyɛn. Nea ɛba wɔ eyi mu ne sɛ nsu a ɛwɔ yɛn nipadua mu no bi, titiriw nsu a ɛyɛ nwini no, yɛ den yiye na ɛyɛ nnam. Susuw ho hwɛ, so nsu a ɛwɔ obi a ɔwɔ apɔwmuden ahurututu ne ne ntini mu no nyɛ hwerɛma te sɛ nsu? Ɛyɛ nea ɛma yɛn mframa kwan no ho tew na eyi mmoawa fi hɔ.

Nanso wɔ nnipa a wɔwɔ cystic fibrosis mu no, saa nsu a ɛyɛ nwini yi yɛ den yiye, te sɛ gluu. Enti saa nsu a ɛyɛ den yi kɔ akwaa a ɛho hia te sɛ ahurututu ne dwensɔtwaa mu , na ɛmma wontumi nyɛ adwuma sɛnea ɛsɛ. Titiriw bere a saa nsu a ɛyɛ den yi boaboa ano wɔ ahurututu no mu no, mframa kwan no fi ase siw. Afei ɛbɛyɛ den yiye sɛ obi bɛhome, na ɔyare mmoawa betumi aba mpɛn pii. Sɛ ɛka dwensɔtwaa no a, aduan mu haw ne aduan pa a wonnya nni betumi aba. Ɛnyɛ eyi nko, na mmom ebetumi aka mmeae te sɛ mmerɛbo, dwensɔtwaa, ne ɔbarima ne ɔbea nna nso.

Cystic fibrosis yɛ yare a enni sabea . Eyi kyerɛ sɛ ɛtra hɔ kyɛ na wontumi nsa koraa. Wobu no nso sɛ yare a ɛkɔ so nya nkɔso . Eyi kyerɛ sɛ yare no ho sɛnkyerɛnne no betumi asɛe nkakrankakra bere a bere kɔ so no na nsɛnnennen betumi aba. Ɛno nti na ɛho hia paa sɛ wuhu no ntɛm na wodi ho dwuma yiye no.

Dɛn ne eyi ho sɛnkyerɛnne wɔ mmofra mu?

Sɛ abofra kumaa bi, titiriw akokoaa bi, wɔ cystic fibrosis a, wobetumi anya saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa. Ɛnyɛ abofra biara na obenya saa sɛnkyerɛnne ahorow yi nyinaa prɛko pɛ, na sɛnea sɛnkyerɛnne ahorow no mu yɛ den no betumi ayɛ soronko wɔ abofra biara mu. Ɛho hia sɛ wokae saa asɛm no.

Saa nneɛma no bi ni:

• Nkɔso a entumi nyɛ yiye: Ɛwom mpo sɛ akokoaa no rema nufu yiye na odi yiye akyiri yi de, nanso ebia ne mu duru renkɔ soro na ebetumi ayɛ te sɛ nea ne mu duru sua bere a wɔde toto nkokoaa afoforo a wɔn mfe yɛ pɛ ho no.
• Nsu a ɛho ayɛ hare anaasɛ srade wom: Ɛtɔ mmere bi a, wo ba no nsu betumi ayɛ mmerɛw kɛse, nsu ayɛ no, anaasɛ srade wom. Ɛtɔ mmere bi a, nsu a ɛwɔ nsu mu no betumi ayɛ hua bɔne.
• Ɔhome a ɛyɛ den:Bere nyinaa wote nka sɛ ɛyɛ den sɛ wobɛhome, te sɛ nea worebɔ wo mu.
• Ahomegye a ɛkɔ so: Nnyigyei a ɛkɔ so yɛ akisikuru a efi koko mu ba. Eyi betumi aba nso wɔ tebea horow te sɛ ayamtu mu, nanso ɛyɛ sɛnkyerɛnne a ɛtaa ba wɔ CF mu.
• Ahurututu mu yare a ɛtaa ba: Sɛ nhwɛso no, ahurututu mu yare ne ahurututu mu yare abu so. Sɛ wunya ahurututu mu yare pɛnkoro anaa mprenu ɔsram biara a, ɛyɛ biribi a ɛsɛ sɛ wohaw wo ho wɔ ho.
• Sinus infections a ɛba mpɛn pii: Nyarewa a ɛtaa ba wɔ hwene no ho atwa ho ahyia (sinus). Nneɛma te sɛ anom a ɛyɛ den ne hwene a ɛtwetwe.
• Ɔfe a ɛkɔ so, ebia ɛyɛ phlegmy: Ɔfe a ɛkɔ so tra hɔ a ɛnyɛ yiye. Ebetumi mpo ayɛ ɔfe a ɛma nsu a ɛyɛ den ba.
• Onyin nkakrankakra: Ɛte sɛ nea abofra tenten ne ne mu duru nyin brɛoo kakra sen mmofra afoforo a wɔn mfe yɛ pɛ.
• Ɛtɔ da bi a akokoaa no honam ani yɛ dɛ sɛ nkyene: Awofo binom nso bɔ amanneɛ sɛ sɛ wɔde wɔn ba no honam ani fifiri twitwiw a, ɛte sɛ nkyene.

Sɛ wususuw sɛ wo ba ketewa no wɔ saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa a, ade a eye sen biara a wobɛyɛ ne sɛ wobɛkɔ mmofra oduruyɛfo nkyɛn akɔhwehwɛ afotu.

Dɛn ne fifiri sɔhwɛ na dɛn na ɛyɛ?

Nnuruyɛfo hu cystic fibrosis denam ɔyarefo no a wɔhwɛ no yiye, tie wɔn yare no ho sɛnkyerɛnne, ne nhwehwɛmu ahorow a wɔyɛ so. Eyi ka awosu mu nhwehwɛmu - a ɛyɛ mogya mu nhwehwɛmu a ɛhwehwɛ nsakrae a ɛba awosu mu - koko ne sinus X-ray, ne ahurututu mu dwumadi mu nhwehwɛmu.

Nanso, sɔhwɛ a ɛho hia na ɛyɛ pintinn sen biara a wode bɛkyerɛ sɛ wowɔ cystic fibrosis anaasɛ wunni bi ne fifiri nhwehwɛmu. Eyi yɛ sɔhwɛ a ɛyɛ mmerɛw yiye a ɛnyɛ yaw. Ɛsusuw chloride dodow a ɛwɔ wo fifiri mu. So wunim sɛ nkyene a yedi no yɛ nnuru abien a wɔfrɛ no chloride ne sodium. Enti, chloride dodow a ɛwɔ nnipa a wɔwɔ cystic fibrosis fifiri mu no dɔɔso sen obi a ɔte ase de.

Nea enti a ɛte saa ne sɛ, esiane awosu mu sintɔ a ɛde cystic fibrosis ba nti, protein bi a ɛboa ma chloride fa yɛn nkwammoaa mu no dwumadi sɛe. Ne saa nti, chloride ntumi nkɔ nkwammoaa no mu anaasɛ mfi mu yiye. Eyi ne bere a chloride boaboa ano wɔ fifiri no mu wɔ ɔkwan a ɛnteɛ so. Ɛwom sɛ ebia ɛbɛyɛ te sɛ nea ɛyɛ mmerɛw koraa de, nanso eyi ne nyansahu mu nnyinaso titiriw a wɔde hu yare yi.

Mpɛn pii no, nnuruyɛfo kamfo fifiri nhwehwɛmu yi kyerɛ sɛ abofra bi wɔ asiane mu sɛ obenya cystic fibrosis (sɛ nhwɛso no, sɛ abusua no mu obi wɔ yare no a), anaasɛ wɔreda sɛnkyerɛnne ahorow a yɛadi kan aka ho asɛm no adi a. Ɛtɔ da bi a, wɔka kyerɛ abofra no nuanom nso sɛ wɔnyɛ sɔhwɛ yi. Eyi yɛ nea wɔde hwɛ sɛ ebia wɔn nso anya saa awosu mu abɔde yi ne sɛ ebia wɔn mma wɔ asiane mu sɛ wobenya saa awosu mu abɔde yi daakye anaa.

Ɔkwan bɛn so na wɔyɛ fifiri sɔhwɛ yi? So ɛyɛ biribi a ɛsɛ sɛ yesuro?

Wobetumi ayɛ saa fifiri nhwehwɛmu yi wɔ obiara a wadi mfe biara so. Nanso, ebia nkokoaa a wɔawo wɔn foforo no rentumi mma fifiri a ɛdɔɔso mma sɔhwɛ yi wɔ wɔn nkwa nna kakraa a edi kan no mu. Enti, wɔtaa yɛ sɔhwɛ yi wɔ nkokoaa a wɔadi fi adapɛn abien kosi anan so , bere a wotumi ma fifiri a ɛdɔɔso no.

Saa sɔhwɛ yi yɛ mmerɛw yiye sɛ wɔbɛyɛ, na ɛnyɛ yaw koraa. Enti nsuro no, ɛyɛ? Nea ɛba ni:

1. Nea edi kan no, akwahosan ho dwumayɛni bi, ɔyarehwɛfo anaa oduruyɛfo, de gel anaa nsu a nnuru bi a wɔfrɛ no pilocarpine wom gu abofra no nsa (mpɛn pii no ne nsateaa) anaa ne nan honam ani. Pilocarpine yɛ aduru a ɛkanyan fifiri ntini ahorow no.

2. Afei, wɔde electrode abien gu beae no so na wɔde anyinam ahoɔden a ɛkanyan ketewaa bi a asiane biara nni ho ma de kanyan fifiri ntini no bio na ɛma fifiri ba. Wɔyɛ eyi bɛyɛ simma 5. Ntini anaa ɛyaw biara nni hɔ koraa. Ebia abofra ketewa no bɛte nka sɛ ne nsa anaa ne nan ho ayɛ hyew kakra anaasɛ ne ho ayɛ hyew, nanso ɛno ara ne no. Nkokoaa dodow no ara nte eyi nka mpo.

3. Afei, woyi electrode ahorow no, tew honam ani baabiara, na wɔde afiri titiriw bi a wɔde boaboa fifiri ano (a ɛyɛ plastic coil, filter krataa, anaa gauze) gu beae no so. Wogyaw eyi wɔ nea ɛwɔ hɔ bɛyɛ simma 30 ma fifiri boaboa ano.

4. Awiei koraa no, wɔde fifiri nhwɛsode a wɔaboaboa ano yi kɔ adwumayɛbea bi a wɔde susuw chloride dodow a ɛwɔ mu no pɛpɛɛpɛ.

Sɔhwɛ no nyinaa gye bɛyɛ dɔnhwerew biako. Sɛ wowɔ agode anaa nufusu toa bi bɛn wo a, ɛnyɛ den sɛ wobɛma wo ba no adwo.

Dɛn na nea efii sɔhwɛ yi mu bae no ka?

Okay, afei momma yɛnhwɛ nea nea efii fifiri sɔhwɛ yi mu bae no ka. Sɛ abofra no wɔ cystic fibrosis a, fifiri nhwehwɛmu no bɛkyerɛ sɛ chloride dodow a ɛboro nea ɛfata wɔ wɔn fifiri mu.

Wɔ nsusuiɛ a wɔasusu ho no, yeinom te sɛ deɛ ɛdidi soɔ yi (saa nsusuiɛ yi bɛtumi ayɛ soronko kakra wɔ lab biara mu, nanso mpɛn pii no ɛte sɛ yei):

• Sɛ wo ba no chloride dodow boro 60 mmol/L (millimol/liter) a : Ɛda adi kɛse sɛ ɔwɔ cystic fibrosis.Mpɛn pii no, sɛ nea efi mu ba te sɛ eyi ba a, wɔsan yɛ sɔhwɛ no de si so dua.
• Chloride dodow a abofra no wɔ no nnu 30 mmol/L (millimol/liter) (akwankyerɛ ahorow bi ka sɛ ennu 40 mmol/L): Yebetumi aka sɛ onni cystic fibrosis.
• Sɛ wo ba no chloride dodow yɛ 30 kosi 59 mmol/L ( wɔ mmeae bi no 40-59 mmol/L): Wobu eyi sɛ nea efi mu ba a ɛwɔ mfinimfini anaa nea ɛwɔ ɔhye so . Wɔ eyi mu no, ebia ebehia sɛ wɔsan yɛ sɔhwɛ no bio . Ebia ɛho behia sɛ wɔyɛ nhwehwɛmu foforo te sɛ awosu mu nhwehwɛmu nso na ama wɔatumi ayi CF ahorow bi a ɛnyɛ nea wɔtaa nya no afi hɔ.

Nea ɛho hia sen biara ne sɛ ɛsɛ sɛ oduruyɛfo na ɔkyerɛ nea efi mu ba yi ase. Enti, sɛ nea efi mu ba no ba a, ade a eye sen biara a ɛsɛ sɛ woyɛ ne sɛ wo ne oduruyɛfo no bɛkasa afa ho na woadi n’akwankyerɛ akyi. Mma wo ho nnyɛ wo hu.

Wobɛyɛ dɛn asiesie wo ba no ama ne fifiri ho nhwehwɛmu? So ɛsɛ sɛ woyɛ biribi titiriw bi?

Eyi yɛ mmerɛw yiye ma maame ne papa nyinaa. Ɛho nhia sɛ woyɛ biribi titiriw biara de siesie wo ba ma fifiri mu nhwehwɛmu.

• Ɛho nhia sɛ wɔsesa anaa wogyae abofra no aduan biara (sɛnea ɔma no aduan, nnuan a ɛyɛ den sɛ wɔma no a), dwumadi ahorow, anaa nnuru a abofra no renom ansa na wɔayɛ sɔhwɛ yi. Ma ɛnkɔ so sɛnea ɛte daa.
• Nea ɛwɔ hɔ ara ne sɛ, mfa nnuru anaa aduru biara nhyɛ wo ba no honam ani nnɔnhwerew 24 ansa na wɔayɛ nhwehwɛmu no. Titiriw no, mfa biribiara nhyɛ abasa anaa nan a wɔresɔ ahwɛ no so. Eyi betumi aka nea efi sɔhwɛ no mu ba no.

Hwɛ, ɛyɛ mmerɛw yiye. Fa ntade a emu yɛ hare na ɛyɛ fɛ hyɛ wo ba no da a wɔbɛyɛ sɔhwɛ no.

Nneɛma a ɛho hia paa a ɛsɛ sɛ yɛkae fi saa asɛm yi mu (Take-Home Message) .

Okay, enti mewɔ anidaso sɛ seesei woanya ntease pa wɔ nea yɛkaa ho asɛm nnɛ, Cystic Fibrosis ne Sweat Test no ho. Ɛwom sɛ eyi betumi ayɛ te sɛ asɛmti a ɛyɛ den de, nanso sɛ wote mfitiasesɛm no ase pɛ a, ɛnyɛ den saa. Sɛ yɛhwɛ nea yɛaka ho asɛm a, nneɛma bi a ɛsɛ sɛ yɛma ɛtra yɛn adwenem ni:

• Cystic fibrosis (CF) yɛ awosu mu yare a ɛma nipadua no mu nsu yɛ den, titiriw ɛka ahurututu ne aduan mu nneɛma.
• Hwɛ yare no ho sɛnkyerɛnne: Sɛ wowɔ saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa, te sɛ wo mu duru a ɛso tew, ɔhome a ɛtaa yɛ tiaa, ɔfe a ɛkɔ so daa, anaa nsu a srade wom a, kɔ oduruyɛfo nkyɛn na wo ne no nsusuw ho.
• Fifiri sɔhwɛ no ne sɔhwɛ titiriw a wotumi de ho to so sen biara a wɔde si cystic fibrosis so dua: ɛsusuw chloride dodow a ɛwɔ fifiri mu.
• Sɔhwɛ no nyɛ yaw na asiane biara nni ho: enti nsuro sɛ wode wo ba no bɛkɔ ama eyi.
• Ɛho hia paa sɛ wubehu yare no ntɛm:Efisɛ ɛno akyi no, wobetumi afi ayaresa ne akwan a ɛho hia a wɔfa so di ho dwuma no ase ntɛm, na atew nsɛnnennen a abofra no betumi ahyia no so na aboa no ma wɔatra ase pa na apɔwmuden wom.

Sɛ wo anaa obi a wunim no rehyia saa ɔhaw yi a, ade a eye sen biara a ɛsɛ sɛ woyɛ ne sɛ woremmɔ hu anaasɛ wubegye biribiara a wubehu wɔ intanɛt so adi, na mmom wo ne oduruyɛfo a ɔfata bɛkasa. Wɔbɛkyerɛ wo kwan yiye na wɔama wo mmoa a wuhia.

` Cystic Fibrosis, fifiri nhwehwɛmu, chloride, mmofra ayaresa, awosu mu nyarewa, ahurututu mu nyarewa