So woasusuw pɛn sɛ wubetumi anya akisikuru ketewaa bi a enyin wɔ w’asaabo mu? Ɛtɔ da bi a, eyinom betumi aba a enni sɛnkyerɛnne biara. Ɛnnɛ, yɛrebɛka akisikuru bi a ebetumi aba wɔ asaabo mu ho asɛm. Wɔfrɛ no angiomyolipoma , nnipa binom nso frɛ no renal angiomyolipoma. Edin no te sɛ nea ɛware kakra, ɛnte saa? Nanso mma ɛnhaw wo, momma yɛmma ɛnyɛ mmerɛw.
Dɛn ankasa ne Angiomyolipoma?
Sɛ yɛbɛka no tiawa a, angiomyolipoma yɛ onyin a ɛba bere a nkwammoaa a ɛwɔ w’asaabo mu no bi nyin wɔ ɔkwan a ɛnteɛ so no. Nnuruyɛfo nso frɛ no akisikuru anaa akisikuru . Nanso asɛmpa no ne sɛ angiomyolipomas dodow no ara nyɛ kokoram (a ɛnyɛ papa) . Eyi kyerɛ sɛ ɛnyɛ nea ɛda adi sɛ wɔde ɔhaw a emu yɛ den biara bɛba.
Saa nnuaba yi yɛ afã atitiriw abiɛsa:
- Adipose tissue , a ɛte sɛ ngo a wɔde ahyɛ mu.
- Ntini a ɛyɛ mmerɛw .
- Mogya ntini yɛ nsukorade nketewa a ɛde mogya kɔ.
Nanso, sɛ saa akisikuru yi nyin kɛse a, ebia sɛnkyerɛnne ahorow bi bɛda adi. Sɛ nhwɛso no, mogya , mogya a ɛtɔ kɔ nipadua mu , atiridii , anaa ɛyaw betumi aba wɔ asaabo no fã .
Hena na ɛda adi sɛ obenya angiomyolipoma?
Ebetumi ato obiara ankasa. Nanso nhwehwɛmu ada no adi sɛ mmea taa nya saa tebea yi, titiriw wɔn a wɔadi fi mfe 40 kosi 60 .
Bio nso, nnipa a wɔwɔ akwahosan tebea horow bi no taa nya angiomyolipomas. Tebea abien a ɛte saa ne:
- Ntini a ɛma mogya tu (LAM) .
- Tuberous Sclerosis Complex (TSC) a Ɛma Ntini Mu Ntini a Ɛyɛ Fɛ (TSC) .
Eyi yɛ den kakra, nanso sɛ wowɔ saa tebea yi a, ɛho hia yiye sɛ wo ne oduruyɛfo kasa na wusua ho ade.
Asaabo mu angiomyolipomas abu so dɛn?
Angiomyolipomas ba wɔ nnipa dodow a ennu 1% mu. Ɛno nkyerɛ sɛ wɔn ho yɛ na, nanso ɛnto obiara nso. Nanso, wɔyɛ asaabo mu akisikuru a ɛnyɛ hu a abu so sen biara .
Eyi abu so kɛse wɔ nnipa a wɔwɔ tuberous sclerosis complex (TSC) a yɛadi kan aka ho asɛm no mu . Eyi kyerɛ sɛ nnipa a wɔwɔ TSC no mu bɛboro fã betumi anya angiomyolipomas.
So angiomyolipoma ahorow ahorow wɔ hɔ?
Yiw, wobetumi akyekyɛ angiomyolipomas mu ayɛ no atitiriw abiɛsa a egyina nkwammoaa ne ntini ahorow a ɛwɔ saa akisikuru yi mu so:
1. 1. Nnipa a wɔte saa.Classic (triphasic) AMLs: Eyi ne nea wɔtaa de di dwuma. Nkwammoaa ahorow abiɛsa a yɛadi kan aka ho asɛm no nyinaa wɔ mu: mogya ntini, srade, ne ntini a ɛyɛ mmerɛw .
2. Monophasic AMLs: Saa akisikuru ahorow yi mu dodow no ara wɔ ntini biako . Sɛ nhwɛso no, ebia ntini a ɛyɛ mmerɛw nkutoo na ɛwɔ mu, anaasɛ srade ntini nkutoo na ɛwom.
3. Epithelioid angiomyolipomas: Eyinom fi epithelioid nkwammoaa a ɛhyehyɛ asaabo no mogya ntini no mu titiriw. Saa akisikuru yi wɔ asiane a ɛkɔ soro kakra sɛ ɛbɛyɛ kokoram sen afoforo no . Enti, wɔde adwene titiriw si eyi so.
Angiomyolipoma betumi ayɛ aniberesɛm dɛn?
Mpɛn pii no, nnipa pii a wɔwɔ angiomyolipomas no nnim mpo sɛ wɔwɔ bi. Ɛte saa efisɛ mpɛn pii no wɔmfa sɛnkyerɛnne biara mma.
Nanso, sɛ saa akisikuru yi nyin boro sɛntimita 4 (a ne kɛse bɛyɛ sɛ walnut a yɛtaa di) a, ɛnde ebetumi afi ase ayɛ mogya (mogya a ɛtɔ) . Mogya a ɛtɔ te sɛɛ no betumi de nkwa ato asiane mu sɛ wɔansa no bere ano a. Ɛno nti na ɛho hia sɛ yɛhwɛ yiye wɔ saa akisikuru yi ho no.
Angiomyolipoma nyin ntɛmntɛm dɛn?
Angiomyolipomas a wɔtaa de di dwuma dodow no ara nnyin koraa . Anaasɛ, sɛ wɔyɛ saa a, enyin nkakrankakra paa . Sɛ wɔkyekyem pɛpɛɛpɛ a, saa akisikuru yi nyin bɛyɛ sɛntimita 0.19 (bɛyɛ nsateakwaa nkyem dunsia mu biako) afe biara.
Nanso, saa akisikuru yi tumi nyin ntɛmntɛm wɔ nyinsɛn mu . Enti, sɛ wowɔ angiomyolipoma na worehwɛ akokoaa kwan a, ebia ɛbɛyɛ nea nyansa wom sɛ wobɛma wɔasa akisikuru no ansa na woanyinsɛn . Ɛyɛ papa sɛ wo ne wo duruyɛfo bɛkasa afa eyi ho.
Dɛn na ɛde angiomyolipoma ba?
Nnuruyɛfo da so ara nnim nea enti a saa ntini yi boaboa ano na ɛyɛ asaabo mu akisikuru ankasa . Nanso, nhwehwɛmufo gye di sɛ nsakrae (nsakrae) bi a ɛba yɛn awosu mu no betumi adi dwuma bi.
Dɛn ne angiomyolipoma ho sɛnkyerɛnne ahorow?
Sɛnea yɛadi kan aka no, nnipa dodow no ara a wɔwɔ angiomyolipoma no nhu sɛnkyerɛnne biara . Nanso, bere a akisikuru no nyin no, sɛnkyerɛnne ahorow bi betumi ada adi. Eyinom bi ne:
- Mogya a ɛtɔ mogya a ɛnam mogya a ɛtɔ so .
- Huraeɛ .
- Flank ɛyaw anaa asaabo mu yaw esiane mogya a ɛretu atwa asaabo no ho ahyia nti.
- Mogya mmoroso (mogya mmoroso) .
- Akisikuru ne ɔfe .
Sɛ wowɔ saa sɛnkyerɛnne yi mu biako anaa nea ɛboro saa a, ɛho hia paa sɛ wobɛkɔ oduruyɛfo nkyɛn ntɛm ara sɛnea wubetumi.
Wobɛyɛ dɛn ahu sɛ wowɔ angiomyolipoma?
Ɛtɔ mmere bi a, ebia wo duruyɛfo behu akisikuru no ara kwa bere a woreyɛ mfoninitwa nhwehwɛmu , te sɛ scan, de ahu akwahosan tebea foforo no. Anaasɛ, sɛ wowɔ sɛnkyerɛnne ahorow a yɛaka ho asɛm wɔ atifi hɔ no a, wo duruyɛfo betumi ahyɛ sɛ wɔnyɛ nhwehwɛmu ahorow yi na ama wɔahu nea ɛde ba.
Sɔhwɛ ahorow bɛn na ɛma wohu eyi?
Nnuruyɛfo taa kamfo kyerɛ sɛ wɔnyɛ mfonini mu nhwehwɛmu te sɛ eyinom:
- CT scan a wɔde yɛ adwuma
- MRI
- Ultrasound a wɔde yɛ nneɛma
Nanso, angiomyolipomas ahorow bi betumi ayɛ te sɛ asaabo mu kokoram wɔ saa mfonini ahorow yi mu. Enti, sɛnea ɛbɛyɛ a wobɛka no yiye no, ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔnyɛ asaabo mu nhwehwɛmu, a nea ɛka ho ne sɛ wobɛfa asaabo no fã ketewaa bi na wɔasɔ ahwɛ .
Mɛyɛ dɛn ahu sɛ me angiomyolipoma no hia ayaresa?
Ɛnyɛ obiara a ɔwɔ angiomyolipoma na obehia ayaresa. Sɛ́ ebia wubehia ayaresa no gyina akisikuru no kɛse , sɛ ebia wowɔ sɛnkyerɛnne ahorow , ne sɛ ebia woreyɛ nhyehyɛe sɛ wubenyinsɛn daakye a enni akyiri so .
Mpɛn pii no, ebehia sɛ wokɔ wo duruyɛfo nkyɛn bɛyɛ pɛnkoro afe biara kɔhwɛ sɛnea akisikuru no nyin. Sɛ akisikuru no sõ sen sɛntimita 4 a , ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔmfa sa yare.
Ɔkwan bɛn so na wɔsa angiomyolipomas?
Ebia oduruyɛfo no bɛkamfo ayaresa ahorow a ɛbɛma akisikuru no agyae anaasɛ ayi afi hɔ. Eyinom bi ne:
- Ablation therapy: Wɔ saa ayaresa yi mu no, nnuruyɛfo de ahoɔden (sɛ nhwɛso no , radiofrequency waves ), ɔhyew a ano yɛ den, anaa mframa a ɛyɛ nwini kɛse di dwuma de sɛe angiomyolipoma no.
- Arterial embolization: Wɔ saa adeyɛ yi mu no, wɔtwa w’asen mu ketewaa bi, wɔde afiri teateaa (catheter) hyɛ mu, na wɔde nhwiren nketenkete fa mu. Saa nhwiren yi siw mogya a ɛkɔ angiomyolipoma no mu no ano. Eyi ma akisikuru no so tew, ɛma mogya no so tew, na ɛma mogya tu no so tew.
- Nephrectomy a edi mũ: Oprehyɛn yi yi asaabo a angiomyolipoma wom no nyinaa fi hɔ .
- Nephrectomy fã bi: Eyi nnyi asaabo no nyinaa mfi hɔ. Asaabo no fã a angiomyolipoma no wom nkutoo na woyi fi hɔ . Wobetumi ayɛ eyi sɛ ahurututu no fã bi a wɔabue mu anaasɛ sɛ robɔt a wɔde twa akisikuru no fã bi .
Ade a ɛho hia sen biara ne sɛ wo ne wo duruyɛfo bɛkasa na wapaw ayaresa a eye ma wo.
So nsɛnnennen anaa nsunsuanso bɔne bi wɔ hɔ wɔ ayaresa akyi?
Ebia asiane ahorow bi wɔ hɔ wɔ asaabo oprehyɛn ne angiomyolipoma ayaresa afoforo akyi. Nhwɛsoɔ:
- Mogya a ɛretu
- Nsaneɛ
- Nkuruwankuruwa
Ɛtɔ mmere bi a, asaabo a entumi nyɛ adwuma yiye wɔ asaabo ayaresa akyi. Nanso eyi ho yɛ na koraa. Wo duruyɛfo no bɛka asiane ahorow yi ho asɛm akyerɛ wo ansa na wɔasa wo yare na wayɛ nneɛma bi de atew so. Sɛ asaabo no ntumi nyɛ adwuma yiye a, wo duruyɛfo no bɛyɛ ayaresa nhyehyɛe bi a ɛbɛboa wo ma woadi wo sɛnkyerɛnne ahorow no ho dwuma na woanya apɔwmuden sɛnea wubetumi biara.
Bere tenten ahe na egye na obi ho atɔ no wɔ ayaresa akyi?
Sɛ wɔatwa wo nephrectomy koraa anaa ne fã bi , ɛho behia sɛ wotra ayaresabea hɔ nna kakraa bi. Nnuruyɛfo nso bɛhwɛ sɛnea w’asaabo yɛ adwuma na wɔahwɛ ahu sɛ wo ho resa yiye.
Sɛ wowɔ ablation therapy anaa arterial embolization , a, ɛho behia sɛ wotra ayaresabea nnɔnhwerew kakraa bi anaa anadwo mũ nyinaa.
So wobetumi asiw angiomyolipoma ano?
Nokwarem no, ɔkwan pɔtee biara nni hɔ a wɔbɛfa so asiw angiomyolipomas a ɛbɛba no ano. Saa akisikuru yi taa ba ara kwa, a enni nea ɛde ba pɔtee biara . Eyi kyerɛ sɛ ɛyɛ den sɛ yɛbɛka nea ɛde AML no bae pɔtee.
So tebea afoforo wɔ hɔ a ɛde me to asiane kɛse mu sɛ menya angiomyolipoma?
Aane. Sɛ wowɔ tuberous sclerosis complex (TSC) anaa lymphangioleiomyotosis (LAM) , a, asiane kɛse wom sɛ wubenya angiomyolipoma. Enti, wo ne wo duruyɛfo nkasa mfa sɛnea wobɛhwɛ w’akwahosan ne nneɛma a wobɛtu de atew asiane a ɛwɔ hɔ no so ho.
Sɛ mewɔ angiomyolipoma a, dɛn na ɛsɛ sɛ mehwɛ kwan?
Sɛ wowɔ angiomyolipoma nanso wunhu sɛnkyerɛnne biara a ɛho behia sɛ wokɔ wo duruyɛfo nkyɛn bɛyɛ pɛnkoro afe biara . Ebia ɛho behia nso sɛ woyɛ mfoninitwa nhwehwɛmu de hwɛ sɛ akisikuru no reyɛ kɛse anaa.
Sɛ wowɔ sɛnkyerɛnne ahorow a , ebia wo duruyɛfo bɛkamfo ayaresa akyerɛ wo na amma asiane a ɛwɔ hɔ sɛ mogya bɛtɔ wo no ano.
So angiomyolipomas betumi de nkɛntɛnso a ɛtra hɔ kyɛ aba?
Sɛ angiomyolipomas nyin yɛ kɛse a, ebetumi mogya anaasɛ apaapae . Enti, wo duruyɛfo bɛhwɛ sɛnea akisikuru no kɛse te daa na sɛ wowɔ asiane mu a, ɔbɛkamfo ayaresa akyerɛ wo.
So metumi anya angiomyolipoma bɛboro pɛnkoro?
Yiw , angiomyolipoma betumi asan anyin wɔ ayaresa akyi.Afei nso, angiomyolipoma bɛboro biako betumi aba, na AML betumi aba asaabo abien no nyinaa mu .
So angiomyolipoma betumi abɛyɛ kokoram?
Saa akisikuru a yɛadi kan aka ho asɛm no, a wɔfrɛ no epithelioid angiomyolipoma no, ɛtɔ mmere bi a ebetumi adan kokoram . Sɛ ɛba saa a, wo duruyɛfo no bɛhwɛ wo yiye na ɔne wo akasa afa nea ɛsɛ sɛ woyɛ akyi.
Sɛ mewɔ angiomyolipoma a, mpɛn ahe na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?
Wo ne wo duruyɛfo nyɛ adwuma na monyɛ ayaresa ho nhyehyɛe . Yɛ bere a wɔde bedi akyi nyinaa so na hwɛ sɛ ebia akisikuru no nyin anaa.
Bere bɛn na ɛsɛ sɛ mefrɛ me duruyɛfo?
Sɛ wunya sɛnkyerɛnne foforo yi bi a, frɛ wo duruyɛfo ntɛm ara :
- Yafunu mu yaw
- Akyi yaw
- Huraeɛ
- Akisikuru ne ɔfe
- Hematuria - mogya a ewo nsuo mu
Nea etwa to no, nneɛma a ɛsɛ sɛ wokae (Take-Home Message) .
Angiomyolipoma yɛ akisikuru a ɛnyɛ hu a ɛtaa ba asaabo no mu. Ebia worennya yare no ho sɛnkyerɛnne biara. Wo duruyɛfo bɛhwɛ akisikuru no afe biara ahwɛ sɛ ɛrenyin anaa. Ebia akisikuru a ne kɛse boro sɛntimita 4 behia ayaresa na amma mogya antɔ.
Nea ɛho hia sen biara ne sɛ, sɛ wowɔ sɛnkyerɛnne biara a, mma wo ho nnpopo na wo ne wo duruyɛfo nkasa ntɛm ara. Wɔbɛma wo ayaresa ne akwankyerɛ a eye sen biara a wuhia.
` Angiomyolipoma, asaabo mu kurukuruwa, asaabo mu yare, akisikuru a ɛnyɛ hu, asaabo mu yaw, mogya a ɛtɔ kɔ nipadua mu, asaabo mu yare











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