So woahu sɛ obi a wunim no sɛ n’adwene mu da hɔ mpofirim pɛn? Anaasɛ woate sɛ obi a ɔwɔ apɔwmuden rewu wɔ wɔn nna mu? Ebia nea ɛde nneɛma a ɛtete saa ba ne komayare bi a ahintaw a nnipa pii nte ho asɛm mpo. Ɛnnɛ yɛreka yareɛ baako a ɛyɛ hu na ɛho hia a ɛsɛ sɛ yɛhunu, Brugada Syndrome ho asɛm.
Dɛn ne Brugada Yare no?
Sɛ yɛbɛka no tiawa a, eyi yɛ ɔhaw wɔ yɛn koma mu anyinam ahoɔden nhyehyɛe no ho. Yɛn koma bɔ te sɛ anyinam ahoɔden nsɛnkyerɛnne nhyehyɛe. Wɔ saa yare yi mu no, anyinam ahoɔden nsɛnkyerɛnne a ɛkɔ koma no mu adan a ɛwɔ fam (ventricles) no mu yɛ nea ɛnkɔ so pɛpɛɛpɛ.
Eyi ma koma no bɔ ntɛmntɛm a asiane wom, ɛkame ayɛ sɛ ɛte sɛ nea ɛrewosow. Wɔfrɛ eyi `Ventricular fibrillation (v-fib)` wɔ aduruyɛ mu. Sɛ eyi ba a, koma no ntumi mfa mogya nkɔ nipadua no mu yiye. Ne titiriw no, sɛ mogya a ɛkɔ amemene no mu no asɛe a, obi betumi atɔ piti.
Ade a asiane wom sen biara wɔ tebea yi ho ne sɛ ebetumi ama koma no awu mpofirim. Eyi taa ba bere a ɔyarefo no regye n’ahome, titiriw bere a wada no. Nhwehwɛmu ada no adi sɛ Brugada syndrome na ɛde koma mu wuwu mpofirim bɛyɛ 4% ba wɔ wiase nyinaa.
Nanso eyi yɛ tebea a ɛntaa nsi koraa. Sɛ wɔkyekyem pɛpɛɛpɛ a, nnipa 10,000 biara mu 3 kosi 5 na wɔwɔ saa yare yi.
Dɛn ne yare yi ho sɛnkyerɛnne?
Ɛwom sɛ Brugada yare no ho sɛnkyerɛnne betumi ada adi wɔ mfe biara mu de, nanso ɛtaa ba bɛyɛ mfe 40. Nea ɛyɛ nwonwa no, nnipa a wɔwɔ saa tebea yi mu bɛboro 70% nkyerɛ sɛnkyerɛnne biara . Obi a onya yare no ho sɛnkyerɛnne no betumi anya nea edidi so yi:
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Fainting/Syncope a ɛyɛ mmerɛw | Koma no a ɛnkɔ so daa no betumi ama mogya a ɛkɔ amemene no mu no asɛe, na ama n’adwene atu afra mpofirim na ahwe ase. |
| Adwene a ɛyɛ basaa | Sɛ wote nka sɛ n’adwene atu afra. |
| Koma a ɛbɔ denneennen | Koma a ɛrebɔ denneennen ho atenka, atenka a ɛte sɛ nea koma no redi akɔneaba wɔ koko no mu. |
| Ɔhome a ɛyɛ den | Ɔhome a ɛyɛ den, titiriw anadwo. |
| Koma a Ɛyɛ Den | Ebia eyi ne sɛnkyerɛnne a edi kan . Eyi nti na nnipa binom wuwu wɔ wɔn nna mu no. |
Dɛn na ɛrema tebea yi mu ayɛ den?
Ɛho hia sɛ wuhu nneɛma bi a ebetumi akanyan anaasɛ ama yare no ho sɛnkyerɛnne asɛe wɔ obi a ɔwɔ Brugada yare no mu.
- Atiridii: Atiridii yɛ yare yi atamfo atitiriw no mu biako. Sɛ wowɔ Brugada syndrome a, ɛho hia sɛ wonom aduru bi te sɛ paracetamol bere a woanya atiridiinini ara pɛ, sɛnea wo duruyɛfo kyerɛ wo no.
- Nsu a ɛho ntew: Bere a nsu nnɔɔso wɔ nipadua no mu.
- Asanom bebrebe: Nsã pii a wɔnom prɛko pɛ.
- Nnuru bi: Nnuru te sɛ `Sodium channel blockers` a wɔde di dwuma ma komayare ahorow bi, ne nnuru a wɔde sa adwenemyare te sɛ `Lithium` ne `Tricyclic antidepressants`.
- Nnubɔne: Nnubɔne te sɛ cocaine ne wii.
Sɛ oduruyɛfo bi si so dua sɛ wowɔ saa yare yi a, hwɛ hu sɛ wobɛbisa wo duruyɛfo no sɛ ɔmma wo nnuru a ɛnsɛ sɛ wonom no din . Sɛ worenom nnuru a wɔde sa tebea foforo biara a, ka kyerɛ oduruyɛfo no sɛ wowɔ Brugada syndrome.
Dɛn nti na saa yare yi ba?
Mpɛn pii no, bɛyɛ 70% no, wontumi nhu nea ɛde saa yare yi ba pɔtee biara. Nanso, wɔ nnipa binom fam no, efi awosu mu. Sɛ yɛbɛka no tiawa a, ɛyɛ awosu.
- Awosu mu nneɛma a ɛde ba: Nsakrae a ɛba awosu mu nneɛma bɛboro 18 mu wɔ yɛn nipadua mu no betumi de eyi aba. Eyinom mu no, nea ɛtaa ba ne nkwaadɔm mu nsakrae a ɛba awosu mu nkwaadɔm `SCN5A` mu. Nsakrae a ɛba saa awosu mu nkwaadɔm yi mu no ma anyinam ahoɔden nsɛnkyerɛnne a ɛkɔ koma no mu no yɛ basaa.
- Awosu: Sɛ ɔwofo biako wɔ awosu mu nkwaadɔm mu nsakrae a ɛbata saa yare yi ho a, ɛyɛ 50% sɛ abofra benya bi.
Hena na ɔwɔ asiane mu kɛse?
- Wɔ mmarima fam no: Saa yare yi abu so wɔ mmarima mu bɛyɛ mpɛn 8-10 sen mmea.
- Abusua abakɔsɛm: Sɛ obi wɔ w’abusua mu wɔ Brugada syndrome, anaasɛ obi wu mpofirim wɔ ne mmofraase a, ebia wo nso wobɛkɔ asiane mu.
- Asia fibea: Wɔahu sɛ saa yare yi abu so kakra wɔ nnipa a wɔwɔ Asia aman mu sen Atɔe Fam aman mu.
Ɔkwan bɛn so na wobetumi ahu yare no pɛpɛɛpɛ?
Sɛ wo tie wo yareɛ no ho sɛnkyerɛnne ne w’abusua abakɔsɛm wie a, wo duruyɛfoɔ bɛhyɛ sɛ wɔnyɛ nhwehwɛmu mpɛn pii mfa nkyerɛ sɛ wowɔ saa yareɛ yi anaa.
| Sɔhwɛ | Dɛn na wode yɛ? |
|---|---|
| Electrocardiogram (EKG) a wɔde kyerɛw koma no . | Sɔhwɛ a ɛkyerɛ anyinam ahoɔden dwumadi a ɛwɔ koma no mu wɔ line graph mu. Nnuruyɛfo hwehwɛ nhyehyɛe pɔtee bi wɔ saa nhyehyɛe yi mu a ɛne yare yi wɔ abusuabɔ. Ɛtɔ mmere bi a ɛnyɛ bere nyinaa na wohu saa nhyehyɛe yi, enti ebia ɛho behia sɛ wɔyɛ EKG no mpɛn pii. |
| EKG sɔhwɛ a wɔde nnuru yɛ (Drug Challenge Test) . | Sɛ EKG a ɛfata da tebea bi a ɛyɛ adwenem naayɛ adi a, wɔde aduru titiriw bi gu ntini bi mu de bɔ mmɔden sɛ wɔbɛda Brugada nhyehyɛe a ahintaw no adi. Wɔyɛ eyi wɔ baabi a ahobammɔ wɔ, te sɛ ayaresabea a wɔhwɛ wɔn a wɔyare denneennen. |
| Awosu mu Nhwehwɛmu | Wobetumi de wo nnompe anaa wo mogya mu nhwɛsode adi dwuma de ahu sɛ ebia wowɔ awosu mu nsakrae bi a ɛne yare yi wɔ abusuabɔ anaa. Sɛ obi wɔ w’abusua mu wɔ yare no a, afoforo nso betumi ayɛ nhwehwɛmu yi. |
| Electrophysiology (EP Sɔhwɛ) . | Sɛ wɔda so ara mu nna hɔ wɔ nhwehwɛmu afoforo akyi a, wɔyɛ sɔhwɛ yi. Nea ɛka eyi ho ne sɛ wɔde kankyee (catheter) a ɛyɛ fɛ yiye fa ntini bi a ɛwɔ nan no mu bɛhyɛ koma no mu na wɔasusuw anyinam ahoɔden dwumadi a ɛwɔ koma no mu no. |
Ɔkwan bɛn so na wɔsa?
Wontumi nsa Brugada yare no koraa. Nanso, wobetumi de ayaresa ama de asiw komayare a ekum mpofirim ano. Botae titiriw a ɛwɔ ayaresa mu ne sɛ wobesiw koma no mu nnyigyei a ɛnyɛ pɛpɛɛpɛ (ventricular arrhythmias) a asiane wom no ano na sɛ ɛba a, wɔadi so.
Ayaresa titiriw a etu mpɔn sen biara ne ICD afiri a wɔde bɛhyɛ nipadua mu .
- ICD (Implantable Cardioverter Defibrillator): Eyi yɛ afiri ketewaa bi. Ɛte sɛ afiri a ɛma obi koma bɔ kɛse. Wɔde oprehyɛn ketewaa bi hyɛ honam ani, bɛn koma no, koko mu. Ɛkɔ so hwɛ sɛnea koma no bɔ denneennen. Sɛ koma no nnyigyei sesa wɔ ɔkwan a ɛyɛ hu so a, saa afiri yi hu na ɛde anyinam ahoɔden ketewaa bi ma de san nnyigyei no san ba. Eyi yɛ mfiri a egye nkwa.
- Nnuru: Nnuru bi, te sɛ `Quinidine`, tumi di koma a ɛnyɛ pɛpɛɛpɛ so. Nanso, eyinom mfata obiara.
- Ablation: Wɔ tebea titiriw bi mu no, ɛyɛ ɔkwan a wɔfa so sa yare a ɛma wohu faako a anyinam ahoɔden nsɛnkyerɛnne a ɛnkɔ so daa wɔ koma no mu na ɛde radio asorɔkye sɛe.
Nnuruyɛfo gyina EKG kyerɛwtohɔ, abusua abakɔsɛm, ne nhwehwɛmu afoforo a efii mu bae so na esi gyinae sɛ ebia wɔbɛsa ayarefo a wonni sɛnkyerɛnne biara. Esiane sɛ ɛtɔ mmere bi a , sɛnkyerɛnne a edi kan ne owu mpofirim nti , ɛho hia sɛ wosusuw asiane a ɛwɔ mu no ho na wosa no sɛnea ɛfata.
Bere bɛn na ɛsɛ sɛ wokɔ Emergency Treatment Unit (ETU)?
Sɛ wo koma atɔ wo mpofirim (cardiac arrest) a, wubehia ayaresa ntɛm ara. Esiane sɛ worentumi mfrɛ mmoa saa bere no nti, ɛho hia paa sɛ wɔbɔ w’abusua ne w’adɔfo amanneɛ wɔ eyi ho.
Sɛ wowɔ asiane mu sɛ koma bɛtɔ wo a, ka kyerɛ w’abusua ne wo nnamfo paa sɛ wonsua sɛnea wɔyɛ CPR (cardiopulmonary resuscitation). Sɛ biribi si ntɛm a, frɛ 1990 na frɛ ambulance. Saa nhumu yi betumi agye wo nkwa.
Nkrasɛm a Wɔde Kɔ Fie
- Brugada yare no yɛ tebea a emu yɛ den a ɛba koma no anyinam ahoɔden nhyehyɛe mu na ebetumi ama obi awu mpofirim mpo.
- Atiridii yɛ ade titiriw a ɛma yare yi mu yɛ den. Sɛ wunya atiridii a, tew so ntɛm.
- Sɛ obi awu mpofirim wɔ w’abusua mu wɔ wo mmofraase anaasɛ wotaa hwere w’adwene a, kɔ oduruyɛfo nkyɛn ntɛm ara na kɔyɛ EKG nhwehwɛmu.
- ICD afiri a wɔde bɛhyɛ nipadua mu no ne ayaresa a eye sen biara a wɔde begye nnipa nkwa afi yare yi mu.
- Sɛ wowɔ saa yare yi a, hwɛ nnuru a wo duruyɛfo de ma wo a ɛmfata sɛ wode bedi dwuma no din bere nyinaa.
💬 Comments (0)
Wɔnnya nyɛɛ nsɛm biara. Fa wo nsɛm no ka ho wɔ ha nea edi kan.
Fa wo nsɛm no ka ho