Ɛtɔ mmere bi a, sɛ yɛte hɔ kɛkɛ a, yɛn nipadua mu ntini bi wosow mpofirim, ɛnte saa? Ebia yɛrebɛda na yɛde ahopopo asɔre. Nneɛma a ɛte sɛɛ taa to obiara. Nanso sɛ ntini a ɛwosow yi kɔ so, sɛ esiw da biara da dwumadi ahorow kwan a, ebetumi ayɛ aduruyɛ tebea bi ho sɛnkyerɛnne. Enti ɛnnɛ, momma yɛnka deɛ ‘Myoclonus’ yi yɛ, deɛ ɛde ba, ne berɛ a ɛsɛ sɛ yɛdwene ho.
Dɛn ne Myoclonus?
Sɛ yɛbɛka no tiawa a, Myoclonus yɛ ntini biako anaa nea ɛboro saa a ɛwosow anaa ɛwosow mpofirim, ɛnyɛ nea wɔpɛ, na ɛyɛ bere tiaa bi. Ebetumi ayɛ te sɛ anyinam ahoɔden a ɛbɔ na ɛtra hɔ sekan fã ketewaa bi. Ebetumi aka ntini biako pɛ wɔ abasa, nan, mmati, asen, akyi, anaa anim, anaasɛ ebetumi aka ntini pii prɛko pɛ.
Obi a ɔwɔ apɔwmuden mpo betumi ahu eyi wɔ n’asetra mu bere bi. Nanso, ɛtɔ mmere bi a, ebetumi nso ayɛ aduruyɛ mu tebea horow a emu yɛ den pii ho sɛnkyerɛnne.
Myoclonus betumi aba wɔ akwan titiriw abien so:
- Positive myoclonus: Eyi ne bere a ntini no twetwe mpofirim.
- Negative myoclonus: Eyi yɛ ntini a ɛma ɛyɛ mmerɛw mpofirim. Wɔ aduruyɛ mu no, wɔsan frɛ no ``Asterixis''. Nea ɛda nsow ne nsa a ɛwosow.
Dɛn ne nneɛma atitiriw a ɛde Myoclonus ba?
Nneɛma pii na ɛde myoclonus ba. Ebinom abu so yiye na wɔhwɛ kwan. Nanso afoforo betumi afi aduruyɛ mu tebea horow a ɛka nhyehyɛe ahorow a ɛwɔ yɛn nipadua mu no mu aba. Abenfo kyekyɛ nneɛma a ɛde ba yi mu akuw atitiriw anan.
Nneɛma a ɛyɛ daa, nipadua mu nneɛma a ɛde ba (Physiological Myoclonus) .
Eyinom yɛ myoclonus ahorow a asiane biara nni ho a nneɛma a ɛkɔ so daa wɔ yɛn nipadua mu na ɛde ba. Biribiara nni hɔ a enti ɛsɛ sɛ yesuro eyi.
- Hiccups: Eyi nso yɛ Myoclonus bi. Nanso, sɛ ɛkɔ so boro nna abien a, ɛbɛyɛ papa sɛ wobɛkɔ oduruyɛfo nkyɛn.
- Sleep myoclonus/Hypnic jerks: Nipadua no a ɛwosow mpofirim , bere a worebɛda anaasɛ worebɛsɔre no. Eyi abu so wɔ nnipa pii fam.
- Startle reflexes: Sɛ ehu ka yɛn mpofirim anaasɛ yɛn ho dwiriw yɛn a, yɛn nipadua wosow a yentumi nni so.
Myoclonus a efi akisikuru mu ba
Saa ntini a ɛtwetwe yi betumi aba wɔ akisikuru tebea horow bi ho. Saa tebea yi taa ba `(myoclonic seizures)` mu titiriw. Ebetumi nso de abata tebea horow te sɛ `(Lennox-Gastaut syndrome)` ne `(juvenile myoclonic epilepsy)` ho.
Sɛ́ aduruyɛ mu tebea foforo ho sɛnkyerɛnne (Secondary Myoclonus) .
Sɛ myoclonus ba sɛ yareɛ foforɔ ho sɛnkyerɛnne a, wɔfrɛ no ‘Secondary Myoclonus’. Nneɛma pii wɔ hɔ a ebetumi de eyi aba. Momma yensua ho nsɛm pii mfi pon a ɛwɔ ase ha no so.
| Ade a ɛde ba | Nkyerɛkyerɛmu ne nhwɛso ahorow |
|---|---|
| Nyarewa a nipadua no tumi ko tia nyarewa | Nyarewa a nipadua no mu tumi a ɛko tia nyarewa no tow hyɛ n’ankasa nkwammoaa so. Sɛ nhwɛso no: (Celiac yare) . |
| Nnuru a ɛnkari pɛ wɔ nipadua no mu | Asaabo anaa mmerɛbo mu yare, thyroid ho haw, vitamin anaa mineral a enni nipadua mu, ne electrolyte a ɛnkari pɛ . |
| Amemene mu akuru | Amemene no mu ntini a ɛsɛe esiane oxygen a enni hɔ nti (amemene mu oxygen a enni hɔ) anaasɛ ɔyare a ɛma obi hwe ase. |
| Amemene mu nyarewa a ɛyɛ mmerɛw | Sɛ nhwɛso no: adwenemhaw a ɛfa (Alzheimer yare) , (Lewy nipadua mu adwenemhaw) , ne (Parkinson yare) ho. |
| Awosu mu nyarewa | Nyarewa a DNA mu nsakrae a wotumi nya fi awofo hɔ de ba. Sɛ nhwɛso no: (Krabbe yare) , (Wilson yare) . |
| Nyarewa a wɔde nyarewa ba | Mmoawa anaa ɔyare mmoawa a ɛka amemene anaa ntini mu yare. Sɛ nhwɛso no: (Herpes simplex mmoawa) , (Lyme yare) .. |
| Ntini anaa akyi berɛmo mu opira | Akwanhyia sɛe nkitahodi a ɛda amemene no ne nipadua no afã horow ntam, na ɛma saa akwaa no yɛ adwuma ara kwa. |
| Nnuru ne nnuru | Eyi betumi afi nnuru a wɔnom a oduruyɛfo nkyerɛw krataa (te sɛ nsa, cocaine, heroin) mu. Ebetumi nso afi nnuru a oduruyɛfo akyerɛw ama obi, te sɛ nnuru a ekum akisikuru, nnuru a ekum adwenemhaw , mogya mmoroso nnuru, ne nnuru a ekum ɔyare mmoawa . |
| Awuduru ne awuduru | Dade a emu yɛ duru te sɛ kɔbere, manganese, mercury a wɔnom. Awuduru te sɛ nnuru a wɔde kum mmoawa (e.g. methyl bromide ). |
Myoclonus a Ɛho Hia
Eyi yɛ awosu mu tebea a efi awo ntoatoaso so kɔ awo ntoatoaso so. Mpɛn pii no, ɛnsɛe hwee na bere kɔ so no, ɛnsɛe kɛse. Nanso, nsa a wɔnom betumi ama ntini mu akisikuru yi ada adi kakra.
So wobetumi asiw tebea yi ano?
Myoclonus yɛ biribi a ɛba mpofirim, a wɔmfa kɔkɔbɔ biara mma. Enti wontumi nsiw myoclonus ahorow a yɛadi kan aka ho asɛm a wɔfrɛ no physiological and essential myoclonus no ano.
Nanso, yebetumi adi myoclonus tebea horow a nyarewa afoforo (a ɛto so abien) ne akisikuru (akisikuru) de ba no so akodu baabi.
- Kwati nnubɔne a wode bedi dwuma: Kwati sɛ wode nnuru a oduruyɛfo nkyerɛw mma wo bedi dwuma. Afei nso, sɛ wuhu saa sɛnkyerɛnne ahorow yi bere a woanom aduru bi a oduruyɛfo akyerɛw ama wo no akyi a, ka kyerɛ wo duruyɛfo ntɛm ara. Wɔwɔ hɔ sɛ wɔbɛboa wo, na ɛnyɛ sɛ wobebu wo atɛn. Enti, ɛho hia ma w’ahobammɔ ne ayaresa a ɛfata sɛ wobɛka biribiara a wode adi dwuma ho asɛm kyerɛ wɔn.
- Bɔ wo ntini ho ban: Sɛ wode ahobammɔ nnwinnade te sɛ dade kyɛw ne ahobammɔ bɛlt di dwuma a, ebetumi asiw w’amemene ne w’akyi berɛmo a wopirapira no ano.
- Di tebea horow a enni sabea ho dwuma: Sɛ wowɔ tebea horow a enni sabea te sɛ akisikuru anaa thyroid yare a, wo duruyɛfo akwankyerɛ a wubedi akyi pɛpɛɛpɛ no betumi aboa ma woasiw myoclonus a ɛba no ano anaasɛ ɛbɛtew so.
Bere bɛn na ɛsɛ sɛ yɛkɔ oduruyɛfo nkyɛn?
Spasticity a ɛtaa ba no nhia ayaresa. Nanso, sɛ saa ntini mu akisikuru yi kɔ so, titiriw sɛ ɛmma wuntumi nkɔ wo da biara da dwumadi anaa wo nna mu a, akyinnye biara nni ho sɛ ɛsɛ sɛ wokɔ oduruyɛfo nkyɛn.
Kae sɛ ɛho nhia sɛ wobɔ hu wɔ biribi te sɛ akisikuru a ɛyɛ daa ho. Nanso sɛ saa akisikuru yi kɔ so a, ebetumi ayɛ biribi a anibere wom ho sɛnkyerɛnne, enti nyansa wom sɛ wobɛhwehwɛ aduruyɛ mu afotu.
Sɛ wususuw sɛ woanom awuduru bi a, kɔ ayaresabea Emergency Treatment Unit (ETU) ntɛm ara. Wubetumi nso afrɛ Ɔman Awuduru Ho Amanneɛbɔbea a ɛwɔ Colombo Ɔman Ayaresabea hɔ akɔhwehwɛ afotu.
Myoclonus ahorow pɔtee afoforo
Myoclonus ahorow pɔtee afoforo pii wɔ hɔ, a ɛba wɔ mfe a wɔadi anaa akwan pɔtee bi so nkutoo.
Nkokoaa a wɔawo wɔn foforo nna a ɛnyɛ hu
Eyi yɛ tebea a ɛka mmofra a wɔawo wɔn foforo. Saa nkokoaa yi nya wɔn akwaa anaa wɔn nipadua a ɛwosow mpofirim bere a wɔada no. Ɛwom sɛ eyi betumi ayɛ te sɛ akisikuru bere a edi kan de, nanso electroencephalogram (EEG) nkyerɛ akisikuru dwumadi biara. Eyi nhaw akokoaa no na ɛtaa yera koraa bere a wadi asram 6 no.
Mfinimfini aso mu ntini a ɛyɛ mmerɛw
Eyi ne bere a ntini bi a wɔfrɛ no tensor tympani a ɛwɔ w’aso mu no twetwe a wuntumi nni so. Mpɛn pii no, saa ntini yi twetwe bere a yɛkasa, didi, anaa yɛserew de bɔ aso a ɛwɔ mu no ho ban. Nanso wɔ eyi mu no, saa ntini yi twetwe wɔ bere a ɛnteɛ mu, na ɛma nnyigyei a ɛbɔ anaasɛ ɛrebɔ bere nyinaa ba aso no mu. Eyi yɛ ahometew, nanso ɛnyɛ nea asiane wom. Wobetumi de oprehyɛn anaa akwan foforo ayɛ ho adwuma.
Opsoclonus-myoclonus yare a ɛma obi nya ɔyare (OMS) .
Opsoclonus yɛ ntini a ɛhwɛ aniwa no kwan a ɛkɔ so no a ɛnyɛ ne pɛ. OMS yɛ tebea a ɛntaa nsi a aniwa a ɛtwetwe ne nipadua mu ntini a ɛtwetwe nyinaa bom ba. Ɛtɔ mmere bi a ɛba bere a yɛn nipadua mu tumi a ɛko tia nyarewa no di mfomso tow hyɛ yɛn ankasa ntini ahorow so no. Wɔ mmofra mu no, amemene mu kokoram bi a wɔfrɛ no neuroblastoma betumi afi nipadua no mu tumi a ɛko tia nyarewa yi mu aba. Wɔ mpanyimfo mu no, tebea no betumi ne ahurututu, nufu, anaa awotwaa mu kokoram abata ho.
Ntini a ɛwɔ anom
Eyi yɛ myoclonus bi a ɛka yɛn anom a ɛyɛ mmerɛw no ntini. Eyi betumi ama ‘klik’ nnyigyei a ɛyɛ soronko aba aso no mu. Eyi betumi afi awosu mu anaasɛ amemene no asɛe bi ho sɛnkyerɛnne. Mpɛn pii no, wobetumi de nnuru adi tebea yi so.
Nkrasɛm a Wɔde Kɔ Fie
- Myoclonus yɛ ntini a ɛtwetwe mpofirim. Nneɛma te sɛ akisikuru ne nna a wɔde nantew yɛ ade a ɛfata na asiane biara nni ho.
- Nanso sɛ saa ntini a ɛwosow yi kɔ so, ɛtaa ba, ɛyɛ den, anaasɛ esiw wo da biara da asetra kwan a, ebetumi ayɛ aduruyɛ mu tebea foforo ho sɛnkyerɛnne.
- Wɔ tebea a ɛte saa mu no, mmu w’ani ngu so, na akyinnye biara nni ho sɛ kɔ wo duruyɛfo nkyɛn.
- Ayaresa no gyina nea ɛde ba no so, na wo duruyɛfo nkutoo na obetumi ahu.
- Sɛ wo ne wo duruyɛfo bɛkasa afa nnuru anaa nneɛma afoforo a worenom ho nokwarem a, ɛho hia yiye na ama woahu yare no pɛpɛɛpɛ na woanya ayaresa a ahobammɔ wom.
👩🏽 ⚕️ Nsɛmmisa foforo (FAQs)
💬 Yareɛ bɛn na wɔkyerɛw Metoprolol Tartrate / Lopressor tablets ma?
Eyi ne ‘koma mu aduru’ a edi mu na tumi wom sen biara, ɛyɛ adwuma ntɛmntɛm sen biara wɔ wiase (Cardioselective Beta-blocker)! Ɛyɛ ‘Tartrate’, enti sɛ wɔfa no a, ɛtwetwe ntɛmntɛm kɔ nipadua no mu. Nnuruyɛfo de di dwuma de siw ‘Mogya Nhyɛso’ a emu yɛ den, angina, ne titiriw no sɛ aduru a edi kan a wɔde gye ɔyarefo no nkwa wɔ bere tiaa bi a edi ‘Koma Yare’ akyi.
💬 Ɔkwan bɛn so na saa instant heart pill (Metoprolol Tartrate) yi brɛ mogya mmoroso ne koma brɛ ase?
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💬 Adɛn nti na wɔka sɛ ɛnsɛ sɛ wogyae saa aduru (Lopressor) yi nom mpofirim? Asiane bɛn na ɛwɔ mu (Black Box Warning)?
Sɛ wonom saa aduru yi asram pii na afei ‘wogyae mpofirim’ a, saa adrenaline agyefo a wɔasiw ano no nyinaa bebue mpofirim a wuntumi nni so! Afei, wɔ simma kakraa bi mu no, wubenya komayare a emu yɛ den na wo koma agyae (Angina Exacerbation / Myocardial Infarction / Severe Tachycardia) a edi awu araa ma wubetumi awu! Afei nso, saa aduru yi betumi ama wo koma ayɛ brɛoo dodo na ama woayɛ basaa/da dodo/da a wuntumi nna/ɔbrɛ.











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