So woasusuw ho pɛn sɛ wobɛhwere w’ani so tumi mpofirim na woahwere wo nan anaa wo nan bi wɔ wo nipadua no fã foforo? Eyi yɛ tebea a ɛyɛ hu na yentumi nsusuw ho ankasa, nanso ɛyɛ biribi a ɛtɔ mmere bi a ɛsɛ sɛ yehyia wɔ yɛn asetra mu. Ɛnnɛ yɛrebɛka tebea bi a ɛntaa nsi a ɛsɛ sɛ obiara hu ho asɛm. Eyi ne nea nnuruyɛfo frɛ no Weber Syndrome .
Dɛn ankasa ne Weber Syndrome?
Sɛ yɛbɛka no tiawa a, Weber Syndrome yɛ tebea bi a efi w’amemene no mfinimfini sɛe . Mfinimfini amemene no yɛ bridge a ɛho hia a ɛde nkrasɛm fi w’amemene mu kɔ w’akyi berɛmo mu. Ɛyɛ w’amemene no fã a ɛwɔ w’amemene no atifi. Ntini abien a ɛho hia a ɛhwɛ ti nhwi so a ɛhwɛ nneɛma te sɛ w’ani a wobɛkanyan ne w’aniwa a wobɛma so —oculomotor nerve ne trochlear nerve —fi ase wɔ amemene no mfinimfini.
Enti, sɛ mfinimfini amemene yi sɛe ɔkwan biara so a, wubenya hemiplegia , a ɛkyerɛ sɛ worentumi nni wo nipadua no fã biako so. Bere koro no ara mu no, wubehyia ɔhaw ahorow wɔ aniwa ne anisoadehu a ɛwɔ ɔfã foforo no ho. Eyi ne nea wohu titiriw wɔ Weber Syndrome mu. Wobu eyi sɛ tebea a ɛntaa nsi koraa .
Nea ɛtaa ma amemene no mfinimfini sɛe ne akisikuru , a ɛyɛ mogya a ɛkɔ amemene no mu a ɛtwa mpofirim. Nanso, ebetumi aba esiane nneɛma afoforo nso nti.
Dɛn ne eyi ho sɛnkyerɛnne? Yɛyɛ dɛn hu no?
Nsɛnkyerɛnne atitiriw pii wɔ hɔ a wobetumi ahu wɔ Weber Syndrome mu. Wɔne:
- Aniwa a ɛhwe ase (ptosis) wɔ aniwa biako mu . Ɛte sɛ nea wɔato aniwa no fã.
- Ebia aniwa a aka no bɛdan akɔ fam na akɔ akyi , a ɛkyerɛ sɛ wontumi nni aniwa no so yiye.
- Nneɛma abien a wubehu prɛko pɛ (diplopia) . Wɔfrɛ eyi anisoadehu abien.
- Abasa ne nan a ɛwɔ nipadua no fã biako no fã bi anaasɛ ɛyɛ obubuafo koraa . Eyi ba wɔ aniwa a ayɛ no yaw no fã a ɛne no bɔ abira no so.
Nea ɛho hia yiye: Sɛ wuhu saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa, anaasɛ sɛnkyerɛnne afoforo pii a ɛkyerɛ sɛ obi akisikuru no mu biara , te sɛ kasa a ɛyɛ mmerɛw , nkate a ɛyera , nhumu a ɛyera , kari pɛ ho nsɛm , anaa w’anim a ɛyɛ mmerɛw , ɛsɛ sɛ wokɔ ayaresabea ntɛm ara. Eyi betumi ayɛ nkwa anaa owu tebea.
Ɛtɔ mmere bi a, nnipa a wɔwɔ Weber Syndrome no anya...Ɔhaw ahorow a ɛfa kari pɛ ne nneɛma a wɔyɛ no pɛpɛɛpɛ ho (ataxia) , a ɛkyerɛ sɛ ɛyɛ den sɛ ɔbɛnantew na wafa nneɛma mu nso betumi aba.
Mpɛn pii no, sɛ Weber Syndrome nkutoo na ɛwɔ hɔ a, ɛnka wo nsusuwii (nkae, nyansa) . Nanso, sɛ amemene no afã afoforo a asɛe no atrɛw a, sɛnkyerɛnne afoforo betumi ada adi. Sɛ nhwɛso no, ɛtɔ mmere bi a, pons, amemene no fã bi a ɛyɛ obubuafo betumi aka Weber Syndrome ho. Sɛ ɛba saa a, wobetumi ahu sɛnkyerɛnne afoforo nso.
Dɛn na ɛde Weber Syndrome ba?
Weber Syndrome fi akuru bi a ɛwɔ w’amemene no mfinimfini fã pɔtee bi a ɛwɔ ventromedial mu. Nneɛma atitiriw a ɛde ɔsɛe a ɛte sɛɛ ba ne:
- Akisikuru: Eyi ne ade a ɛtaa de ba. Ebetumi afi mogya ntini bi a ɛde mogya kɔ amemene no fã no mu a asiw anaa apaapae mu aba.
- Brain aneurysm (mogya ntini bi a ɛpae na ɛpae wɔ amemene no mu).
- Amemene mu mogya a ɛtɔ.
- Amemene mu akisikuru.
- Nyarewa a ɛma mogya tu , te sɛ Multiple Sclerosis sɛe myelin aduru a atwa ntini ahorow no ho ahyia no.
Hena na ɛda adi sɛ obenya eyi? (Nneɛma a ɛde asiane ba) .
Sɛnea yɛadi kan aka ho asɛm no, ade titiriw a ɛde Weber Syndrome ba ne ɔyare a ɛma obi hwe ase, enti asiane koro no ara a ɛka akisikuru no nso ka no. Ɛyɛ:
- Mogya mmoroso (Mogya mmoroso / Hypertension).
- Cholesterol a ɛkɔ soro wɔ mogya mu (High cholesterol / Hyperlipidemia).
- Asikyireyareɛ.
- Sigaretnom.
Sɛ wowɔ asiane ahorow yi mu biako anaa nea ɛboro saa a, ɛho hia yiye sɛ wunya aduruyɛ mu afotu daa na wudi so. Saa a wɔbɛyɛ no betumi atew asiane a ɛwɔ hɔ sɛ obi benya tebea horow te sɛ obubuafo ne Weber Syndrome no so.
Ɔkwan bɛn so na nnuruyɛfo hu eyi? (Nyare a Wɔahu) .
Sɛ wowɔ sɛnkyerɛnne ahorow a ɛfa Weber Syndrome ho a, nnuruyɛfo bedi kan abɔ mmɔden sɛ wobehu sɛ ebia worenya akisikuru anaa. Nea enti a ɛte saa ne sɛ ayaresa a wɔde ma ntɛm ne ade a ɛho hia sen biara. Sɛ wobɛyɛ eyi a:
- Wɔbɛyɛ wo ntini mu nhwehwɛmu a edi mũ wɔ wo ntini mu .
- Wɔyɛ amemene mu CT scan ntɛm ara.
- Ɛtɔ mmere bi a, wobetumi akamfo akyerɛ sɛ wɔnyɛ scan soronko de hwehwɛ mogya ntini a ɛwɔ ti ne kɔn mu ne amemene no MRI scan nso.
Sɛ wo yare no ho sɛnkyerɛnne ne saa mfonini ahorow yi si so dua sɛ w’amemene no mfinimfini asɛe a, nnuruyɛfo bɛka sɛ wowɔ Weber Syndrome.
Dɛn ne ayaresa a wɔde sa eyi?
Sɛ wɔresa Weber Syndrome a, nea edi kan a wɔde wɔn adwene si so ne sɛ wɔbɛsa nea ɛde ba (mpɛn pii no ɛyɛ akisikuru). W’aduruyɛfo kuw no bɛhwɛ wo mframa kwan no so ntɛm ara na wɔasan de mogya akɔ w’amemene mu. Wɔ tebea horow bi mu no , ebia amemene mu oprehyɛn (ntini mu oprehyɛn) nso ho behia.
Akwan a wɔfa so siesie wɔn ho ne ayaresa titiriw a wɔde di dwuma titiriw ma Weber Syndrome.
Dɛn ne ahosiesie? Ɛho hia dɛn?
Nnipa pii a wɔanya akisikuru no ho a wɔbɛsan asiesie no yɛ ade titiriw a ɛma wɔn ho tɔ wɔn. Nea ɛka ho ne sɛ wɔbɛboa wo ma woasan anya ahokokwaw a woahwere esiane nsakrae a ɛbaa w’amemene mu nti, anaasɛ wɔbɛboa wo ma woasua sɛnea wobɛtra ase ne nsakrae no. Kuw a wɔatete wɔn titiriw a wɔde sa akisikuru a ɛma obi hwe ase anaasɛ apɔw-mu-teɛteɛ ho ɔyaresafo betumi aboa wo wɔ eyi mu. Ɛyɛ papa sɛ wubefi saa nhyehyɛe a wɔde bɛsan asiesie yi ase ntɛm ara sɛnea wubetumi.
Weber Syndrome ne mfinimfini amemene mu yare a wɔbɛsan asiesie no betumi ayɛ:
- Apɔw-mu-teɛteɛ a ɛboa ma obi akwaa a abubu (Range-of-motion exercises) .
- Apɔw-mu-teɛteɛ a wɔde bɛma kari pɛ na wɔayɛ biako atu mpɔn.
- Ma wɔnhwɛ w’ani na yɛ apɔw-mu-teɛteɛ a ɛfata na ama w’ani a wohu mmɔho abien no so atew.
- Ebia nnipa binom rentumi nni wɔn nsu a wɔtow (urinary incontinence) so. Ntetee titiriw ho hia ma ɛno (Akisikuru ntetee) .
- Nnuru ne nneɛma afoforo a wɔde wɔn ho bɛhyɛ mu ho hia na ama wɔatumi asiw nneɛma a ɛde akisikuru a ɛwɔ hɔ dedaw no ano na wɔasiw akisikuru a ɛbɛba daakye ano.
Bere tenten ahe na ebegye na obi ho atɔ no afi tebea yi mu? (Wɔhwɛ kwan sɛ ne ho bɛtɔ no) .
Nneɛma pii nya obi a ɔwɔ Weber Syndrome nkɔmhyɛ so nkɛntɛnso, a nea ɛka ho ne:
- Dɛn nti na ɛte saa?
- Hwɛ sɛnea wo nsa kaa ayaresa ntɛmntɛm .
- So Weber Syndrome nkutoo na wowɔ, anaasɛ amemene no afã afoforo nso asɛe ?
- Hwɛ sɛnea woreyɛ yiye de asiw mmubuafo daakye ano .
Mpɛn pii no, nnipa a wɔwɔ Weber Syndrome nkutoo, a wɔn amemene mu nneɛma foforo asɛe no, nya nkɔmhyɛ pa . Afei nso, sɛ wofi ase siesie wo ho ntɛm a , ɛho hia yiye ma ahotɔ nhyehyɛe no.
Sɛ wɔsan siesie wɔn a, ebia nnipa binom bɛsan ayɛ adwuma bi wɔ wɔn akwaa ne wɔn aniwa a ɛka wɔn no mu. Nanso, afoforo betumi anya ɔhaw a ɛtra hɔ daa wɔ sɛnea wɔbɛkɔ baabiara ne ntini mu nsɛnnennen afoforo.
Wo nnuruyɛfo kuw no betumi ama wo nea wobɛhwɛ kwan ho adwene a emu da hɔ a egyina wo tebea no so.
Nsɛnnennen afoforo bɛn na ebetumi aba esiane Weber Syndrome nti?
Weber Syndrome taa de nsɛnnennen ba, titiriw sɛ woada mpa so a. Ɛno nti na w’aduruyɛ kuw no bɛbɔ mmɔden sɛ wɔbɛma woatu ntɛmntɛm na ahobammɔ wom sɛnea wobetumi no. Nsɛnnennen a ebetumi aba no bi ne:
- Ntini a ɛyɛ den ne nea ɛtwetwe .
- Mpa so akisikuru .
- Aspiration pneumonia ba bere a aduan anaa anonne hyɛn mframa kwan no mu na ɛde ahurututu mu nyarewa ba no.
- Mogya a ɛtɔ wɔ nan no ntini a emu dɔ mu (Deep vein thrombosis - DVT) .
- Saa mogya a ɛtɔ no kɔ ahurututu mu (ahurututu mu ntini a ɛma mogya tu) .
- Nsuo mu yareɛ (UTIs) .
Nea etwa to no, ade a ɛho hia sen biara a ɛsɛ sɛ yɛkae
Akisikuru betumi adan w’asetra ayɛ basaa prɛko pɛ. Enti, ɛho hia yiye sɛ wubehu ne sɛnkyerɛnne ahorow no yiye na sɛ wo anaa obi a ɔbɛn wo nya sɛnkyerɛnne a ɛte saa a, wokɔ ayaresabea ntɛm ara. Weber Syndrome betumi ayɛ tebea a ɛntaa nsi, na ebia wobɛte ehu ne dadwen nka bere a wote ho asɛm no. Nanso kae ade biako ne sɛ, w’aduruyɛfo kuw no ayɛ krado bere nyinaa sɛ wɔbɛboa wo na wɔaka wo ho wɔ w’akwantu a wode bɛsan agye wo ho no mu. Enti ma w’adwene nyɛ den na di afotu a wɔde ama no akyi.
` Weber Syndrome, obubuafo, amemene mu yare, amemene mfinimfini, aniwa mu sɛnkyerɛnne, ntini mu nyarewa, ahosiesie











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