Ðewohĩ èxɔa ʋuʋudedi kple ʋuʋudedi ƒomevi ɖesiaɖe le wò ŋutigbalẽ ŋu, alo? Ɣeaɖewoɣi la, woɖea lã eye woƒe ʋeʋẽ lilili geɖe. Zi geɖe la, míesusuna be nusiawo nye nusiwo ŋu nulɔdɔ le, eczema, alo psoriasis si sɔ ko. Gake ŋutigbalẽ ƒe kuxi si nɔa anyi ɖaa si mehayana o ƒe geɖe ate ŋu anye nusi nu sẽ vie wu ɣeaɖewoɣi. Ema nye nɔnɔme mawo siwo mebɔ o siwo ŋu wòle be mí katã míanya la dometɔ ɖeka.
Nukae nye Cutaneous T-cell Lymphoma (CTCL) ƒe dɔléle?
Kpuie ko la, CTCL nye ʋumenugbagbeviɣidɔ ƒomevi aɖe si mebɔ kura o si gblẽa nu le míaƒe ŋutigbalẽ ŋu. Ŋutilãe nye ŋutinu gãtɔ kekeake le míaƒe ŋutilã me. Kansa sia gblẽa nu le míaƒe ŋutigbalẽ ŋu tẽ. Le nyateƒe me la, ele kansa ƒe ƒuƒoƒo gã aɖe si woyɔna be `(non-Hodgkin lymphoma)` me.
Fifia ɖewohĩ ànɔ ɖokuiwò biam be aleke kansa si le ʋu me ate ŋu aɖo ŋutigbalẽa me hã. Enyo, ʋumenugbagbevi ɣi ƒomevi aɖe si woyɔna be ``lymphocytes`` le míaƒe ʋu me. Esiawo nye míaƒe ŋutilã ƒe dɔlélenutsiŋutete ƒe akpa vevi aɖe ŋutɔ. Woyɔa ʋumenugbagbevi siawo ƒe ƒomevi ɖeka be ``T-cells``. Le CTCL me la, T-lãmenugbagbevi siawo zua kansa lãmenugbagbeviwo eye wodzea mama gɔme le mɔ si dzi womate ŋu aɖu o nu. Emegbe kansa lãmenugbagbevi siawo vaa ŋutigbalẽa me heƒoa ƒu. Ɣemaɣie ŋutigbalẽ ƒe dzesiwo dzea egɔme dzena.
Mègavɔ̃ be yeagblɔ be kansae o. Ame geɖe siwo ŋu CTCL le ateŋu aɖu dɔlélea dzi le atikewɔwɔ vɔ megbe (`remission`). Eyata woate ŋu anɔ agbe si sɔ evɔ womagblẽ nu boo aɖeke o. Gake esɔ be nàlé blanui ne èva nya be kansa le ye ŋu. Wò ɖɔkta kple atikewɔlawo ƒe ƒuƒoƒoa le klalo ɣesiaɣi be yewoakpe ɖe ŋuwò.
Nukawoe nye CTCL ƒomevi veviwo?
CTCL ƒomevi vovovowo li. Gake le wo dome la, ƒomevi vevi eve li siwo wokpɔna. Mina míase esiawo gɔme nyuie.
| Kansa ƒomevi | Nuɖᴐɖᴐ |
|---|---|
| Mycosis fungoides ƒe dɔléle | Esiae nye ƒomevi si bɔ wu, eye wòdzea CTCL dɔnɔwo ƒe afã lɔƒo dzi. Eƒe nu tɔxɛe nye be etsia blewu ŋutɔ.Le afisia la, zi geɖe la, ŋutigbalẽa me koe kansa ƒe T-lãmenugbagbeviwo nɔa wo ŋu. Gake ɣeaɖewoɣi la, ɖewo hã te ŋu zɔa mɔ yia ʋukawo kple ʋu me. Woyɔa kansa lãmenugbagbevi siwo zɔa mɔ yia ʋua me alea be Sézary lãmenugbagbeviwo. |
| Sézary ƒe dɔlélea | Esia nye CTCL ƒomevi si le dzidzim ɖe edzi kabakaba ŋutɔ . Le go sia me la, àte ŋu akpɔ Sézary lãmenugbagbevi gbogbo aɖewo le wò ŋutigbalẽ kple ʋu me. Ɣeaɖewoɣi la, mycosis fungoides ate ŋu asẽ eye wòava zu Sézary ƒe dɔléle. Amesiwo ŋu dɔléle sia le ate ŋu ade dzesi ŋutigbalẽ ƒe amadede ƒe tɔtrɔ le woƒe ŋutilã katã me. |
Nukawoe ate ŋu anye dɔléle sia ƒe dzesiwo?
CTCL ƒe dzesiwo ate ŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ. Woɖi ŋutigbalẽdɔléle siwo bɔ hã ŋutɔ. Esia tae ate ŋu asesẽ be woakpɔ dɔlélea.
- Kpe siwo dzena le ŋutigbalẽa dzi. Ɣeaɖewoɣi la, esiawo ate ŋu agbã eye woazu abi.
- Taɖa ƒe ʋuʋu .
- Nɔnɔme si le abe ʋuʋudedi ene si dzena le ŋutilã bliboa me eye wònɔa ʋuʋum ɣesiaɣi .
- Nusiwo ƒe amadede trɔ le ŋutigbalẽa ŋu ƒe dzedzeme.
- Kpe siwo le ʋuʋum, siwo me ʋuʋudedi le ɣeaɖewoɣi, siwo do tso ŋutigbalẽa me.
- Glands ƒe vuvu ( le ŋɔti me , akɔta, akɔta, kple bubuawo me).
- Ŋutilã si le asibidɛwo kple afɔkpodziwo ŋu ƒe ƒoƒo kple eƒe ƒuƒu .
Nukatae dɔléle sia ƒomevi dzɔna?
Wogblɔ na mí be le CTCL me la, T-lãmenugbagbeviwo zua kansa lãmenugbagbeviwo. Gake ɖɔktawo menya nusita tututu nusia dzɔna haɖe o. Gake nu eve aɖewo li siwo wosusu be wowɔa akpa aɖe.
1. Domenyiŋusẽfianu ƒe vovototowo: Domenyiŋusẽfianue kpɔa míaƒe lãmenugbagbeviwo ƒe dɔwɔwɔ dzi. Numekulawo kpɔe be tɔtrɔ (trɔtrɔ) le domenyiŋusẽfianu aɖewo me ate ŋu ahe dɔléle sia vɛ.
2. Dɔlékuiwo: Bu nusi dzɔna ne dɔlékui sesẽ aɖe xɔ míaƒe ŋutilã ŋu kpɔ. Míaƒe dɔlélenutsiŋutete dzrana ɖo be yeawɔ avu. Ema fia be míaƒe ƒumeŋuɖui dzea ʋumenugbagbevi ɣiwo, vevietɔ ʋumenugbagbevi dzĩwo, wɔwɔ gɔme kabakaba. Ele abe dɔwɔƒe aɖe si le ewɔwɔ dzim ɖe edzi zi ɖeka ene. Ne èle dɔ wɔm kabakaba alea la, vodadawo ate ŋu adzɔ ɣeaɖewoɣi. Aleae vodadawo ate ŋu adzɔ le lãmenugbagbeviwo ƒe DNA me, si ana mɔnukpɔkpɔ si li be kansa lãmenugbagbeviwo nadzi ɖe edzi.
Nu vevitɔ kekeakee nye be CTCL menye dɔléle si xɔa ame me o. Eye menye nusi nàte ŋu awɔe wònye o.
Amekawoe le afɔku me wu be woaxɔ dɔléle sia?
Afɔku siwo ate ŋu ado tso eme koe esiawo nye. Menye amesiame si ŋu wo le lae axɔ dɔlélea o.
- Le amesiwo xɔ wu ƒe 50 gome .
- Ŋutsuwo le afɔku me vie wu nyɔnuwo.
- Le amesiwo ƒe dɔlélenutsiŋutete gbɔdzɔ gome (le kpɔɖeŋu me, amesiwo wodo ŋutinuwo na).
- Le numekuku aɖewo nu la, amesiwo tso Afrika.
Aleke ɖɔkta awɔ ake ɖe esia ŋu?
Ne èyi ɖɔkta gbɔ le ŋutigbalẽ ƒe kuxi aɖe ta la, abia wò gbã tso wò dzesiwo ŋu. Emegbe woalé ŋku ɖe wò ŋutigbalẽ ŋu nyuie. Gake be nàɖo kpe edzi be CTCL le ŋuwò hã la, ehiã be nàwɔ dodokpɔ geɖe.
| Dodokpɔ | Kpuie ko la,... |
|---|---|
| Ŋutilã ƒe lãmenugbagbeviwo ƒe dɔwɔwɔ | Esiae nye dodokpɔ vevitɔ kekeake. Nusi wowɔna le afisiae nye be woɖea ŋutigbalẽ sue aɖe tso abi alo teƒe aɖe me hedoa ekpɔ le nusuekpɔmɔ̃ me. Esia ate ŋu anya ne kansadɔlékuiwo li hã. |
| Ʋudodokpɔwo | Esia kpena ɖe ame ŋu wòléa ŋku ɖe kansa lãmenugbagbeviwo (Sézary lãmenugbagbeviwo) le ʋua me, kpakple nu bubu siwo mesɔ o hã ŋu. |
| Lãmetsiŋusẽ ƒe dɔwɔwɔ ŋuti numekuku | Ne ʋuka aɖe vuvu la, woɖea eƒe akpa sue aɖe hedonɛ kpɔna be kansa la kaka ɖe eme hã. |
| Nɔnɔmetatawo ɖeɖe ƒe dodokpɔwo | Dodokpɔwo abe CT scan alo PET scan ene ate ŋu anya ne kansa la kaka ɖe ŋutilã ƒe ŋutinu ememetɔwo me. |
Nukawoe nye atike siwo wozãna na CTCL?
Wonɔa te ɖe ƒomevi, afɔɖeɖe, kple wò lãmesẽ bliboa dzi daa CTCL. Atikewɔwɔ ɖeka aɖeke meli si sɔ na amewo katã o. Wò ɖɔkta awɔ atikewɔwɔ ƒe ɖoɖo si anyo na wò.
- Kreme kple ami siwo wotsɔna ƒoa ŋutigbalẽa: Esiawo nye atike siwo me atikewo abe steroid ene le. Esiawo ate ŋu asu na dɔnɔ siwo le eƒe gɔmedzedze.
- Kekeli ƒe dɔdamɔnu (Fotodada): Woɖoa kekeli tɔxɛ aɖe si woyɔna be ultraviolet (UV) ɖe ŋutigbalẽa ŋu be wòatsrɔ̃ kansa lãmenugbagbeviwo.
- Extracorporeal photopheresis (ECP): Esia nye atikewɔwɔ si sesẽ vie wu. Le afisia la, woɖea wò ʋu ƒe ɖe, toa mɔ̃ aɖe me, afisi wotsɔa atike kple akaɖi da dɔ le be woatsɔ ada kansadɔlékuiawoe, eye emegbe wogadea wò ʋu me ake.
- Kekeli ƒe dɔdamɔnu: Wozãa keklẽŋusẽ si me ŋusẽ geɖe le tsɔ tsrɔ̃a kansadɔlékui siwo le ŋutigbalẽa me.
- Dɔlélenutsiŋutete ƒe atikewɔwɔ: Míenaa atike siwo doa ŋusẽ mía ŋutɔwo ƒe dɔlélenutsiŋutete eye wònana wòwɔa avu kple kansa lãmenugbagbeviwo.
- Atikewɔwɔ: Atike sesẽ siwo wua kansa lãmenugbagbeviwo. Woate ŋu ana esiawo abe atikekuiwo alo atikekuiwo ene.
Aleke agbea anɔ kple dɔléle sia?
Esiae nye nyabiase gãtɔ kekeake si le amesiame ƒe susu me. CTCL ƒomevi akpa gãtɔ tsina blewu ŋutɔ. Eya ta womedea ame ƒe agbe afɔku me o. Togbɔ be ɖɔktawo mate ŋu ada dɔléle sia keŋkeŋ o hã la, atikewɔwɔ ate ŋu aɖu dzesiawo dzi dzidzedzetɔe.
Gake ehiã hã be míase nyateƒea gɔme. Abe kansa ɖesiaɖe ene la, CTCL ate ŋu awu ame ne eɖo afisi wòde ŋgɔ wu.
Esia tae míegblɔ be ele vevie ŋutɔ be nàyi ɖɔkta gbɔ ne ènya de dzesi tɔtrɔ aɖe le wò ŋutigbalẽ ŋu ko . Zi alesi nèdze atikewɔwɔ gɔme kaba la, zi nenemae mɔnukpɔkpɔ asu asiwò be nànɔ agbe nyuie wu.
Numekukuwo ɖee fia be ame 9 le 10 siwo ŋu wokpɔ dɔlélea le le eƒe gɔmedzedze (afɔɖeɖe I alo II) me la gakpɔtɔ le agbe le ƒe 10 megbe. Ema nye agbetsitsi ƒe agbɔsɔsɔme si nye 90%. Le amesiwo ŋu dɔléle si de ŋgɔ le gome la, agbɔsɔsɔa nye 53% ko. Akɔntabubuwo koe esiawo nye. Ame nyuitɔ si anya nusi tututu wò nɔnɔmea nye enye wò ɖɔkta.
Aleke míawɔ alé be na míaƒe ŋutigbalẽ ahaɖe afɔkua dzi akpɔtɔ?
Naneke meli míate ŋu awɔ atsɔ axe mɔ ɖe CTCL nu o, elabena womate ŋu atrɔ afɔku siwo gblẽa nu le eŋu o. Gake míaƒe dɔlélenutsiŋutete ƒe ŋusẽ léle ɖe asi nyo na dɔlélewo katã.
Azɔ hã, ne CTCL le ŋuwò la, ele vevie ŋutɔ be nàlé be na wò ŋutigbalẽ.
- Na wò ŋutigbalẽ nade tsi: Zã tsilénu nyui aɖe le tsilele vɔ megbe kple le ŋkekea me katã. Esia akpe ɖe ŋuwò nàɖe ƒuƒu, eƒe ŋeŋe, kple eƒe ʋeʋẽ dzi akpɔtɔ.
- Takpɔ ɖokuiwò ta tso ŋutigbalẽ me dɔlékuiwo me: Zã adzalẽ siwo me ʋeʋẽ lilili mele o kple atike siwo wotsɔna klɔa nu ŋu. Do awu siwo tsyɔa wò ŋutigbalẽ dzi ne èle ŋdɔ me yim, eye nàtsɔ ɣe ƒe keklẽŋusẽtike asisi ɖe eŋu. Do awu siwo me mekɔ o, siwo me gbɔgbɔ le.
- Dzudzɔ ʋuʋudedi: Ʋuʋudedie nye kuxi gãtɔ kekeake si dzea ŋgɔ dɔnɔ siawo. Ne wole ƒoƒom la, wogbãa ŋutigbalẽa eye dɔlékuiwo te ŋu gena ɖe eme, si ahe dɔlékuiwo vɛ. Eyata ɖu ƒoƒoa dzi alesi nàte ŋui. Àte ŋu akpɔ gbɔdzɔe ne èwɔ nuwo abe tsi fafɛ kɔklɔ, tsilele le oatmeal tsi me, kple atike siwo wua histamine siwo wò ɖɔkta kafu na wò zazã ene.
Ɣeyiɣi kawoe nye nyuitɔ kekeake siwo nàte ŋu ayi ɖɔkta gbɔ?
Ne ènya dze atikewɔwɔ gɔme ko la, ele be wò ɖɔkta nakpɔ wò edziedzi. Gake ne nane si le abe esia ene dzɔ le ɣeyiɣi sia me la, kpɔ egbɔ be yeƒo nu kple wò ɖɔkta.
- Ne ède dzesi tɔtrɔ yeye aɖewo le wò ŋutigbalẽ ŋu .
- Ne èse le ɖokuiwò me be ŋutigbalẽ me dɔléle aɖe le ye ŋu (e.g., ebiã, ese veve, evuvu, alo ʋuʋudedi le dodom).
- Ne asrã le ŋuwò wu Fahrenheit 100.4 (Celsius 38) .
Zi geɖe la, ne míexɔ ʋuʋudedi alo ʋuʋudedi le míaƒe ŋutigbalẽ ŋu la, míesusuna be esɔ. Ame aɖeke mesusui be ate ŋu anye kansa si mebɔ o abe esia ene o. Gake nu vevitɔe nye be, ne èkpɔ tɔtrɔ aɖe le wò ŋutigbalẽ ŋu la, mègaŋe aɖaba ƒu edzi nàtsɔe afia ɖɔkta o. Ðewohĩ menye kansae o. Gake ne ele nenema la, atikewɔwɔ gɔmedzedze kaba nye nu nyuitɔ kekeake si nàte ŋu awɔ na wò agbe.
Gbedasi si Wotsɔ Yi Aƒeme
- CTCL nye ʋumenugbagbeviɣidɔ ƒomevi aɖe si mebɔ o si gblẽa nu le ŋutigbalẽ ŋu. Eƒe dzesiwo ɖi ŋutigbalẽ ƒe nɔnɔme siwo bɔ abe eczema kple psoriasis ene ŋutɔ.
- Ne ŋutigbalẽ ƒe kuxi siwo nu metsina o le ŋuwò le ɣeyiɣi didi aɖe megbe la, mègaŋe aɖaba ƒu wo dzi eye nàyi ɖɔkta gbɔ o.
- Zi alesi wokpɔ dɔléle sia kaba la, zi nenemae mɔnukpɔkpɔ si li be woadae dzidzedzetɔe eye woanɔ agbe nyuie wu.
- CTCL menye dɔléle si xɔa ame me o. Atikewɔwɔ ate ŋu aɖu dzesiawo dzi eye wòalé agbenɔnɔ nyui me ɖe asi.











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