Ua ʻike mākou a pau he like nā hunaola koko keʻokeʻo i loko o ko mākou kino me nā koa e pale aku iā mākou mai nā maʻi. Akā, e noʻonoʻo, he aha ka mea e hana ai inā ulu nui kēia mau hunaola pale, i kapa ʻia ʻo nā histiocytes, i loko o ko mākou kino? ʻO ia ka manawa e hoʻomaka ai ka pilikia. Hiki i kēia mau hunaola ke hōʻiliʻili a hana i nā puʻupuʻu a me nā ʻeha ma nā wahi like ʻole o ke kino. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi maʻi laha ʻole e ulu ana e like me kēia.
He aha ka LCH (Langerhans cell histiocytosis)?
I ka ʻōlelo maʻalahi, ʻo LCH (Langerhans Cell Histiocytosis) he maʻi laha ʻole e like me kekahi mau ʻano maʻi kanesa. Ma kēia kūlana, ulu kahi ʻano cell immune i kapa ʻia ʻo Langerhans me ka ʻole o ka hoʻomalu ʻia a hōʻiliʻili ma nā ʻāpana like ʻole o ke kino.
ʻIke pinepine ʻia kēia maʻi i nā keiki ʻōpio a me nā pēpē , akā hiki nō hoʻi ke loaʻa i nā pākeke. ʻOiai i kekahi manawa ua manaʻo ʻia he maʻi kanesa, ʻaʻole ia he maʻi kanesa maoli. Eia nō naʻe, ua mālama ʻia e nā kauka oncologists. No laila, mai hopohopo. E nānā hou aku kākou i kēia.
He aha nā hōʻailona o kēia maʻi?
Hiki i ka LCH ke hoʻopilikia i kekahi ʻōkana o ke kino. No ka laʻana, hiki iā ia ke hoʻopilikia i nā māmā, ke akepaʻa, ka lolo, ka spleen, a i ʻole nā kikowaena lymph. Eia nō naʻe, ʻike ʻia nā hōʻailona maʻamau i ka ʻili a me nā iwi.
Hiki i kekahi poʻe ke ʻike i nā hōʻailona palupalu loa a hoʻōla iā lākou iho me ka ʻole o ka lāʻau lapaʻau. Eia nō naʻe, no kekahi poʻe, hiki ke lilo i maʻi lōʻihi e hoʻopilikia i nā ʻāpana he nui o ke kino.
E nānā kākou i ka papa ma lalo nei e ʻike i nā hōʻailona e hōʻike ai ʻo LCH ke hoʻopilikia ia i nā ʻāpana like ʻole o ke kino.
| ʻĀpana kino i hoʻopilikia ʻia | Nā hōʻailona e ʻike ʻia |
|---|---|
| Nā iwi | I ka manawa pinepine, e hoʻokumu ʻia nā pehu ʻeha a i ʻole nā puʻupuʻu (granulomas) i loko o ke poʻo a me nā iwi ʻē aʻe. Hiki i kēia ke hana i ka ʻeha o ka iwi, ka pehu ʻana, a i kekahi manawa hiki i nā haki ma nā lālā. |
| ʻIli | Nā puʻupuʻu ʻulaʻula a unahi i nā ʻili (e like me nā ʻāʻī lima, ka ʻūhā). Hiki i nā pēpē ke loaʻa nā ʻāpana ʻulaʻula a unahi ma ke poʻo. I kekahi manawa hiki ke kuhihewa ʻia kēia me ke pāpale cradle, he maʻi maʻamau ia. |
| Ake | Hoʻopilikia pinepine ʻia ke akepaʻa i nā hihia koʻikoʻi o ka maʻi. ʻO nā hōʻailona e komo pū me ka melemele o ka ʻili (jaundice) a me ka manawa lōʻihi no ke koko e paʻa ai. |
| Nā Pūnaehana Lymph | Pehu ʻana o nā kelepaʻi ma hope o nā pepeiao, ma ka ʻāʻī, a ma nā wahi ʻē aʻe. Eia kekahi, hiki ke paʻakikī ka hanu ʻana a me ke kuni ʻana. |
Pehea e ʻike pono ai i ka maʻi?
Inā kānalua kāu kauka i kēia maʻi, pono lākou e hana i kahi biopsy e hōʻoia i ka hōʻailona. Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai kahi kānalua a nānā ʻia ma lalo o kahi microscope e kahi pathologist. E nānā kēia i nā protein kikoʻī a me nā māka ʻē aʻe e pili ana i ka maʻi.
Eia kekahi, hiki i kāu kauka ke kauoha i nā hoʻokolohua hou aʻe ma muli o kāu mau hōʻailona.
- Nā hoʻāʻo X-ray: E nānā i ke kūlana o kou mau māmā a me nā iwi.
- Biopsy iwi ʻiʻo: Nānā i nā pūnaewele LCH i loko o ka iwi ʻiʻo.
- Nā hoʻāʻo kemika koko: E nānā i ka hana o nā puʻupaʻa, ke akepaʻa, ke kalena thyroid, a me ka ʻōnaehana pale.
- ʻO MRI, PET, a me CT scan: E kiʻi i nā kiʻi kikoʻī o loko o ke kino.
- Urinalysis: E nānā i nā pae o nā hunaola ʻulaʻula a me keʻokeʻo, ka protein, a me ke kō i loko o ka mimi.
He aha ke kumu o ka LCH?
ʻAʻole maopopo iā mākou ke kumu e loaʻa ai i kekahi poʻe ka LCH. Akā ua ʻike ʻia aia ma kahi o ka hapalua o ka poʻe me ka maʻi he gene hewa ko lākou e hoʻoulu ai i nā hunaola Langerhans e ulu aʻe me ke kaohi ʻole. ʻO ka mea nui, ʻo kēia loli genetic (mutation) e hana ʻia ma hope o ka hānau ʻana. ʻO ke ʻano kēia, ʻaʻole ia he maʻi i hoʻoilina ʻia mai nā mākua mai .
Eia kekahi, manaʻo nā mea noiʻi he nui nā kumu ʻē aʻe e hoʻopilikia i kēia:
- Puhi paka.
- Ka ʻike ʻana o nā mākua i nā mea ʻawahia o ke kaiapuni e like me ka benzene a i ʻole ka lepo lāʻau.
- Nā maʻi i ka wā hānau hou.
- Loaʻa kahi moʻolelo ʻohana o ka maʻi thyroid.
He aha nā lāʻau lapaʻau no kēia?
Hoʻohana ʻia ka chemotherapy i kekahi manawa e mālama i ka LCH, no ka mea, hoʻohana ʻia ia e mālama i kekahi mau ʻano maʻi kanesa. No laila, mālama ʻia ka poʻe he nui me kēia maʻi e nā oncologists a me nā hematologists.
Akā e hoʻomanaʻo, ʻaʻole e like me ke kanesa, nā ʻano palena o LCH i kekahi manawa e hoʻoholo iā lākou iho me ka ʻole o ka lāʻau lapaʻau.
E nānā kākou i nā koho lapaʻau ma ka papa ma lalo nei.
| ʻAno lapaʻau | He wehewehe maʻalahi |
|---|---|
| Kemoterapia | Ke hoʻolako ʻana i nā lāʻau lapaʻau e luku i nā hunaola maʻi. |
| Hoʻōla radiation | Hoʻouna ʻia ka radiation haʻahaʻa i ka ʻāpana o ke kino i hoʻopilikia ʻia e ka maʻi. |
| ʻoki kino | Ka wehe ʻana i nā puʻupuʻu a i ʻole nā ʻeha i hoʻokumu ʻia e LCH ma ke ʻoki kino. |
| Nā steroid | Ke hoʻolako nei i nā steroids a i ʻole nā lāʻau anti-inflammatory ʻē aʻe e like me prednisone. |
| Hoʻōla kukui UV | He lāʻau lapaʻau no nā maʻi ʻili me ka hoʻohana ʻana i kahi kukui kūikawā. |
| Hoʻoili pūnaewele kumu | He ʻano lapaʻau i manaʻo ʻia i nā hihia koʻikoʻi loa. |
Hoʻōla ka hapa nui o ka poʻe me LCH ma hope o ka mālama ʻana. Inā ua hoʻopilikia ka maʻi i kou spleen, ate, a i ʻole ka iwi iwi, ua kapa ʻia ʻo ia ʻo 'high-risk LCH'. ʻOiai ma kēia hihia, ma kahi o 80% o ka poʻe e hoʻōla piha . No laila he mea nui e noho me ka manaʻolana.
Leka Lawe-Home
- He maʻi laha ʻole ka LCH. ʻAʻole ia he maʻi kanesa ponoʻī, akā ua mālama ʻia ia ma ke ʻano like me ke kanesa.
- ʻOiai ʻike pinepine ʻia kēia i nā keiki ʻōpio, hiki iā ia ke ulu i loko o kekahi o nā makahiki.
- Inā loaʻa iā ʻoe nā hōʻailona e like me nā ʻeha ʻili, ka ʻeha iwi, a i ʻole ka pehu ʻana, mai hoʻowahāwahā iā lākou.
- Inā kānalua ʻoe a i ʻole kāu keiki e pili ana i kēia mau hōʻailona, e ʻike pono i kāu kauka . Mai hopohopo a hoʻāʻo e nānā iā ʻoe iho ma ka pūnaewele.
- Me ka mālama kūpono, hoʻōla piha ka hapa nui o nā maʻi LCH. No laila, he mea nui loa ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono.
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