ʻAʻole paha ʻoe i lohe i kēia inoa ma mua. He maʻi kanesa kakaikahi loa ka Epithelioid Hemangioendothelioma (EHE), e kū ana ma kahi o hoʻokahi i loko o hoʻokahi miliona kānaka. He paʻakikī iki ka inoa, no laila hiki ke hopohopo. Akā, mai hopohopo. He mea nui e hoʻomaopopo maʻalahi a maopopo i kēia ʻano kakaikahi. No laila, i kēia lā, e kamaʻilio kākou e pili ana i ke ʻano o ka EHE.
I ka ʻōlelo maʻalahi, he aha ke ʻano o ka maʻi kanesa ʻo EHE?
E noʻonoʻo ʻoe ua like nā kīʻaha koko ( nā aʻa koko , nā veins, a me nā capillaries) ma loko o ko kākou kino me kahi pūnaewele o nā alanui e hohola ana ma waena o kahi ʻāina. Ua uhi ʻia ka ʻaoʻao o loko o kēia mau alanui me kahi papa lahilahi loa o nā cell. Ua kapa ʻia kēia mau cell he mau cell endothelial i ka ʻepekema lapaʻau.
Hoʻomaka ka maʻi ʻaʻai endothelial i loko o nā pūnaewele e hoʻopili ana i nā kīʻaha koko. ʻOiai aia nā kīʻaha koko ma nā wahi a pau o ko kākou kino, hiki i ka maʻi ʻaʻai EHE ke ulu ma nā wahi a pau o ke kino. Eia nō naʻe, hoʻomaka pinepine kēia mau puʻupuʻu i loko o ke akepaʻa, nā māmā, a i ʻole nā iwi . Eia nō naʻe, hiki iā lākou ke ulu ma nā wahi ʻē aʻe, e like me ke poʻo, ka ʻāʻī, ka thyroid, ka ʻōpū, nā ovaries, ka prostate, ka lolo, a me ke kaula spinal.
I kekahi manawa hiki ke ʻike ʻia ka EHE ma ke ʻano he puʻupuʻu hoʻokahi. I kekahi manawa, hiki ke ʻike ʻia he mau puʻupuʻu he nui i loko o ka ʻōkana hoʻokahi a i ʻole i loko o nā ʻōkana he nui. I ka manawa pinepine, ke ʻike ʻia ka EHE, ua pālahalaha mua ke kanesa i nā ʻōkana he nui.
He ʻano sarcoma anei ʻo EHE?
ʻAe, pololei kēlā. ʻO Sarcoma kahi ʻano maʻi kanesa e ulu ana i loko o nā ʻiʻo palupalu o ko mākou kino, e like me nā kīʻaha koko. No ka mea hoʻomaka ka maʻi kanesa EHE i loko o nā cell endothelial o nā kīʻaha koko, ua hoʻokaʻawale ʻia ʻo ia he ʻano sarcoma.
He maʻi ʻino anei kēia maʻi ʻaʻai?
ʻAe, he ʻino ka EHE, ʻo ia hoʻi he ʻano ʻino a maʻi kanesa paha. ʻAʻole e like me nā puʻupuʻu maikaʻi ʻole, hiki i kēia mau hunaola kanesa ke ulu me ka ʻole o ke kāohi ʻia, laha (metastasize) i nā ʻāpana ʻē aʻe o ke kino, a hōʻino i nā ʻiʻo olakino.
Akā eia kekahi mea e hoʻomanaʻo ai. He paʻakikī loa ka maʻi kanesa EHE. Hoʻolaha koke kekahi mau puʻupuʻu EHE, e like me nā maʻi kanesa ʻino loa. Akā ulu mālie kekahi, i nā makahiki he nui. ʻO ka mea kupanaha, ua loaʻa nā hōʻike e pili ana i ka emi ʻana o kēia mau puʻupuʻu me ka ʻole o ka lāʻau lapaʻau. Ma muli o kēia ʻano loli, he paʻakikī ke wānana i ke koʻikoʻi o kēia maʻi kanesa a pehea e pane ai i ka lāʻau lapaʻau.
He aha nā hōʻailona o ka EHE?
ʻAʻole ʻike ka nui o nā maʻi me EHE i kekahi mau hōʻailona i ka wā mua. ʻO ia ke kumu e ʻike pinepine ʻia ai i ka wā o nā hoʻokolohua no kekahi maʻi ʻē aʻe. Eia nō naʻe, inā loaʻa nā hōʻailona, e hilinaʻi lākou i kahi o ka puʻupuʻu kanesa.
ʻO kekahi mau hōʻailona maʻamau e ʻike ʻia:
- He puʻupuʻu i hiki ke ʻike ʻia ma lalo o ka ʻili (hiki paha kēia a ʻaʻole paha he ʻeha)
- ʻO ka pohō kaumaha me ke kumu ʻole
- Kuni a me ka luhi nui
E nānā kākou pehea e ʻokoʻa ai nā hōʻailona ma muli o ka wahi o ke kanesa.
| Kahi o ke kanesa | Nā hōʻailona hiki ke loaʻa |
|---|---|
| Ake | ʻEha ka ʻōpū, pehu. |
| Nā māmā | Paʻakikī i ka hanu ʻana, ʻūhū, ʻūhū koko, kalapu. |
| Nā iwi | ʻEha iwi, haki pinepine. |
| iwi kuamoʻo | Paʻakikī ke hele a neʻe paha, ʻeha ke kua. |
He aha ke kumu o ka maʻi ʻaʻai EHE?
Hoʻomohala ʻia nā maʻi kanesa e like me EHE ke loli kahi cell olakino i cell cancer a hoʻomaka e māhelehele me ke kāohi ʻole.
I ka hoʻāʻo ʻana e ʻike i ke kumu o kēia, ua ʻike nā kānaka noiʻi ua hoʻokumu ʻia e kahi mutation genetic kikoʻī. I ka ʻōlelo maʻalahi, ua hoʻopili hewa ʻia nā chromosomes ʻelua i loko o kā mākou mau cell, e hoʻopili ai i ʻelua mau genes. Ua kapa ʻia kēia mau genes ʻo (WWTR1) (i kapa ʻia hoʻi ʻo (TAZ) ) a me (CAMTA1) . Ke hoʻopili ʻia kēia mau genes ʻelua, e hoʻomaka ana ke kūkulu ʻana o nā cell cancer EHE.
No laila, hiki i kāu kauka ke hoʻāʻo no kēia hui chromosome maʻamau i ka wā e hana ai i kahi hōʻailona.
Pehea e hana ʻia ai ka hōʻailona?
E like me kā mākou i kūkākūkā ai ma mua, ʻike pinepine ʻia ka EHE ma ke ʻano ulia. ʻIke wale nā kauka i ka puʻupuʻu i ka wā o kahi hoʻāʻo kiʻi, e like me ka CT scan a i ʻole MRI scan, no kekahi kumu ʻē aʻe. A laila e nānā lākou i kahi, ka nui, a inā ua pālahalaha i nā wahi ʻē aʻe.
ʻO kēia nā hoʻokolohua i hoʻohana pinepine ʻia e ʻike i ka EHE.
| Hoʻāʻo | I ka ʻōlelo maʻalahi, he aha ka mea e hana ʻia? |
|---|---|
| CT Scan | Hoʻohana ʻia nā kukuna X e lawe i kekahi mau kiʻi ʻokiʻoki o loko o kou kino. Hiki i kēia ke kōkua i ka ʻike ʻana i nā puʻupuʻu EHE i loko o ka umauma, ka ʻōpū, a me ke pelvis. Kōkua kēia i ka ʻike maopopo ʻana i nā mea i loko o nā ʻōpū, nā iwi, a me nā ʻiʻo. |
| MRI scan (MRI) | Hoʻohana ʻia kahi magnet ikaika a me nā nalu lekiō e hana i nā kiʻi maopopo loa o loko o ke kino. He mea pono loa kēia no ka nānā ʻana i nā puʻupuʻu EHE i loko o ke akepaʻa a me nā iwi. I kekahi manawa, hiki i kahi MRI kino holoʻokoʻa, e uhi ana i ke kino holoʻokoʻa mai ke poʻo a ka wāwae, ke kōkua i ka ʻike ʻana i nā puʻupuʻu i pālahalaha i nā iwi. |
| ʻO ka Biopsy Nila Koʻikoʻi | ʻO kēia ka hoʻāʻo koʻikoʻi loa e hōʻoia inā he EHE kahi puʻupuʻu ma hope o ka scan. Wehe ʻia kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka puʻupuʻu me ka hoʻohana ʻana i kahi nila hakahaka kūikawā. Nānā kekahi kauka loea i kapa ʻia he pathologist i kēia ʻāpana o ka ʻiʻo ma lalo o kahi microscope e hoʻoholo ai inā he mau hunaola kanesa a me ke ʻano o lākou. |
Eia kekahi, e ʻike i nā puʻupuʻu a ʻike inā ua pālahalaha lākou (ultrasound) a i ʻoleHiki i kāu kauka ke ʻōlelo aku i nā hoʻokolohua ʻē aʻe, e like me ka PET scan .
He aha nā lāʻau lapaʻau no EHE?
No ka mea, he ʻano laha ʻole ka EHE, ʻaʻohe alakaʻi lapaʻau maʻamau no ia mea. No laila, e mālama ʻia ʻoe e kahi hui kauka multidisciplinary i loaʻa ka ʻike i ka mālama ʻana i nā sarcomas. Hiki i kēia hui ke komo pū me kahi oncologist ʻoki kino , kahi radiologist , a, ma muli o ke kino i loaʻa ai ke kanesa (no ka laʻana, iwi), kahi kauka ʻoki kino orthopedic , a i ʻole kahi loea hoʻoili ake.
ʻO ke ʻano o ka lāʻau lapaʻau āu e loaʻa ai ma muli o kekahi mau kumu, me ka nui o ka puʻupuʻu, kona wahi, ehia mau puʻupuʻu i loaʻa, a inā ua pālahalaha ke kanesa.
Eia kekahi mau koho lapaʻau:
Ke Kali Makaʻala
Inā ʻaʻohe ou hōʻailona a ʻaʻole ʻoe he moho maikaʻi no ke ʻoki ʻana, hiki i kāu kauka ke hoʻoholo ʻaʻole e mālama iā ʻoe i ka wā mua a nānā pono i kou kūlana. ʻO kēia no ka mea i kekahi manawa hiki i nā hopena ʻaoʻao o ka mālama ʻana ke ʻoi aku ma mua o nā pono. E like me kā mākou i ʻōlelo ai ma mua, e emi ana kekahi mau puʻupuʻu EHE me ka ʻole o ka mālama ʻana a ulu lohi paha. Eia nō naʻe, inā ʻoi aku ka ʻino o ke kūlana, hiki i kāu kauka ke kuhikuhi i kahi koho lapaʻau ʻē aʻe.
ʻoki kino
ʻO ke ʻoki ʻana ka lāʻau lapaʻau maʻamau no kahi puʻupuʻu hoʻokahi. Ma kēia kaʻina hana, wehe ke kauka ʻoki i ka puʻupuʻu kanesa a me kahi liʻiliʻi o nā ʻiʻo olakino a puni ia mea e hōʻoia ʻaʻohe mau hunaola kanesa i koe.
ʻO ka hoʻopili ʻana o ke koko
ʻO kēia ke kāohi ʻana i nā kīʻaha koko e hoʻolako ana i ke koko i ka puʻupuʻu. E like me ka make ʻana o kahi mea kanu ke hoʻōki ʻoe i ka hoʻoinu ʻana iā ia, ke ʻoki ʻia ke kahe koko, ʻaʻole hiki i ka puʻupuʻu ke ulu a emi paha. Hiki ke hana ʻia kēia e hoʻemi i ka puʻupuʻu ma mua o ke ʻoki ʻana a i ʻole ma ke ʻano he lāʻau lapaʻau nui. ʻO ka transarterial chemoembolization (TACE) a me ka radioembolization ʻelua mau lāʻau lapaʻau.
Hoʻōla i kuhikuhi ʻia
ʻO kēia ka lāʻau lapaʻau maʻamau no ka EHE holomua. Hoʻohana kēia lāʻau lapaʻau i nā lāʻau lapaʻau e ālai i nā meaola a me ka oxygen e pono ai nā hunaola kanesa e ulu.
Hoʻōla Pāhawewe
Hiki ke hoʻohana ʻia kēia lāʻau lapaʻau e luku i nā hunaola kanesa e koe paha ma hope o ke ʻoki ʻana. Hiki ke hāʻawi ʻia ka lāʻau lapaʻau radiation ma ke ʻano he lāʻau lapaʻau nui no kekahi mea hiki ʻole ke hana ʻoki ʻia. Ma kēia lāʻau lapaʻau, hoʻohana ʻia nā kukuna ikehu kiʻekiʻe i kuhikuhi ʻia o ka radiation e luku i nā hunaola kanesa.
Kemoterapia
No ka EHE (Chemotherapy)ʻAʻole hoʻohana pinepine ʻia, akā inā ua pae holomua ke kanesa, hiki ke ʻōlelo ʻia e hui pū me nā lāʻau lapaʻau ʻē aʻe.
Hoʻoili ʻana o nā kino
Inā ua hoʻopilikia nā ʻōpena he nui i kahi ʻōkana nui (ʻo ka hapa nui o ke akepaʻa), hiki i ke kauka ke ʻōlelo aku i kahi hoʻoili ʻōkana.
Ke hoʻomau nei ka noiʻi ʻana i ka EHE, a ke hoʻāʻo ʻia nei nā lāʻau lapaʻau hou i nā hoʻokolohua lapaʻau . Ma muli o ke koʻikoʻi o kou kūlana, hiki i kāu kauka ke kuhikuhi iā ʻoe e komo i kekahi o kēia mau lāʻau lapaʻau e pili ana i ka noiʻi.
ʻEhia ka lōʻihi e hiki ai iā ʻoe ke ola me EHE?
Ke lohe ʻoe i kēia, e noʻonoʻo paha ʻoe, 'Pehea ka lōʻihi o koʻu ola ʻana?' ʻO kaʻoiaʻiʻo, he paʻakikī ke hāʻawi i kahi pane pololei i kēlā nīnau. No ka mea, he maʻi kakaikahi loa ʻo EHE, ke hōʻiliʻili ʻia nei ka ʻike e pili ana i ia mea.
Eia kekahi, e like me kā mākou i kūkākūkā ai ma mua, ʻaʻole like ke ʻano o kēia maʻi kanesa i nā kānaka a pau. No kekahi poʻe, hiki i ke kanesa ke laha koke me ka mālama ʻia. No kekahi poʻe, hiki i ke kanesa ke ola no nā makahiki me ka ʻole o nā hōʻailona nui a i ʻole ka laha ʻana o ka puʻupuʻu. Hoʻemi kekahi mau puʻupuʻu me ka ʻole o ka mālama ʻia.
No laila, ʻo ka ʻike maikaʻi loa e pili ana i kou kūlana a me ka wā e hiki mai ana hiki ke loaʻa mai kāu kauka lapaʻau wale nō. E noʻonoʻo ʻo ia i kāu mau hōʻike hoʻāʻo a pau a me ke kūlana a hāʻawi iā ʻoe i ka ʻike pololei loa.
Nā nīnau e nīnau aku ai i kāu kauka
He mea maʻamau ka loaʻa ʻana o nā nīnau he nui ke aʻo ʻoe e pili ana i ia ʻano maʻi laha ʻole. Ke hele ʻoe e ʻike i kāu kauka, mai poina e nīnau i kēia mau nīnau.
| Nīnau e nīnau ai | No ke aha he mea nui e ʻike i kēia? |
|---|---|
| ʻAuhea koʻu puʻupuʻu maʻi ʻaʻai? | ʻOkoʻa nā hōʻailona a me nā lāʻau lapaʻau ma muli o ka wahi. |
| He aha nā hōʻailona e hiki ke kōkua iaʻu e ʻike inā e ulu ana ka puʻupuʻu? | E kōkua kēia iā ʻoe e hoʻomaopopo koke ʻia inā he mau loli. |
| He aha nā mea e hoʻopilikia ai i ka wānana o koʻu maʻi? | He mea nui kēia no ka loaʻa ʻana o kahi ʻike maoli o kou kūlana. |
| He aha nā lāʻau lapaʻau āu e ʻōlelo mai ai noʻu? He aha ko lākou mau hopena ʻaoʻao? | Hiki iā ʻoe ke hoʻoholo maopopo e pili ana i ka lāʻau lapaʻau a e mākaukau no nā hopena ʻaoʻao. |
| ʻO wai nā loea i komo i kaʻu hui lapaʻau? | E hoʻomaopopo i ka hui e mālama nei iā ʻoe. |
| ʻEhia pinepine e pono ai iaʻu e hele mai no ka nānā ʻana? | E aʻo pehea e mālama ai i kou olakino. |
He mea nui mau ka ʻimi ʻana i ka lāʻau lapaʻau mai nā kauka āu e hilinaʻi nei. ʻOi aku ka nui o ia mea i ka wā e pili ana i kahi maʻi laha ʻole e like me EHE. ʻOiai he nui nā mea a mākou i ʻike ʻole ai e pili ana i kēia, ʻo ka ʻimi ʻana i ka lāʻau lapaʻau mai nā kauka i loaʻa ka ʻike i ka mālama ʻana i nā sarcomas a me nā maʻi ʻaʻai paʻakikī hiki ke hana i kahi ʻokoʻa nui i kāu huakaʻi hoʻōla.
Leka Lawe-Home
- ʻO ka Epithelioid Hemangioendothelioma (EHE) kahi ʻano maʻi ʻaʻai kakaikahi loa e hoʻomaka ana i loko o nā pūnaewele e hoʻopili ana i nā kīʻaha koko.
- Hiki ke ʻokoʻa loa ke ʻano o kēia maʻi kanesa mai kēlā kanaka a kēia kanaka. Ulu koke kekahi, aʻo kekahi e ulu lohi loa a emi paha me ka ʻole o ka lāʻau lapaʻau.
- He pinepine ʻole ia he asymptomatic a hiki ke ʻike ʻia ma kahi ulia i ka wā o kahi scan i hana ʻia no kekahi kumu ʻē aʻe.
- He mea nui ka biopsy e hōʻoia i ka maʻi.
- Hoʻopilikino ʻia nā ʻano lapaʻau e kūpono i kēlā me kēia mea maʻi a hiki ke komo pū me ka nānā ʻana, ke ʻoki ʻana, a me nā hoʻoponopono i hoʻolālā ʻia.
- ʻOiai he maʻi laha ʻole kēia, he mea nui e ʻimi i ka lāʻau lapaʻau mai kahi hui o nā loea i ʻike i ka sarcoma. E nīnau i kāu kauka a e loaʻa kahi ʻike maikaʻi o kou kūlana.
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