Ke loaʻa iā ʻoe kahi pēpē hou, ʻo ka manaʻolana nui loa āu e loaʻa ai ma ke ʻano he makuahine a makua paha, ʻo ia ke ʻike i kāu pēpē olakino. Akā i kekahi manawa, pono mākou e hopohopo iki ma muli o kekahi mau pilikia e kū mai ana i ka wā e noho ana ke pēpē i loko o ka ʻōpū. I kēia lā, e kamaʻilio mākou e pili ana i kekahi mau loli a i ʻole nā kīnā i loko o ka ʻōnaehana mimi o ke pēpē i hānau ʻia mai ka hānau ʻana. Ma nā ʻōlelo lapaʻau, kapa mākou i kēia mau mea ʻo 'Congenital Urinary Abnormalities'. Mai makaʻu i kou lohe ʻana i ka inoa, inā ʻike pono ʻoe i kēia, e maʻalahi iā mākou ke kū i kekahi mea.
I ka ʻōlelo maʻalahi, he aha kēia mau pilikia o ka ʻōnaehana mimi hānau?
ʻO ke ʻano o ka huaʻōlelo 'congenital' ʻo ia hoʻi 'mai ka hānau ʻana'. ʻO ia hoʻi, aia kēia mau kūlana i ka wā e noho ana ke pēpē i loko o ka ʻōpū a i ka wā hānau paha. Hiki iā lākou ke hoʻopilikia i ka ʻōnaehana mimi a i kekahi manawa i ka ʻōnaehana hānau hou.
E noʻonoʻo i ka ʻōnaehana mimi i loko o ko kākou kino e like me kahi ʻōnaehana e kānana ana i ka wai, hōʻiliʻili iā ia i loko o kahi pahu, a laila hoʻokuʻu iā ia ma o kahi paipu. Aia kekahi mau ʻāpana nui o kēia ʻōnaehana:
- Nā puʻupaʻa: ʻO kēia nā kānana nui ʻelua i loko o ko kākou kino. ʻO ka hana nui o nā puʻupaʻa, ʻo ia ke kānana i nā paʻakai pono ʻole, ka wai, nā mea ʻawahia, a me nā huahana ʻōpala mai ke koko a hana i ka mimi . ʻO ka maʻamau, loaʻa i kēlā me kēia kanaka ʻelua puʻupaʻa.
- ʻO ka ʻōpū mimi: He ʻeke liʻiliʻi kēia, elastic e mālama ana i ka mimi i hana ʻia e nā puʻupaʻa.
- Nā Ureters: ʻO kēia nā ʻōmole ʻelua e lawe ana i ka mimi mai nā puʻupaʻa a i ka ʻōpū mimi.
No laila, ʻo kēia mau mea ʻē aʻe i hānau ʻia a mākou e kamaʻilio nei, he mau loli a kīnā paha e kū mai ana ma nā ʻāpana e like me nā puʻupaʻa, ka ʻōpū mimi, a i ʻole ka urethra i ka wā e hana ʻia ai.
He aha nā pilikia hānau maʻamau o ka ʻōnaehana urinary?
Aia kekahi mau ʻano o ia mau kūlana. He mea maʻamau loa kekahi, a ʻo kekahi he mea kākaʻikahi loa. E hoʻomaopopo wale kākou i nā ʻano nui. Ua kau wau i kēia ʻike i loko o kahi papa no ka maʻalahi o ka hoʻomaopopo ʻana.
| Inoa o ke Kūlana | He aha ka mea e hana ʻia ma kēia kūlana? |
|---|---|
| ʻO ka Hydronephrosis | I ka ʻōlelo maʻalahi, ke pehu nei nā pōhaku puʻupaʻa. Ma muli o kahi paʻa ma kekahi wahi o ke ala mimi, ʻaʻole hiki i ka mimi ke kahe mai nā puʻupaʻa a i ka ʻōpū mimi. A laila, piha ka mimi i loko o nā puʻupaʻa, e hoʻoulu ai i ka pehu ʻana o nā puʻupaʻa. Hiki ke hana kēia i kekahi a i ʻole nā puʻupaʻa ʻelua. |
| Nā Testicles i iho ʻole ʻia (Cryptorchidism) | He kūlana kēia e pili ana i nā keikikāne. Hoʻomohala pinepine ʻia nā testicles i loko o ka ʻōpū o ke pēpē. A laila iho mālie lākou i lalo i loko o ka scrotum, kahi ʻeke ma hope o ka penis. Ma kēia kūlana, ua paʻa kekahi a i ʻole nā testicles ʻelua i ka ʻaoʻao o luna o ke kino ma kahi o ka iho ʻana. |
| Nā Hypospadias | Hoʻopilikia pū kēia i nā keikikāne. ʻO ka urethra ka ʻōmole e puka ai ka mimi a me ka sperm mai ke kino. ʻO ka maʻamau, aia ka puka i loko o kēia ʻōmole ma ka piko o ka penis. Akā i nā keikikāne me kēia maʻi, aia ka puka ma lalo o ka penis. |
| Spine Bifida | Hana ʻia kēia no ka mea ʻaʻole pani piha ka lolo, ke kaula kuamoʻo, a me nā membrane a puni i ka wā e ulu ana ke pēpē i loko o ka ʻōpū. I nā hihia koʻikoʻi, hiki i kēia ke hōʻino i nā aʻalolo a hoʻoulu i nā kūlana e like me ka maʻi lolo. Hiki i kēia ke alakaʻi i nā pilikia me ka kaohi ʻana o ka ʻōpū mimi (neurogenic bladder). |
| ʻO ka Reflux Vesicoureteral (VUR) | ʻO ka maʻamau, kahe ka mimi mai nā puʻupaʻa a i ka ʻōpū mimi. Akā ma kēia kūlana, kahe ka mimi mai ka ʻōpū mimi i hope, i luna o nā ureters, a i loko o nā puʻupaʻa. E like me ka wai e kahe ana i luna o ka muliwai. Hiki i kēia ke alakaʻi i nā maʻi ʻaʻai mimi pinepine (UTIs) a me ka hōʻino ʻana o nā puʻupaʻa. |
| ʻO ka exstrophy o ka ʻōpū | He kūlana kākaʻikahi loa kēia. ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka huli ʻana o ka ʻōpū mimi o ke pēpē i loko i waho, e waiho ana i kahi puka ma ka ʻili o ka ʻōpū. No laila, ma kahi o ka puka ʻana ma o ka urethra maʻamau, kahe ka mimi i waho ma o kēia puka i loko o ka ʻōpū. |
| ʻO ka maʻi ʻōpū Prune | He maʻi laha ʻole nō hoʻi kēia. ʻO ke ʻano nui o kēia, ʻo ia ka nāwaliwali loa o nā ʻiʻo o ka ʻōpū a ʻaʻohe paha. ʻO ka hopena, ua like ka ʻili ma ka ʻōpū me he hua waina lā. Eia kekahi, ʻaʻole i iho nā testicles a ʻike ʻia nā pilikia ʻē aʻe me ka ʻōnaehana mimi. |
| ʻO ka Valve Urethral Hope (PUV) | He mea kēia e hana wale ʻia i nā pēpē kāne. Ma ke kua o ka urethra, hana ʻia kekahi mea e like me ka membrane keu, e ālai ana i ke kahe ʻana o ka mimi. A laila, ʻaʻole hiki i ka mimi ke kahe i waho a kahe i hope, e hoʻoulu ai i ka ʻōpū mimi e pehu. Hiki i kēia ke hōʻino i ka urethra a me nā puʻupaʻa. |
ʻO ke kūlana maʻamau i ʻike ʻia i nā keiki kāne , ʻo ia nā testicles i iho ʻole i lalo .
ʻO ka Vesicoureteral reflux (VUR) kahi maʻi maʻamau i nā kaikamahine .
He aha nā hōʻailona o kēia?
ʻOkoʻa nā hōʻailona e kū mai me kēia mau kūlana. ʻAʻole hōʻeha kekahi mau kūlana a i ʻole nā hōʻailona ʻike ʻia. Hiki ke ʻike ʻia ma o nā hoʻokolohua e like me nā scans. Eia nō naʻe, aia kekahi mau hōʻailona maʻamau e ʻike ʻia.
- ʻEha ma ka ʻōpū, ka ʻōpū, a i ʻole ke kua.
- ʻEha a wela paha i ka wā e mimi ai (dysuria).
- Hoʻohuli ʻia ke kahawai mimi i kahi ʻē aʻe ma kahi o ke kahe pololei ʻana.
- Ke kahe ʻana o ka mimi ma mua o ka maʻamau.
- Ke koko i loko o ka mimi (hematuria).
- Ka luaʻi a me ka luaʻi.
- Nā kūlana hernia.
- Nā maʻi ʻōpū mimi pinepine (UTI).
- ʻAʻole e ulu ana ke keiki e like me ka mea i manaʻo ʻia.
No ke aha e kū ai nā kūlana e like me kēia?
He mea paʻakikī loa ke kuhikuhi i hoʻokahi kumu. He mea paʻakikī iki. Manaʻo nā kauka ua hoʻokumu pinepine ʻia e ka hui pū ʻana o nā mea pili i ke kaiapuni a me nā mana hoʻoilina .
Nā kumu kaiapuni e hiki ke hoʻopilikia:
- Loaʻa i ka makuahine ka maʻi diabetes i ka wā hāpai.
- ʻAʻole lawa ka lawe ʻana i nā huaora a me nā minelala koʻikoʻi e like me ka folate a me ka hao i ka wā hāpai.
- ʻO kekahi mau lāʻau lapaʻau i lawe ʻia i ka wā hāpai, ʻoiai nā lāʻau lapaʻau no ka maʻi epilepsy, hiki ke hōʻino i nā puʻupaʻa.
Ma ke ʻano he genetics, hiki ke hana ʻia kēia e kekahi mau loli (mutations) i loko o nā genes e hoʻopilikia i ka ulu ʻana o ke keiki. Akā, ʻaʻole pono ʻoe e hopohopo nui e pili ana i kēia mau mea. ʻO ka mea nui, ʻo ia ka hoʻomaopopo ʻana ʻaʻole kēia kou hewa a i ʻole kekahi mea ʻē aʻe.
Pehea e ʻike ai i kēia mau ʻano?
ʻIke pinepine ʻia kēia ʻano pilikia hānau i ka wā o nā ultrasounds prenatal . Ke nānā nei i ka ulu ʻana o kahi pēpē, nānā pū nā kauka i ka wai amniotic e hoʻopuni ana i ka pēpē. Ma hope o 20 mau pule o ka hāpai ʻana, ʻo ka hapa nui o kēia wai amniotic i hana ʻia i ka mimi o ka pēpē. No laila, inā he haʻahaʻa ka nui o kēia wai, hiki i nā kauka ke kānalua i kahi pilikia me ka ʻōnaehana urinary.
Inā ʻaʻole i ʻike ʻia ma mua o ka hānau ʻana, hiki i nā kauka ke kānalua i kēia i ka wā kamaliʻi a i ʻole ka wā kamaliʻi ma muli o nā hōʻailona o ke keiki. A laila, hana ʻia nā hoʻokolohua like ʻole e hōʻoia i ke kūlana.
- ʻO ke scan Ultrasound: Lawe kēia i nā kiʻi o nā ʻōpū o ke kino.
- Ka nānā ʻana i ka mimi: E nānā no nā maʻi ʻōpū mimi.
- Nā Hoʻāʻo Koko: E ana i ka maikaʻi o ke kānana ʻana o nā puʻupaʻa i ke koko.
- CT Scan: Hoʻohana i kahi nui o nā kukuna X-ray e hana i nā kiʻi kikoʻī ʻekolu-dimensional o loko o ke kino.
- MRI Scan: Hoʻohana i nā magnet a me nā nalu lekiō e hana i nā kiʻi maopopo loa o nā ʻōpū.
- VCUG (Voiding Cystourethrogram): He hoʻāʻo X-ray kūikawā kēia. Kōkua ia e ʻike i ka mea e hana ʻia ke piha a hakahaka ka ʻōpū mimi. He mea nui loa kēia e nānā no VUR.
- Renal Scan: Hoʻokomo ʻia kahi liʻiliʻi o ka mea radioactive i loko o nā puʻupaʻa e hāʻawi i kahi nānā kikoʻī i ka hana o nā puʻupaʻa a me ke kahe o ka mimi.
Pehea e mālama ʻia ai?
Aia nā koho lapaʻau i ke kūlana kūikawā o ke keiki a me kona koʻikoʻi.
ʻAʻole pono nā kūlana āpau i ka mālama ʻia. Hiki i kekahi mau pilikia liʻiliʻi ke hoʻoponopono iā lākou iho i ka hala ʻana o ka manawa, a i ʻole e koi wale ʻia ka mālama lapaʻau maʻamau.
Ma kekahi ʻaoʻao, pono kekahi mau kūlana i ka mālama ʻia. Hiki i kēia mau mea ke komo pū me:
- Nā lāʻau lapaʻau antibiotic: Kāohi a mālama paha i nā maʻi ʻōpū mimi.
- ʻO ke ʻoki kino: Pono paha ke ʻoki kino e wehe i nā mea e ālai ai, hoʻoponopono i ka urethra, a hoʻoponopono paha i nā hemahema ʻē aʻe.
- Dialysis: Inā pilikia nui nā puʻupaʻa (hāʻule ʻana o ka puʻupaʻa), pono e hoʻohana ʻia kahi mīkini e wehe i nā ʻōpala mai ke kino.
- Hoʻoili Puʻupaʻa: I ke kahua hope loa o ka hāʻule ʻana o ka puʻupaʻa, hiki i ka hoʻoili puʻupaʻa olakino ke lilo i mea hoʻonā.
E nānā pono ke kime lapaʻau e mālama ana i kāu keiki i ke kūlana o kāu keiki a hoʻomohala i ka hoʻolālā lapaʻau kūpono loa nona.
He aha kāu e manaʻo ai no ka wā e hiki mai ana o kāu keiki?
Aia wale nō kēia i ke kūlana o ke keiki a pehea e pili ai iā lākou. Pono paha kekahi mau keiki i ka mālama olakino no ke koena o ko lākou ola. Akā, mai hopohopo. E hana pū ke kime lapaʻau me ʻoe e hoʻomohala i kahi hoʻolālā e kōkua i kāu keiki e ola i kahi ola palekana, olakino, a kūʻokoʻa .
I ka ulu ʻana o ke keiki, hiki ke kū mai nā pilikia e like me ka paʻakikī o ka kaohi ʻana i ka mimi a me ka ʻōpala, nā maʻi pinepine o ke ala mimi, a me ka hōʻino ʻana o nā puʻupaʻa. Aia kekahi pilikia o ka hāʻule ʻana o nā puʻupaʻa ma muli o ka hōʻino nui ʻana o nā puʻupaʻa.
Eia kekahi, hiki i kēia mau kūlana ke hoʻopilikia i ke olakino noʻonoʻo o ke keiki. Hiki i ke keiki ke hopohopo e pili ana i ko lākou kino a me ka manaʻo o haʻi iā lākou. No laila, he mea nui loa ka hāʻawi ʻana i ke keiki i ke kākoʻo noʻonoʻo e pono ai a ʻimi i ke kōkua mai ka hui lapaʻau.
Āhea wau e ʻike ai i ke kauka? Āhea wau e hele ai i ka ETU?
Inā loaʻa i kāu keiki kēia maʻi, e hōʻoia e hele i nā lā o ke keʻena lapaʻau i hāʻawi ʻia e ke kauka. He mea nui e nānā i ka ulu ʻana o ke keiki a me kona kūlana.
Eia kekahi, inā ʻike ʻia kekahi o nā hōʻailona ulia pōpilikia ma lalo nei, e lawe koke i ke keiki i ka Emergency Treatment Unit (ETU) kokoke loa.
- ʻEha koke a ʻeha ʻole paha ma ka ʻōpū, ka ʻaoʻao, a i ʻole ke kua.
- He kuni ma luna o 100.5 Fahrenheit (38 Celsius).
- Nā loli i ka mimi ʻana: ka nui a emi mai paha o ka mimi ma mua o ka maʻamau, ka hiki ʻole ke mimi, ka ʻeha i ka wā e mimi ai, a i ʻole ke koko i loko o ka mimi .
I ia mau hihia, mai kali ma ka home. Hiki i ke kōkua lapaʻau koke ke pale i nā pilikia koʻikoʻi.
Leka Lawe-Home
- ʻO nā 'ʻano ʻino o ke ala mimi hānau' he mau kūlana ia e kū mai ana i ka wā e ulu ana ke pēpē i loko o ka ʻōpū o ka makuahine. ʻAʻole kēia he hewa o nā mākua.
- Hiki ke ʻike mua ʻia he nui o kēia mau mea ma o nā scan i ka wā hāpai.
- Inā pilikia kāu keiki i ka mimi ʻana, loaʻa pinepine nā maʻi, a i ʻole ke hōʻike nei i nā hōʻailona ʻē aʻe, mai hoʻowahāwahā iā ia. E lawe koke i kāu keiki i ke kauka.
- ʻAʻole pono nā kūlana āpau i ke ʻoki kino a i ʻole ka mālama ʻino. Aia ke ʻano o ka mālama ʻana i ke kūlana kikoʻī o ke keiki.
- Me ka mālama kūpono a me ka mālama olakino lōʻihi, hiki i ka hapa nui o nā keiki me kēia mau maʻi ke ola olakino a maʻamau. E kōkua kāu hui lapaʻau iā ʻoe e hana i kēlā.











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