Ke nānā ʻoe i kāu pēpē hānau hou, ua ʻike anei ʻoe he uliuli iki kona mau lehelehe a me kona mau manamana lima? Ke ʻano luhi loa nei ʻo ia, ua hou, a ua hiamoe hoʻi ma hope o ka hānai ʻana? He mea maʻamau no ka makuahine a makua paha ke makaʻu nui i ka wā e ʻike ai lākou i kēia mau mea. I kekahi manawa, ma hope o ia mau hōʻailona, aia paha kahi maʻi puʻuwai hānau kakaʻikahi i kapa ʻia ʻo Truncus Arteriosus. Mai makaʻu ke lohe ʻoe i kēia inoa. E kamaʻilio kākou e pili ana i kēia me ka maʻalahi a me ka maopopo.
I ka ʻōlelo maʻalahi, he aha kēia Truncus Arteriosus?
Me he mea lā he mea paʻakikī iki kēia ke hoʻomaopopo, akā he mea maʻalahi loa ia. E noʻonoʻo he ʻelua mau kīʻaha koko nui (nā aʻa) o kahi pēpē olakino e puka mai ana mai loko mai o kona puʻuwai.
1. ʻAʻa Pulmonary: Lawe kēia i ke koko "lepo" me nā pae oxygen haʻahaʻa mai ka puʻuwai a i nā māmā. Lawe nā māmā i ka oxygen mai kēia koko.
2. Aorta: ʻO kēia ka mea e lawe ai i ke koko "maʻemaʻe" i hoʻopiha ʻia me ka oxygen mai nā māmā i ka puʻuwai, a mai laila aku e pamu ʻia ai i ke kino holoʻokoʻa.
Ua maopopo iā ʻoe i kēia manawa? Ua like ia me nā alanui ʻelua. Hoʻokahi i nā māmā, ʻo kekahi i ke kino.
Eia nō naʻe, i loko o kahi pēpē me Truncus Arteriosus , ua pani ʻia kēia mau kīʻaha koko ʻelua e hoʻokahi wale nō kīʻaha koko nui . ʻO kēia ke kumu o ka hui pū ʻana o ke koko i loaʻa ka oxygen a me ke koko i loaʻa ka oxygen.
Hele kēia koko i hui pū ʻia i ke kino holoʻokoʻa o ka pēpē. Ua like kēia me ke kāwili ʻana i kahi kerosene liʻiliʻi me ka ʻaila a hoʻokomo iā ia i loko o ke kaʻa. Manaʻo kaumaha loa ka ʻenekini, ʻeā? Pēlā ka puʻuwai liʻiliʻi a me nā māmā o ka pēpē e hāpai ai i kahi kaumaha nui a me ka hoʻoikaika nui.
No kēia kumu, manaʻo nā kauka he kīnā puʻuwai hānau koʻikoʻi loa kēia. Pono e hoʻoponopono ʻia ke kūlana ma o ke ʻoki ʻana ma hope koke iho o ka hānau ʻana o ka pēpē.
Pehea e ʻike ai inā loaʻa kēia maʻi i kaʻu pēpē?
Hoʻomaka pinepine kēia mau hōʻailona e ʻike ʻia i loko o nā lā mua ma hope o ka hānau ʻana o ke pēpē. Pono ʻoe e makaʻala loa i kēia.
| Hōʻailona | Wehewehena |
|---|---|
| ʻIli polū a hina paha (Cyanosis) | Polū nā lehelehe, nā manamana lima, a me nā kui o ke pēpē, ʻoi aku hoʻi a puni ka waha. Ma muli kēia o ka emi ʻana o ka nui o ka oxygen i loko o ke koko e kahe ana i ke kino. |
| Paʻakikī ka hanu ʻana | Ke hanu wikiwiki nei ke pēpē. Me he mea lā e komo ana ka umauma i loko i ka wā e hanu ana. |
| Ka paʻakikī o ka inu ʻana i ka waiū | Ua luhi au ma hope o ka inu ʻana i ka waiū. Ke hou nei au i ka wā e inu ana i ka waiū, a hiamoe paha au. |
| Hiamoe nui | Ua hiamoe mau ke pēpē. ʻAʻohe ona hoihoi i ka pāʻani a i ʻole ka hana ʻeleu. |
| ʻAʻole e piʻi ke kaumaha | ʻOiai inā inu pono ka pēpē i ka waiū, ʻaʻole e piʻi maʻamau ke kaumaha o ka pēpē. |
| Puʻuwai wikiwiki a me ka pulse nāwaliwali | Ke kau ʻoe i kou lima ma ka umauma o ke pēpē, e wikiwiki paha ka puʻuwai. Hiki ke nāwaliwali hoʻi ka pulse. |
Inā ʻike ʻoe i kekahi o kēia mau hōʻailona, e lawe koke aku i kāu pēpē i ke kauka . Mai hoʻokaʻulua.
No ke aha e loaʻa ai kēia ʻano maʻi i kahi pēpē?
I ka hapa nui o ka manawa, ʻaʻole hiki i nā kauka ke ʻōlelo pololei i ke kumu o kēia hana i kekahi mau pēpē. Akā ʻo ke kumu nui , aia kahi kīnā e kū mai ana i ka wā e ulu ai ka puʻuwai i nā wā mua o ka ulu ʻana o ka pēpē i loko o ka ʻōpū o ka makuahine. Ua pili mua kēlā mau kīʻaha koko ʻelua a mākou i kamaʻilio ai ma mua. Ma hope mai, ua māhele lākou i ʻelua. I kēia hihia, ʻaʻole hana pono kēlā mahele ʻana.
Hiki ke pili kēia kīnā puʻuwai me kekahi mau kūlana genetic, e like me ka maʻi DiGeorge , a hiki ke ʻoi aku ka nui o ka hiki ke kū mai ma muli o kekahi mau kumu pilikia e kū nei i ka makuahine i ka wā hāpai.
Nā mea pilikia i ka wā hāpai
- ʻO ka makuahine me ka maʻi diabetes
- Ke hoʻomohala nei i kekahi mau maʻi viral, e like me ka rubella
- Ka hoʻohana ʻana i ka waiʻona a i ʻole ka lāʻau lapaʻau
- He mea ʻino i nā pēpē e like me ke kēpauKa ʻike ʻia ʻana i nā kemika ʻawahia
Pehea e ʻike ai nā kauka i kēia?
I kekahi manawa, hiki ke kānalua ʻia kēia i ka wā o nā hoʻokolohua maʻamau i hana ʻia ma ka haukapila ma hope o ka hānau ʻana o ka pēpē. Inā hōʻike ka hoʻāʻo pulse oximetry , ka mea e ana i nā pae oxygen o ka pēpē, i nā pae oxygen haʻahaʻa, e hana nā kauka i nā hoʻokolohua hou aʻe.
ʻO ka hoʻāʻo nui e hōʻoia i kēia maʻi he echocardiogram . He scan kēia o ka puʻuwai. Hiki iā ʻoe ke ʻike maopopo i ke ʻano o ka puʻuwai, kahi o nā kīʻaha koko, a me ke ʻano o ke kahe ʻana o ke koko.
I kekahi manawa, inā ʻike ke kauka i kekahi mau mea ʻē aʻe i loko o ka puʻuwai i ka wā o ka ultrasound prenatal, hiki iā ia ke ʻōlelo aku i kahi echocardiogram fetal , kahi e nānā pono ai i ka puʻuwai o ke pēpē.
He aha nā lāʻau lapaʻau no kēia? Pono anei ke ʻoki kino?
ʻAe. ʻAʻole hiki ke ho'ōla ʻia kēia maʻi me ka lāʻau lapaʻau wale nō. He mea nui e hana ʻia ke ʻoki puʻuwai o ka pēpē i loko o nā pule mua o ka hānau ʻana. He mea kēia e hana ʻia e hoʻopakele i ke ola o ka pēpē.
ʻO ke ʻoki kino nui no kēia ua kapa ʻia ʻo ia he hoʻoponopono Rastelli . Ma kēia, hana nā kauka ʻoki kino i:
- Ua pani ʻia ka lua ma ka paia o ka puʻuwai (ka `VSD`) me kahi ʻāpana.
- Hoʻokumu ʻia kahi aorta hou me ka hoʻohana ʻana i ke kīʻaha koko nui wale nō ('truncus').
- Me ka hoʻohana ʻana i kahi conduit a me ka valve hana, hana ʻia kahi aʻa pulmonary hou e lawe i ke koko i nā māmā.
I ka ʻōlelo maʻalahi, kūkulu hou nā kauka i nā aʻa ʻelua i nalowale i loko o ka puʻuwai. ʻOiai he ʻoki paʻakikī loa kēia, hana pono nā kauka akamai o ka puʻuwai ma Sri Lanka i kēia mau ʻoki.
ʻO ka mea nui, ʻoiai ke ulu nei ka pēpē, ʻaʻole e ulu nui ka conduit artificial (`conduit`). No laila, pono ʻoe e hana i hoʻokahi a ʻoi aku paha mau ʻokiʻoki i ka wā e hiki mai ana e pani iā ia i ka wā e ulu ana ka pēpē. E haʻi hou aku kāu kauka iā ʻoe e pili ana i kēia.
Hiki i kahi pēpē ke ola me kēia maʻi?
ʻO kēia nīnau paha ka makaʻu nui loa i loko o kou manaʻo. ʻO ka pane, ʻae, hiki nō ia. Akā inā wale nō ʻoe e hana ʻoki kino. Inā ʻaʻole mālama ʻia, aia kahi pilikia nui i ke ola o kahi pēpē i loko o ka makahiki mua.
Eia nō naʻe, ʻoi aku ka kiʻekiʻe o nā helu ola ma hope o ke ʻoki ʻana. Wahi a ka ʻikepili hou loa, ʻo ka nui o ka holomua o ke ʻoki ʻana he 80% a 97% . ʻO kahi pēpē i loko o hoʻokahi makahiki o ke ʻoki ʻana he ʻoi aku ka nui ma mua o 92% o ka manawa e ola ai a hiki i ka 20 makahiki.
Mai makaʻu i kēia mau helu. He ʻokoʻa kēlā me kēia pēpē. ʻAʻole i hoʻoholo ʻia ka wā e hiki mai ana o kāu pēpē e kēia mau helu. ʻO ka mea nui loa, ʻo ia ka hāʻawi ʻana i kāu pēpē i ka mālama olakino āna e pono ai a me kou aloha a me kou mālama.
Hiki iā lākou ke ola i kahi ola maʻamau, akā i kekahi manawa e luhi iki paha lākou i ka wā e holo ai a pāʻani e like me nā keiki ʻē aʻe. Akā hiki iā lākou ke hele i ke kula, e aʻo, a hana i kā lākou hana. ʻO ka mea nui loa, ʻo ia ke noho ma lalo o ka nānā ʻana a kahi kauka puʻuwai i ko lākou ola a pau .
Leka Lawe-Home
- He maʻi puʻuwai hānau koʻikoʻi ʻo Truncus Arteriosus, akā hiki ke mālama ʻia.
- Inā ʻike ʻoe i nā hōʻailona e like me ka uliuli ʻana o ka ʻili o kāu pēpē, ka paʻakikī o ka hanu ʻana, a i ʻole ka paʻakikī o ka hānai waiū, e ʻike koke i ke kauka.
- He mea nui ka ʻoki puʻuwai i hana ʻia i loko o nā pule mua ma hope o ka hānau ʻana no ka hoʻopakele ʻana i ke ola o ke pēpē.
- ʻOiai ma hope o ke ʻoki ʻana, pono kāu keiki i ka nānā ʻana i ke kauka cardiologist no kona ola holoʻokoʻa.
- Manaʻo paha ʻoe he paʻakikī kēia huakaʻi, akā, ʻaʻole ʻoe hoʻokahi. E kiʻi i ke kākoʻo mai kāu kauka, nā limahana o ka haukapila, a me nā mākua ʻē aʻe i loaʻa nā ʻike like.











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