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Ke ʻike nei ʻoe i ka pehu, ka ʻoʻoleʻa, a me ka ʻeha ma lalo o kou ʻili? E kamaʻilio kākou e pili ana i ka Eosinophilic Fasciitis!

Ke ʻike nei ʻoe i ka pehu, ka ʻoʻoleʻa, a me ka ʻeha ma lalo o kou ʻili? E kamaʻilio kākou e pili ana i ka Eosinophilic Fasciitis!

Ua ʻike koke anei ʻoe i kahi puʻupuʻu, pehu, a ʻeha paha ma lalo o ka ʻili o kou lima a wāwae paha? Malia paha ua hana ʻia ma hope o kahi hoʻoikaika kino maikaʻi. Ua ʻike anei ʻoe i kekahi mea e like me kēia? No laila, eia kahi kūlana i ʻike iki ʻia he mea nui paha iā ʻoe.

He aha ka Eosinophilic Fasciitis?

I ka ʻōlelo maʻalahi, ʻo ka Eosinophilic Fasciitis kahi maʻi kahi e lilo koke ai ka ʻiʻo e uhi ana i ko mākou mau ʻiʻo a me nā ʻiʻo ma lalo o ko mākou ʻili - kapa mākou he fascia ma nā ʻōlelo lapaʻau - i ka mumū, mānoanoa, a paʻa. E noʻonoʻo iā ia e like me ka ʻupena e hoʻopaʻa ana i ko mākou ʻili a me nā ʻiʻo a kōkua iā lākou e neʻe a puni, e like me ka ʻupena a mākou e kau ai i loko o ka pahu o kā mākou kaʻa i ka wā e kūʻai ai mākou.

Ua hoʻokaʻawale ʻia kēia he 'maʻi autoimmune' . ʻO ke ʻano kēia, hoʻomaka hewa ka ʻōnaehana pale o ko mākou kino, ʻo ia hoʻi ka ʻōnaehana pale, e hoʻouka i nā ʻāpana olakino o ko mākou kino ponoʻī. Ua like ia me ka hoʻouka ʻana i ko mākou mau ʻohana ponoʻī ke manaʻo lākou ua ʻaihue ʻia lākou.

Inā ʻaʻole i ʻike ʻia a mālama ʻia i ka wā mua, hiki iā ia ke hoʻololi mau i ka ʻili a me ka nalowale o ka neʻe ʻana o nā hono . No laila, he mea nui loa e ʻimi i ke kōkua lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona.

Pehea ka hopena nui o kēia kūlana? ʻO wai ka mea e hoʻopilikia ʻia ai?

Hiki i ka Eosinophilic Fasciitis ke hoʻopilikia i ka fascia ma nā wahi āpau o ke kino, akā ʻo ka mea maʻamau ka hoʻopilikia ʻana i nā lima a me nā wāwae . No nā poʻe he nui, ʻike mua ʻia nā hōʻailona, ​​​​e like me ka ʻeha a i ʻole ka pehu ʻana, ma hope o ka hoʻoikaika kino a i ʻole kahi hana e pono ai ke kū i ka lā a pau.

Hiki i kēia mau hōʻailona, ​​e like me ka ʻeha o nā ʻiʻo a me ka pehu ʻana, ke like me nā maʻi maʻamau ʻē aʻe, no laila he mea nui e ʻike koke i ke kauka inā ʻike ʻoe i kekahi mau loli hou a ʻeha paha i kou ʻili, nā ʻiʻo, a i ʻole nā ​​hono. Pono paha ʻoe e ʻike i kahi rheumatologist, he kauka loea i nā hono a me nā maʻi mumū ʻē aʻe.

ʻAʻohe lāʻau lapaʻau no kēia maʻi i kēia manawa . Eia nō naʻe, ʻo ka nūhou maikaʻi, no ka hapa nui o nā kānaka, e pau nā hōʻailona i loko o kekahi mau makahiki, ʻo ia hoʻi, e komo ka maʻi i ke kūlana "hoʻomaha", a i ʻole kahi kūlana hiamoe. Eia nō naʻe, hiki i kekahi poʻe ke ʻike hou i nā hōʻailona.

ʻOkoʻa ma waena o ka Eosinophilic Fasciitis a me Scleroderma

I ke kamaʻilio ʻana e pili ana i kēia mau maʻi ʻelua, hiki i kekahi poʻe ke huikau iā lāua me kekahi maʻi ʻē aʻe i kapa ʻia ʻo 'Scleroderma'. ʻO 'Eosinophilic Fasciitis' a me 'Scleroderma' he mau maʻi 'autoimmune' kakaikahi loa. Eia kekahi, i loko o kēia mau maʻi ʻelua, lilo nā ʻiʻo o ke kino i mānoanoa a ʻoʻoleʻa.

No laila he aha ka ʻokoʻa? Aia ka ʻokoʻa ma nā ʻano o nā ʻiʻo i hoʻopilikia ʻia.

  • I loko o ka Eosinophilic Fasciitis, e like me kā mākou i kūkākūkā ai ma mua, ua hoʻopilikia ʻia ka fascia, kahi ʻiʻo hoʻohui lahilahi a elastic ma lalo o ka ʻili. I ka hala ʻana o ka manawa, mānoanoa a hoʻonui kēia fascia, e paʻakikī ai ka hoʻoneʻe ʻana i ka ʻāpana kino i hoʻopilikia ʻia.
  • Akā i loko o ka `Scleroderma`, hoʻoulu ka ʻōnaehana pale i nā cell ʻē aʻe e hana i kahi protein i kapa ʻia ʻo `collagen` (kahi mea e hāʻawi ai i ka ikaika i ko mākou ʻili a me nā ʻiʻo). Hoʻokomo ʻia kēia collagen keu i loko o ka ʻili a me nā ʻōpū o loko, e hoʻolilo ana iā lākou i mānoanoa a paʻakikī, e like me kahi ʻeha kahiko. Akā ma kahi o ka ho'ōla ʻana i kahi ʻeha, hiki i kēia collagen keu ke hōʻino i nā ʻiʻo olakino.

ʻO ka Eosinophilic Fasciitis a me COVID-19

ʻO ka poʻe me nā maʻi autoimmune e like me ka Eosinophilic Fasciitis ua manaʻo ʻia he kiʻekiʻe iki aʻe ka pilikia o ka loaʻa ʻana o COVID-19 ma mua o ka heluna kanaka maʻamau.

ʻAʻole maopopo i nā loea inā paha e loaʻa i ka poʻe me kēia maʻi nā hōʻailona koʻikoʻi mai COVID-19. No laila, ʻoi aku ka maikaʻi o ka hahai ʻana i nā ʻōlelo aʻoaʻo a nā luna olakino, e like me ke Centers for Disease Control and Prevention (CDC), e pale iā ʻoe iho mai ka maʻi.

ʻO wai ka mea i loaʻa pinepine i kēia maʻi?

Hiki i ka Eosinophilic Fasciitis ke hoʻopilikia i kekahi, akā ʻo ka hapa nui e pili ana i ka poʻe ma waena o 30 a me 60 mau makahiki.

Eia kekahi, ʻoi aku ka nui o ka poʻe me kekahi mau maʻi olakino mau e loaʻa i kēia maʻi. ʻO kekahi o kēia mau kūlana:

  • ʻAneemia aplastic (anemia aplastic - kahi anemia kahi e emi ai ka hana ʻana o nā hunaola koko)
  • ʻO ka anemia hemolytic (kahi anemia kahi e haki koke ai nā hunaola koko ʻulaʻula)
  • Lymphoma (ka maʻi ʻaʻai o ka ʻōnaehana lymphatic)
  • Leukemia (ka maʻi ʻaʻai o nā hunaola koko)
  • Kekahi mau ʻano o ka maʻi thyroid

Pehea ka maʻamau o kēia?

He maʻi laha ʻole ka Eosinophilic Fasciitis. A hiki i kēia manawa, he kakaikahi wale nō nā hihia, ma kahi o 300, i hōʻike ʻia ma nā puke pai ʻepekema ma ka honua holoʻokoʻa. Eia nō naʻe, ma muli paha o ka hemahema o ka ʻike ʻana a i ʻole ka hōʻike ʻole ʻia ʻana, ʻoi aku paha ka nui o nā hihia.

Pehea ka hopena o ka Eosinophilic Fasciitis i koʻu kino?

E like me kā mākou i kūkākūkā ai ma mua, ua hoʻokumu ʻia kēia ʻano maʻi e ka mumū o ka fascia, kahi ʻiʻo hoʻohui lahilahi a palupalu ma lalo o ka ʻili. Uhi kēia papa o ka fascia a pale i ko mākou mau ʻiʻo a me kekahi mau ʻōpū o loko. Hoʻopaʻa pū ia i ka ʻili a me nā ʻiʻo i kahi a kākoʻo iā lākou i ka wā e neʻe ai lākou.

E noʻonoʻo e pili ana i ia mea, kōkua kēia fascia i ka mālama ʻana i ko mākou mau lālā i ka palupalu, akā ʻaʻole wale ke kau ʻana i lalo. Akā i loko o kekahi me ka 'Eosinophilic Fasciitis', lilo kēia membrane fascia i pehu, e mānoanoa mālie ana, a e ʻoʻoleʻa ana. I ka hopena, ʻo kēia pehu e paʻakikī ai ka hoʻoneʻe ʻana i ka ʻili a me nā ʻiʻo a puni. Inā ʻaʻole mālama ʻia, hiki i kēia fascia ke paʻa i kahi hoʻokahi a paʻa. I kekahi manawa ua kapa ʻia kēia ʻo 'contracture'. ʻO ia hoʻi, he kūlana kahi hiki ʻole ke hoʻolōʻihi ʻia a kulou paha kahi hui.

Ma kahi o ka elasticity maʻamau o ka fascia, ʻeha a paʻakikī paha nā ʻāpana o ke kino i hoʻopilikia ʻia e neʻe.

ʻO nā ʻāpana o ke kino i hoʻopilikia pinepine ʻia:

  • Nā lima (ʻoi aku ka pāma, ʻo ia hoʻi, ka ʻaoʻao o loko o ka lima)
  • Nā wāwae (ʻoi aku ka mua, ma ka iwi ʻūhā)
  • Nā hono a i ʻole nā ​​​​wahi a puni

ʻOiai he mea kakaikahi, hiki i kēia ʻano ke hoʻopili i ka ʻili ma ka maka, ka umauma, a me ka ʻōpū.

Hiki i kekahi mau maʻi me ka Eosinophilic Fasciitis ke loaʻa i ka mumū o nā hono e like me ka Rheumatoid Arthritis. Inā ʻaʻole i kāohi ʻia kēia mumū o nā hono, hiki ke hōʻino ʻia ke cartilage i loko o nā hono, e alakaʻi ana i ka arthritis lōʻihi.

Eia kekahi, inā pili kēia maʻi i ka fascia i kou lima a i ʻole ka pulima lima, hiki i ka mumū ke hoʻopili i ke aʻalolo median, kekahi o nā aʻalolo nui ma ka lima, e hoʻoulu ai i kahi kūlana i kapa ʻia ʻo Carpal Tunnel Syndrome (ka maneʻo, ka ʻeha, a me ka nāwaliwali i ka lima).

ʻO ka mea nui, ʻo ka Eosinophilic Fasciitis kahi maʻi e hiki ke loli a ulu koke. Hiki iā ʻoe ke hoʻomaka e ʻike i nā hopena i ʻike ʻia i loko o kahi manawa pōkole, e like me kekahi mau pule. No laila, inā ʻike ʻoe i kekahi mau hōʻailona a i ʻole nā ​​​​loli i kou kino, e ʻike koke i ke kauka.

He aha nā hōʻailona o ka Eosinophilic Fasciitis?

No laila, pehea ʻoe e kānalua ai i kēia maʻi? Eia kekahi o nā hōʻailona nui:

  • ʻEha ʻiʻo .
  • ʻIli palupalu .
  • Ka mumū a i ʻole ka pehu ʻana .
  • Nā hōʻailona o ka 'Carpal Tunnel Syndrome' (e like me ka mae ʻole, ka ʻeha, ka nāwaliwali o ka lima).
  • ʻO ka ʻāʻī (arthritis - pehu ʻana o nā hono, ʻeha, ʻoʻoleʻa o ke kakahiaka).
  • ʻOi aku ka mānoanoa a me ka paʻa o ka ʻili ma mua o ka maʻamau.
  • Ma kekahi mau wahi, ʻano ʻūlū a ʻāwiliwili ka ʻili, e like me ka ʻili o ka ʻalani (ʻili ʻūlū a i ʻole "peau d'orange").

He aha ke kumu o kēia?

ʻO kaʻoiaʻiʻo, ʻaʻole ʻike ka poʻe loea i ke kumu kikoʻī o ka Eosinophilic Fasciitis. E like me nā maʻi autoimmune he nui, hiki ke hiki koke mai, i kekahi manawa me ke kumu ʻole.

Eia nō naʻe, ua ʻike ʻia kekahi mau noiʻi e hiki ke "hoʻoulu ʻia" kēia mau maʻi autoimmune e kekahi mau mea. ʻO ia hoʻi, hiki i ka maʻi ke ulu ma muli o kekahi mea ʻē aʻe. Eia kekahi laʻana:

  • ʻO kekahi mau ʻano maʻi .
  • Kekahi mau hopena alerika .
  • Ke hoʻohana nei i kekahi mau lāʻau lapaʻau .
  • Ke hoʻohana nei i kekahi mau lāʻau lapaʻau .

Wahi a kekahi poʻe me ka Eosinophilic Fasciitis, ua ʻike ʻia kā lākou mau hōʻailona mua ma hope o ka hana kino ikaika , e like me ka holo ʻana, ka hāpai ʻana i nā mea kaumaha, a i ʻole ka hoʻoikaika kino ʻana, a i ʻole e hana ana i kahi hana e pono ai ka nui o ka hoʻoikaika ma ko lākou mau lima a me nā wāwae.

He manaʻo maikaʻi e kamaʻilio me kāu kauka e pili ana i kāu mau kumu pilikia no ka hoʻomohala ʻana i kahi maʻi autoimmune e like me kēia.

Pehea e ʻike ai nā kauka i kēia maʻi? (Diagnosis)

Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​​​hiki i ke kauka ke hana i kekahi mau hoʻokolohua e ʻike ai inā he Eosinophilic Fasciitis kāu:

1. Fascia Biopsy: ʻO ka biopsy ka wā e lawe ai kāu kauka i kahi hāpana liʻiliʻi o kāu ʻiʻo a hoʻouna iā ia i kahi keʻena hoʻokolohua e nānā iā ia ma lalo o kahi microscope. Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻili i hoʻopilikia ʻia a me ka fascia ma lalo a nānā iā ia. I ka hapanui o nā hihia, ʻo ia ke ala hilinaʻi loa e ʻike ai i ke kūlana.

2. Hoʻāʻo koko: Inā loaʻa iā ʻoe ka Eosinophilic Fasciitis, loaʻa paha iā ʻoe nā pae kiʻekiʻe o kahi ʻano koko keʻokeʻo i kapa ʻia ʻo Eosinophils i loko o kou koko (ʻo ia kahi i loaʻa ai ka inoa o ka maʻi). Eia naʻe, ʻaʻole hiki i nā hoʻāʻo koko wale nō ke hōʻoia i ka maʻi. I ka manawa pinepine, pono kahi biopsy.

3. Nā hoʻāʻo kiʻi: Hiki i nā hoʻāʻo e like me MRI (Magnetic Resonance Imaging) ke kōkua i ka ʻike ʻana i ka mumū i loko o ke kino, ʻoi aku hoʻi i ka fascia a me nā ʻiʻo a puni. Eia nō naʻe, e like me nā hoʻāʻo koko, ʻaʻole lākou i kikoʻī e like me ka biopsy e ʻike ai i ka maʻi.

Lapaʻau no ka Eosinophilic Fasciitis

I ka hapanui o ka manawa, e nalowale paha nā hōʻailona iā lākou iho me ka ʻole o ka lāʻau lapaʻau. Akā i ka hapa nui o ka manawa, mālama nā kauka i ka Eosinophilic Fasciitis me kahi ʻano lāʻau i kapa ʻia ʻo corticosteroids . He ʻano steroid kēia.

Hana nā Corticosteroids ma ka hōʻemi ʻana i ka mumū i loko o ke kino a me ke kāohi ʻana i ka ʻōnaehana pale hana nui. ʻO Prednisone ka corticosteroid i kuhikuhi pinepine ʻia.

Hiki i kāu kauka ke kuhikuhi i nā lāʻau ʻē aʻe ma waho aʻe o nā corticosteroids, e like me:

  • ʻO nā `NSAID`: ʻO nā lāʻau anti-inflammatory non-steroidal (NSAID) i loaʻa ma ka hale kūʻai lāʻau lapaʻau - no ka laʻana, ibuprofen a me diclofenac - hiki ke hōʻemi i nā hōʻailona e like me ka ʻeha a me ka pehu. Eia nō naʻe, inā ʻoe e lawe nei i nā `corticosteroids`, e kamaʻilio me kāu kauka ma mua o ka lawe ʻana i nā `NSAID`. Mai lawe i nā `NSAID` no nā lā he 10 a ʻoi aku i ka manawa me ka ʻae ʻole o kāu kauka.
  • Nā lāʻau lapaʻau e kāohi ana i ka ʻōnaehana pale: Ma muli o ke koʻikoʻi o kou kūlana, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau ʻē aʻe (e like me, Methotrexate) e kāohi ana i ka ʻōnaehana pale overactive e hoʻoulu ai i ka Eosinophilic Fasciitis.
  • Hoʻōla kino: Hiki i ka hoʻōla kino ke kōkua i ka hoʻolōʻihi a me ka wehe ʻana i kou fascia ke paʻa, a kōkua i ka mālama ʻana i ka neʻe ʻana o nā hono. E aʻo aku kāu kauka a mea hoʻōla kino paha iā ʻoe i nā hoʻomaʻamaʻa a me nā hoʻolōʻihi e kūpono i kāu mau hōʻailona.
  • Ke mālama ʻana i nā kūlana ʻē aʻe: Hiki iā ʻoe ke ʻoluʻolu hou aku ma ka mālama ʻana i nā hōʻailona o nā kūlana ʻē aʻe, e like me ka carpal tunnel syndrome a i ʻole ka arthritis.
  • ʻOki kino: Inā koʻikoʻi kou Eosinophilic Fasciitis e hiki ai ke hoʻoulu i nā ʻūmiʻi, pono paha ʻoe e hana i ke ʻoki kino e hoʻokuʻu a wehe paha i kahi ʻāpana o kou fascia (fascial release). ʻO kēia ka hopena hope loa.

Pehea e mālama ai i nā hōʻailona?

  • He mea nui loa e lawe i ka lāʻau lapaʻau e like me ka ʻōlelo a ke kauka, no ka lōʻihi o ka manawa i kauoha ʻia.
  • Inā hāʻawi kāu kauka a mea hoʻōla kino paha iā ʻoe i nā hoʻolōʻihi a i ʻole nā ​​​​hoʻoikaika kino ʻē aʻe, e hana iā lākou i nā manawa he nui e like me kā lākou e ʻōlelo ai iā ʻoe e kōkua i ka hoʻolōʻihi ʻana i ka fascia i hoʻopilikia ʻia. ʻOiai he mea paʻakikī kēia, hiki ke lilo i mea pono inā ʻoe e hoʻomau i ka hana ʻana iā lākou.
  • Inā loaʻa iā ʻoe ʻo Carpal Tunnel Syndrome, pono paha ʻoe e komo i kahi mea kākoʻo e hoʻopaʻa i kou pulima lima i kou wahi hiamoe. E hoʻohana e like me ke kuhikuhi a kāu kauka.

Pehea ka wikiwiki o koʻu ʻoluʻolu ma hope o ka lāʻau lapaʻau?

Pono e hoʻomaka ka mumū i hoʻokumu ʻia e ka Eosinophilic Fasciitis e emi i loko o kekahi mau hola o ka lawe ʻana i ka mahele mua o nā corticosteroids. Hiki ke lilo kēia hōʻoluʻolu i mea manawa pōkole, a hiki ke hoʻi hou mai nā hōʻailona i ka pau ʻana o ka lāʻau. No laila, he mea nui e lawe i ka lāʻau no ka manawa piha i kuhikuhi ʻia e kāu kauka.

Hiki ke pale ʻia ka Eosinophilic Fasciitis?

ʻO ka mea pōʻino, ʻaʻohe ala kikoʻī e pale aku ai i kēia maʻi. ʻAʻole ʻike maopopo ka poʻe loea i ke kumu o nā maʻi autoimmune a pehea paha e hoʻoulu ʻia ai, no laila ʻaʻole hiki iā lākou ke ʻōlelo i ka wā a i ʻole ke kumu e loaʻa ai iā ʻoe kekahi.

He aha ka mea e manaʻo ai kekahi me kēia maʻi?

Inā ua ʻike ʻia ʻoe me ka Eosinophilic Fasciitis, pono ʻoe e manaʻo e hoʻokele i kāu mau hōʻailona no kekahi manawa. Inā ʻike ʻoe i kekahi mau loli i kāu mau hōʻailona, ​​​​ʻoiai inā e ʻoi aku ka ʻino, e kamaʻilio koke me kāu kauka.

E like me kā mākou i ʻōlelo ai ma mua, ʻaʻohe lāʻau lapaʻau no kēia. Noho ka poʻe he nui me ia no kekahi mau makahiki, a laila nalowale nā ​​​​hōʻailona (hele i ke 'remission'). ʻAʻole loaʻa hou i kekahi poʻe, akā hiki i kekahi ke loaʻa nā hōʻailona e hoʻi hou mai ma hope (`recur`).

ʻAʻole hiki iā ʻoe ke hele i ka hana a i ke kula paha?

Inā hiki iā ʻoe ke hana i kāu hana a i ʻole ka hana kula me ka ʻole o ke kaumaha nui ma kou fascia i hoʻopilikia ʻia, pono ʻoe e hoʻi i ka hana a i ʻole ke kula a hiki i kou hoʻōla ʻana mai ka Eosinophilic Fasciitis. Eia nō naʻe, e haʻi aku kāu kauka iā ʻoe i nā hana āu e pale aku ai a hiki i kou hoʻōla ʻana. He mea nui e hahai i kēia mau kuhikuhi.

E kamaʻilio me kāu kauka a e ʻae iā ʻoe ma mua o ka hoʻi hou ʻana i nā hana kino ikaika e like me ka holo ʻana, ka hāpai ʻana i nā mea kaumaha, a i ʻole ka hoʻoikaika kino.

Āhea ʻoe e ʻike ai i ke kauka?

  • Inā ʻike ʻoe i kekahi mau hōʻailona hou ma kou mau lima, nā wāwae, a i ʻole nā ​​​​hui - ʻoiai inā he ʻeha a pehu paha kou e nalowale ʻole ma hope o kekahi mau lā o ka hoʻomaha - e ʻike koke i ke kauka.
  • Inā ua ʻike mua ʻia ʻoe me ka Eosinophilic Fasciitis, e haʻi koke i kāu kauka inā e ʻoi aʻe ka ʻino o kāu mau hōʻailona, ​​a inā ʻike ʻoe i kekahi ʻāpana o kou kino e ʻoʻoleʻa a mae paha.

I ka manawa hea ʻoe e hele ai i kahi Emergency Treatment Unit (ETU) ?

Inā hiki ʻole iā ʻoe ke neʻe a hoʻohana paha i kahi ʻāpana o kou kino, a inā ʻoe e ʻeha nui, e hele koke i ka lumi pilikia kokoke loa .

He aha nā nīnau āu e nīnau ai i ke kauka?

Ke hele ʻoe e ʻike i ke kauka, hiki iā ʻoe ke nīnau i nā nīnau e like me kēia:

  • Loaʻa iaʻu ka Eosinophilic Fasciitis, a i ʻole kekahi mea ʻē aʻe?
  • Pehea ka wikiwiki o ka ʻino ʻana o koʻu mau hōʻailona?
  • He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu? Pehea ka lōʻihi e pono ai iaʻu ka lāʻau lapaʻau?
  • E pono anei iaʻu ke ʻoki kino?
  • Āhea e hiki ai iaʻu ke hoʻi hou i ka hana kino maʻamau?
  • Pehea ka hopena o kēia kūlana i koʻu ola o kēlā me kēia lā?

ʻO kekahi o nā mea nui e pono ai kākou e hoʻomanaʻo mai kēia moʻolelo

He maʻi laha ʻole akā koʻikoʻi ka Eosinophilic fasciitis e hiki ke hoʻopilikia koke iā ʻoe. Inā ʻike ʻoe i ka ʻeha hou, ka pehu ʻana, a i ʻole ka paʻa ʻana i kou mau lima a i ʻole kou mau wāwae, ʻoiai inā ʻaʻole ia e nalo i loko o kekahi mau lā, mai hoʻokaʻulua i ka ʻike ʻana i ke kauka. No ka mea hiki ke ulu koke kēia maʻi , ʻo ka wikiwiki o kou nānā ʻana i kāu mau hōʻailona, ​​ʻo ka wikiwiki o kāu kauka e ʻike ai i ke kumu a hoʻomaka i ka lāʻau e pono ai.

E hoʻohui kāu kauka i nā corticosteroids a me nā lāʻau lapaʻau ʻē aʻe inā pono e kōkua i ka kaohi ʻana i kāu mau hōʻailona. Mai hopohopo, akā e makaʻala i kāu mau hōʻailona a e hahai pono i nā ʻōlelo a kāu kauka. Ke makemake nei iā ʻoe e ho'ōla koke!


ʻO ka Eosinophilic Fasciitis, Eosinophilic Fasciitis, Nā Maʻi ʻIli, Fascia, ʻEha Hui, ʻEha ʻIʻo, Nā Maʻi Autoimmune

Frequently Asked Questions (FAQ)

Pehea ka wikiwiki o koʻu ʻoluʻolu ma hope o ka lāʻau lapaʻau?

Pono e hoʻomaka ka mumū i hoʻokumu ʻia e ka Eosinophilic Fasciitis e emi i loko o kekahi mau hola o ka lawe ʻana i ka mahele mua o nā corticosteroids. Hiki ke lilo kēia hōʻoluʻolu i mea manawa pōkole, a hiki ke hoʻi hou mai nā hōʻailona i ka pau ʻana o ka lāʻau. No laila, he mea nui e lawe i ka lāʻau no ka manawa piha i kuhikuhi ʻia e kāu kauka.

ʻAʻole hiki iā ʻoe ke hele i ka hana a i ke kula paha?

Inā hiki iā ʻoe ke hana i kāu hana a i ʻole ka hana kula me ka ʻole o ke kaumaha nui ma kou fascia i hoʻopilikia ʻia, pono ʻoe e hoʻi i ka hana a i ʻole ke kula a hiki i kou hoʻōla ʻana mai ka Eosinophilic Fasciitis. Eia nō naʻe, e haʻi aku kāu kauka iā ʻoe i nā hana āu e pale aku ai a hiki i kou hoʻōla ʻana. He mea nui e hahai i kēia mau kuhikuhi.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ke ʻike nei ʻoe i ka pehu, ka ʻoʻoleʻa, a me ka ʻeha ma lalo o kou ʻili? E kamaʻilio kākou e pili ana i ka Eosinophilic Fasciitis!
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Ke ʻike nei ʻoe i ka pehu, ka ʻoʻoleʻa, a me ka ʻeha ma lalo o kou ʻili? E kamaʻilio kākou e pili ana i ka Eosinophilic Fasciitis!

Ua ʻike koke anei ʻoe i kahi puʻupuʻu, pehu, a ʻeha paha ma lalo o ka ʻili o kou lima a wāwae paha? Malia paha ua hana ʻia ma hope o kahi hoʻoikaika kino maikaʻi. Ua ʻike anei ʻoe i kekahi mea e like me kēia? No laila, eia kahi kūlana i ʻike iki ʻia he mea nui paha iā ʻoe.

He aha ka Eosinophilic Fasciitis?

I ka ʻōlelo maʻalahi, ʻo ka Eosinophilic Fasciitis kahi maʻi kahi e lilo koke ai ka ʻiʻo e uhi ana i ko mākou mau ʻiʻo a me nā ʻiʻo ma lalo o ko mākou ʻili - kapa mākou he fascia ma nā ʻōlelo lapaʻau - i ka mumū, mānoanoa, a paʻa. E noʻonoʻo iā ia e like me ka ʻupena e hoʻopaʻa ana i ko mākou ʻili a me nā ʻiʻo a kōkua iā lākou e neʻe a puni, e like me ka ʻupena a mākou e kau ai i loko o ka pahu o kā mākou kaʻa i ka wā e kūʻai ai mākou.

Ua hoʻokaʻawale ʻia kēia he 'maʻi autoimmune' . ʻO ke ʻano kēia, hoʻomaka hewa ka ʻōnaehana pale o ko mākou kino, ʻo ia hoʻi ka ʻōnaehana pale, e hoʻouka i nā ʻāpana olakino o ko mākou kino ponoʻī. Ua like ia me ka hoʻouka ʻana i ko mākou mau ʻohana ponoʻī ke manaʻo lākou ua ʻaihue ʻia lākou.

Inā ʻaʻole i ʻike ʻia a mālama ʻia i ka wā mua, hiki iā ia ke hoʻololi mau i ka ʻili a me ka nalowale o ka neʻe ʻana o nā hono . No laila, he mea nui loa e ʻimi i ke kōkua lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona.

Pehea ka hopena nui o kēia kūlana? ʻO wai ka mea e hoʻopilikia ʻia ai?

Hiki i ka Eosinophilic Fasciitis ke hoʻopilikia i ka fascia ma nā wahi āpau o ke kino, akā ʻo ka mea maʻamau ka hoʻopilikia ʻana i nā lima a me nā wāwae . No nā poʻe he nui, ʻike mua ʻia nā hōʻailona, ​​​​e like me ka ʻeha a i ʻole ka pehu ʻana, ma hope o ka hoʻoikaika kino a i ʻole kahi hana e pono ai ke kū i ka lā a pau.

Hiki i kēia mau hōʻailona, ​​e like me ka ʻeha o nā ʻiʻo a me ka pehu ʻana, ke like me nā maʻi maʻamau ʻē aʻe, no laila he mea nui e ʻike koke i ke kauka inā ʻike ʻoe i kekahi mau loli hou a ʻeha paha i kou ʻili, nā ʻiʻo, a i ʻole nā ​​hono. Pono paha ʻoe e ʻike i kahi rheumatologist, he kauka loea i nā hono a me nā maʻi mumū ʻē aʻe.

ʻAʻohe lāʻau lapaʻau no kēia maʻi i kēia manawa . Eia nō naʻe, ʻo ka nūhou maikaʻi, no ka hapa nui o nā kānaka, e pau nā hōʻailona i loko o kekahi mau makahiki, ʻo ia hoʻi, e komo ka maʻi i ke kūlana "hoʻomaha", a i ʻole kahi kūlana hiamoe. Eia nō naʻe, hiki i kekahi poʻe ke ʻike hou i nā hōʻailona.

ʻOkoʻa ma waena o ka Eosinophilic Fasciitis a me Scleroderma

I ke kamaʻilio ʻana e pili ana i kēia mau maʻi ʻelua, hiki i kekahi poʻe ke huikau iā lāua me kekahi maʻi ʻē aʻe i kapa ʻia ʻo 'Scleroderma'. ʻO 'Eosinophilic Fasciitis' a me 'Scleroderma' he mau maʻi 'autoimmune' kakaikahi loa. Eia kekahi, i loko o kēia mau maʻi ʻelua, lilo nā ʻiʻo o ke kino i mānoanoa a ʻoʻoleʻa.

No laila he aha ka ʻokoʻa? Aia ka ʻokoʻa ma nā ʻano o nā ʻiʻo i hoʻopilikia ʻia.

  • I loko o ka Eosinophilic Fasciitis, e like me kā mākou i kūkākūkā ai ma mua, ua hoʻopilikia ʻia ka fascia, kahi ʻiʻo hoʻohui lahilahi a elastic ma lalo o ka ʻili. I ka hala ʻana o ka manawa, mānoanoa a hoʻonui kēia fascia, e paʻakikī ai ka hoʻoneʻe ʻana i ka ʻāpana kino i hoʻopilikia ʻia.
  • Akā i loko o ka `Scleroderma`, hoʻoulu ka ʻōnaehana pale i nā cell ʻē aʻe e hana i kahi protein i kapa ʻia ʻo `collagen` (kahi mea e hāʻawi ai i ka ikaika i ko mākou ʻili a me nā ʻiʻo). Hoʻokomo ʻia kēia collagen keu i loko o ka ʻili a me nā ʻōpū o loko, e hoʻolilo ana iā lākou i mānoanoa a paʻakikī, e like me kahi ʻeha kahiko. Akā ma kahi o ka ho'ōla ʻana i kahi ʻeha, hiki i kēia collagen keu ke hōʻino i nā ʻiʻo olakino.

ʻO ka Eosinophilic Fasciitis a me COVID-19

ʻO ka poʻe me nā maʻi autoimmune e like me ka Eosinophilic Fasciitis ua manaʻo ʻia he kiʻekiʻe iki aʻe ka pilikia o ka loaʻa ʻana o COVID-19 ma mua o ka heluna kanaka maʻamau.

ʻAʻole maopopo i nā loea inā paha e loaʻa i ka poʻe me kēia maʻi nā hōʻailona koʻikoʻi mai COVID-19. No laila, ʻoi aku ka maikaʻi o ka hahai ʻana i nā ʻōlelo aʻoaʻo a nā luna olakino, e like me ke Centers for Disease Control and Prevention (CDC), e pale iā ʻoe iho mai ka maʻi.

ʻO wai ka mea i loaʻa pinepine i kēia maʻi?

Hiki i ka Eosinophilic Fasciitis ke hoʻopilikia i kekahi, akā ʻo ka hapa nui e pili ana i ka poʻe ma waena o 30 a me 60 mau makahiki.

Eia kekahi, ʻoi aku ka nui o ka poʻe me kekahi mau maʻi olakino mau e loaʻa i kēia maʻi. ʻO kekahi o kēia mau kūlana:

  • ʻAneemia aplastic (anemia aplastic - kahi anemia kahi e emi ai ka hana ʻana o nā hunaola koko)
  • ʻO ka anemia hemolytic (kahi anemia kahi e haki koke ai nā hunaola koko ʻulaʻula)
  • Lymphoma (ka maʻi ʻaʻai o ka ʻōnaehana lymphatic)
  • Leukemia (ka maʻi ʻaʻai o nā hunaola koko)
  • Kekahi mau ʻano o ka maʻi thyroid

Pehea ka maʻamau o kēia?

He maʻi laha ʻole ka Eosinophilic Fasciitis. A hiki i kēia manawa, he kakaikahi wale nō nā hihia, ma kahi o 300, i hōʻike ʻia ma nā puke pai ʻepekema ma ka honua holoʻokoʻa. Eia nō naʻe, ma muli paha o ka hemahema o ka ʻike ʻana a i ʻole ka hōʻike ʻole ʻia ʻana, ʻoi aku paha ka nui o nā hihia.

Pehea ka hopena o ka Eosinophilic Fasciitis i koʻu kino?

E like me kā mākou i kūkākūkā ai ma mua, ua hoʻokumu ʻia kēia ʻano maʻi e ka mumū o ka fascia, kahi ʻiʻo hoʻohui lahilahi a palupalu ma lalo o ka ʻili. Uhi kēia papa o ka fascia a pale i ko mākou mau ʻiʻo a me kekahi mau ʻōpū o loko. Hoʻopaʻa pū ia i ka ʻili a me nā ʻiʻo i kahi a kākoʻo iā lākou i ka wā e neʻe ai lākou.

E noʻonoʻo e pili ana i ia mea, kōkua kēia fascia i ka mālama ʻana i ko mākou mau lālā i ka palupalu, akā ʻaʻole wale ke kau ʻana i lalo. Akā i loko o kekahi me ka 'Eosinophilic Fasciitis', lilo kēia membrane fascia i pehu, e mānoanoa mālie ana, a e ʻoʻoleʻa ana. I ka hopena, ʻo kēia pehu e paʻakikī ai ka hoʻoneʻe ʻana i ka ʻili a me nā ʻiʻo a puni. Inā ʻaʻole mālama ʻia, hiki i kēia fascia ke paʻa i kahi hoʻokahi a paʻa. I kekahi manawa ua kapa ʻia kēia ʻo 'contracture'. ʻO ia hoʻi, he kūlana kahi hiki ʻole ke hoʻolōʻihi ʻia a kulou paha kahi hui.

Ma kahi o ka elasticity maʻamau o ka fascia, ʻeha a paʻakikī paha nā ʻāpana o ke kino i hoʻopilikia ʻia e neʻe.

ʻO nā ʻāpana o ke kino i hoʻopilikia pinepine ʻia:

  • Nā lima (ʻoi aku ka pāma, ʻo ia hoʻi, ka ʻaoʻao o loko o ka lima)
  • Nā wāwae (ʻoi aku ka mua, ma ka iwi ʻūhā)
  • Nā hono a i ʻole nā ​​​​wahi a puni

ʻOiai he mea kakaikahi, hiki i kēia ʻano ke hoʻopili i ka ʻili ma ka maka, ka umauma, a me ka ʻōpū.

Hiki i kekahi mau maʻi me ka Eosinophilic Fasciitis ke loaʻa i ka mumū o nā hono e like me ka Rheumatoid Arthritis. Inā ʻaʻole i kāohi ʻia kēia mumū o nā hono, hiki ke hōʻino ʻia ke cartilage i loko o nā hono, e alakaʻi ana i ka arthritis lōʻihi.

Eia kekahi, inā pili kēia maʻi i ka fascia i kou lima a i ʻole ka pulima lima, hiki i ka mumū ke hoʻopili i ke aʻalolo median, kekahi o nā aʻalolo nui ma ka lima, e hoʻoulu ai i kahi kūlana i kapa ʻia ʻo Carpal Tunnel Syndrome (ka maneʻo, ka ʻeha, a me ka nāwaliwali i ka lima).

ʻO ka mea nui, ʻo ka Eosinophilic Fasciitis kahi maʻi e hiki ke loli a ulu koke. Hiki iā ʻoe ke hoʻomaka e ʻike i nā hopena i ʻike ʻia i loko o kahi manawa pōkole, e like me kekahi mau pule. No laila, inā ʻike ʻoe i kekahi mau hōʻailona a i ʻole nā ​​​​loli i kou kino, e ʻike koke i ke kauka.

He aha nā hōʻailona o ka Eosinophilic Fasciitis?

No laila, pehea ʻoe e kānalua ai i kēia maʻi? Eia kekahi o nā hōʻailona nui:

  • ʻEha ʻiʻo .
  • ʻIli palupalu .
  • Ka mumū a i ʻole ka pehu ʻana .
  • Nā hōʻailona o ka 'Carpal Tunnel Syndrome' (e like me ka mae ʻole, ka ʻeha, ka nāwaliwali o ka lima).
  • ʻO ka ʻāʻī (arthritis - pehu ʻana o nā hono, ʻeha, ʻoʻoleʻa o ke kakahiaka).
  • ʻOi aku ka mānoanoa a me ka paʻa o ka ʻili ma mua o ka maʻamau.
  • Ma kekahi mau wahi, ʻano ʻūlū a ʻāwiliwili ka ʻili, e like me ka ʻili o ka ʻalani (ʻili ʻūlū a i ʻole "peau d'orange").

He aha ke kumu o kēia?

ʻO kaʻoiaʻiʻo, ʻaʻole ʻike ka poʻe loea i ke kumu kikoʻī o ka Eosinophilic Fasciitis. E like me nā maʻi autoimmune he nui, hiki ke hiki koke mai, i kekahi manawa me ke kumu ʻole.

Eia nō naʻe, ua ʻike ʻia kekahi mau noiʻi e hiki ke "hoʻoulu ʻia" kēia mau maʻi autoimmune e kekahi mau mea. ʻO ia hoʻi, hiki i ka maʻi ke ulu ma muli o kekahi mea ʻē aʻe. Eia kekahi laʻana:

  • ʻO kekahi mau ʻano maʻi .
  • Kekahi mau hopena alerika .
  • Ke hoʻohana nei i kekahi mau lāʻau lapaʻau .
  • Ke hoʻohana nei i kekahi mau lāʻau lapaʻau .

Wahi a kekahi poʻe me ka Eosinophilic Fasciitis, ua ʻike ʻia kā lākou mau hōʻailona mua ma hope o ka hana kino ikaika , e like me ka holo ʻana, ka hāpai ʻana i nā mea kaumaha, a i ʻole ka hoʻoikaika kino ʻana, a i ʻole e hana ana i kahi hana e pono ai ka nui o ka hoʻoikaika ma ko lākou mau lima a me nā wāwae.

He manaʻo maikaʻi e kamaʻilio me kāu kauka e pili ana i kāu mau kumu pilikia no ka hoʻomohala ʻana i kahi maʻi autoimmune e like me kēia.

Pehea e ʻike ai nā kauka i kēia maʻi? (Diagnosis)

Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​​​hiki i ke kauka ke hana i kekahi mau hoʻokolohua e ʻike ai inā he Eosinophilic Fasciitis kāu:

1. Fascia Biopsy: ʻO ka biopsy ka wā e lawe ai kāu kauka i kahi hāpana liʻiliʻi o kāu ʻiʻo a hoʻouna iā ia i kahi keʻena hoʻokolohua e nānā iā ia ma lalo o kahi microscope. Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻili i hoʻopilikia ʻia a me ka fascia ma lalo a nānā iā ia. I ka hapanui o nā hihia, ʻo ia ke ala hilinaʻi loa e ʻike ai i ke kūlana.

2. Hoʻāʻo koko: Inā loaʻa iā ʻoe ka Eosinophilic Fasciitis, loaʻa paha iā ʻoe nā pae kiʻekiʻe o kahi ʻano koko keʻokeʻo i kapa ʻia ʻo Eosinophils i loko o kou koko (ʻo ia kahi i loaʻa ai ka inoa o ka maʻi). Eia naʻe, ʻaʻole hiki i nā hoʻāʻo koko wale nō ke hōʻoia i ka maʻi. I ka manawa pinepine, pono kahi biopsy.

3. Nā hoʻāʻo kiʻi: Hiki i nā hoʻāʻo e like me MRI (Magnetic Resonance Imaging) ke kōkua i ka ʻike ʻana i ka mumū i loko o ke kino, ʻoi aku hoʻi i ka fascia a me nā ʻiʻo a puni. Eia nō naʻe, e like me nā hoʻāʻo koko, ʻaʻole lākou i kikoʻī e like me ka biopsy e ʻike ai i ka maʻi.

Lapaʻau no ka Eosinophilic Fasciitis

I ka hapanui o ka manawa, e nalowale paha nā hōʻailona iā lākou iho me ka ʻole o ka lāʻau lapaʻau. Akā i ka hapa nui o ka manawa, mālama nā kauka i ka Eosinophilic Fasciitis me kahi ʻano lāʻau i kapa ʻia ʻo corticosteroids . He ʻano steroid kēia.

Hana nā Corticosteroids ma ka hōʻemi ʻana i ka mumū i loko o ke kino a me ke kāohi ʻana i ka ʻōnaehana pale hana nui. ʻO Prednisone ka corticosteroid i kuhikuhi pinepine ʻia.

Hiki i kāu kauka ke kuhikuhi i nā lāʻau ʻē aʻe ma waho aʻe o nā corticosteroids, e like me:

  • ʻO nā `NSAID`: ʻO nā lāʻau anti-inflammatory non-steroidal (NSAID) i loaʻa ma ka hale kūʻai lāʻau lapaʻau - no ka laʻana, ibuprofen a me diclofenac - hiki ke hōʻemi i nā hōʻailona e like me ka ʻeha a me ka pehu. Eia nō naʻe, inā ʻoe e lawe nei i nā `corticosteroids`, e kamaʻilio me kāu kauka ma mua o ka lawe ʻana i nā `NSAID`. Mai lawe i nā `NSAID` no nā lā he 10 a ʻoi aku i ka manawa me ka ʻae ʻole o kāu kauka.
  • Nā lāʻau lapaʻau e kāohi ana i ka ʻōnaehana pale: Ma muli o ke koʻikoʻi o kou kūlana, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau ʻē aʻe (e like me, Methotrexate) e kāohi ana i ka ʻōnaehana pale overactive e hoʻoulu ai i ka Eosinophilic Fasciitis.
  • Hoʻōla kino: Hiki i ka hoʻōla kino ke kōkua i ka hoʻolōʻihi a me ka wehe ʻana i kou fascia ke paʻa, a kōkua i ka mālama ʻana i ka neʻe ʻana o nā hono. E aʻo aku kāu kauka a mea hoʻōla kino paha iā ʻoe i nā hoʻomaʻamaʻa a me nā hoʻolōʻihi e kūpono i kāu mau hōʻailona.
  • Ke mālama ʻana i nā kūlana ʻē aʻe: Hiki iā ʻoe ke ʻoluʻolu hou aku ma ka mālama ʻana i nā hōʻailona o nā kūlana ʻē aʻe, e like me ka carpal tunnel syndrome a i ʻole ka arthritis.
  • ʻOki kino: Inā koʻikoʻi kou Eosinophilic Fasciitis e hiki ai ke hoʻoulu i nā ʻūmiʻi, pono paha ʻoe e hana i ke ʻoki kino e hoʻokuʻu a wehe paha i kahi ʻāpana o kou fascia (fascial release). ʻO kēia ka hopena hope loa.

Pehea e mālama ai i nā hōʻailona?

  • He mea nui loa e lawe i ka lāʻau lapaʻau e like me ka ʻōlelo a ke kauka, no ka lōʻihi o ka manawa i kauoha ʻia.
  • Inā hāʻawi kāu kauka a mea hoʻōla kino paha iā ʻoe i nā hoʻolōʻihi a i ʻole nā ​​​​hoʻoikaika kino ʻē aʻe, e hana iā lākou i nā manawa he nui e like me kā lākou e ʻōlelo ai iā ʻoe e kōkua i ka hoʻolōʻihi ʻana i ka fascia i hoʻopilikia ʻia. ʻOiai he mea paʻakikī kēia, hiki ke lilo i mea pono inā ʻoe e hoʻomau i ka hana ʻana iā lākou.
  • Inā loaʻa iā ʻoe ʻo Carpal Tunnel Syndrome, pono paha ʻoe e komo i kahi mea kākoʻo e hoʻopaʻa i kou pulima lima i kou wahi hiamoe. E hoʻohana e like me ke kuhikuhi a kāu kauka.

Pehea ka wikiwiki o koʻu ʻoluʻolu ma hope o ka lāʻau lapaʻau?

Pono e hoʻomaka ka mumū i hoʻokumu ʻia e ka Eosinophilic Fasciitis e emi i loko o kekahi mau hola o ka lawe ʻana i ka mahele mua o nā corticosteroids. Hiki ke lilo kēia hōʻoluʻolu i mea manawa pōkole, a hiki ke hoʻi hou mai nā hōʻailona i ka pau ʻana o ka lāʻau. No laila, he mea nui e lawe i ka lāʻau no ka manawa piha i kuhikuhi ʻia e kāu kauka.

Hiki ke pale ʻia ka Eosinophilic Fasciitis?

ʻO ka mea pōʻino, ʻaʻohe ala kikoʻī e pale aku ai i kēia maʻi. ʻAʻole ʻike maopopo ka poʻe loea i ke kumu o nā maʻi autoimmune a pehea paha e hoʻoulu ʻia ai, no laila ʻaʻole hiki iā lākou ke ʻōlelo i ka wā a i ʻole ke kumu e loaʻa ai iā ʻoe kekahi.

He aha ka mea e manaʻo ai kekahi me kēia maʻi?

Inā ua ʻike ʻia ʻoe me ka Eosinophilic Fasciitis, pono ʻoe e manaʻo e hoʻokele i kāu mau hōʻailona no kekahi manawa. Inā ʻike ʻoe i kekahi mau loli i kāu mau hōʻailona, ​​​​ʻoiai inā e ʻoi aku ka ʻino, e kamaʻilio koke me kāu kauka.

E like me kā mākou i ʻōlelo ai ma mua, ʻaʻohe lāʻau lapaʻau no kēia. Noho ka poʻe he nui me ia no kekahi mau makahiki, a laila nalowale nā ​​​​hōʻailona (hele i ke 'remission'). ʻAʻole loaʻa hou i kekahi poʻe, akā hiki i kekahi ke loaʻa nā hōʻailona e hoʻi hou mai ma hope (`recur`).

ʻAʻole hiki iā ʻoe ke hele i ka hana a i ke kula paha?

Inā hiki iā ʻoe ke hana i kāu hana a i ʻole ka hana kula me ka ʻole o ke kaumaha nui ma kou fascia i hoʻopilikia ʻia, pono ʻoe e hoʻi i ka hana a i ʻole ke kula a hiki i kou hoʻōla ʻana mai ka Eosinophilic Fasciitis. Eia nō naʻe, e haʻi aku kāu kauka iā ʻoe i nā hana āu e pale aku ai a hiki i kou hoʻōla ʻana. He mea nui e hahai i kēia mau kuhikuhi.

E kamaʻilio me kāu kauka a e ʻae iā ʻoe ma mua o ka hoʻi hou ʻana i nā hana kino ikaika e like me ka holo ʻana, ka hāpai ʻana i nā mea kaumaha, a i ʻole ka hoʻoikaika kino.

Āhea ʻoe e ʻike ai i ke kauka?

  • Inā ʻike ʻoe i kekahi mau hōʻailona hou ma kou mau lima, nā wāwae, a i ʻole nā ​​​​hui - ʻoiai inā he ʻeha a pehu paha kou e nalowale ʻole ma hope o kekahi mau lā o ka hoʻomaha - e ʻike koke i ke kauka.
  • Inā ua ʻike mua ʻia ʻoe me ka Eosinophilic Fasciitis, e haʻi koke i kāu kauka inā e ʻoi aʻe ka ʻino o kāu mau hōʻailona, ​​a inā ʻike ʻoe i kekahi ʻāpana o kou kino e ʻoʻoleʻa a mae paha.

I ka manawa hea ʻoe e hele ai i kahi Emergency Treatment Unit (ETU) ?

Inā hiki ʻole iā ʻoe ke neʻe a hoʻohana paha i kahi ʻāpana o kou kino, a inā ʻoe e ʻeha nui, e hele koke i ka lumi pilikia kokoke loa .

He aha nā nīnau āu e nīnau ai i ke kauka?

Ke hele ʻoe e ʻike i ke kauka, hiki iā ʻoe ke nīnau i nā nīnau e like me kēia:

  • Loaʻa iaʻu ka Eosinophilic Fasciitis, a i ʻole kekahi mea ʻē aʻe?
  • Pehea ka wikiwiki o ka ʻino ʻana o koʻu mau hōʻailona?
  • He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu? Pehea ka lōʻihi e pono ai iaʻu ka lāʻau lapaʻau?
  • E pono anei iaʻu ke ʻoki kino?
  • Āhea e hiki ai iaʻu ke hoʻi hou i ka hana kino maʻamau?
  • Pehea ka hopena o kēia kūlana i koʻu ola o kēlā me kēia lā?

ʻO kekahi o nā mea nui e pono ai kākou e hoʻomanaʻo mai kēia moʻolelo

He maʻi laha ʻole akā koʻikoʻi ka Eosinophilic fasciitis e hiki ke hoʻopilikia koke iā ʻoe. Inā ʻike ʻoe i ka ʻeha hou, ka pehu ʻana, a i ʻole ka paʻa ʻana i kou mau lima a i ʻole kou mau wāwae, ʻoiai inā ʻaʻole ia e nalo i loko o kekahi mau lā, mai hoʻokaʻulua i ka ʻike ʻana i ke kauka. No ka mea hiki ke ulu koke kēia maʻi , ʻo ka wikiwiki o kou nānā ʻana i kāu mau hōʻailona, ​​ʻo ka wikiwiki o kāu kauka e ʻike ai i ke kumu a hoʻomaka i ka lāʻau e pono ai.

E hoʻohui kāu kauka i nā corticosteroids a me nā lāʻau lapaʻau ʻē aʻe inā pono e kōkua i ka kaohi ʻana i kāu mau hōʻailona. Mai hopohopo, akā e makaʻala i kāu mau hōʻailona a e hahai pono i nā ʻōlelo a kāu kauka. Ke makemake nei iā ʻoe e ho'ōla koke!


ʻO ka Eosinophilic Fasciitis, Eosinophilic Fasciitis, Nā Maʻi ʻIli, Fascia, ʻEha Hui, ʻEha ʻIʻo, Nā Maʻi Autoimmune

Frequently Asked Questions (FAQ)

Pehea ka wikiwiki o koʻu ʻoluʻolu ma hope o ka lāʻau lapaʻau?

Pono e hoʻomaka ka mumū i hoʻokumu ʻia e ka Eosinophilic Fasciitis e emi i loko o kekahi mau hola o ka lawe ʻana i ka mahele mua o nā corticosteroids. Hiki ke lilo kēia hōʻoluʻolu i mea manawa pōkole, a hiki ke hoʻi hou mai nā hōʻailona i ka pau ʻana o ka lāʻau. No laila, he mea nui e lawe i ka lāʻau no ka manawa piha i kuhikuhi ʻia e kāu kauka.

ʻAʻole hiki iā ʻoe ke hele i ka hana a i ke kula paha?

Inā hiki iā ʻoe ke hana i kāu hana a i ʻole ka hana kula me ka ʻole o ke kaumaha nui ma kou fascia i hoʻopilikia ʻia, pono ʻoe e hoʻi i ka hana a i ʻole ke kula a hiki i kou hoʻōla ʻana mai ka Eosinophilic Fasciitis. Eia nō naʻe, e haʻi aku kāu kauka iā ʻoe i nā hana āu e pale aku ai a hiki i kou hoʻōla ʻana. He mea nui e hahai i kēia mau kuhikuhi.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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