Ke manaʻo nei hoʻi ʻoe he ʻano pōwehiwehi iki ke ala ʻoe i ke kakahiaka? Ke ʻano nei anei e ʻoi aku ka ʻino i ka hala ʻana o ke ao? A i ʻole ke paʻakikī nei iā ʻoe ke ʻike i nā kukui i ka wā e hoʻokele ana i ka pō? ʻOiai ke ʻano o kēia mau mea he mau mea maʻamau, hiki ke lilo ia i hoʻomaka o kahi pilikia maka liʻiliʻi. ʻO ia ke ʻano o ka maʻi a mākou e kamaʻilio ai i kēia lā, a ʻo ia hoʻi ʻo Fuchs' Dystrophy .
He aha ka maʻi Fuchs' Dystrophy?
I ka ʻōlelo maʻalahi, ʻo Fuchs' Dystrophy kahi maʻi e hoʻopilikia ai i ka cornea o kou mau maka ʻelua. Ua ʻike anei ʻoe i ke ʻano o ka cornea? ʻO ia ka membrane aniani e like me ke aniani e uhi ana i mua o kou maka. Ua uhi ʻia ka ʻāpana kala o kou maka, ka iris , a me ka pupil e kēia cornea. Ua kapa ʻia hoʻi kēia ʻo 'Fuchs' corneal dystrophy' a me 'Fuchs' endothelial dystrophy'.
No laila, ke loaʻa iā ʻoe ka Fuchs' dystrophy, make mālie nā cell i loko o ka papa o loko o kou cornea, i kapa ʻia ʻo ka corneal endothelium . He ʻāpana koʻikoʻi loa kēia endothelium. Hana ia e like me ka pamu wai liʻiliʻi. Kōkua ia i ka wehe ʻana i ka wai pono ʻole mai ka cornea a mālama iā ia i ka maopopo a me ka maʻemaʻe.
E noʻonoʻo, he aha ka mea e hana ʻia ke make nā pūnaewele e hana ana i loko o kēia pamu? Hoʻomaka ka wai e hōʻiliʻili i loko o ka cornea. A laila pehu ka cornea, e lilo ana e like me ka huʻahuʻa i piha i ka wai. ʻO ia ke kumu e hoʻomaka ai nā maka e nānā pōwehiwehi, a i kekahi manawa hiki ke nānā aku me he noe lā i hana ʻia ma luna o ka maka. I nā hihia koʻikoʻi, hiki ke hana ʻia nā pehu wai liʻiliʻi ma luna o ka cornea. Hiki i kēia mau pehu ke hōʻeha a me ka ʻoluʻolu ʻole i ka maka.
He aha nā pae o ka Fuchs' Dystrophy?
ʻElua mau pae nui o ka dystrophy o Fuchs.
- Kahua mua: ʻO ka hōʻailona nui e loaʻa iā ʻoe i kēia pae, ʻo ia ka ʻike pōwehiwehi i ke kakahiaka . Ua like ia me ke aniani i uhi ʻia i ka noe ke ala ʻoe. Eia nō naʻe, i kou hele ʻana i kāu mau hana o kēlā me kēia lā, i loko o kekahi mau hola, e emi mālie ana kēia pōwehiwehi a e ʻoi aku ka maopopo o kou ʻike. ʻAʻole paha i loaʻa i kekahi poʻe nā hōʻailona nui i kēia pae.
- Kahua Hope: I ka holomua ʻana o ka maʻi, hoʻomaka ka palalulu i ke kakahiaka wale nō e hoʻomau i ka lā a pau. Lilo ka pehu ʻana o ka cornea i mea mau loa. ʻO ke ʻano kēia, hiki ke palalulu kou ʻike i kēlā me kēia manawa o ke ao, ka pō, a i ʻole ke kakahiaka.
He aha nā hōʻailona o ka Fuchs' Dystrophy?
I nā pae mua, ʻaʻole paha ʻoe e ʻike i kekahi mau hōʻailona. Eia nō naʻe, i ka holomua ʻana o ka maʻi, hiki iā ʻoe ke ʻike i nā hōʻailona e like me:
- Hoʻemi ʻia ka ʻike pō: Ua like kēia me ka ʻike ʻana i ka ʻālohilohi a me nā halos a puni nā kukui uila i ka wā e hoʻokele ana i ka pō.
- Paʻakikī ke ʻike ʻana i nā lā ua: Ke pouli iki ke kaiapuni, he mea paʻakikī ke ʻike maopopo i nā mea.
- Paʻakikī ke hoʻokaʻawale ma waena o nā mea (ʻike ʻokoʻa maikaʻi ʻole): No ka laʻana, paʻakikī paha ke loaʻa kahi kuapo keʻokeʻo ma ka paia keʻokeʻo.
- ʻIke i ke kukui ʻālohilohi: Lilo nā maka i polū loa a ʻaʻole hiki ke nānā aku i ka lā a i ʻole nā kukui ʻālohilohi ma ka home.
- Me he mea lā he one a lepo paha i loko o kou mau maka. He manaʻo hoʻonāukiuki wale nō ia me he mea lā ua paʻa kekahi mea i loko.
- Pahū nā pehu ma ka cornea a hōʻeha i ka maka. He hōʻailona koʻikoʻi kēia.
- ʻŌpala: Hoʻokumu mua kēia mau ʻōpala ma waenakonu o ka cornea. Hiki i kēia mau ʻōpala ke hoʻopilikia mau i ka ʻike.
He aha ke kumu o ka Fuchs' Dystrophy?
ʻO ke kumu nui o ka ulu ʻana o ka Fuchs dystrophy, he hoʻoilina ia . ʻO ke ʻano kēia, inā loaʻa i kou makuahine a makua paha ka maʻi, hiki nō hoʻi iā ʻoe ke loaʻa. Ua kapa ʻia kēia he autosomal dominant inheritance i ka ʻepekema lapaʻau. Eia nō naʻe, i kekahi manawa hiki i kekahi ke loaʻa iā ia i ka manawa ʻole, ʻoiai inā ʻaʻohe mea o ka ʻohana i loaʻa i ka maʻi.
Eia kekahi, hiki i kekahi mau mea ke hoʻonui i ka ʻino o ka dystrophy o Fuchs .
- Puhipaka: ʻOi aku ka nui o ka poʻe puhipaka i ka loaʻa ʻana o kēia maʻi.
- Ka ʻike ʻia ʻana i ka lā (ka ʻike ʻia ʻana o ke kukui UV): ʻAʻole maikaʻi ka ʻike pinepine ʻia ʻana i nā kukuna ultraviolet ʻino.
- Loaʻa i ka maʻi diabetes mellitus: Hiki i kēia maʻi ke ʻoi aku ka ʻino i nā poʻe me ka maʻi diabetes.
ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka Fuchs' Dystrophy?
ʻOi aku ka nui o ka loaʻa ʻana o ka maʻi Fuchs' dystrophy i kekahi poʻe ma mua o kekahi. E nānā kākou i kēlā.
- Makahiki: Hiki i ke kauka ke ʻike i nā hōʻailona mua o kēia maʻi ma waena o 30 a me 40 mau makahiki. Eia nō naʻe, hoʻopilikia pinepine ʻia ka ʻike ma hope o 50 mau makahiki .
- Kāne: ʻOi aku ka nui o ka loaʻa ʻana o kēia maʻi i nā wahine ma mua o nā kāne.
- Moʻolelo ʻohana: E like me ka mea i ʻōlelo ʻia ma mua, inā loaʻa i kekahi o ka ʻohana ka Fuchs' dystrophy, aia kekahi i ka pilikia o ka loaʻa ʻana iā ia.
Pehea e ʻike ai nā kauka i ka Fuchs' Dystrophy?
Inā loaʻa iā ʻoe kēia mau hōʻailona, ʻo ka mea mua āu e hana ai, ʻo ia ke ʻike i kahi loea mālama maka . E nīnau mua ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, e nānā i kāu mōʻaukala olakino, a laila e hana i kahi hoʻokolokolo maka piha.
I loko o kēia hoʻokolokolo maka, hiki i ke kauka ke ʻike i kekahi mau hōʻailona e hōʻike ana he Fuchs' dystrophy kona.
- Hiki iā ʻoe ke ʻike ua mānoanoa kekahi o nā papa o ka cornea .
- NāuHiki ke ʻike ʻia nā loli i ke ʻano o ka endothelium.
- E ʻike paha ʻoe i nā puʻupuʻu liʻiliʻi i kapa ʻia ʻo guttae ma loko o ka cornea. He hōʻailona kēia o nā pūnaewele endothelial i nāwaliwali.
Nā hoʻāʻo e hōʻoia i ka Fuchs' Dystrophy
No ka hōʻoia ʻana i ka maʻi, hiki i ke kauka ke hana i kekahi mau hoʻokolohua, e like me:
- Microscopy: Hana ʻia kēia mau mea me ka hoʻohana ʻana i nā microscope kūikawā. ʻO nā hiʻohiʻona e komo pū me ka hoʻokolokolo ʻana o ke kukui slit a me ka microscope confocal/specular . ʻAe kēia iā mākou e ʻike i ka cornea ma ka pae cellular.
- Pachymetry: He hoʻāʻo ʻeha ʻole kēia. Ana ia i ka mānoanoa o kou cornea. Inā pehu ka cornea, ua mānoanoa loa ia, ʻeā?
- ʻO ka Optical Coherence Tomography (OCT): He scan maka ʻole kēia, ʻaʻohe ʻeha. Hoʻohana ia i ka mālamalama e lawe i nā kiʻi maopopo o loko o kou maka, ʻoiai kahi ʻāpana kea o ka cornea.
He aha nā lāʻau lapaʻau no ka Fuchs' Dystrophy?
Me nā holomua ʻepekema o kēia manawa, hiki ke mālama ʻia ka dystrophy o Fuchs, akā ʻaʻole hiki ke ho'ōla ʻia . I nā pae mua o ka maʻi, inā ʻaʻohe hōʻailona nui, hiki i kāu kauka ke mālama wale iā ʻoe. ʻO ke ʻano kēia e noi ʻia paha ʻoe e hele mai no ka hoʻokolokolo maka i nā manawa maʻamau.
Eia nā ʻano lapaʻau ʻē aʻe:
- Nā ʻaila poni a me nā kulu maka: Inā ʻaʻole koʻikoʻi kou mau hōʻailona, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e hōʻemi i ka pehu ʻana i loko o ka cornea a kōkua i ka hoʻokahe ʻana i ka wai keu. ʻO ka hōʻoluʻolu mai kēia mau mea he manawa pōkole wale nō.
- Mea hoʻomaloʻo lauoho lima: Mai kahaha, he lāʻau lapaʻau nō hoʻi kēia! No ka hōʻemi ʻana i ka pehu kakahiaka, ua ʻike ʻia ka puhi ʻana i ka ea anuanu ma kou maka mai kahi mea hoʻomaloʻo lauoho (ma kahi mamao a me ke akahele) e kōkua i ka hoʻomaloʻo ʻana i ka makū keu i loko o ka cornea. Pono ʻoe e nīnau i kāu kauka no ke ʻano pololei.
- Hoʻoili Corneal: Ke hoʻomaka ka palena nui o kou ʻike e ka dystrophy o Fuchs, ʻo ke ʻoki kino ka lāʻau lapaʻau maikaʻi loa. Hiki paha iā ʻoe ke loaʻa i kahi kaʻina hana endothelial keratoplasty (EK) , kahi e hoʻoili wale ai i kahi hapa o ka cornea. A i ʻole hiki paha iā ʻoe ke loaʻa i kahi cornea hou. Ua holomua loa ke ʻoki kino EK i kēia manawa no ka mea e pili ana i ka wehe ʻana i ka papa maʻi o ka endothelium a hoʻololi iā ia me kahi papa olakino.
- ʻO ka wehe wale ʻana o Descemet (DSO):He lāʻau lapaʻau hou kēia. Pili ia i ke kahili ʻana i kahi ʻāpana o nā hunaola maʻi ma waenakonu o ka cornea. ʻAe kēia i nā hunaola olakino a puni ka cornea e ulu a hoʻopiha i nā hakahaka. ʻAʻole paha e holo pono kēia no nā mea āpau, a na ke kauka e hoʻoholo.
He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka e pili ana i ka Fuchs' Dystrophy?
He mea nui e kūkulu i kahi pilina maikaʻi me kāu kauka maka. E hōʻoia e hele i kāu mau hoʻokolohua maka i nā lā a kāu kauka e ʻōlelo ai. E haʻi koke i kāu kauka inā loaʻa iā ʻoe kekahi mau hōʻailona hou a inā e ʻoi aʻe ka ʻino o kāu mau hōʻailona.
Hiki iā ʻoe ke nīnau i ke kauka i nā nīnau e like me kēia:
- He aha nā hōʻailona e pono ai iaʻu e ʻike iā ʻoe i ka wā hikiwawe loa?
- He aha ka lāʻau lapaʻau āu e ʻōlelo mai ai noʻu? He aha nā pōmaikaʻi a me nā pōʻino?
- Aia kekahi mau hoʻokolohua lapaʻau e hiki iaʻu ke komo?
- Inā maikaʻi ʻole koʻu ʻike maka, aia kekahi mau mea kōkua ʻike maka haʻahaʻa e hiki ke kōkua iaʻu?
Hiki ke pale ʻia ka Fuchs' Dystrophy?
ʻO kaʻoiaʻiʻo, ʻaʻohe ala e pale aku ai i ka dystrophy o Fuchs i kēia manawa . Eia nō naʻe, inā ʻoe e puhipaka, hiki i ka haʻalele ʻana ke kōkua. Inā loaʻa iā ʻoe ka maʻi diabetes, he mea nui hoʻi e hana pū me kāu kauka e kaohi i kou pae kō koko.
He aha kaʻu e manaʻo ai inā loaʻa iaʻu ka Fuchs' Dystrophy?
Ma muli o ke koʻikoʻi o ka Fuchs' dystrophy, inā ʻaʻole ʻoe e loaʻa i ka lāʻau kūpono, hiki iā ʻoe ke ʻeha nui, nalowale ka ʻike, a me ka makapō paha .
Akā me ka mālama kūpono, hiki i kou kūlana ke hoʻomaikaʻi nui. Ma hope o kekahi mau ʻoki kino (me nā aniani), hiki i kou ʻike ke hoʻi i 20/20, e like me ke kanaka olakino, i loko o kekahi mau lā. No laila he mea nui e hana pū me kāu kauka e ʻimi i ka lāʻau kūpono iā ʻoe.
Hiki ke hopohopo ka ʻike ʻana i nā hōʻailona o kekahi maʻi maka, a ʻaʻole ʻokoʻa ka dystrophy o Fuchs. Inā loaʻa iā ʻoe nā hōʻailona e like me ka ʻeha o ka maka a i ʻole ka ʻike pohihihi, e ʻike koke i ke kauka. E hoʻomanaʻo, ʻo ka ʻike mua a me ka mālama ʻana e alakaʻi pinepine i nā hopena maikaʻi loa. Ke hoʻomohala mau nei nā mea noiʻi i nā ala hou e hoʻokele a mālama ai i ka dystrophy o Fuchs a me nā maʻi maka ʻē aʻe.
Leka Lawe-Home
ʻAe, no laila ke lana nei koʻu manaʻo ua ʻike maikaʻi ʻoe i ka Fuchs' Dystrophy, a mākou i kamaʻilio ai i kēia lā.
- He maʻi hoʻoilina kēia e hoʻopilikia ai i ka cornea o ka maka.
- ʻO nā hōʻailona nui ka ʻike maka pōwehiwehi i ke kakahiaka , ka ʻike maka pōwehiwehi i ka lā a pau, ka ʻike ʻana i nā apo i ka wā e nānā ana i nā kukui, a me ka ʻeha o nā maka.
- Hiki i nā mea e like me ka puhipaka, nā kukui UV koʻikoʻi, a me ka maʻi diabetes ke hoʻonui i ka maʻi.
- Hiki i ke kauka ophthalmologist ke nānā pono i kēia a kuhikuhi i ka lāʻau kūpono nou.
- Aia nā lāʻau lapaʻau e like me ka lāʻau lapaʻau a me nā ʻoki kūikawā (corneal transplant, DSO).
- He mea nui loa ka ʻike koke ʻana a me ka mālama ʻana i ka maʻi.
Inā loaʻa iā ʻoe kēia mau hōʻailona, mai makaʻu e ʻike i ke kauka. He mea waiwai nui nā maka, no laila ʻo kā mākou kuleana ke mālama iā lākou.
ʻO ka Fuchs ' Dystrophy, Cornea, Maʻi Maka, ʻIke Pōwehiwehi, ʻEha Maka, Hoʻoili Corneal











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