Ua kuhikuhi anei kāu kauka iā ʻoe a i ʻole kekahi o kou ʻohana i kahi lāʻau i kapa ʻia ʻo Glycerol Phenylbutyrate? He lāʻau ia me kahi inoa ʻē, no laila he nui paha kāu mau nīnau e pili ana i ia mea. Mai hopohopo, i kēia lā e kamaʻilio wale mākou e pili ana i kēia lāʻau, kāna hana, pehea e hoʻohana ai, a me nā mea e makaʻala ai.
I ka ʻōlelo maʻalahi, he aha kēia lāʻau lapaʻau?
ʻO Glycerol Phenylbutyrate (i ʻike ʻia hoʻi e ka inoa inoa ʻo RAVICTI) kahi lāʻau lapaʻau i hoʻohana ʻia e kāohi i ka nui o ka ammonia i loko o ke koko o ka poʻe me nā maʻi pōʻaiapuni urea .
E noʻonoʻo e pili ana i ia mea, ke hoʻohana ko mākou kino i ka protein, hana ia i ka ammonia ma ke ʻano he huahana ʻōpala. I loko o ke kanaka olakino, hoʻololi ke kaʻina hana urea i kēia ammonia i urea ʻino ʻole a hoʻokuʻu iā ia i loko o ka mimi. Akā i loko o kekahi me ka maʻi kaʻina hana urea, ʻaʻole hiki i ke kino ke hana pono i kēia hana. A laila, hiki i ka ammonia ke hōʻiliʻili i loko o ke kino a hōʻino i ka lolo a me ka ʻōnaehana nerve.
Kōkua kēia lāʻau lapaʻau i ka wehe ʻana i ka ammonia keu mai ke kino. Akā, hoʻokahi mea e pono e hoʻomanaʻo ʻia. ʻAʻole kēia he lāʻau lapaʻau e hoʻōla loa i ka maʻi. He lāʻau lapaʻau wale nō kēia e kōkua ai i ka kaohi ʻana i ka maʻi.
ʻO ka maʻamau, i ka wā e hāʻawi ʻia ai kēia lāʻau lapaʻau, pono ʻoe e hahai i kahi papaʻai haʻahaʻa protein kūikawā i kauoha ʻia e kāu kauka, a malia paha e lawe i nā mea hoʻopihapiha meaʻai hou aʻe.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i ka lāʻau lapaʻau
Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui e haʻi i kāu kauka i kēia mau ʻike. Mai hūnā i kēia mau mea, no ka mea, he mea nui loa ia no kou palekana.
| Ke kūlana āu e pono ai e hōʻike | No ke aha he mea nui kēlā? |
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| Nā pilikia ʻōpū | Hiki ke hoʻopilikia ʻia ke kino e ka omo ʻana o ka lāʻau lapaʻau. |
| Maʻi puʻupaʻa, akepaʻa a i ʻole ka pancreas | Ma muli o ka hoʻokuʻu ʻia ʻana o ka lāʻau lapaʻau mai ke kino ma o kēia ʻōkana, pono paha e hoʻoponopono ʻia ka nui inā he mau pilikia olakino. |
| Nā maʻi ʻaleka | E hōʻoia e haʻi i kāu kauka inā he mau maʻi ʻaleka kou i kēia lāʻau lapaʻau, nā lāʻau lapaʻau ʻē aʻe, nā meaʻai, nā mea hoʻomalu, a i ʻole nā mea hoʻoluʻu. |
| Inā hāpai ʻoe a i ʻole e hoʻāʻo nei e hāpai | Pono ʻoe e kamaʻilio me kāu kauka e pili ana i ka hopena o ka lāʻau lapaʻau i ka pēpē i loko o ka ʻōpū. |
| Inā hānai ʻia ka pēpē me ka waiū | E kūkākūkā me kāu kauka inā paha e hele ka lāʻau lapaʻau i ka pēpē ma o ka waiū umauma. |
Pehea pololei kaʻu e hoʻohana ai i kēia lāʻau lapaʻau?
Loaʻa kēia lāʻau lapaʻau ma ke ʻano he wai hoʻoheheʻe waha, no laila e makaʻala i kēia mau mea.
- E lawe ma ka waha: He lāʻau lapaʻau kēia i lawe ʻia ma ka waha.
- E ana pololei: E hoʻohana i ka puna kūikawā, ke kīʻaha, a i ʻole ka syringe e hele mai me ka lāʻau lapaʻau e ana . Mai hoʻohana i nā tīpune maʻamau ma ka home, no ka mea, ʻaʻole pololei loa lākou.
- E lawe pū me ka meaʻai: ʻOi aku ka maikaʻi o ka lawe ʻana i kēia lāʻau lapaʻau me ka ʻai a i ʻole, no nā pēpē, me ka waiū waiū .
- E lawe i ka lāʻau i ka manawa i kuhikuhi ʻia: E lawe i ka lāʻau i ka manawa i kuhikuhi ʻia, ma nā manawa i kuhikuhi ʻia, e like me ke kauoha a kāu kauka. Mai lawe ʻoi aku ma mua o ka nui i kuhikuhi ʻia.
- Mai ho'ōki: Mai ho'ōki koke i ka lawe ʻana i ka lāʻau lapaʻau me ka ʻole o ke aʻo ʻana a ke kauka.
- Ke hāʻawi ʻia i nā keiki: I kekahi manawa ua kuhikuhi ʻia kēia lāʻau lapaʻau i nā pēpē hānau hou. Eia nō naʻe, aia nā hana palekana kūikawā e hahai ai. No laila, e kamaʻilio pono me kāu kauka pediatric e pili ana i kēia a e kiʻi i ka ʻōlelo aʻo.
He aha inā piʻi ka nui o ka lāʻau lapaʻau (overdose)?
Inā manaʻo ʻoe ua lawe nui ʻoe i ka lāʻau lapaʻau, ʻo ka mea mua āu e hana ai, ʻo ke kelepona ʻana i ke Kikowaena ʻIke ʻAi ʻona Lahui ma ka Halemai Lahui ʻo Colombo . A i ʻole e hele i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa. Mai hoʻopaneʻe i kēia.
He aha kāu e hana ai inā e poina ʻoe i kahi mahele o ka lāʻau lapaʻau?
Inā poina iā ʻoe ke lawe i kahi lāʻau, e lawe koke i ka wā e hoʻomanaʻo ai ʻoe. Eia nō naʻe, inā kokoke ka manawa no kāu lāʻau aʻe, e kāpae i ka lāʻau i hala ʻole a lawe i kāu lāʻau aʻe i ka manawa i hoʻonohonoho ʻia. Mai lawe i ʻelua mau lāʻau i ka manawa hoʻokahi no kekahi kumu.
Nā mea ʻē aʻe e launa pū me kēia lāʻau lapaʻau
Hiki i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei ke launa pū me kēia lāʻau lapaʻau, no laila e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei (me nā huaora, nā lāʻau lapaʻau lāʻau, a me nā mea hoʻohui).
| Nā ʻano lāʻau lapaʻau e hiki ai ke hoʻoulu i nā hakakā (nā laʻana) |
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| Nānā: ʻAʻole kēia he papa inoa piha. E haʻi pū i kāu kauka inā ʻoe e puhipaka ana, inu waiʻona, a hoʻohana paha i nā lāʻau ʻē aʻe. |
Nā hopena ʻaoʻao paha o ka lawe ʻana i ka lāʻau lapaʻau
E like me nā lāʻau lapaʻau āpau, hiki i kēia ke hana i kekahi mau hopena ʻaoʻao. He koʻikoʻi kekahi, he mea maʻamau kekahi.
| Nā hopena ʻaoʻao e pono ʻoe e hōʻike koke i kāu kauka |
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| Nā hopena ʻaoʻao e pono e hōʻike ʻia i ke kauka inā hoʻomau lākou a hoʻopilikia paha |
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Inā loaʻa iā ʻoe kekahi mau hōʻailona ʻē aʻe i ʻōlelo ʻole ʻia ma kēia papa inoa, e kamaʻilio pū me kāu kauka e pili ana iā lākou.
Pehea e mālama ai i ka lāʻau lapaʻau?
- E mālama ʻia mai nā keiki aku.
- E mālama ma ka mahana o ka lumi, ma waena o 20 a me 25 kekelē Celsius (68-77 Fahrenheit).
- E hoʻolei i nā lāʻau lapaʻau i pau ka lā.
Leka Lawe-Home
- ʻAʻole ʻo Glycerol Phenylbutyrate kahi lāʻau lapaʻau e ho'ōla ai i nā maʻi pōʻaiapuni urea, he lāʻau ia e kōkua ai i ka kaohi ʻana i nā pae ammonia i loko o ke koko.
- E lawe mau i kēia lāʻau lapaʻau me ka ʻai, me ka hoʻohana ʻana i ke kīʻaha ana kūikawā e hele mai me ia.
- E hahai pono i ka papaʻai haʻahaʻa-protein i kauoha ʻia e kāu kauka.
- Mai ho'ōki i ka lawe ʻana i ka lāʻau me ka ʻole o ke aʻo ʻana a kāu kauka.
- Inā lawe ʻoe i ka nui o ka lāʻau lapaʻau a i ʻole ʻike ʻoe i nā hopena ʻaoʻao koʻikoʻi, e ʻimi koke i ke kōkua lapaʻau.
- E haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei (me nā huaora a me nā lāʻau lapaʻau kuʻuna).
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