Ke paʻakikī nei hoʻi iā ʻoe ke hanu i ka wā e luhi iki ai ʻoe, ke piʻi ʻoe i kahi alapiʻi? Loaʻa iā ʻoe i kekahi manawa kahi ʻū mau a maloʻo me ka ʻole o ka phlegm no ke kumu ʻike ʻole ʻia? Hoʻopoina pinepine mākou he luhi maʻamau kēia mau hōʻailona a i ʻole he allergy liʻiliʻi. Eia nō naʻe, hiki iā lākou ke lilo i mau hōʻailona mua o nā loli koʻikoʻi e hana nei i loko o ko mākou mau māmā. I kēia lā e kamaʻilio mākou e pili ana i kekahi o ia ʻano maʻi, ʻo Interstitial Lung Disease, a i ʻole ILD no ka pōkole.
I ka ʻōlelo maʻalahi, he aha ka Interstitial Lung Disease (ILD)?
E noʻonoʻo i ko kākou mau māmā e like me nā huʻahuʻa ʻelua i piha i nā miliona o nā pehu ea liʻiliʻi. Ua kapa ʻia kēia mau ʻeke ea liʻiliʻi he alveoli . Ke hanu kākou, hoʻohui ʻia ka oxygen a kākou e lawe ai i ko kākou koko ma o kēia mau ʻeke ea. A hoʻokuʻu ʻia hoʻi ke kalapona ʻokikene i makemake ʻole ʻia i loko o ke koko ma o kēia mau ʻeke ea.
I kēia manawa, ma waena o kēia mau ʻeke ea, e like me ka sima ma waena o nā piliki i loko o ka pā piliki, aia kahi pūnaewele o nā ʻiʻo palupalu. ʻO kēia ka mea a mākou e kapa nei he interstitium . I ka ILD, ua hōʻino ʻia kēia pūnaewele o nā ʻiʻo palupalu, a i ʻole ua hōʻino ʻia, a mānoanoa mālie, paʻakikī, a loaʻa ka ʻeha (fibrosis) .
I ka pololei, nalowale ko kākou mau māmā i ko lākou ʻano palupalu a palupalu a lilo i ʻoʻoleʻa a paʻakikī. Ua kapa ʻia kēia ma ke ʻano lapaʻau ʻo Pulmonary Fibrosis . Akā e hoʻomanaʻo, ʻaʻole nā ILD āpau he Pulmonary Fibrosis, akā ʻo Pulmonary Fibrosis kahi ʻano ILD.
Ke mānoanoa ka ʻiʻo o ka māmā ma kēia ʻano, ua ālai ʻia ke kaʻa ʻana o ka oxygen mai nā ʻeke ea i ke koko. ʻO ka hopena, ʻaʻole i loaʻa i ko mākou kino ka nui o ka oxygen e pono ai. ʻO kēia ke kumu nui o nā hōʻailona e like me ka pōkole o ka hanu a me ka luhi.
ʻAʻole he maʻi hoʻokahi ʻo ILD. Aia ma mua o 200 mau kūlana i hoʻokaʻawale ʻia ma lalo o kēia inoa. ʻO ka hiʻohiʻona maʻamau o lākou āpau ka hōʻino ʻana i ka ʻiʻo interstitial o nā māmā.
He aha nā hōʻailona o kekahi me ILD?
ʻAʻole paha e koʻikoʻi loa nā hōʻailona o ka ILD i ka wā mua. Eia nō naʻe, i ka hala ʻana o ka manawa, i nā mahina a i ʻole nā makahiki, e piʻi mālie kēia mau hōʻailona. ʻO kēia nā hōʻailona i ʻike ʻia e ka hapa nui o ka poʻe.
| Hōʻailona | Wehewehena |
|---|---|
| Pōkole o ka hanu | I ka wā mua, ʻike wale ʻia i ka wā e hoʻoikaika kino ai, e like me ka wā e hoʻoikaika kino ai a i ʻole e piʻi ana i nā alapiʻi. Akā i ka holomua ʻana o ka maʻi, hiki ke paʻakikī ke hanu ʻoiai ke kū mālie wale nō. |
| ʻŪhū maloʻo | He hōʻailona nui kēia no nā kānaka he nui. Hōʻike ia ma ke ʻano he ʻū mau e hana ʻole ana i ka mucus. |
| Luhi | No ka mea, ʻaʻole i loaʻa i ke kino ka nui o ka oxygen e pono ai, hiki iā ʻoe ke luhi mau a ʻaʻole hiki ke hana i kekahi mea. |
| ʻO ka ʻeha o ka umauma | Hiki i kekahi poʻe ke manaʻo i ka ʻeha o ka umauma a i ʻole ka ʻūmiʻi. |
Inā loaʻa iā ʻoe kēia mau hōʻailona, mai manaʻo ʻoe he ILD kou. Akā, mai hoʻowahāwahā iā lākou. He mea nui e ʻike i kāu kauka , ʻoiai inā he pōkole kou hanu a me ka ʻū maloʻo i mau no nā mahina .
No ke aha e loaʻa ai kēia ʻano maʻi? He aha nā kumu?
Hiki ke puʻunaue ʻia nā kumu o ILD i ʻelua mau māhele: nā kumu i ʻike ʻia a me nā kumu i ʻike ʻole ʻia/idiopathic .
1. Nā Kumu i ʻIke ʻia
ʻO ke ʻano o kēia, hiki iā mākou ke ʻōlelo me ka maopopo, "ʻO kēia ke kumu o kēia maʻi."
- Nā maʻi Autoimmune a i ʻole nā maʻi pili: I kekahi manawa hoʻomaka ka ʻōnaehana pale ponoʻī o ko mākou kino e hoʻouka i nā ʻiʻo olakino o ko mākou kino. ʻO ka poʻe me nā maʻi e like me Rheumatoid Arthritis (RA) , Lupus , a me Scleroderma e ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka ILD.
- Nā pilikia o ka hana a me ke kaiapuni: Hiki i kekahi o nā ʻāpana lepo a mākou e hanu ai ke hōʻeha i nā māmā i ka wā lōʻihi.
- Lepo silica: No ka poʻe e hana ana i nā lua pōhaku, nā lua ʻeli, a me nā hale hana keramika.
- Nā olonā asbestos:No ka poʻe e wāwahi ana i nā hale kahiko, hana ma ka ʻoihana hoʻouna moku, a hana me nā paleki i loko o kekahi mau kaʻa.
- Lepo palaoa, mauʻu maloʻo, ʻōpala manu: He ʻano i kapa ʻia ʻo Hypersensitivity Pneumonitis hiki ke loaʻa i nā poʻe mahiʻai a hānai holoholona paha.
- ʻŌpala a me nā Fungi: No ka poʻe e hana ana i nā wahi pulu a maikaʻi ʻole ka ea.
- ʻO kekahi mau lāʻau lapaʻau a me nā ʻano lapaʻau:
- Nā lāʻau lapaʻau e like me ka amiodarone, i hoʻohana ʻia e mālama i kekahi mau maʻi puʻuwai.
- Kekahi mau lāʻau anti-cancer (nā lāʻau Chemotherapy) .
- Lapaʻau radiation no ka maʻi ʻaʻai umauma a i ʻole ka maʻi ʻaʻai māmā.
- ʻO kekahi mau maʻi: Hiki ke loaʻa ka ʻeha o nā māmā ma hope o nā maʻi koʻikoʻi e like me ka maʻi puʻupuʻu a me ka niumonia .
2. Nā kumu i ʻike ʻole ʻia (Idiopathic)
I nā hihia he nui, ʻaʻohe kumu kikoʻī e loaʻa ai no ka ILD. ʻAʻohe maʻi ʻē aʻe o ka mea maʻi a i ʻole ka pili ʻana i kahi mea ʻino, akā ua ʻeha ka ʻiʻo o ka māmā. Kāhea mākou i kēia mau hihia he idiopathic , ʻo ia hoʻi "no ke kumu i ʻike ʻole ʻia."
ʻO ka maʻi maʻamau a koʻikoʻi loa o kēia mau mea ʻo ia ka Idiopathic Pulmonary Fibrosis (IPF) .
ʻO wai ka mea i ʻoi aku ka pilikia no ka ILD?
ʻOiai hiki i kekahi ke loaʻa i ka ILD, ʻoi aku ka maʻalahi o kekahi poʻe i ia.
| Kumu pilikia | Wehewehena |
|---|---|
| Makahiki | ʻOi aku ka maʻamau o nā ʻano ILD he nui i nā poʻe ma luna o 70 mau makahiki. |
| Wahine/kāne | ʻO kekahi mau ʻano ILD, ʻoi aku ka IPF, ʻoi aku ka maʻamau i nā kāne ma mua o nā wahine. |
| Puhipaka | He kiʻekiʻe loa ka pilikia o ka poʻe puhipaka a i ʻole i puhipaka ma mua i ka hoʻomohala ʻana i ka ILD. |
| Nā kūlana olakino ʻē aʻe | ʻO nā maʻi e like me nā maʻi autoimmune i ʻōlelo ʻia ma luna, COPD, a me ka hepatitis C. |
| Ka hana a me ke kaiapuni | Ka ʻike ʻia ʻana i nā mea e like me ka asbestos a me ka silica. |
| Moʻolelo ʻohana | Inā ua loaʻa i kekahi o ka ʻohana ka ILD, hiki ke hoʻonui iki ʻia ka pilikia. |
Pehea e ʻike ai ke kauka i kēia maʻi?
Ke ʻike ʻoe i ke kauka me nā hōʻailona āu i ʻōlelo ai ma luna, e hana ʻo ia i kekahi mau hoʻokolohua e ʻike pololei ai i kēia maʻi.
1. Ke nīnau ʻana iā ʻoe e pili ana i kāu mau hōʻailona: ʻO ka mea mua, e nīnau lākou iā ʻoe e pili ana i kāu mau hōʻailona, ka lā i hoʻomaka ai lākou, ka wā i ʻoi aku ai ka ʻino, a pēlā aku. E nīnau pū lākou e pili ana i kāu ʻoihana, inā paha ua loaʻa i kekahi o kou ʻohana nā maʻi like, a me nā lāʻau lapaʻau ʻē aʻe āu e lawe nei.
2. Hoʻokolokolo kino: E kau ke kauka i kahi stethoscope ma kou umauma a hoʻolohe i nā leo āu e hana ai ke hanu ʻoe. Nui ka poʻe me ILD e lohe i nā "crackles" i loko o ko lākou mau māmā, e like me ka wehe ʻia ʻana o Velcro .
3. Nā Hoʻāʻo Hana Pulmonary (PFT): Ma kēia hoʻāʻo, ua noi ʻia ʻoe e hanu i loko a i waho ma o kahi paipu i hoʻopili ʻia i kahi mīkini. Ana kēia hoʻāʻo i ka nui o ka ea e hiki i kou mau māmā ke paʻa a me ka wikiwiki o kou hoʻokuʻu ʻana i waho. Ma ILD, ua hoʻemi ʻia ka hiki o ka māmā.
4. Nā Hoʻāʻo Kiʻi:
- X-ray o ka umauma: Hiki i kahi X-ray o ka umauma ke hāʻawi i kahi manaʻo maʻamau inā he mau ʻeha i loko o nā māmā.
- ʻO ke Kiʻi CT Hoʻonā Kiʻekiʻe (HRCT): ʻO kēia ka hoʻāʻo koʻikoʻi loa no ka ʻike ʻana i ka ILD. Hiki iā ia ke hana i nā kiʻi ʻoi aku ka maopopo a me nā kikoʻī ma mua o ka CT scan maʻamau. Hiki iā ia ke hōʻike maikaʻi i ke ʻano o ka ʻōpala i loko o nā māmā a pehea i laha ai (nā ʻano e like me "honeycombing").
5. Nā Hoʻāʻo Koko: Hoʻāʻo ʻia nā hāpana koko e ʻike i nā kūlana olakino ʻē aʻe, e like me nā maʻi autoimmune.
6. Bronchoscopy: I kekahi mau hihia, hoʻokomo ʻia kahi ʻōmole lahilahi me kahi kāmela i hoʻopili ʻia ma ka ihu a i ʻole ka waha i loko o nā māmā, kahi e nānā ʻia ai i loko a lawe ʻia kahi hāpana ʻiʻo (biopsy).
7.Biopsy ʻoki kino: Inā ʻaʻole i hoʻoholo ʻia nā hoʻokolohua i luna, hana ʻia kahi hana ʻoki liʻiliʻi e wehe i kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka māmā no ka hoʻokolokolo ʻana.
He aha nā lāʻau lapaʻau no ka ILD?
ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau no ka ILD i kēia manawa, ʻo ia hoʻi, ʻaʻohe lāʻau lapaʻau no ka ʻeha e kū mai ana i loko o nā māmā. Eia nō naʻe, he nui nā lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i ka holomua o ka maʻi, hōʻemi i nā hōʻailona, a hoʻomaikaʻi i kou ʻano ola. Aia ka lāʻau lapaʻau i ke ʻano o ka ILD āu e loaʻa ai, ke koʻikoʻi o ka maʻi, a me kou olakino holoʻokoʻa.
ʻO ka mea nui loa, ʻo ia ka ʻike mua ʻana i ka maʻi a hoʻomaka i ka lāʻau lapaʻau. Hiki i kēia ke hōʻemi i ka hōʻino hou ʻana i nā māmā.
Eia kekahi o nā ʻano lapaʻau nui:
- Nā lāʻau lapaʻau:
- Corticosteroids: Hoʻemi nā lāʻau lapaʻau e like me Prednisolone i ka mumū i loko o nā māmā.
- Nā lāʻau anti-fibrotic: Hiki i nā lāʻau e like me Pirfenidone lāua ʻo Nintedanib ke hoʻolohi i ka wikiwiki o ka ʻeha o ka māmā. Hāʻawi kūikawā ʻia kēia mau mea i nā poʻe maʻi me IPF.
- Nā Immunosuppressants: Hāʻawi ʻia nā kānaka me ILD ma muli o nā maʻi autoimmune i nā lāʻau lapaʻau e hōʻemi ana i ka hana o ka ʻōnaehana pale.
- Lapaʻau Oxygen: No ka poʻe me nā pae oxygen koko haʻahaʻa, hāʻawi ʻia ka oxygen pākuʻi ma o ka ʻōmole ihu a i ʻole ka pale maka. Hiki i kēia ke kōkua i ka hōʻemi ʻana i ka hanu pōkole a me ka luhi.
- Hoʻōla hou ʻana i ka puʻuwai: Ua like kēia me ke 'physiotherapy' no nā māmā. E hāʻawi aku kahi hui i hoʻomaʻamaʻa kūikawā ʻia iā ʻoe i nā hoʻomaʻamaʻa hanu, hoʻoikaika kino, a me nā ʻōlelo aʻoaʻo meaʻai. E hoʻonui kēia i kou ikaika a kōkua iā ʻoe e ola me kāu mau hōʻailona.
- Hoʻoili Mama: No ka poʻe i koʻikoʻi loa ko lākou maʻi a ʻaʻole hiki ke kaohi ʻia e kekahi lāʻau ʻē aʻe, ʻo ke koho hope loa, ʻo ia ke hoʻoili ʻana i kahi mama olakino.
He aha kaʻu e hana ai i koʻu noho ʻana me ILD?
He mea maʻamau ke kaumaha a me ka makaʻu ke loaʻa iā ʻoe kahi hōʻailona ILD. Eia nō naʻe, ma ka hana ʻana i nā hoʻololi liʻiliʻi i kou nohona a me ka hahai ʻana i nā ʻōlelo aʻoaʻo a kāu kauka, hiki iā ʻoe ke ola i kahi ola maikaʻi me kēia maʻi.
- E pale loa i ka puhipaka: Inā he mea puhipaka ʻoe, ʻo ka mea maikaʻi loa hiki iā ʻoe ke hana, ʻo ia ke haʻalele i kēia lā.
- E ʻai i ka meaʻai olakino: ʻO ka ʻai ʻana i ka meaʻai kaulike e kōkua i ka mālama ʻana i ka ikehu o ke kino.
- E hoʻoikaika kino i nā manawa a pau:E nīnau i kāu kauka a e hoʻoikaika kino māmā e kūpono iā ʻoe. ʻOiai kekahi mea e like me ka hele wāwae ua lawa ia.
- E hoʻomaha: He mea nui loa ka hāʻawi ʻana i ke kino i ka hoʻomaha e pono ai.
- E pale iā ʻoe iho mai nā maʻi: E ʻaʻahu i ka pale maka i ka wā e hele ai i nā wahi piha kanaka, holoi pinepine i kou mau lima, a kamaʻilio me kāu kauka e pili ana i ka loaʻa ʻana o nā lāʻau pale no ka maʻi pneumonia a me ka maʻi influenza.
- E noʻonoʻo i kāu hana: Inā pili kāu hana i ka hanu ʻana i nā mea ʻino i kou mau māmā, makemake paha ʻoe e noʻonoʻo e hoʻohana i nā ʻano hana palekana a i ʻole ka hoʻololi ʻana i nā hana.
E hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi. E kamaʻilio me kāu kauka, ʻohana, a me nā hoaaloha e pili ana i kou mau manaʻo. E ʻimi i ke aʻo ʻana inā pono.
Leka Lawe-Home
- ʻO ka maʻi puʻuwai interstitial (ILD) kahi hui o nā maʻi e hoʻoulu ai i ka mānoanoa a me ka ʻōpala o nā ʻiʻo ma waena o nā ʻeke ea o nā māmā.
- ʻO nā hōʻailona nui ka pōkole o ka hanu a me ka ʻūlū maloʻo e mau ana no nā mahina.
- Hiki i kekahi mau kūlana olakino, nā pilikia hana, a me kekahi mau lāʻau lapaʻau ke hana i kēia , a pinepine ʻole hiki ke loaʻa kahi kumu kikoʻī.
- ʻOiai ʻo ka pōʻino i nā māmā i hoʻokumu ʻia e ka ILD he mea hiki ʻole ke hoʻihoʻi ʻia, hiki i ka ʻike mua ʻana a me ka mālama ʻana ke kaohi i ka maʻi a hoʻomaikaʻi i ka maikaʻi o ke ola.
- Inā loaʻa iā ʻoe nā hōʻailona i luna, mai hopohopo a hoʻowahāwahā paha iā lākou, akā e ʻike koke i kāu kauka a e ʻimi i ke kōkua lapaʻau.











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