Ua pehu iki a kaumaha paha kou wāwae hema ma mua o kekahi? I kekahi manawa ʻeha wale nō ia a manaʻo ʻia e like me ka ʻūlū ʻana? ʻAʻole nui ka poʻe e nānā nui i kēia mau hōʻailona. Akā i kekahi manawa hiki i ke kumu ma hope o kēia ke ʻoi aku ka koʻikoʻi ma mua o kou manaʻo. ʻO kekahi kumu o ia ʻano, ʻo ia paha kēia maʻi i kapa ʻia ʻo 'May-Thurner Syndrome'. E nānā maʻalahi kākou i ke ʻano o ia mea.
I ka pōkole, he aha ka May-Thurner Syndrome?
Maʻalahi loa. ʻElua ʻano o nā kīʻaha koko i loko o ko kākou kino. Kāhea mākou i nā aa koko e lawe ana i ke koko i hoʻopiha ʻia me ka oxygen mai ka puʻuwai a i ke koena o ke kino he 'Arteries' . Pēlā nō, kapa mākou i nā aa koko e lawe ana i ke koko i hoʻohana ʻia me ka oxygen i hoʻihoʻi ʻia i ka puʻuwai he 'Veins' .
Ma kēia kūlana i kapa ʻia ʻo Turner syndrome, hele ke aʻa nui e lawe ana i ke koko i kou wāwae ʻākau (ʻākau iliac artery) ma luna o ke aʻa nui e lawe ana i ke koko i kou puʻuwai mai kou wāwae hema (hema iliac vein) a ʻomi iā ia. E noʻonoʻo e like me kekahi e hehi ana ma luna o kahi paipu wai. A laila ua hoʻopau ʻia ke kahe ʻana o ka wai, ʻeā? Ma ke ʻano like, i ka wā e ʻomi ai kēlā aʻa i ke aʻa, ua hoʻopau ʻia ke kahe ʻana o ke koko mai ka wāwae hema. Ua kapa ʻia hoʻi kēia kūlana ʻo `(Cockett syndrome)`.
Pehea ka hopena o kēia kūlana i ke kino?
Ke ālai ʻia ke kahe o ke koko mai ka wāwae hema a i luna, hoʻomaka kekahi koko e hōʻiliʻili a kū paha ma ka wāwae hema. ʻO ka mea weliweli loa e pili ana i kēia, ʻo ia ka wā e hōʻiliʻili ai ke koko ma kahi hoʻokahi e like me kēia, piʻi nui ka manawa e hana ʻia ai kahi ʻūpā koko i loko o kēlā aʻa koko. Ma nā ʻōlelo lapaʻau, kapa mākou i kēia ʻo 'deep vein thrombosis' (DVT) .
He maʻi koʻikoʻi ka DVT e hiki ke hiki koke mai. Inā haki kēia ʻūpā koko a paʻa i loko o kahi aʻa koko i loko o nā māmā, hiki ke hoʻoweliweli i ke ola.
ʻO ka maʻamau, hiki ke ʻike ʻia nā hōʻailona e like me kēia ke ulu aʻe kahi DVT.
| Nā hōʻailona o ka DVT | |
|---|---|
| Ka pehu a me ke kaumaha | Ka pehu ʻana a me ke kaumaha, pinepine ma kekahi wāwae (i kēia hihia, ka wāwae hema). |
| ʻEha | He ʻeha ʻoi a i ʻole he manaʻo ʻūlū ma ka wāwae, ʻoi aku hoʻi ma ka ʻāpana groin. |
| ʻOle ke kala ʻili | Ka ʻulaʻula a polū paha o ka ʻili ma ka wāwae. |
| Puka ʻana o ke aʻa koko | Pehu nā aa koko ma nā wāwae a hoʻomaka e ʻike ʻia ma luna o ka ʻili. |
Eia kekahi, hiki i kekahi mau wahine ke hoʻomohala i kahi maʻi i kapa ʻia ʻo pelvic congestion syndrome me May-Turner syndrome, ʻo ia ke ʻano e pilikia ai nā pilikia me nā aʻa koko ma ka ʻōpū haʻahaʻa e hoʻoulu ai i ka ʻeha mau.
ʻO wai ka mea kūpono loa e ʻike i kēia maʻi?
ʻOi aku ka maʻamau o ka maʻi May-Turner i nā wahine , a he mea maʻamau nō hoʻi i nā pākeke ma waena o 20 a me 50 mau makahiki .
Akā, ʻo ka mea kupanaha, ʻo ia hoʻi, hoʻokahi o kēlā me kēia ʻelima mau kānaka i loaʻa i kēia maʻi i kapa ʻia ʻo "iliac vein compression." Akā, ʻaʻole i loaʻa i nā kānaka a pau nā hōʻailona. ʻIke wale ka poʻe he nui iā lākou ka maʻi May-Turner ma hope o ka loaʻa ʻana o kahi DVT. A hiki i kēlā manawa, ʻaʻohe o lākou hōʻailona.
Pehea e ʻike ʻia ai ka maʻi May-Turner?
Ma hope o kou haʻi ʻana i kāu kauka e pili ana i kāu mau hōʻailona, e nānā ʻo ia iā ʻoe a e ʻōlelo paha i kekahi mau hoʻokolohua kūikawā e nānā i kou mau kīʻaha koko e hōʻoia i ke kūlana.
| ʻAno hoʻāʻo | Ua wehewehe maʻalahi ʻia |
|---|---|
| ʻO ke kiʻi ʻana o ka ultrasound `(Ultrasound)` | He hoʻāʻo ʻeha ʻole e hoʻohana ana i nā nalu kani e nānā i nā kīʻaha koko i loko o ke kino. ʻO kēia ka hana mua i ka nānā ʻana no ka DVT. |
| Nā scan CT | Ke kiʻi ʻana i nā kiʻi kikoʻī o nā kīʻaha koko me kahi mīkini X-ray kūikawā. |
| Nā Kiʻi MRI (MRI) | Ke loaʻa ʻana o nā kiʻi maopopo loa o nā kīʻaha koko me ka hoʻohana ʻana i nā magnet a me nā nalu lekiō. |
| Venogram | Hoʻokomo ʻia kahi wai kūikawā (contrast dye) i loko o kahi aa koko a hoʻohana ʻia nā kukuna X e nānā i ke kahe o ke koko. Hiki i kēia ke kōkua i ka ʻike pololei ʻana i kahi o ka paʻa ʻana o ke aa koko. |
| Ultrasound Intravascular | He ʻano hana pololei loa kahi e hoʻokomo ʻia ai kahi paipu (catheter) me kahi kāmela liʻiliʻi loa i loko o kahi kīʻaha koko a nānā ʻia ke kīʻaha mai loko mai. |
He aha nā lāʻau lapaʻau no kēia?
ʻO ka pahuhopu nui o ka mālama ʻana no ka maʻi May-Turner, ʻo ia ka hoʻihoʻi ʻana i ke aʻa koko i hoʻopaʻa ʻia i ka maʻamau, hoʻomaikaʻi i ke kahe koko, a hoʻemi i ka pilikia o DVT.
Inā he mau hōʻailona wale nō
ʻO ka maʻamau, no kahi mea ʻaʻohe DVT a loaʻa wale nā hōʻailona e like me ka pehu ʻana o ka wāwae a me ka ʻeha, hiki i ke kauka ke ʻōlelo i nā lāʻau lapaʻau penei:
- ʻO Angioplasty a me ka stenting: Pili kēia i ke kau ʻana i kahi ʻōmole liʻiliʻi me ka piko baluna i loko o ke aʻa a me ka hoʻopiha ʻana i ka baluna ma kahi i haiki ʻia. Wehe kēia i ke aʻa a ʻae i ke koko e kahe. A laila hoʻokomo ʻia kahi mea cylindrical e like me ka mesh i kapa ʻia he stent i loko o ke aʻa e pale aku ai i ka haiki hou ʻana.
- ʻOki kino: I kekahi mau hihia, hiki ke hana ʻia ke ʻoki kino e hoʻoneʻe i ke aʻa i haiki ʻia mai ke aʻa koko. A i ʻole, hiki ke hana ʻia ke ʻoki kino bypass e hana i ala hou no ke kahe ʻana o ke koko a puni ka wahi i haiki ʻia.
Inā hele pū me ka DVT
Inā loaʻa iā ʻoe kahi DVT ma muli o ka maʻi May-Turner, me nā lāʻau lapaʻau i ʻōlelo ʻia ma luna, pono ʻoe e hana i kēia mau mea:
- Nā Anticoagulants: Hāʻawi ʻia kēia mau lāʻau lapaʻau e pale i ke kūkulu ʻana o nā ʻōpū koko a e pale i nā ʻōpū koko e ulu nui ana.
- Lāʻau lapaʻau hoʻoheheʻe koko: I kekahi manawa, hoʻokomo pololei ʻia ka lāʻau lapaʻau i loko o ke koko ma o kahi catheter e hoʻoheheʻe a wehe iā ia.
- Kānana Vena cava: I kekahi manawa, ua kau ʻia kahi mea i kapa ʻia he kānana no kekahi manawa a mau loa paha i loko o kahi aa koko nui i loko o ko mākou kino (inferior vena cava) e pale ai i ka hemo ʻana o ke koko i loko o ka wāwae a hele i nā māmā.
ʻO ka pilikia weliweli loa: Pulmonary Embolism
ʻO ka mea weliweli loa e pili ana i ka maʻi May-Turner ʻo ia ka ulu ʻana o ka DVT. ʻO ka mea ʻoi aku ka weliweli ke haki kahi ʻāpana o kēlā DVT, hele pū me ke koko, a paʻa i loko o kahi kīʻaha koko ma laila. Kāhea mākou i kēia ʻo 'Pulmonary Embolism' .
He pilikia olakino koʻikoʻi loa kēia a hoʻoweliweli i ke ola! Inā loaʻa koke iā ʻoe a i ʻole kekahi āu i ʻike ai kekahi o kēia mau hōʻailona, e lawe koke iā lākou i ka ʻOihana Pilikia o ka haukapila (ETU) .
- Ka paʻakikī koke o ka hanu ʻana (dyspnea)
- ʻEha nui o ka umauma e hoʻonui ana i ka hanu ʻana
- Ke kahe koko me ka mucus
- Nā palpitations o ka puʻuwai (palpitations)
Nā mea hiki iā mākou ke hana e hōʻemi i ka pilikia
ʻAʻohe ala kikoʻī e pale aku ai i ka maʻi May-Turner, ʻoiai ʻaʻole ʻike ʻia kona kumu pololei. Eia nō naʻe, hiki i kēia mau mea ke kōkua i ka mālama ʻana i ke kahe koko maikaʻi a hoʻemi i kou pilikia o nā ʻūpā koko:
- Mai noho ma ke kūlana hoʻokahi no ka manawa lōʻihi. ʻOi loa aku inā he hana noho wale kāu, e ala a hele a puni ma ka liʻiliʻi i hoʻokahi manawa i ka hola.
- E inu i ka wai nui.
- E hoʻoikaika kino mau, ʻoiai hoʻi ka hoʻoikaika kino aerobic.
- Inā loaʻa iā ʻoe nā maʻi ʻē aʻe e like me ka maʻi diabetes a i ʻole ke koko kiʻekiʻe, e kaohi pono iā lākou e like me nā kuhikuhi a kāu kauka.
- Inā ʻoe e puhipaka ana, e hoʻōki koke.
- Inā ʻōlelo ʻia e kāu kauka, e ʻaʻahu i nā kāʻei hoʻopaʻa kūikawā.
Inā he mau nīnau hou aku kāu e pili ana i ka maʻi May-Turner, mai makaʻu e nīnau i kāu kauka. E wehewehe ʻo ia i nā mea āpau iā ʻoe.
Leka Lawe-Home
- ʻO ka maʻi May-Turner kahi kūlana i ʻomi ʻia ai ke aʻa e lawe ana i ke koko i ka wāwae ʻākau a me ke aʻa e lawe ana i ke koko mai ka wāwae hema.
- Hiki i kēia ke kumu e ālai ʻia ai ke kahe o ke koko i ka wāwae hema, e alakaʻi ana i nā hōʻailona e like me ka pehu ʻana o ka wāwae a me ka ʻeha.
- ʻO ka pilikia nui a weliweli loa o kēia kūlana ʻo ia ka hoʻokumu ʻia ʻana o ka deep vein thrombosis (DVT).
- ʻO ka embolism pulmonary (kahi ʻaʻa koko e haki ana mai kahi DVT a noho i loko o nā māmā) he pilikia hoʻoweliweli i ke ola.
- Inā he pehu, ʻeha, a kaumaha paha kou wāwae hema me ka ʻike ʻole ʻia, he mea nui e ʻimi i ke kōkua lapaʻau.
- He kūlana kēia e hiki ke mālama pono ʻia me ka lāʻau lapaʻau.











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