Ke loaʻa nei i kāu pēpē hānau hou kahi ʻōpū paʻa? E kamaʻilio kākou e pili ana i ka Meconium Ileus

Ke hoʻi mai kahi pēpē hānau hou i ka home, hopohopo nā mākua a pau no nā mea liʻiliʻi a pau e pili ana i ka pēpē. He mea nui loa ia e hōʻoia i ka inu ʻana o ka pēpē i ka waiū, ka hiamoe maikaʻi, ka noho mahana ʻana, a me ka ʻōpala pono ʻana o ka pēpē. I kekahi manawa, pilikia iki nā pēpē hānau hou i ka hoʻopuka ʻana i kā lākou ʻōpala mua. ʻO ia ka manawa e kamaʻilio ai mākou e pili ana i kahi kūlana kūikawā i kapa ʻia ʻo Meconium Ileus. Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana i kēia.

He aha ka Meconium Ileus? I ka ʻōlelo maʻalahi...

ʻO ka Meconium Ileus kahi paʻa i loko o ka ʻōpū liʻiliʻi o kāu pēpē hānau hou . ʻO ke kumu nui o kēia ka neʻe mua ʻana o ka ʻōpū o ka pēpē, i kapa ʻia ʻo meconium, he mea mānoanoa a pipili .

I kēia manawa, ke noʻonoʻo nei paha ʻoe i ke ʻano o ka meconium. He mea maʻalahi loa ia. Ke noho kāu pēpē i loko o ka ʻōpū, aia kahi wai e hoʻopuni ana i ka pēpē, a mākou e kapa nei he "wai Amniotic". Moni ka pēpē i kēia "wai Amniotic". No laila, i ka hele ʻana o kēia wai ma loko o nā ʻōpū o ka pēpē, ua komo ka wai i loko o ke kino. ʻO ka mea i koe he mea ʻeleʻele, mānoanoa, a pipili . ʻO ia ka mea i kapa ʻia ai ka meconium. ʻO ka maʻamau, hele kahi pēpē hānau hou i kēia ʻōpala mua, ʻo ia hoʻi ka meconium, ma waena o 24 a me 48 mau hola .

Eia nō naʻe, i kekahi manawa inā lilo kēia meconium i mānoanoa loa, e like me ke kēpau, hiki ke paʻa i ka ʻāpana hope loa o ka ʻōpū liʻiliʻi o ka pēpē, ʻo ia hoʻi ka ileum. Ua like ia me kahi paipu wai i paʻa i loko o ko mākou hale. He aha ka mea e hana ai? Hoʻomaka ka ʻōpū liʻiliʻi ma luna o ka mea i paʻa ʻia e hoʻonui, me he mea lā ua piha i ka wai. ʻO ka hopena, hoʻomaka ka ʻōpū o ka pēpē e pehu. ʻOi aku ka haiki o ka ʻōpū nui ma lalo o ka mea i paʻa ʻia ma mua o ka maʻamau.

E noʻonoʻo i ka mea e hana ʻia ke paʻa ka lua i ka nui o ka pepa lua? Piha ka wai a me ka ʻōpala, akā ʻaʻohe mea e hele ana ma o nā paipu, ʻeā? ʻO ia ka mea e hana ʻia ma ʻaneʻi.

Aia kekahi mau ʻano like ʻole o kēia?

ʻAe, hiki ke hoʻokaʻawale ʻia ka Meconium Ileus i ʻelua mau ʻano nui:

1. ʻIleus Meconium maʻalahi: Ma kēia, ua paʻa wale ka meconium o ke pēpē i ka ileum a me ka ʻōpū liʻiliʻi. Akā, ʻaʻohe pilikia koʻikoʻi ʻē aʻe e kū mai ana.

2. ʻO ka Ileus Meconium Paʻakikī: He ʻoi aku ka koʻikoʻi o kēia. Hōʻiliʻili ka Meconium i loko o nā ʻōpū, e hana ana i ke kaomi nui a me ka pehu. Hiki i kēia ke alakaʻi i nā pilikia koʻikoʻi. E nānā kākou i ke ʻano o lākou:

• Malrotation: ʻO ke ʻano kēia, ʻaʻole i hana pono ʻia nā ʻōpū o ka pēpē. I kekahi manawa hiki i nā ʻōpū ke wili a puni iā ​​​​lākou iho, ka mea i kapa ʻia ʻo prenatal volvulus. He mea weliweli loa kēia no ka mea hiki ke ʻoki i ke kahe koko i nā ʻōpū.
• ʻO ka atresia ʻōpū:E like me ka mea i ʻōlelo ʻia ma mua, inā e wili ka ʻōpū a ʻoki ʻia ke kahe koko i kēlā wahi, ʻaʻole paha e ulu pono kekahi mau ʻāpana o ka ʻōpū.
• ʻO ka puka ʻana o ka ʻōpū: He kūlana weliweli loa kēia. Hiki i kahi lua i loko o ka ʻōpū ke hoʻoheheʻe i ka meconium i loko o ka lua ʻōpū o ka pēpē. Inā hana ʻia kēia puka ma hope o ka hānau ʻana o ke pēpē, hiki i ka meconium ke kahe a hoʻoulu i nā maʻi koʻikoʻi, ka haʻalulu, a me ka make.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?

Hoʻopili pinepine ʻia ka Meconium Ileus me ka maʻi genetic cystic fibrosis. ʻO ka ʻoiaʻiʻo, ma waena o 10% a me 20% o nā keiki me ka cystic fibrosis e ʻike i ka meconium ileus ma ke ʻano he hōʻailona mua o ka maʻi. Ua hōʻike kekahi mau noiʻi a hiki i ka 90% o nā pēpē me ka meconium ileus hiki ke loaʻa i ka cystic fibrosis.

No ke aha e hana ʻia ai kēia? He aha nā kumu o ka Meconium Ileus?

E like me ka mea i ʻōlelo ʻia ma mua, ʻo Meconium Ileus ka hōʻailona mua o ka cystic fibrosis. He maʻi hoʻoilina ka Cystic fibrosis . ʻO kēia ka wā e lilo ai nā mea huna (ʻo ia hoʻi nā wai) i loko o nā ʻōpū o kahi pēpē i mānoanoa a pipili. Hoʻopili kēia mau mea huna mānoanoa i ka uhi o nā ʻōpū, e hana ana i nā ālai. No laila, inā loaʻa i kāu pēpē ka Meconium Ileus, hiki iā ia ke loaʻa nā hōʻailona ʻē aʻe o ka cystic fibrosis ma hope o ke ola.

He aha nā hōʻailona o kēia? Pehea ʻoe e ʻike ai?

Inā ʻaʻole i loaʻa i kāu pēpē hānau hou ko lākou neʻe ʻana o ka ʻōpū mua i loko o 24 a 48 mau hola, he hōʻailona paha ia o ka meconium ileus. E nānā pū i kēia mau hōʻailona:

• Ka luaʻi ʻana
• Pehu ʻōpū: Hiki i kēia pehu ke paʻakikī i ka pēpē ke hanu.
• I kekahi manawa, ke paʻi ke kauka i ka ʻōpū o kahi pēpē, loaʻa paha iā lākou nā ʻāpana o ka ʻōpū liʻiliʻi i hoʻonui ʻia.

Inā ua lilo nā ʻōpū o kāu pēpē i perforated (perforated), hiki iā lākou ke hōʻike i nā hōʻailona e like me:

• ʻUlaʻula o ka ʻili ma ka ʻōpū.
• Ke ʻike nei i kahi ʻano ʻūlū a ʻeha paha i ka wā e pā ai i ka ʻōpū.
• Kuni.
• Pūʻiwa.

Pehea e ʻike ai nā kauka i kēia? (Diagnosis)

I kekahi manawa, hiki ke ʻike ʻia ka meconium ileus ma mua o ka hānau ʻana o ka pēpē. Hiki i kahi ultrasound prenatal o ka ʻōpū o ka makuahine ke hōʻike i nā hōʻailona o kahi ālai ʻana o ka ʻōpū .

Eia nō naʻe, ʻike pinepine ʻia ma hope o ka hānau ʻana o ka pēpē. Manaʻo nā kauka i kēia ma muli o nā hōʻailona a ka pēpē e hōʻike nei. ʻOi aku hoʻi i nā hihia e like me kēia, nānā nui lākou i ka Meconium Ileus:

• Kekahi o kou ʻohanaInā loaʻa iā ʻoe ka cystic fibrosis.
• Inā ua hōʻoia ʻia he cystic fibrosis ka pēpē hānau hou ma o nā hoʻokolohua nānā ʻana i nā keiki hānau hou.

He aha nā ʻano hoʻokolohua i hana ʻia no kēia?

Inā kānalua ke kauka i ka meconium ileus, hiki iā lākou ke hana i nā hoʻokolohua aʻe:

• ʻŌpū X-ray: Hōʻike kēia i nā ʻāpana i hoʻonui ʻia o ka ʻōpū liʻiliʻi. I kekahi manawa hiki i ka meconium ke hui pū me ka ea a ka pēpē e moni ai, e hāʻawi ana i ka X-ray i kahi ʻano "pōpō kopa" . Inā he poloka piha, ʻaʻohe ea i loko o ka rectum o ka pēpē.
• ʻEnema hoʻohālikelike: Pili kēia i ke kau ʻana i kahi wai kūikawā e ʻike ʻia ma kahi X-ray i loko o ka anus o ke pēpē. Hiki i kēia ke kōkua i ka ʻike ʻana inā ʻoi aku ka haiki o ka ʻōpū nui o ke pēpē ma mua o ka maʻamau. Hiki iā ia ke kōkua i ka ʻike ʻana inā he kūlana ʻē o ka ʻōpū (malrotation). Inā kānalua ʻia ka malrotation, e kauoha nā kauka i kahi moʻo gastrointestinal kiʻekiʻe (UGI) . Hiki i kēia UGI ke hōʻoia i ka malrotation a ʻike pololei i kahi i wili ʻia ai ka ʻōpū.
• Hoʻāʻo hou: Hana ʻia kēia e hōʻoia inā he cystic fibrosis kou a ʻaʻole paha.

He aha nā lāʻau lapaʻau no kēia?

Inā he meconium ileus paʻakikī ko ka pēpē (ʻo ia hoʻi, ua wili ʻia a puka paha ka ʻōpū), e pono koke ʻia ke ʻoki kino.

Akā inā he ileus meconium maʻalahi ka pēpē, e hoʻāʻo mua nā kauka e hoʻomaʻemaʻe i ka mea paʻa me kahi enema. Hoʻoheheʻe kēia enema i ka meconium mānoanoa a hoʻohui i kahi lāʻau kūikawā e palupalu ai. Hiki i kēia hopena enema ke kōkua i ka meconium e hele ma waena o nā ʻōpū o ka pēpē a puka i waho ma o ka anus.

E hoʻokomo mālie nā kauka i kēia hopena ma o kahi catheter i hoʻokomo ʻia i loko o ka rectum o ka pēpē. Ke hana lākou i kēia, hoʻohana lākou i kahi ʻano hana kiʻi lapaʻau kūikawā i kapa ʻia ʻo fluoroscopy . ʻO ka Fluoroscopy e pili ana i ka hoʻouna ʻana i nā kukuna X ma ke kino o ka pēpē a me ka nānā ʻana i kahi wikiō ola o nā ʻiʻo i loko.

Inā ʻaʻole hiki i ka enema ke wehe i ka mea i ālai ʻia, pono nā kauka e hana i ke ʻoki ʻana.

ʻO ke ʻoki kino e pili ana i ka ʻoki ʻana i nā ʻōpū o ka pēpē a me ka wehe ʻana i ka meconium i loko. Ma muli o ke kūlana o ka pēpē, i kekahi manawa hiki ke hana ʻia kahi ileostomy, kahi e lawe ʻia ai nā wēlau ʻelua o nā ʻōpū i ʻoki ʻia ma o ka ʻili o ka ʻōpū. A laila, hāʻawi ʻia nā enemas hou aʻe ma o nā wēlau i wehe ʻia a hoʻomau ʻia ka mālama ʻana a hiki i ka wehe ʻia ʻana o ka meconium āpau. A laila, hana ʻia kekahi ʻoki kino e hoʻopili hou i nā wēlau ʻelua o nā ʻōpū.

Aia kekahi ala e pale aku ai i kēia mai ka hiki ʻana mai i kā mākou pēpē?

ʻOiaʻiʻo, ʻaʻohe ala e pale aku ai i kēia maʻi i kapa ʻia ʻo Meconium Ileus. No ka mea, ʻo ke kumu nui o kēia, ʻo ia ka maʻi genetic i kapa ʻia ʻo Cystic Fibrosis. He mea ia i hoʻoili ʻia mai kēlā hanauna a i kēia hanauna.

Inā hāpai ʻoe a i ʻole e hoʻolālā ana e hāpai, makemake paha ʻoe e noʻonoʻo i ka nānā ʻana i ka mea lawe cystic fibrosis prenatal . Hiki i kēia hoʻāʻo ke kōkua iā ʻoe e hoʻomaopopo i kou pilikia o ka loaʻa ʻana o kahi keiki me ka cystic fibrosis.

Inā hana kēia i ka pēpē, pehea lā ka wā e hiki mai ana? (Kūpono ʻole)

I ke ʻano o ka Meconium Ileus, ʻoiai i nā hihia paʻakikī, inā ʻike mua ʻia ka maʻi a mālama pono ʻia, maikaʻi ka wā e hiki mai ana o ka pēpē.

ʻO ka Meconium Ileus pinepine kahi hōʻailona o ka cystic fibrosis. Eia nō naʻe, inā ʻike ʻia a mālama ʻia i ka wā mua, hiki ke mālama ʻia ka hana māmā o ka pēpē, ka meaʻai, a me ka pilikia o ka maʻi i kahi pae maikaʻi i ka wā lōʻihi. Eia nō naʻe, inā waiho ʻole ʻia ka meconium ileus me ka mālama ʻole ʻia, hiki i ke kūlana o ka pēpē ke ʻoi aku ka ʻino. No laila, inā manaʻo ʻoe he meconium ileus kāu pēpē, he mea nui loa ia e ʻimi koke i ka lāʻau lapaʻau.

He mea maʻamau ka makaʻu a me ka huikau ke lohe ʻoe ua loaʻa i kāu pēpē ka Meconium Ileus. Akā e hoʻomanaʻo, e like me nā maʻi he nui, hiki i ka ʻike mua ʻana a me ka mālama ʻana ke alakaʻi i nā hopena holomua. ʻOiai ʻo Meconium Ileus kahi hōʻailona o Cystic Fibrosis, e hoʻomanaʻo he maʻi hiki ke mālama ʻia ka Cystic Fibrosis. E kamaʻilio me ke kauka o kāu pēpē e pili ana i nā hopohopo a i ʻole nā ​​nīnau āu e loaʻa ai. E hiki iā lākou ke kōkua iā ʻoe a hāʻawi i kāu pēpē i ka hopena maikaʻi loa.

Nā mea nui a mākou e hoʻomanaʻo ai (Leka Lawe-Home)

• Inā ʻaʻole i pau ka ʻōpū mua o kāu pēpē hānau hou (meconium) i loko o 48 mau hola, ua pehu ka ʻōpū, a i ʻole e luaʻi ana, e ʻike koke i ke kauka.
• Hoʻohui pinepine ʻia ka Meconium ileus me ka maʻi genetic cystic fibrosis.
• ʻO ka ʻike mua ʻana a me ka mālama ʻana i ka maʻi hiki ke hāʻawi i ka pēpē i kahi ho'ōla maikaʻi a me kahi wā e hiki mai ana.
• Aia nā enemas a me ke ʻoki kino ma ke ʻano he mau ʻano lapaʻau.
• ʻOiai ʻaʻole hiki ke pale ʻia kēia maʻi, e makaʻala i ka hoʻāʻo ʻana i ka genetic prenatal .
• E kamaʻilio ākea me ke kauka o kāu pēpē e pili ana i nā nīnau a hopohopo paha āu e loaʻa ai. Ua mākaukau lākou e kōkua iā ʻoe a me kāu pēpē.

`Meconium Ileus, Hānau Hou, Pale ʻŌpū, Cystic Fibrosis, Noho Mua o ka Pēpē, Ola Kino o ka Pēpē