Aia kekahi mau maʻi, kahi e pono ai ke hoʻohana ʻia nā ʻano lāʻau lapaʻau kikoʻī loa. No laila, inā ua kuhikuhi ʻia ʻoe i kēlā ʻano lāʻau lapaʻau, he mea nui loa ia e ʻike pono e pili ana i ia mea. ʻO Mitapivat kekahi o ia mau lāʻau lapaʻau kūikawā. Ma kēia ʻatikala i kēia lā, e kamaʻilio mākou e pili ana i kēia lāʻau lapaʻau i kapa ʻia ʻo Mitapivat, me he mea lā e kamaʻilio ana mākou me kahi hoaaloha.
He aha ke ʻano o ka lāʻau lapaʻau ʻo Mitapivat?
I ka ʻōlelo maʻalahi, aia i loko o ko kākou koko nā hunaola koko ʻulaʻula. ʻO kēia nā hunaola e lawe ana i ka oxygen ma ke kino holoʻokoʻa. Hānau ʻia kekahi poʻe me kahi maʻi genetic e hoʻoulu ai i ka nele o kahi enzyme i kapa ʻia ʻo 'Pyruvate Kinase'. Ke haʻahaʻa kēia enzyme, haki nā hunaola koko ʻulaʻula i ka wā mua a luku ʻia. Ua kapa ʻia kēia maʻi ʻo 'hemolytic anemia' , ʻo ia hoʻi ka anemia i hoʻokumu ʻia e ka haki ʻana o nā hunaola koko ʻulaʻula.
No laila, ʻo ka hana a kēia lāʻau lapaʻau i kapa ʻia ʻo Mitapivat, ʻo ia ke kāohi ʻana i kēlā mau hunaola koko ʻulaʻula mai ka haki koke ʻana. Loaʻa pū ia ma lalo o ka inoa inoa ʻo 'PYRUKYND'. Hoʻoulu kēia lāʻau lapaʻau i ka hana o kēlā enzyme a hoʻonui i ke ola o nā hunaola koko ʻulaʻula. No laila, ua kāohi ʻia ka anemia.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i ka lāʻau lapaʻau
Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui e hoʻomaopopo i kāu kauka e pili ana i kekahi mau ʻoiaʻiʻo e pili ana i kou kūlana olakino. A laila hiki iā ʻoe ke hoʻoholo pono inā kūpono ia iā ʻoe a pehea e hāʻawi ai.
| Ke kūlana āu e pono ai e hōʻike | No ke aha mai kēlā? (Koʻikoʻi) |
|---|---|
| Maʻi akepaʻa | Hoʻomaʻemaʻe ʻia kēia lāʻau lapaʻau mai ke kino ma o ke akepaʻa, no laila inā he maʻi kou, pono paha e hoʻoponopono ʻia kāu dosage. |
| Nā maʻi ʻaleka | Inā loaʻa iā ʻoe kahi maʻi allergy ʻaʻole wale i kēia lāʻau Mitapivat, akā i kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, a i ʻole kala, e ʻoluʻolu e haʻi mai iā mākou e pili ana. |
| Ke hāpai nei a ke hoʻolālā nei paha e hāpai | Inā hāpai ʻoe a i ʻole e hoʻolālā ana e loaʻa kahi pēpē, pono ʻoe e kamaʻilio me kāu kauka e pili ana i ka hopena o kēia lāʻau lapaʻau i ka pēpē. |
| Inā he makuahine hānai ʻoe | E ʻike inā hiki i ka lāʻau lapaʻau ke hele i ka pēpē ma o ka waiū umauma, a e hoʻomaopopo i kāu kauka inā he makuahine hānai ʻoe. |
Pehea e pono ai iaʻu ke hoʻohana i ka lāʻau lapaʻau?
He pila kēia e lawe ʻia ma ka waha. He mea nui loa e lawe i ka nui like me ke kauoha a kāu kauka.
- E lawe i ka manawa kūpono: I nā manawa hiki, e ho'āʻo e lawe i kāu lāʻau lapaʻau i ka manawa like i kēlā me kēia lā . E kōkua kēia i ka mālama ʻana i nā pae o ka lāʻau lapaʻau i loko o kou kino i kūlike.
- ʻAi ʻia: ʻO kēia ka mea nui loa. Mai uhaʻi, kuʻi, a nau paha i ka papa. E ale holoʻokoʻa i ka papa me kahi aniani wai.
- Mai ho'ōki: Mai ho'ōki i ka lawe ʻana i kāu lāʻau lapaʻau a hiki i ka wā e ʻōlelo aku ai kāu kauka iā ʻoe. He mea nui e hoʻomau i ka lawe ʻana i kāu lāʻau lapaʻau, ʻoiai inā ua maikaʻi kou manaʻo.
- Inā hāʻawi ʻia i nā keiki: Inā hāʻawi ʻia kēia lāʻau lapaʻau i nā keiki, pono paha ka mālama kūikawā. E hahai pono i nā ʻōlelo a ke kauka.
Hoʻolohe: Overdose
Inā manaʻo ʻoe ua lawe ʻoe i kahi overdose, mai hopohopo a kāhea koke aku i ke Kikowaena ʻIke Poisons National ma ka Halemai Lahui ʻo Colombo. A i ʻole e hele i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa. He mea nui loa kēia.
A e hoʻomanaʻo, ua kuhikuhi ʻia kēia lāʻau lapaʻau nou wale nō. Mai kaʻana like me kekahi.
He aha kāu e hana ai inā e poina ʻoe i kahi mahele o ka lāʻau lapaʻau?
ʻO ka poina ʻana i ka lawe ʻana i kahi mahele lāʻau lapaʻau he mea ia e hiki ke hana i kekahi. Inā hana ʻoe, e lawe koke iā ia i kou hoʻomanaʻo ʻana. Eia nō naʻe, inā ʻoi aku ma mua o 4 mau hola ma hope o ka manawa āu e lawe mau ai, e kāpae i ka mahele i hala. E lawe i ka mahele aʻe i ka manawa i hoʻonohonoho ʻia. Mai lawe i ʻelua mau mahele i ka manawa hoʻokahi e hoʻopiha ai i kahi mahele i poina.
Nā lāʻau lapaʻau ʻē aʻe e launa pū me kēia lāʻau lapaʻau
Hiki i ka Mitapivat ke launa pū me nā lāʻau lapaʻau ʻē aʻe āu e lawe nei, hiki ke hōʻemi i ka pono o kēia lāʻau lapaʻau a hoʻonui paha i nā hopena ʻaoʻao.
| ʻAno lāʻau lapaʻau | Nā Laʻana |
|---|---|
| Nā lāʻau hoʻomalu hānau | Nā lāʻau hoʻomalu hānau |
| Kekahi mau fungicides | ʻO Fluconazole, Itraconazole, Ketoconazole |
| Nā lāʻau lapaʻau no ka maʻi HIV | Efavirenz |
| Lāʻau hoʻomaha/lāʻau hiamoe | Midazolam |
| ʻO kekahi mau lāʻau lapaʻau no ka maʻi puʻupuʻu | ʻO Rifampin |
ʻAʻole kēia he papa inoa piha. No laila, e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau , nā syrup, nā mea kanu, nā huaora, a me nā mea hoʻohui āu e lawe nei. He mea nui hoʻi e haʻi i kāu kauka inā ʻoe e puhipaka a inu waiʻona paha.
He aha nā hopena ʻaoʻao e hiki mai ana?
E like me nā lāʻau lapaʻau āpau, hiki i kēia ke loaʻa kekahi mau hopena ʻaoʻao. He koʻikoʻi kekahi, he mea maʻamau kekahi.
| 🚨 Nā hopena ʻaoʻao e pono e hōʻike koke ʻia i ke kauka | |
|---|---|
| Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, nā maka, nā lehelehe, ke alelo a i ʻole ka puʻu, paʻakikī ke hanu. |
| ✅ E haʻi i kāu kauka inā hoʻomau a hoʻopilikia paha | |
| ʻEha hope | ʻEha hope |
| ʻEha hui | ʻEha hui |
Inā loaʻa iā ʻoe kekahi mau hōʻailona ʻē aʻe i ʻōlelo ʻole ʻia ma kēia papa inoa, e ʻoluʻolu e kelepona i kāu kauka no ka ʻōlelo aʻo.
Pehea e mālama ai i ka lāʻau lapaʻau?
- E mālama ʻia mai nā keiki: E mālama mau i nā lāʻau lapaʻau mai ka hiki ʻana aku o nā keiki a me nā holoholona.
- Mahana: E mālama ma ka mahana o ka lumi (ma waena o 20-25 kekelē Celsius). E pale mai ka wela nui a i ʻole ka makū.
- Pahu kumu: ʻOi aku ka maikaʻi o ka mālama ʻana i ka lāʻau lapaʻau i loko o ka ʻōmole kumu i loaʻa ai.
- Nā lāʻau lapaʻau i pau: Mai hoʻohana i nā lāʻau lapaʻau ma hope o ka lā pau. E hoʻolei pono i nā lāʻau lapaʻau i pau a i ʻole nā lāʻau lapaʻau i makemake ʻole ʻia. Loaʻa paha i kekahi mau hale kūʻai lāʻau lapaʻau haukapila nā papahana e ʻae i nā lāʻau lapaʻau kahiko. A i ʻole, e lawe i nā pila mai loko mai o ka ʻōmole, e kāwili iā lākou me kahi mea e like me ke kope kope i hoʻohana ʻia a i ʻole ka lepo, e hoʻokomo iā lākou i loko o kahi ʻeke i hoʻopaʻa pono ʻia, a e hoʻolei iā lākou i loko o ka ʻōpala. Mai hoʻolei i nā lāʻau lapaʻau i loko o ka lua no kekahi kumu.
Leka Lawe-Home
- He lāʻau lapaʻau kūikawā ʻo Mitapivat no ka anemia i hoʻokumu ʻia e ka hemahema o Pyruvate Kinase. E lawe i ka nui i kuhikuhi ʻia e like me ke kauoha a kāu kauka.
- Mai uhaʻi, wili, a nau paha i ka papa. E ale holoʻokoʻa.
- E hōʻoia e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei, nā huaora, a me nā kūlana olakino āu e lawe nei.
- Inā ʻoe e hala i kahi mahele lāʻau ma mua o 4 mau hola, e hōʻalo i kēlā mahele lāʻau a lawe i ka mahele lāʻau aʻe i ka manawa i hoʻonohonoho ʻia. Mai pāpālua i ka mahele lāʻau.
- Inā manaʻo ʻoe ua nui ka overdose, e hele koke i ka National Poisons Information Center a i ʻole ka haukapila kokoke loa ʻo ETU.
- Inā loaʻa koke iā ʻoe nā hōʻailona maʻi ʻaleka (pehu ʻana o ka maka, paʻakikī ka hanu ʻana), e ʻimi koke i ke kōkua lapaʻau.











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