Ke paʻakikī nei ʻoe i kekahi manawa ke ala aʻe mai kahi noho, piʻi i nā alapiʻi, a i ʻole e hana i nā hana maʻalahi e like me ke kāhili ʻana i kou lauoho? Ke manaʻo nei anei kou mau ʻiʻo he nāwaliwali a make? ʻO ke kumu o kēia ʻano he ʻano i kapa ʻia ʻo myopathy. He mea hou paha kēia inoa iā ʻoe. Akā, mai hopohopo, e kamaʻilio mākou e pili ana i nā mea āpau ma ke ʻano maʻalahi e hiki ai iā ʻoe ke hoʻomaopopo.
He aha maoli ka Myopathy?
I ka ʻōlelo maʻalahi, ʻo ka myopathy kahi huaʻōlelo maʻamau no ka hoʻonāwaliwali ʻana o ko kākou mau ʻiʻo iwi , nā ʻiʻo e pili ana i ko kākou mau iwi a hoʻoneʻe iā kākou. E noʻonoʻo i ko kākou kino e like me ke kaʻa. Hoʻohana ʻia kēia kaʻa e kahi ʻenekini i kapa ʻia ʻo muscle. ʻO ka myopathy kahi kūlana kahi i hōʻino ʻia ai nā olonā ʻiʻo i loko o kēia mau ʻiʻo, e hōʻemi ana i ka mana o kēlā ʻenekini. ʻAʻole kēia he maʻi hoʻokahi, akā he hui o nā maʻi.
Aia kekahi mau ʻano nui o ka myopathy?
ʻAe, hiki ke hoʻokaʻawale ʻia ka myopathy i ʻelua ʻano nui. Ua like ia me kekahi mau pilikia a mākou e hoʻoilina ai mai ka hānau ʻana a me kekahi mau pilikia e ulu aʻe i ko mākou ola ʻana.
| ʻAno Myopathy | I ka ʻōlelo maʻalahi... |
|---|---|
| Nā Myopathies i hoʻoilina ʻia | He mau kūlana kēia i hoʻokumu ʻia e kahi kīnā hoʻoilina. ʻO ia hoʻi, nā maʻi i hoʻokumu ʻia e kahi gene kīnā i hoʻoilina ʻia mai ka makuahine a i ʻole ka makuakāne. |
| Nā Myopathies i loaʻa | Hoʻokumu ʻia kēia e kekahi maʻi ʻē aʻe, maʻi, lāʻau lapaʻau i lawe ʻia, a i ʻole kekahi kumu waho ʻē aʻe i ke ola. |
I kēia manawa, e nānā kākou i kēia mau ʻano me nā kikoʻī hou aku.
Nā Myopathies i hoʻoilina ʻia
Hoʻokumu ʻia kēia e nā kumu genetic, no laila he pinepine lākou i ka hoʻoilina.
- Nā Myopathies hānau ʻia:He mau kūlana kēia e kū nei i ka wā hānau. Hiki i kekahi mau keiki ke hōʻike koke i nā hōʻailona. Akā no kekahi poʻe, hiki ke ulu aʻe nā hōʻailona ma hope o ke ola a i ʻole ma hope o ke ola. ʻO ka mea kūikawā e pili ana i kēia kūlana, ʻo ia ka nāwaliwali e hoʻopilikia i ka aneane o nā ʻiʻo āpau o ke kino, a ʻoi aku ka ʻino i ka hala ʻana o ka manawa.
- Nā Mitochondrial Myopathies: I ka ʻōlelo maʻalahi, ʻo mitochondria nā pila e hoʻoikaika i kā mākou mau cell. Ke hana hewa kēia mau pila, ʻaʻole loaʻa i nā ʻiʻo ka ikehu e pono ai lākou, a nāwaliwali lākou. Hiki i kēia kūlana ke hoʻopilikia ʻaʻole wale i nā ʻiʻo, akā i nā ʻōpū ʻē aʻe e pono ai ka nui o ka ikehu, e like me ka puʻuwai, ka lolo, a me ka ʻōnaehana hoʻoheheʻe.
- Nā Myopathies Metabolic: Pono ko kākou mau ʻiʻo i nā kemika kūikawā i kapa ʻia he enzymes e hana pono ai. Hoʻokumu ʻia kēia kūlana e kahi kīnā i loko o nā genes e hana ai i kēia mau enzymes. I kēia hihia, hiki ke loaʻa ka ʻeha nui a me ka ʻūlū ʻana o nā ʻiʻo, ʻoiai ma nā wahi e like me nā poʻohiwi a me nā ʻūhā, i ka wā e hoʻoikaika kino ai. I kekahi manawa, hiki ke loaʻa kahi kūlana koʻikoʻi i kapa ʻia ʻo "Rhabdomyolysis", kahi e haki ai nā olonā ʻiʻo.
- Nā Dystrophies Muscular: Ua lohe paha ʻoe i kēia inoa ma mua. He ʻano kēia e emi mālie ai nā ʻiʻo a nāwaliwali ma muli o ka nele o ka hana ʻana o nā protein e pono ai e mālama i ke ʻano o nā ʻiʻo. Hiki i kēia ke hoʻopilikia i nā ʻiʻo o nā lima, nā wāwae, a i kekahi manawa ke alo a me nā maka.
Nā Myopathies i loaʻa
ʻAʻole kēia nā mea i hānau ʻia me ʻoe. He mau kūlana ia e kū mai ana ma muli o nā kumu like ʻole i kou wā e ola ai.
| Kumu | Nā Laʻana a me nā Kikoʻī |
|---|---|
| Nā pilikia o ka ʻōnaehana pale (Autoimmune/Inflammatory) | Nā kūlana e kū mai ana i ka wā e hoʻouka hewa ai ka ʻōnaehana pale o ko mākou kino (ʻōnaehana pale) i kona mau ʻiʻo ponoʻī. |
| Nā mea ʻawahia a lāʻau lapaʻau paha (Toxic Myopathy) | Hiki i kekahi mau mea ke hōʻino i nā ʻiʻo. ʻO nā laʻana e komo pū me ka inu nui ʻana i ka waiʻona, ka hanu ʻana i ka uahi mai kekahi mau ʻano pena, a me kekahi mau lāʻau lapaʻau (e.g., kekahi mau lāʻau hoʻohaʻahaʻa cholesterol (statins), steroids (corticosteroids), a me kekahi mau lāʻau i hoʻohana ʻia e mālama i ka maʻi HIV). |
| Nā pilikia Hormonal (Endocrine Myopathies) | Hiki ke hoʻonāwaliwali ʻia nā ʻiʻo e nā hormonal i loko o ke kino. ʻO nā laʻana e komo pū me ka thyroid hana ʻole (hypothyroidism) a i ʻole ka thyroid hana nui (hyperthyroidism), nā pilikia hormone parathyroid, a me nā maʻi adrenal gland. |
| Nā maʻi maʻi (Infectious Myopathies) | Hiki i nā maʻi like ʻole ke hoʻopilikia i nā ʻiʻo. ʻO nā laʻana: HIV, nā virus e like me ka influenza, nā maʻi bacteria, a me nā maʻi parasitic. |
| Ke kaulike ʻole o ka electrolyte | ʻO ka emi ʻana a i ʻole ka piʻi ʻana o nā pae electrolytes koʻikoʻi e like me ka potassium a me ka magnesium i loko o ke kino e hoʻopilikia i ka hana ʻiʻo. |
| ʻO ka Myopathy maʻi koʻikoʻi | Ka nāwaliwali o nā ʻiʻo ma muli o ka maʻi nui ʻana ma kahi e like me ka lumi mālama koʻikoʻi (ICU), ka noho ʻana ma kahi moe no ka manawa lōʻihi, a me kekahi o nā lāʻau lapaʻau ikaika i hāʻawi ʻia i kēlā manawa. |
He aha nā hōʻailona o ka myopathy?
ʻOiai he nui nā ʻano o ka myopathy, aia kekahi mau hōʻailona maʻamau e ʻike ʻia ma aneane o lākou āpau.
- Nāwaliwali o nā ʻiʻo: Nāwaliwali, ʻoiai ma nā ʻiʻo kokoke i ka ʻāpana waena o ke kino (nā poʻohiwi, nā lima o luna, nā pūhaka, a me nā ʻūhā).
- ʻŌwiliwili ʻia nā ʻiʻo, ka ʻoʻoleʻa, a me ka ʻeha.
- Manaʻo nui i ka luhi ma hope o ka hana ʻana i kahi hana liʻiliʻi.
- Ka nele o ka ikehu.
Hoʻopilikia like kēia nāwaliwali i nā ʻaoʻao ʻelua o ke kino, ʻo ia hoʻi, ua like ka nāwaliwali o ka lima hema me ka lima ʻākau.
Pehea kou manaʻo no kēia nāwaliwali?
Hiki i kēia nāwaliwali o nā ʻiʻo ke hoʻolilo iā ia i mea paʻakikī e hana i nā hana o kēlā me kēia lā. E noʻonoʻo wale...
- ʻOiai nā hana maʻalahi e like me ke kāhili ʻana i kou lauoho, ke komo ʻana i nā lole, a me ka ʻauʻau ʻana, ua paʻakikī nō hoʻi.
- He mea paʻakikī ke ala aʻe mai kahi noho e noho ana.
- Lilo ka piʻi ʻana i nā alapiʻi i mea luhi loa.
- He mea paʻakikī ke hāpai i kou lima e kiʻi i kahi mea mai kahi papa ma luna o kou poʻo.
- Ke luhi iki au, manaʻo wau he pilikia koʻu hanu ʻana.
Ma waho aʻe o kēia, hiki ke ʻike ʻia nā hōʻailona kikoʻī ʻē aʻe ma muli o ke ʻano o ka myopathy. No ka laʻana, hiki i kekahi mau keiki ke lohi i ka hoʻomaka ʻana e hele a lele. ʻAʻole hiki iā lākou ke holo a lele paha i ka wā e pāʻani ana me ko lākou mau hoa. Hiki i kekahi ke paʻakikī i ka moni ʻana a me ka slurring i kā lākou mau ʻōlelo i ka wā e ʻōlelo ana.
Pehea e ʻike ai inā loaʻa iaʻu kēia maʻi?
Inā loaʻa iā ʻoe kēia mau hōʻailona, ʻo ka mea nui e hana ai, ʻo ia ke ʻike i kāu kauka ʻohana. E lawe ʻo ia i kahi mōʻaukala piha o kāu mau hōʻailona, kou mōʻaukala olakino ʻohana, a me nā lāʻau lapaʻau āu e lawe nei. A laila e hana lākou i kahi hoʻokolokolo kino a, inā pono, e kuhikuhi iā ʻoe i kahi loea, e like me ke kauka neurologist a i ʻole rheumatologist.
Hiki ke hana ʻia kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
| Hoʻāʻo | He aha ka mea e nānā ai kēia? (He aha ka mea e nānā ai?) |
|---|---|
| Nā hoʻāʻo koko | Nānā ʻia nā enzymes i hoʻokuʻu ʻia i loko o ke koko i ka wā e hōʻino ʻia ai nā ʻiʻo (e.g., Creatine Kinase (CK)), nā pae lawai, nā pae hormone, a me nā māka o nā pilikia o ka ʻōnaehana pale. |
| Hoʻāʻo EMG (Electromyography) | He hoʻāʻo kūikawā e hoʻouna ana i nā hōʻailona uila maalea i nā ʻiʻo a me nā aʻalolo e ana i kā lākou hana a me ka nui o ka pōʻino. |
| ʻIke MRI (Kiʻi Resonance Magnetic) | Hiki ke ʻike maopopo ʻia ke ʻano o nā ʻiʻo a me nā loli i hana ʻia i loko o lākou. |
| Nā Hoʻāʻo Genetic | Inā he kānalua no ka myopathy congenital, hana ʻia kēia hoʻāʻo e hōʻoia inā he mau kīnā genetic e pili ana me ia. |
| ʻO ka Biopsy ʻiʻo | Hoʻopau ʻia kahi ʻāpana liʻiliʻi o kahi puʻupuʻu kānalua me ke ʻoki ʻana a nānā ʻia ma lalo o kahi microscope e ʻike pololei ai i ka maʻi. |
He aha nā lāʻau lapaʻau no ka myopathy?
Aia ka lāʻau lapaʻau i ke ʻano o ka myopathy āu e loaʻa ai. ʻAʻohe lāʻau lapaʻau hoʻokahi e kūpono i nā mea āpau.
- Lapaʻau Laulā: He mea nui ka hoʻōla kino a me ka hoʻōla hana no nā maʻi myopathic he nui. Hiki i kēia mau mea ke kōkua i ka mālama ʻana i ka ikaika a me ka maʻalahi o nā ʻiʻo a kōkua iā ʻoe e hana maʻalahi i nā hana o kēlā me kēia lā.
- No nā pilikia o ka ʻōnaehana pale: Hāʻawi ʻia nā lāʻau lapaʻau e kāohi ana i ka ʻōnaehana pale, e like me nā immunosuppressants a me nā corticosteroids.
- No nā myopathies hānau ʻole: ʻAʻohe lāʻau lapaʻau paʻa no ka hapa nui o kēia mau maʻi. Eia nō naʻe, hiki ke hoʻomalu ʻia nā hōʻailona a hoʻomaikaʻi ʻia ke ʻano o ke ola. Loaʻa nā lāʻau lapaʻau hou no kekahi mau kūlana kikoʻī (e.g., Duchenne muscular dystrophy, Pompe disease).
- No nā myopathies lua ʻē aʻe: Kuhikuhi ʻia ka lāʻau lapaʻau i ke kumu nui o ka myopathy. No ka laʻana, inā he pilikia hormonal, hoʻoponopono ʻia, inā he maʻi ia, hāʻawi ʻia nā antibiotics, a inā i hoʻokumu ʻia e kahi lāʻau lapaʻau, hoʻōki ʻia ka lāʻau lapaʻau.
Pehea lā wau e mālama ai iaʻu iho?
ʻOiai he maʻi lōʻihi ka myopathy, hiki iā ʻoe ke kaohi i ka maʻi a ola i ke ola olakino ma ka hoʻololi ʻana i kou nohona a me ka hoʻokele pono ʻana.
- E ʻai i ka meaʻai maikaʻi a momona hoʻi. He mea nui loa ka ʻai kaulike me ka nui o nā mea kanu a me nā huaʻai.
- E noho hana. E hoʻoikaika kino māmā. Akā e hoʻomanaʻo, ma mua o ka hoʻomaka ʻana i kekahi papahana hoʻoikaika kino, pono ʻoe e kamaʻilio me kāu kauka a nīnau i nā hoʻoikaika kino kūpono no kou kūlana.
- E mālama i ke kaumaha o ke kino kūpono.
- Inā pilikia ʻoe i ka moni ʻana, e ʻai i nā meaʻai palupalu a wai. E kuʻi maikaʻi i ka meaʻai a ʻai.
- E lawe i ka lāʻau lapaʻau i kauoha ʻia e ke kauka i ka manawa kūpono.
- E makaʻala i nā loli i kou kino. Inā ʻike ʻoe i kekahi mau loli a i ʻole ka piʻi ʻana o nā hōʻailona, e hoʻomaopopo koke i kāu kauka.
Leka Lawe-Home
- ʻO ka myopathy kahi inoa maʻamau no kekahi mau kūlana e hoʻonāwaliwali ai i nā ʻiʻo.
- Hiki i kēia ke hānau ʻia (genetic) a i ʻole hiki ke ulu i ka wā o ke ola no nā kumu ʻē aʻe.
- ʻO ka nāwaliwali o nā ʻiʻo, ka ʻoʻoleʻa, a me ka luhi loa me nā hana liʻiliʻi nā hōʻailona nui.
- Inā loaʻa iā ʻoe kēia mau hōʻailona, he mea nui loa e ʻimi koke i ke kōkua lapaʻau.
- ʻOkoʻa nā koho lapaʻau ma muli o ke kumu o ka maʻi. Me ka hoʻokele kūpono a me ka mālama ʻana, hiki ke hoʻomalu maikaʻi ʻia nā kūlana he nui a alakaʻi i kahi ola maʻamau.
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