Aia ka aorta o ka puʻuwai o kāu keiki liʻiliʻi ma kahi ʻē aʻe? E aʻo kākou e pili ana i kēia (Overriding Aorta)!

I kekahi manawa, hele mai kā mākou poʻe liʻiliʻi i kēia ao me nā loli liʻiliʻi i loko o ko lākou mau puʻuwai. He mea maʻamau loa ia no ʻoe, ma ke ʻano he makuahine a he makuakāne paha, ke makaʻu nui a hopohopo hoʻi ke lohe ʻoe i kekahi mea e like me ia. Akā, mai hopohopo, no ka mea, i kēia lā e kamaʻilio ana mākou e pili ana i kahi maʻi i kapa ʻia ʻo "Overriding Aorta", he maʻi puʻuwai hānau. E kamaʻilio mākou e pili ana i nā mea he nui ma nā ʻōlelo maʻalahi, e like me ke ʻano o kēia, no ke aha e hana ʻia ai, he aha nā hōʻailona, ​​a he aha nā lāʻau lapaʻau. Inā maopopo iā ʻoe kēia mau mea, e hāʻawi ia iā ʻoe i ka ikaika nui e hāʻawi i ka mālama olakino maikaʻi loa no kāu pēpē.

He aha kēia `(Overriding Aorta)`? E hoʻomaopopo maʻalahi kākou, ʻeā?

ʻAe, e nānā mua kākou i ke ʻano o kēia `(Overriding Aorta)`. I ka ʻōlelo maʻalahi, he kīʻaha koko nui kēia i loko o ka puʻuwai o kā mākou pēpē, ʻo ia hoʻi ka aorta, aia ma kahi ʻokoʻa iki ma mua o kahi e pono ai.

I kēia manawa, e nānā, i loko o kahi puʻuwai olakino maʻamau, aia kēia aʻa nui `(Aorta)` ma ka ʻaoʻao hema o ka puʻuwai, ʻo ia hoʻi, pili i ka ventricle hema. Ua ʻike anei ʻoe i ke aha? ʻO ia kahi e hiki ai ke hoʻolaha ʻia ke koko maʻemaʻe a waiwai i ka oxygen e puka mai ana mai nā māmā i loko o ke kino. ʻO ia kāna hana nui.

Akā i ke ʻano o `(Overriding Aorta)`, aia kēia aorta ma luna o ka paia ma waena o ka ventricle hema a me ka ʻākau o ka puʻuwai (ua kapa ʻia kēia ʻo `Ventricular Septum`), a i ʻole ma luna o kahi lua ma kēlā paia (`Ventricular Septal Defect` a i ʻole VSD). E noʻonoʻo, ʻo ka mea e hana ʻia ma ʻaneʻi ua like ia me ke kau ʻana i kahi hose pamu wai i ka pahu kūpono ʻole.

He aha ka mea e hana ʻia ma muli o kēia? ʻO ka ʻaoʻao ʻākau o ka puʻuwai he emi ka oxygen, ʻo ia hoʻi ua hoʻohana ʻia, he koko "lepo" iki. Ma muli o kēlā lua (`VSD`) a me ka aorta ma kahi kūpono ʻole, komo kekahi o kēia koko i emi ka oxygen i loko o ka aorta a hui pū me ke koko e kaʻapuni ana ma ke kino. ʻO ia hoʻi, ua emi ka nui o ka oxygen i loko o ke koko e hiki ana i nā ʻāpana like ʻole o ke kino o ka pēpē. ʻO kēia ka pilikia nui.

He aha ka pilina ma waena o kēia a me ke kūlana i kapa ʻia ʻo `(Tetralogy of Fallot)`?

ʻAʻole ʻo Overriding Aorta kahi kūlana e kū hoʻokahi wale nō. ʻO ia kekahi o nā hiʻohiʻona nui ʻehā o kahi maʻi puʻuwai hānau paʻakikī i kapa ʻia ʻo Tetralogy o Fallot . ʻO "Tetralogy" ke ʻano he ʻehā. No laila, ma kēia kūlana, ʻike pū ʻia nā pilikia puʻuwai nui ʻehā:

1. `(Ke Kāohi nei i ka Aorta)`: Aia ka aorta a mākou i kamaʻilio ai ma kahi kūpono ʻole.

2. Ventricular Septal Defect (VSD): He lua ma ka paia ma waena o nā keʻena hema a me ka ʻākau o ka puʻuwai. Hoʻopili kēia i ke koko waiwai i ka oxygen me ke koko nele i ka oxygen.

3. Pulmonary Stenosis: ʻO ke aʻa pulmonary, ka mea e lawe ana i ke koko oxygenated mai ka ʻaoʻao ʻākau o ka puʻuwai i nā māmā, ua ālai ʻia a i ʻole kona valve, ka mea i wehe pono ʻole, e hōʻemi ana i ka nui o ke koko e hele ana i nā māmā.

4. Mānoanoa o nā paia o ka ventricle ʻākau o ka puʻuwai (`Right Ventricular Hypertrophy`):Ma muli o ke ālai ʻia ʻana o kēlā aʻa pulmonary, pono ka ventricle ʻākau e hana ikaika e pamu i ke koko. E like me ka nui ʻana o nā ʻiʻo ke hoʻoikaika kino ʻoe, mānoanoa nā paia o kēia ventricle i ka hala ʻana o ka manawa.

E noʻonoʻo, me he mea lā ʻaʻohe pā ma waena o ka wahi puhipaka a me ka wahi ʻaʻole puhipaka i loko o kahi hale ʻaina. A laila neʻe maʻalahi ka uahi mai kekahi wahi a i kekahi, a ʻaʻohe mea e maikaʻi. ʻO ia ka mea e hana ʻia ma kēia kūlana `(Tetralogy of Fallot)`. Hoʻohuihui ʻia ke koko me ka haʻahaʻa o ka oxygen a me ke koko me ka nui o ka oxygen.

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia maʻi (Overriding Aorta)?

ʻO kēia kūlana, i kapa ʻia ʻo "Tetralogy of Fallot", ʻo ia hoʻi ka "Overriding Aorta," ʻike pinepine ʻia i nā pēpē kāne ma mua o nā pēpē wahine.

Eia kekahi, ʻo nā pēpē me kekahi mau ʻano chromosomal, e like me Down syndrome, ʻoi aku ka nui o ka loaʻa ʻana o Tetralogy of Fallot. Hiki ke ʻike ʻia kēia pilikia puʻuwai me nā maʻi ʻē aʻe kakaikahi loa, e like me Apert syndrome a me Williams syndrome.

Pehea ka maʻamau o kēia kūlana?

Ua ʻōlelo ʻia ma kahi o hoʻokahi i loko o kēlā me kēia 100 pēpē i hānau ʻia ma ka honua e loaʻa paha kekahi ʻano kīnā puʻuwai hānau. Ke nānā ʻoe i kēlā ʻano, ma kahi o 10% o kēlā mau pēpē me nā kīnā puʻuwai, ʻo ia hoʻi, ma kahi o hoʻokahi i loko o 3,000 mau pēpē hānau hou, e loaʻa paha kahi maʻi i kapa ʻia ʻo `(Tetralogy of Fallot)`, ʻo ia hoʻi ʻo `(Overriding Aorta)`. No laila, ʻaʻole kēia he mea maʻamau loa, akā he ʻano ia e ʻike pinepine ai nā kauka.

He aha nā hōʻailona o kēia maʻi?

ʻAʻole like nā hōʻailona o nā pēpē a pau me Tetralogy of Fallot. Loaʻa paha i kekahi nā hōʻailona palupalu loa, aʻo kekahi poʻe he mau hōʻailona koʻikoʻi paha. ʻO ke ʻano o kēia mau hōʻailona e pili nui ana i ka nui o ke aʻa pulmonary i ālai ʻia. ʻO ia hoʻi, ka nui o ke koko e hiki ana i nā māmā. Inā ʻaʻole mālama ʻia, hiki i kēia mau hōʻailona ke ʻoi aku ka ʻino i ka hala ʻana o ka manawa.

Nā hōʻailona liʻiliʻi

Hiki i kekahi mau pēpē ke hōʻike i nā hōʻailona maʻalahi e like me kēia:

• ʻIli polū (`Cyanosis`): ʻIke nui ʻia kēia kala polū ma nā wahi e like me nā lehelehe, ke alelo, a me nā kui. Ma muli kēia o ka emi ʻana o ka nui o ka oxygen i loko o ke koko.
• Manaʻo koke i ka luhi: Me he mea lā e luhi koke ana kāu pēpē ma hope o ka pāʻani ʻana a i ʻole ka hānai ʻana.
• Pōkole o ka hanu: Loaʻa paha iā ʻoe ka pilikia o ka hanu ʻana, ʻoiai ke hana nei ʻoe.
• Nā pilikia makemake ʻai a me ka piʻi ʻana o ke kaumaha: ʻAʻole paha e ʻai maikaʻi ka pēpē a ʻaʻole paha e piʻi ke kaumaha.

Nā ʻŌuli Koʻikoʻi a me nā `(Nā Kilokilo Tet)`

I kekahi manawa, hāʻule koke ka pae oxygen o ka pēpē, e hana ana i nā "kupu Tet".Hiki ke loaʻa kahi kūlana weliweli i kapa ʻia he tet spell. Hiki ke hana koke ʻia kēia, e mau ana mai kekahi mau minuke a i kekahi mau hola. E noʻonoʻo i kahi pēpē e pāʻani ana a huli koke i ka uliuli a paʻakikī i ka hanu ʻana.

Hiki ke ʻike ʻia nā hōʻailona koʻikoʻi e like me kēia i ka wā o nā kilokilo Tet:

• Lilo koke ka ʻili i polū ʻeleʻele.
• Luhi loa ke kino, me he mea lā ua mae wale.
• Hiki ke hiki mai ka nāwaliwali.
• Nā ʻōhūhū.
• Paʻakikī ka hanu ʻana, ka hanu wikiwiki.
• Hiki i ke pēpē ke hoʻomaka koke e uē a laila hemo.

Ma hope o kahi "kupu Tet" e like me kēia, hiki i ka pēpē ke hiamoe no ka manawa lōʻihi. ʻO kēia mau "kupu Tet" he kūlana e pono ai ke kōkua koke ʻia e ke kauka.

No ke aha e kū mai ai nā kūlana e like me ka "Overriding Aorta"?

ʻO kaʻoiaʻiʻo, i ka hapa nui o ka manawa, he paʻakikī ke loaʻa kahi kumu kikoʻī no ia mau kīnā i ka wā e ulu ai ka puʻuwai o kahi pēpē i loko o ka ʻōpū. ʻO ia hoʻi, ʻaʻole maopopo ke kumu ('nā kumu i ʻike ʻole ʻia'). Eia naʻe, ua ʻike ʻia ma kahi o 25% o nā pēpē me kēia maʻi `(Tetralogy of Fallot)` (ʻo ia hoʻi ʻo `(Overriding Aorta)`) he mau kīnā hānau a pilikia paha ma nā ʻāpana ʻē aʻe o ko lākou kino .

Pehea e ʻike ai nā kauka i kēia maʻi (Overriding Aorta)?

I ka wā e hānau ai kāu pēpē, e nānā nā kauka a me nā kahu maʻi ma ka haukapila i ke olakino o ka pēpē. I ka manawa like, e nānā pono lākou i nā ʻano ʻē aʻe o ka puʻuwai.

• ʻO ka Pulse Oximetry: Hoʻokomo ʻia kahi sensor liʻiliʻi ma ka lima a i ʻole ka wāwae o ke pēpē e ana i ka nui o ka oxygen i loko o ke koko. Hiki i nā pae oxygen haʻahaʻa ke lilo i hōʻailona o ka maʻi puʻuwai. He hoʻāʻo maʻalahi kēia a ʻeha ʻole.
• ʻŌhūhū Puʻuwai: Ke hoʻolohe ke kauka i ka puʻuwai o ka pēpē me ka stethoscope, inā he kūlana e like me ka "Overriding Aorta", hiki ke lohe ʻia kahi leo ʻē aʻe, i kapa ʻia ʻo "heart murmur" , ma waho aʻe o ka puʻuwai maʻamau. Eia naʻe, ʻaʻole weliweli nā ʻōhūhū āpau, akā i kēia hihia, he hōʻailona koʻikoʻi ia.

Nā hoʻāʻo e hōʻoia

Inā loaʻa nā hōʻailona i luna, e kauoha nā kauka i nā hoʻokolohua e like me kēia e hōʻoia i ke kūlana a hoʻoholo i ke ʻano pololei o ka pilikia o ka puʻuwai:

• ʻEchocardiogram (Echo): Ua like kēia me ke kiʻi ultrasound o ka puʻuwai. Hiki iā ia ke ʻike maopopo i nā mea āpau mai ke ʻano o ka puʻuwai, ka hana o nā valves, ke ʻano o ke kahe ʻana o ke koko, ka nui o ka VSD, a me kahi o ka aorta. ʻO kēia ka hoʻāʻo nui e ʻike ai i ka Tetralogy o Fallot.
• Electrocardiogram (ECG/EKG): Hoʻopaʻa kēia i ka hana uila o ka puʻuwai. Hiki iā ia ke ʻike i nā mea e like me nā keʻena puʻuwai i hoʻonui ʻia a me nā pilikia rhythm.
• X-ray umauma:Hiki i kēia ke hāʻawi i kahi manaʻo o nā mea e like me ka nui a me ke ʻano o ka puʻuwai a inā paha he liʻiliʻi a nui loa paha ka nui o ke koko e hele ana i nā māmā.
• ʻO ka Computed Tomography (CT) scan a i ʻole MRI scan o ka puʻuwai: I kekahi manawa, hana ʻia kēia mau hoʻokolohua inā pono ka ʻike kikoʻī e pili ana i ka puʻuwai a me nā kīʻaha koko nui.
• Ka Catheterization o ka Puʻuwai: Ma kēia, ua hoʻokomo ʻia kahi ʻōmole lahilahi loa (catheter) ma o kahi kīʻaha koko ma ka ʻūhā a i ʻole ka lima o ke pēpē i ka puʻuwai, kahi e ana ʻia ai ke kaomi i loko o ka puʻuwai, nānā ʻia nā pae oxygen, a i kekahi manawa ua hoʻokomo ʻia kahi dye a lawe ʻia nā kiʻi X-ray. He mea kōkua nui kēia i ka loiloi pololei ʻana i ke kūlana o ka puʻuwai ma mua o ke ʻoki ʻana.
• Nā hoʻāʻo koko: Kōkua kēia i ka nānā ʻana i nā mea e like me ka pae oxygen i loko o ke koko a me ka nui o nā hunaola koko ʻulaʻula (Hemoglobin).

Pehea e mālama ʻia ai kēia maʻi `(Overriding Aorta)`?

ʻO ka lāʻau lapaʻau maikaʻi loa a mau loa wale nō no kēia kūlana (Tetralogy of Fallot) ʻo ia ke ʻoki ʻana e hoʻoponopono i nā hemahema ʻehā o ka puʻuwai. Hana pinepine ʻia kēia ma ke ʻano he ʻoki puʻuwai hāmama .

• Ka Manawa o ke ʻoki kino: I ka hapanui o nā hihia, ʻōlelo nā kauka e hana i kēia ʻoki kino ma mua o ka piha ʻana o ka pēpē i 6 mahina, a i ʻole i loko o ka makahiki mua . Aia kekahi mau manawa e hana ʻia ai ma mua no kekahi mau pēpē, ma muli o ke kūlana o ka pēpē.
• He aha ka mea e hana ʻia i ka wā o ke ʻoki kino?: Pani ke kauka ʻoki i ka lua ma ka paia ma waena o nā ventricles (VSD) me kahi ʻāpana kūikawā. Wehe pū ʻo ia i ka mea paʻa i loko o ke aʻa pulmonary a me ka valve, e ʻae ana i ke koko e kahe pono. Ke hoʻoponopono ʻia kēia mau mea, hoʻoponopono ʻia ka pilikia o ka aorta overriding a me ka mānoanoa o ka ventricle ʻākau.
• ʻO ka Shunt Manawa: He liʻiliʻi loa kekahi mau pēpē, a he liʻiliʻi loa ko lākou mau aʻa pulmonary, no laila he mea paʻakikī paha ke hana koke i ke ʻoki piha. I kēlā mau hihia, hiki i ke kauka lapaʻau ke kau i kahi shunt no kekahi manawa. Pili kēia i ka lawe ʻana i kahi lālā mai ka aorta o ka pēpē a i ʻole kekahi aʻa nui ʻē aʻe a hoʻopili iā ia i ke aʻa pulmonary. Hoʻonui kēia i ka nui o ke koko e hele ana i nā māmā, e hāʻawi ana i ka hōʻoluʻolu a hiki i ka wā e ʻelemakule iki ai ka pēpē a hiki ke hana ʻia ke ʻoki piha.

Ua hana nā kauka i kēia ʻoki puʻuwai hāmama e mālama ai iā Tetralogy of Fallot mai ka makahiki 1950, no laila he hana i hoʻokumu paʻa ʻia ma ke kahua lapaʻau.

Nā ʻano lāʻau i hoʻohana ʻia

Ma waho aʻe o ke ʻoki ʻana, hoʻohana ʻia kekahi mau lāʻau lapaʻau e kāohi i nā hōʻailona a pale i nā pilikia:

• Nā lāʻau lapaʻau Beta-blocker (e like me Propranolol): Kōkua kēia i ka pale ʻana i kēlā mau kilokilo Tet weliweli mai ka hanana ʻana a hoʻēmi i ko lākou koʻikoʻi inā hana ʻia.
• Nā Diuretics: Kōkua kēia i ka hōʻemi ʻana i ka wai pono ʻole i loko o ke kino a hoʻemi i ke kaomi ma ka puʻuwai (i nā kūlana e like me ka hāʻule ʻana o ka puʻuwai).
• `(Nā lāʻau ʻaʻai)` (Nā lāʻau ʻaʻai):ʻO nā pēpē me kēia ʻano maʻi puʻuwai e pilikia ana i ka loaʻa ʻana o kahi maʻi o ka ʻili o loko o ka puʻuwai ('Infective Endocarditis'), ʻoiai i ka wā o kekahi mau kaʻina hana lapaʻau e like me ka unuhi ʻana i nā niho. No laila, hāʻawi ʻia kēia lāʻau lapaʻau e pale aku i ia mau maʻi.

Aia kekahi mau pilikia me ka lāʻau lapaʻau?

ʻOiai inā ua holomua ke ʻoki ʻana, hiki ke kū mai kekahi mau pilikia i ka hala ʻana o ka manawa.

• I ka hoʻoponopono ʻana i ka Tetralogy o Fallot, hoʻonui iki nā kauka ʻoki i ka valve pulmonary, no laila e ʻike paha ka poʻe he nui i kahi liʻiliʻi o ke koko e kahe ana i hope ma o kēlā valve (pulmonary regurgitation).
• Hoʻonui kēia i ka pilikia o ka hoʻomohala ʻana i nā pilikia o ka puʻuwai puʻuwai (arrhythmias).
• I ka hala ʻana o ka manawa, piʻi aʻe kēia liki o ka valve, e kau ana i ke kaumaha ma ka ʻaoʻao ʻākau o ka puʻuwai, e hoʻonui ai i kēlā ʻāpana, a hiki ke alakaʻi i ka hāʻule ʻana o ka puʻuwai.
• He mau makahiki ma hope o ke ʻoki ʻana, hiki ke loaʻa nā mea e like me ka aorta i hoʻonui ʻia (aortic root dilatation) a i ʻole kahi valve tricuspid leaky. Inā hana ʻia kēia, pono paha ʻoe i kahi ʻoki hou a i ʻole kekahi lāʻau ʻē aʻe. No laila he mea nui e hoʻomau i ka nānā mau ʻana.

Pehea e kāohi ai i nā hōʻailona o ka pēpē a hiki i ke ʻoki ʻana?

A hiki i ka pau ʻana o ke ʻoki ʻana, e hana nā kauka i kēia mau mea e kāohi ai i nā hōʻailona o ka pēpē a hāʻawi i ka hōʻoluʻolu i ka pēpē:

• Inā pono, e hāʻawi i nā lāʻau lapaʻau no ka puʻuwai (e.g., beta-blockers).
• E hōʻoia ana ua loaʻa i ke pēpē ka nui o nā wai a me nā meaʻai.
• E nānā pinepine i ka pae hemoglobin o ke koko a, inā pono, e hāʻawi i nā syrup i loaʻa ka hao (e pale aku i ka anemia).
• E pale i nā hana e hoʻoluhi nui ai i ka pēpē, e like me ka uē ʻana no ka manawa lōʻihi.
• Inā loaʻa kahi "tet spell", ʻo ke paʻa ʻana i nā kuli o ke pēpē kokoke i kona umauma (ke "kūlana kuli-umauma") e hāʻawi paha i ka hōʻoluʻolu. Na kāu kauka e aʻo iā ʻoe pehea e hana ai i kēia.

Hiki ke hoʻēmi ʻia ka pilikia o kēia hana?

ʻOiai ʻaʻole ʻike pinepine ʻia ke kumu o ka maʻi puʻuwai i nā pēpē hānau hou, manaʻoʻiʻo nā kānaka noiʻi hiki i ke olakino o ka makuahine a me kona nohona i ka wā hāpai ke hoʻopilikia iā ia. Hiki i nā mea aʻe ke hoʻonui i ka pilikia o ka loaʻa ʻana o ka maʻi puʻuwai i kahi pēpē:

• Loaʻa ka maʻi puʻuwai hānau ma ka makuahine, ka makuakāne, a i ʻole kekahi lālā ʻē aʻe o ka ʻohana.
• Ka puhipaka ʻana o ka makuahine i ka wā hāpai.
• Loaʻa i ka makuahine kahi maʻi e like me ka "Rubella" (German measles) i nā wā mua o ka hāpai ʻana.
• Loaʻa i ka makuahine ka maʻi diabetes i kāohi ʻole ʻia.
• ʻO ka lawe ʻana i kekahi mau lāʻau lapaʻau (e laʻa, kekahi mau lāʻau hoʻopaʻa) i nā mahina ʻekolu mua o ka hāpai ʻana.
• Ka hoʻohana ʻana o ka makuahine i ka waiʻona.
• Nā hemahema o ka meaʻai i ka wā hāpai.
• ʻOi aku ka nui o nā makahiki o ka makuahine ma mua o 40 mau makahiki i ka wā hāpai.

No laila, i mea e hōʻemi ai i kēia pilikia i nā hāpai ʻana e hiki mai ana, he mea nui loa ia e mālama i kou olakino ma mua o ka hāpai ʻana, e kāohi i nā kūlana olakino e kū nei (e like me ka maʻi diabetes), e pale loa i ka puhipaka a me ka waiʻona, a mai lawe i kekahi lāʻau lapaʻau me ka ʻole o ka ʻae ʻia e kāu kauka. Inā loaʻa i kekahi o kou ʻohana ka maʻi puʻuwai, he mea naʻauao nō hoʻi ke ʻimi i ka ʻōlelo aʻo mai kahi kākāʻōlelo genetic.

He aha ke ʻano o ka wā e hiki mai ana e hiki i kahi pēpē me ka `(Orriding Aorta)` ke manaʻo?

He mea weliweli paha kēia iā ʻoe, akā ʻo ka ʻoiaʻiʻo, hoʻomau ka hapa nui o nā pēpē i ke ola maʻamau a olakino ma hope o ke ʻoki ʻana.

• ʻOi aku ma mua o 90% o nā pēpē i hana pono ʻia no ke ʻoki ʻana no Tetralogy of Fallot (ʻo ia hoʻi ʻo Overriding Aorta) e ulu maikaʻi ana a ola i ke ola makua maʻamau. Hele lākou i ke kula, pāʻani, hana, a loaʻa nā ʻohana. Ola kekahi i nā ola olakino a hiki i ko lākou mau makahiki 70 a me 80.
• Eia nō naʻe, inā ʻaʻole hana ʻia ke ʻoki ʻana, he mea weliweli ke kūlana. Inā hana ʻia kēlā, e ʻoi aku ka ʻino o nā hōʻailona i ka hala ʻana o ka manawa, e kaupalena ana i kou ola. ʻAʻole paha ʻoe e ola a hiki i 20 mau makahiki.

No laila, ʻo ka mea nui ka hāʻawi ʻana i ka lāʻau lapaʻau kūpono i ka manawa kūpono.

Pehea e mālama ai i ke keiki ma hope o ke ʻoki kino?

Ke lawe mai ʻoe i kāu pēpē i ka home ma hope o ke ʻoki ʻana, he kuleana nui kou.

• Nā kipa hahai mau: Pono kāu pēpē i nā kipa hahai mau me ke kauka puʻuwai keiki. Hiki ke pinepine pinepine kēia i ka wā mua, a laila pinepine. Mai hōʻalo i kēia mau mea.
• Ke pale ʻana i nā maʻi hanu: Hiki i nā keiki i hana ʻia i ke ʻoki puʻuwai e like me kēia ke loaʻa i nā maʻi hanu, hiki ke alakaʻi koke i nā pilikia. No laila e mālama i kāu pēpē mai ka poʻe me ke anu a me ke kuni. Inā ulu kēlā ʻano maʻi, e ʻimi koke i ke kōkua lapaʻau.
• Nā lāʻau lapaʻau: Hiki i nā kauka ke ʻōlelo aku i nā lāʻau lapaʻau ma mua o kekahi mau kaʻina hana niho a i ʻole nā ​​ʻoki kino liʻiliʻi ʻē aʻe e pale aku ai i nā maʻi puʻuwai (endocarditis). E nīnau i kāu kauka e pili ana i kēia.
• ʻAi a me ka ulu ʻana: E mālama i ka meaʻai a me ka ulu ʻana o kāu pēpē.
• Nā Hana: Ke ulu aʻe kāu pēpē, e kamaʻilio me kāu kauka e pili ana i nā hana a me nā pāʻani hiki iā ia ke hana. ʻO ka hapa nui o ka manawa, hiki iā ia ke hana maʻamau i nā mea āpau.

I ko kākou ʻelemakule ʻana, hiki ke kū mai nā pilikia puʻuwai hou, no laila he mea nui loa e hoʻomau i kēia mau hoʻokolohua loea puʻuwai a hiki i ka wā makua.

Āhea wau e ʻike ai i ke kauka?

Inā hōʻike kāu pēpē i kekahi o kēia mau hōʻailona, ​​e ʻike koke i ke kauka a lawe paha iā ia i ka haukapila:

• Inā ʻike ʻia nā hōʻailona hou.
• Inā ʻike ʻia kou ʻili, kou lehelehe, a me kou alelo e polū ana.
• Inā pilikia ʻoe i ka hanu ʻana.
• Inā kānalua ʻoe e inu i ka waiū a ʻai paha i ka meaʻai.
• Inā ʻike ʻia ʻoe e luhi koke ana.

Āhea wau e hele ai i ka lumi pilikia (ER)?

Inā loaʻa i kāu pēpē kahi "Tet spell" koʻikoʻi, ʻo ia hoʻi, huli koke lākou i ka uliuli, paʻakikī ka hanu ʻana, a kokoke paha e hemo, e kelepona koke i ka 911 a lawe iā lākou i ka lumi pilikia o ka haukapila kokoke loa. Ma laila, hiki ke hāʻawi ʻia iā lākou ka oxygen a/a i ʻole nā ​​​​lāʻau lapaʻau e like me "Morphine" e kāohi i ke kūlana.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

I ka manawa e like me kēia, nui paha nā nīnau ma kou manaʻo. Mai makaʻu e nīnau i kāu kauka e pili ana i kēia mau mea:

• Pono anei au e kaupalena i nā haʻuki a kaʻu keiki a i ʻole nā ​​hana ʻē aʻe?
• ʻEhia pinepine e pono ai kaʻu pēpē e hele mai no nā nānā kino?
• E pono anei kaʻu pēpē i nā ʻoki kino hou aku? Inā pēlā, āhea?
• He aha nā pilikia lōʻihi e manaʻo ʻia? He aha ka mea e hiki ke hana ʻia e pale aku ai iā lākou?
• He aha nā lāʻau lapaʻau e pono e hāʻawi ʻia i ka pēpē? Pehea ka lōʻihi e hāʻawi ʻia ai? He mau hopena ʻaoʻao paha ko lākou?

ʻO nā mea nui a mākou e makemake ai e lawe i ka home mai kēia moʻolelo

ʻAe, ua kamaʻilio nui mākou e pili ana i ka Overriding Aorta a me Tetralogy of Fallot. Ke manaʻo nei paha ʻoe i ke kaumaha nui i kēia manawa. Akā, e hoʻomanaʻo i kēia mau mea:

• ʻO ka Aorta ma luna he kīnā puʻuwai hānau i kapa ʻia ʻo Tetralogy of Fallot. ʻO kēia ka wā e kū pono ʻole ai ka aorta o ke pēpē, e kahe ana ke koko nele i ka oxygen ma ke kino holoʻokoʻa.
• Hiki i nā hōʻailona ke komo pū me ka ʻili polū, ka luhi koke, ka paʻakikī o ka hanu ʻana, a me nā "kupu Tet" weliweli.
• Hiki ke mālama pono ʻia kēia maʻi me ke ʻoki ʻana. Ua hana maikaʻi loa nā kauka ʻoki i kēia ʻoki no nā makahiki he ʻumi.
• Ma hope o ke ʻoki ʻana, nui nā pēpē e ola olakino a maʻamau.
• ʻO nā nānā kino maʻamau a me ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau nā mea nui loa. ʻAʻole ʻoe hoʻokahi i kēia huakaʻi. Aia nā kauka akamai, nā kahu maʻi, a me nā limahana mālama ola e kōkua a alakaʻi iā ʻoe a me kāu pēpē. No laila e hoʻoikaika.

Inā e kali ana kāu pēpē hānau hou no ke ʻoki ʻana, e nīnau pono i ke kauka a me nā limahana hānai e pili ana i nā mea hiki iā ʻoe ke hana e kōkua i kāu pēpē i ka wā o ke kaʻina hana, a me ka mea e hana ai inā loaʻa kahi "tet spell". E lilo kēlā ʻike i mea kōkua nui iā ʻoe.

ʻo ka aorta ma luna, tetralogy o fallot, kīnā puʻuwai hānau, kīnā septal ventricular, cyanosis, nā ʻōlelo tet, ʻoki puʻuwai hāmama, maʻi puʻuwai, nā kīnā hānau, pēpē polū, tetralogy o fallot, ʻoki puʻuwai, maʻi puʻuwai pediatric