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Ke loaʻa nei iā ʻoe nā pehu ma kou ʻili? Ke loaʻa nei iā ʻoe nā ʻeha waha? Hiki paha iā ia ke Pemphigus Vulgaris? E kamaʻilio kākou e pili ana i kēia!

Ke loaʻa nei iā ʻoe nā pehu ma kou ʻili? Ke loaʻa nei iā ʻoe nā ʻeha waha? Hiki paha iā ia ke Pemphigus Vulgaris? E kamaʻilio kākou e pili ana i kēia!

Loaʻa iā ʻoe i kekahi manawa nā pehu ʻeha a me nā ʻeha ma kou kino, ʻoi aku hoʻi i loko o kou waha? Poha maʻalahi lākou a paʻakikī ke ʻai a inu paha? A laila he mea nui paha kēia iā ʻoe. Kāhea mākou i kēia maʻi ʻo Pemphigus Vulgaris. Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana.

He aha ka maʻi ʻo Pemphigus Vulgaris?

I ka ʻōlelo maʻalahi, ʻo Pemphigus Vulgaris kahi maʻi i hoʻokumu ʻia e kahi hana hewa i loko o kāu ʻōnaehana pale . Kāhea mākou i kēia he maʻi autoimmune. ʻO ke kuleana o kā mākou ʻōnaehana pale, ʻo ia ke pale iā mākou mai nā germs haole, bacteria, a me nā virus. Ua like ia me kahi pūʻali koa e pale ana i kahi ʻāina. Eia nō naʻe, ma Pemphigus Vulgaris, hoʻouka hewa kāu ʻōnaehana pale ponoʻī i kāu mau ʻili olakino a me nā membrane mucous. ʻO nā membrane mucous nā uhi palupalu a pulu e hoʻopili ana i loko o kou waha, ihu, puʻu, ala hanu, ala ʻai, ala mimi, a me ke ala genital.

ʻO kēia hoʻouka kaua ke kumu o nā pehu e hana ʻia ma ka ʻili a me nā membrane mucous. ʻO ka pinepine, ʻo ka poʻe me Pemphigus Vulgaris e loaʻa mua nā pehu i loko o ka waha . He palupalu loa kēia mau pehu a pohā maʻalahi. A laila lilo lākou i mau ʻeha ʻeha.

ʻO Pemphigus vulgaris ke ʻano maʻamau o ka pemphigus.

Pehea ka maʻamau o kēia? ʻO wai ka mea i loaʻa pinepine?

He maʻi laha ʻole ʻo Pemphigus Vulgaris. ʻOiai hiki ke hoʻopilikia i kekahi, hoʻopilikia pinepine ia i ka poʻe ma luna o 40 mau makahiki. He mea laha ʻole loa ia i nā pēpē a me nā keiki.

Pehea ka hopena o Pemphigus Vulgaris i koʻu kino?

Hoʻomaka pinepine nā hōʻailona o Pemphigus Vulgaris i loko o kou waha . Hoʻokumu ʻia nā pehu ʻeha ma laila, e paʻakikī ai ka ʻai ʻana a me ka inu ʻana. E noʻonoʻo he mau ʻeha ʻeha ma kou waha a puni. ʻAʻole hiki iā ʻoe ke nānā aku i kāu meaʻai punahele no ka mea he ʻeha a ʻā. He pilikia kekahi poʻe i ka inu ʻana i ka wai.

Ma hope o ka hoʻopilikia ʻana i nā membrane mucous o ka waha, hiki i nā hōʻailona ke laha i ka ʻili ma nā wahi ʻē aʻe o kou kino. He lahilahi loa kēia mau pehu, no laila e pohā maʻalahi lākou. Ke pohā nā pehu, hiki iā lākou ke hoʻokahe i ka wai, a i kekahi manawa e puka mai ka pus. A laila lilo kēia mau wahi i mau ʻeha hāmama.

He aha nā hōʻailona o kēia?

ʻAʻole like nā hōʻailona o ka maʻi Pemphigus Vulgaris i nā kānaka a pau, a hiki ke ʻokoʻa ko lākou koʻikoʻi mai kēlā kanaka a kēia kanaka . ʻO nā hōʻailona maʻamau:

  • ʻIke ʻia kahi pehu piha i ka wai. He apo ʻulaʻula paha kēia a puni, a he keʻokeʻo poni māmā paha ke kikowaena.
  • Poha maʻalahi nā pehu, e kahe ana ka wai maopopo a i ʻole ke koko paha.
  • Hiki ke hana ʻia kahi ʻōpala a unahi paha ma luna a puni paha o ka pehu.
  • Ke ʻili nei ka ʻili ma luna a puni paha o ka pehu.
  • Ke pahū ka pehu, hana ʻia nā ʻeha hāmama.
  • Aia ka ʻeha nui i loko a puni nā pehu.

Mai hoʻopā i nā pehu - hiki iā lākou ke lilo i maʻi!

Mai ʻānai a ʻōʻili paha i kou mau pehu, no ka mea hiki i kēia ke lilo i mau ʻeha hāmama a alakaʻi maʻalahi i nā maʻi. Hiki i nā hōʻailona o kahi maʻi ke komo pū me:

  • Ke puka mai nei kahi kahe e like me ka pus keʻokeʻo a melemele paha mai loko mai o ka pehu.
  • Ua pehu ka pehu a ʻeha loa ke ʻano.
  • Hoʻokumu ʻia kahi ʻili melemele ma luna a i ʻole a puni ka pehu.
  • Pehu a hoʻonui ʻia ka ʻili a puni ka pehu.
  • ʻAʻole e ho'ōla ana ka pehu.

E hoʻomanaʻo, inā loaʻa iā ʻoe nā hōʻailona e like me kēia, pono ʻoe e ʻike koke i ke kauka.

Ma hea e ʻike ʻia ai nā hōʻailona?

Hoʻopilikia nā hōʻailona o Pemphigus Vulgaris i kou ʻili a me nā membrane mucous. ʻO nā wahi maʻamau e ʻike ʻia ai nā hōʻailona :

  • Waha a me ka puʻu
  • Ihu
  • Nā maka
  • Wahi ʻōpū kāne `(genitals)`
  • Umauma
  • Ma waho
  • Nā lima a me nā wāwae
  • Iwi poʻo

He aha ke kumu o Pemphigus Vulgaris?

ʻAʻole i ʻike ʻia ke kumu maoli o Pemphigus Vulgaris .

E like me kā mākou i kūkākūkā ai ma mua, he maʻi autoimmune kēia, kahi e kuhi hewa ai nā antibodies o kāu ʻōnaehana pale - nā protein e pale aku i kou kino mai nā germs, bacteria, a me nā mea ʻē aʻe - i kāu mau cell olakino ponoʻī a hoʻouka iā lākou me he mea lā he poʻe komo hewa lākou. ʻO kēia hoʻouka ʻana i nā cell olakino ke kumu o nā hōʻailona o ka pehu ʻana ma ka ʻili a me nā membrane mucous.

Hiki ke hana ʻia kēia kūlana e kekahi mau lāʻau lapaʻau?

ʻAʻole pinepine loa, hiki i kou kino ke pane maikaʻi ʻole i kekahi mau lāʻau lapaʻau a hana i nā hōʻailona o ka pemphigus vulgaris. ʻO kekahi o kēia mau lāʻau lapaʻau:

  • Nā mea hoʻopaʻa ACE: ʻO kēia nā lāʻau lapaʻau i hāʻawi ʻia no ke koko kiʻekiʻe.
  • Nā 'Chelating agents': He mau lāʻau lapaʻau kēia e wehe ai i kekahi mau mea mai ke koko.
  • Nā lāʻau lapaʻau
  • Nā lāʻau anti-inflammatory nonsteroidal (NSAIDs)

He mea laha anei kēia?

ʻAʻole, ʻaʻole he maʻi lele ʻo Pemphigus Vulgaris. ʻAʻole hiki iā ʻoe ke hoʻolaha iā ia i kekahi. No laila, ʻaʻohe mea e hopohopo ai.

Pehea ʻoe e ʻike ai i kēia?

E nānā mua kāu kauka iā ʻoe a nīnau e pili ana i kāu mau hōʻailona. E nīnau lākou e pili ana i kou mōʻaukala olakino a inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like. A laila, e hana paha lākou i kekahi mau hoʻokolohua e hōʻoia i ke kūlana.

He aha nā hoʻokolohua e hana ʻia nei?

No ka hōʻoia ʻana i ka maʻi, hiki i kāu kauka ke hana i kahi biopsy ʻili . Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka ʻili i hoʻopilikia ʻia, mai kahi paha i loaʻa ai nā pehu, a nānā iā ia ma lalo o kahi microscope. Hiki paha i kēia ke komo pū me kahi hoʻāʻo kūikawā i kapa ʻia he hoʻāʻo immunofluorescence.

ʻO kekahi hoʻāʻo he hoʻāʻo koko . Nānā kēia i nā antibodies i loko o kou koko e hoʻoulu ai i kāu mau hōʻailona.

He aha nā lāʻau lapaʻau?

ʻO ka mālama ʻana no ka pemphigus vulgaris e kālele ana i ka kaohi ʻana i nā hōʻailona a me ka pale ʻana i nā pilikia e like me ka maʻi . Hiki ke ʻokoʻa nā koho lapaʻau mai kēlā kanaka a kēia kanaka. Hiki iā lākou ke komo pū me:

  • Inā he maʻi, e hāʻawi iā ia i ka lāʻau.
  • Inā he mau lāʻau lapaʻau e like me ke kumu o nā hōʻailona, ​​​​e hoʻōki i ka lawe ʻana iā lākou.
  • Ke hoʻohana nei i nā lāʻau lapaʻau, nā kirīmi, a me nā ʻaila e ho'ōla i nā ʻeha a hōʻemi i ka ʻeha.
  • E mālama pono i nā ʻeha a me nā pehu, e like me kāu e mālama ai i kahi kuni a ʻeha paha.
  • Inā ʻaʻole hiki iā ʻoe ke ʻai ma muli o nā ʻeha waha, ʻo ka ʻai ʻana i kahi meaʻai palaka, ʻai ʻole, a i ʻole kekahi manawa meaʻai IV, hiki ke kōkua i ka pale ʻana i ka ʻai ʻole.
  • Ke hoʻohana nei i ka lāʻau hoʻomāmā e hōʻemi i ka ʻeha o nā pehu waha.

He aha nā lāʻau lapaʻau no ka hoʻohana ʻana iā Pemphigus Vulgaris?

Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia e hōʻemi i nā hōʻailona, ​​​​pale i nā ʻōhū, a mālama paha i nā maʻi:

  • ʻO nā Corticosteroids, i hoʻopili ʻia i ka ʻili a i lawe ʻia paha ma ka waha, kōkua i ka hoʻēmi ʻana i ka mumū.
  • Nā lāʻau hoʻopau i ka ʻōnaehana pale . ʻO nā laʻana e komo pū me ka azathioprine, cyclosporine, mycophenolate, cyclophosphamide, methotrexate, a i ʻole rituximab. Hana kēia mau mea ma ka hōʻemi ʻana i ka hana o ka ʻōnaehana pale a me ke kāohi ʻana iā ia mai ka hoʻouka ʻana i nā ʻāpana olakino.
  • Nā lāʻau antibiotic a i ʻole antifungal. Hāʻawi ʻia kēia mau mea inā he maʻi.

Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?

ʻAʻole like nā lāʻau lapaʻau a pau, no laila hiki ke loaʻa nā hopena ʻaoʻao ma muli o ke ʻano o ka lāʻau lapaʻau a kāu kauka i kuhikuhi ai. Ma mua o ka hoʻomaka ʻana i kahi lāʻau lapaʻau hou, pono ʻoe e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, nā mea hoʻohui āu e lawe nei, a me nā maʻi āpau āu e loaʻa ai. E nānā kāu kauka i kou kūlana a me ka holomua o kāu lāʻau lapaʻau. Hiki iā ia ke hana i nā hoʻāʻo koko a mimi paha e nānā i nā hopena ʻaoʻao.

He aha kāu e ʻai ai a inu ai i kēia maʻi?

Hiki ke paʻakikī ka ʻai ʻana a me ka inu ʻana i ka wā e loaʻa ai iā ʻoe ʻo Pemphigus Vulgaris, ʻoiai inā he mau pehu a me nā ʻeha i loko o kou waha . No laila, e koho i nā meaʻai palupalu, wai, a me nā meaʻai ʻaʻole ʻōniʻoniʻo . ʻAʻole ʻeha kēia mau mea no nā ʻeha. E pale i nā meaʻai ʻakika, ʻala, a me nā meaʻai ʻōniʻoniʻo (e.g., lemona, ʻalani, chili, ʻuala palai).

Inā ʻaʻole hiki iā ʻoe ke ʻai a inu paha, e ʻike koke i ke kauka.

ʻEhia ka manawa e ʻoi aku ai koʻu maikaʻi ma hope o ka hoʻomaka ʻana o ka lāʻau lapaʻau?

ʻOkoʻa ka manawa ho'ōla mai kēlā kanaka a kēia kanaka. ʻO ka maʻamau, hiki ke hala i kekahi mau pule ma hope o ka hoʻomaka ʻana o ka lāʻau no nā pehu hou e oki ai ke kūkulu ʻana . Ma hope o kēlā, hiki ke hala i kekahi mau mahina no ka ho'ōla ʻana o kou ʻili.

He maʻi mau loa ʻo Pemphigus vulgaris, ʻo ia hoʻi, hiki ke hoʻi hou mai nā hōʻailona ma hope o ka mālama ʻia ʻana.

Hiki ke pale ʻia ka Pemphigus Vulgaris?

No ka mea, ʻaʻole ʻike ʻia ke kumu pololei, ʻaʻohe ala e pale aku ai iā Pemphigus Vulgaris. Eia nō naʻe, hiki i ka lāʻau lapaʻau ke hōʻemi i nā hōʻailona.

He aha ka mea e hana inā loaʻa iaʻu ʻo Pemphigus Vulgaris?

Me ka mālama ʻana, hiki iā ʻoe ke kāohi i ka pemphigus vulgaris. ʻAʻole pinepine kēia ʻano e hoʻopilikia i kou ola. Eia nō naʻe, inā koʻikoʻi nā hōʻailona, ​​​​hiki iā lākou ke hoʻopau iā ʻoe no kekahi manawa. ʻO ke ʻano kēia he mea paʻakikī paha ke hana i kāu mau hana o kēlā me kēia lā a i ʻole e hele i ka hana. ʻAʻole hiki i kekahi poʻe ke hiamoe maikaʻi a hōʻemi paha i ke kaumaha inā ʻaʻole hiki iā lākou ke ʻai pono ma muli o nā ʻeha waha.

He mea kākaʻikahi nā ʻōpala ke ho'ōla ʻia nā pehu. Eia nō naʻe, inā pohā kahi ʻeha a paʻakikī ke ho'ōla, hiki ke waiho i nā ʻōpala a i ʻole nā ​​māka i hoʻololi ʻia ke kala ma ka ʻili.

Inā ʻaʻole mālama ʻia, hiki i nā hōʻailona ke laha ma ke kino a alakaʻi i nā pilikia e hoʻoweliweli i ke ola (e.g., ka ʻai ʻole, ka maloʻo ʻana o ka wai, ka sepsis - he maʻi koʻikoʻi). ʻO ka pilikia koʻikoʻi loa o ka pemphigus vulgaris i mālama ʻole ʻia he maʻi koʻikoʻi, mālama ʻole ʻia.

ʻAʻohe lāʻau lapaʻau no Pemphigus Vulgaris. Ke hoʻomau nei ka noiʻi ʻana i ke kumu a me nā lāʻau lapaʻau hou.

Pehea ka lōʻihi o kēia kūlana?

He maʻi lōʻihi (mau) ʻo Pemphigus Vulgaris, no laila hiki iā ʻoe ke ʻike i nā hōʻailona i kou ola a pau. Hoʻomaka pinepine nā hōʻailona ma waena o 40 a me 60 mau makahiki. Hiki i nā hōʻailona ke hele mai a hele (flare-ups). Hiki i ka lāʻau lapaʻau ke kōkua i ka hōʻemi ʻana i kāu mau hōʻailona.

Pehea lā wau e mālama ai iaʻu iho?

Hiki iā ʻoe ke mālama iā ʻoe iho ma ka home a hoʻokele i nā hōʻailona o Pemphigus Vulgaris ma ka hana ʻana i kēia mau mea:

  • E ʻai i ka meaʻai palupalu, palupalu, a wai hoʻi ke loaʻa iā ʻoe nā ʻeha waha.
  • E mālama i kou mau pehu a me kou mau ʻeha, e like me kou mālama ʻana i kahi ʻoki a i ʻole ke kuni.
  • E ʻaʻahu i nā lole pale a hoʻohana i ka sunscreen e pale i kou ʻili mai nā kukuna UV ʻino o ka lā.
  • E hoʻohana i nā kopa a me nā lotion ʻala ʻole e palupalu i kou ʻili.

Āhea wau e ʻike ai i ke kauka?

Pono ʻoe e ʻike i ke kauka inā loaʻa iā ʻoe kēia mau hōʻailona:

  • Inā ʻaʻole e ola nā ʻeha.
  • Inā he mau pehu ma luna o kahi ʻāpana nui o ke kino.
  • Inā e kahe ana nā pehu ʻeha i kahi wai melemele a keʻokeʻo paha, a inā paha e kū mai ana kahi ʻili melemele a puni lākou (he mau hōʻailona paha kēia o ka maʻi).
  • Inā he pehu i loko a puni paha o nā pehu.
  • Inā paʻakikī ke ʻai a me ka inu.
  • Inā loaʻa iā ʻoe nā hōʻailona e like me ke kuni, ka ʻūhā, a me ka ʻehaʻeha o nā ʻiʻo.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Ke hele ʻoe e ʻike i ke kauka, hiki iā ʻoe ke nīnau i nā nīnau e like me kēia:

  • He aha ke ʻano o ka lāʻau lapaʻau āu e paipai nei?
  • Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
  • Pehea e hiki ai iaʻu ke pale aku i nā maʻi?
  • Pehea e hiki ai iaʻu ke mālama i koʻu mau ʻeha ma ka home?

He aha ka ʻokoʻa ma waena o Pemphigus Vulgaris a me Bullous Pemphigoid?

ʻO Pemphigus Vulgaris a me Bullous Pemphigoid nā maʻi autoimmune e hoʻopilikia i kou ʻili. Hoʻopilikia pinepine nā mea ʻelua i nā poʻe ma luna o 65 mau makahiki. Eia nō naʻe, ʻo ka ʻokoʻa nui ma waena o nā maʻi ʻelua e pili ana i nā ʻeha e kū mai ana a me ke kumu .

Hoʻokumu ʻo Pemphigus vulgaris i nā ʻūlū liʻiliʻi piha i ka wai ma kou ʻili a me nā membrane mucous, e like me kou waha.

ʻO ka bullous pemphigoid ke kumu o ka ʻili ʻānai, piʻi, a ʻulaʻula i nā kiko ma ka ʻili i kapa ʻia he hive-like welts . Uhi pinepine ʻia kēia mau kiko me nā pehu paʻakikī a ʻaʻole i haki.

E lawe i ka leka i ka home

He maʻi ʻili lōʻihi ka Pemphigus Vulgaris e mau ana no ke ola holoʻokoʻa. Hiki ke ʻoluʻolu ʻole nā ​​hōʻailona a hiki ke hoʻoulu i nā ʻeha ʻili a me ka waha. ʻO ka mea nui loa, ʻo ia ka ʻai pono ʻana a pale i nā hemahema meaʻai ke loaʻa iā ʻoe kēia maʻi . E kamaʻilio me kāu kauka e pili ana i nā koho lapaʻau maikaʻi loa no kāu mau hōʻailona. Mai hopohopo, ʻo ka mea nui loa, ʻo ia ka makaʻala a loaʻa ka lāʻau kūpono.


pemphigus vulgaris, maʻi ʻili, pehu, ʻōpū waha, autoimmune, pale ʻana, maʻi ʻili

Frequently Asked Questions (FAQ)

He aha nā lāʻau lapaʻau no ka hoʻohana ʻana iā Pemphigus Vulgaris?

Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia e hōʻemi i nā hōʻailona, ​​​​pale i nā ʻōhū, a mālama paha i nā maʻi:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ke loaʻa nei iā ʻoe nā pehu ma kou ʻili? Ke loaʻa nei iā ʻoe nā ʻeha waha? Hiki paha iā ia ke Pemphigus Vulgaris? E kamaʻilio kākou e pili ana i kēia!

Ke loaʻa nei iā ʻoe nā pehu ma kou ʻili? Ke loaʻa nei iā ʻoe nā ʻeha waha? Hiki paha iā ia ke Pemphigus Vulgaris? E kamaʻilio kākou e pili ana i kēia!

Loaʻa iā ʻoe i kekahi manawa nā pehu ʻeha a me nā ʻeha ma kou kino, ʻoi aku hoʻi i loko o kou waha? Poha maʻalahi lākou a paʻakikī ke ʻai a inu paha? A laila he mea nui paha kēia iā ʻoe. Kāhea mākou i kēia maʻi ʻo Pemphigus Vulgaris. Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana.

He aha ka maʻi ʻo Pemphigus Vulgaris?

I ka ʻōlelo maʻalahi, ʻo Pemphigus Vulgaris kahi maʻi i hoʻokumu ʻia e kahi hana hewa i loko o kāu ʻōnaehana pale . Kāhea mākou i kēia he maʻi autoimmune. ʻO ke kuleana o kā mākou ʻōnaehana pale, ʻo ia ke pale iā mākou mai nā germs haole, bacteria, a me nā virus. Ua like ia me kahi pūʻali koa e pale ana i kahi ʻāina. Eia nō naʻe, ma Pemphigus Vulgaris, hoʻouka hewa kāu ʻōnaehana pale ponoʻī i kāu mau ʻili olakino a me nā membrane mucous. ʻO nā membrane mucous nā uhi palupalu a pulu e hoʻopili ana i loko o kou waha, ihu, puʻu, ala hanu, ala ʻai, ala mimi, a me ke ala genital.

ʻO kēia hoʻouka kaua ke kumu o nā pehu e hana ʻia ma ka ʻili a me nā membrane mucous. ʻO ka pinepine, ʻo ka poʻe me Pemphigus Vulgaris e loaʻa mua nā pehu i loko o ka waha . He palupalu loa kēia mau pehu a pohā maʻalahi. A laila lilo lākou i mau ʻeha ʻeha.

ʻO Pemphigus vulgaris ke ʻano maʻamau o ka pemphigus.

Pehea ka maʻamau o kēia? ʻO wai ka mea i loaʻa pinepine?

He maʻi laha ʻole ʻo Pemphigus Vulgaris. ʻOiai hiki ke hoʻopilikia i kekahi, hoʻopilikia pinepine ia i ka poʻe ma luna o 40 mau makahiki. He mea laha ʻole loa ia i nā pēpē a me nā keiki.

Pehea ka hopena o Pemphigus Vulgaris i koʻu kino?

Hoʻomaka pinepine nā hōʻailona o Pemphigus Vulgaris i loko o kou waha . Hoʻokumu ʻia nā pehu ʻeha ma laila, e paʻakikī ai ka ʻai ʻana a me ka inu ʻana. E noʻonoʻo he mau ʻeha ʻeha ma kou waha a puni. ʻAʻole hiki iā ʻoe ke nānā aku i kāu meaʻai punahele no ka mea he ʻeha a ʻā. He pilikia kekahi poʻe i ka inu ʻana i ka wai.

Ma hope o ka hoʻopilikia ʻana i nā membrane mucous o ka waha, hiki i nā hōʻailona ke laha i ka ʻili ma nā wahi ʻē aʻe o kou kino. He lahilahi loa kēia mau pehu, no laila e pohā maʻalahi lākou. Ke pohā nā pehu, hiki iā lākou ke hoʻokahe i ka wai, a i kekahi manawa e puka mai ka pus. A laila lilo kēia mau wahi i mau ʻeha hāmama.

He aha nā hōʻailona o kēia?

ʻAʻole like nā hōʻailona o ka maʻi Pemphigus Vulgaris i nā kānaka a pau, a hiki ke ʻokoʻa ko lākou koʻikoʻi mai kēlā kanaka a kēia kanaka . ʻO nā hōʻailona maʻamau:

  • ʻIke ʻia kahi pehu piha i ka wai. He apo ʻulaʻula paha kēia a puni, a he keʻokeʻo poni māmā paha ke kikowaena.
  • Poha maʻalahi nā pehu, e kahe ana ka wai maopopo a i ʻole ke koko paha.
  • Hiki ke hana ʻia kahi ʻōpala a unahi paha ma luna a puni paha o ka pehu.
  • Ke ʻili nei ka ʻili ma luna a puni paha o ka pehu.
  • Ke pahū ka pehu, hana ʻia nā ʻeha hāmama.
  • Aia ka ʻeha nui i loko a puni nā pehu.

Mai hoʻopā i nā pehu - hiki iā lākou ke lilo i maʻi!

Mai ʻānai a ʻōʻili paha i kou mau pehu, no ka mea hiki i kēia ke lilo i mau ʻeha hāmama a alakaʻi maʻalahi i nā maʻi. Hiki i nā hōʻailona o kahi maʻi ke komo pū me:

  • Ke puka mai nei kahi kahe e like me ka pus keʻokeʻo a melemele paha mai loko mai o ka pehu.
  • Ua pehu ka pehu a ʻeha loa ke ʻano.
  • Hoʻokumu ʻia kahi ʻili melemele ma luna a i ʻole a puni ka pehu.
  • Pehu a hoʻonui ʻia ka ʻili a puni ka pehu.
  • ʻAʻole e ho'ōla ana ka pehu.

E hoʻomanaʻo, inā loaʻa iā ʻoe nā hōʻailona e like me kēia, pono ʻoe e ʻike koke i ke kauka.

Ma hea e ʻike ʻia ai nā hōʻailona?

Hoʻopilikia nā hōʻailona o Pemphigus Vulgaris i kou ʻili a me nā membrane mucous. ʻO nā wahi maʻamau e ʻike ʻia ai nā hōʻailona :

  • Waha a me ka puʻu
  • Ihu
  • Nā maka
  • Wahi ʻōpū kāne `(genitals)`
  • Umauma
  • Ma waho
  • Nā lima a me nā wāwae
  • Iwi poʻo

He aha ke kumu o Pemphigus Vulgaris?

ʻAʻole i ʻike ʻia ke kumu maoli o Pemphigus Vulgaris .

E like me kā mākou i kūkākūkā ai ma mua, he maʻi autoimmune kēia, kahi e kuhi hewa ai nā antibodies o kāu ʻōnaehana pale - nā protein e pale aku i kou kino mai nā germs, bacteria, a me nā mea ʻē aʻe - i kāu mau cell olakino ponoʻī a hoʻouka iā lākou me he mea lā he poʻe komo hewa lākou. ʻO kēia hoʻouka ʻana i nā cell olakino ke kumu o nā hōʻailona o ka pehu ʻana ma ka ʻili a me nā membrane mucous.

Hiki ke hana ʻia kēia kūlana e kekahi mau lāʻau lapaʻau?

ʻAʻole pinepine loa, hiki i kou kino ke pane maikaʻi ʻole i kekahi mau lāʻau lapaʻau a hana i nā hōʻailona o ka pemphigus vulgaris. ʻO kekahi o kēia mau lāʻau lapaʻau:

  • Nā mea hoʻopaʻa ACE: ʻO kēia nā lāʻau lapaʻau i hāʻawi ʻia no ke koko kiʻekiʻe.
  • Nā 'Chelating agents': He mau lāʻau lapaʻau kēia e wehe ai i kekahi mau mea mai ke koko.
  • Nā lāʻau lapaʻau
  • Nā lāʻau anti-inflammatory nonsteroidal (NSAIDs)

He mea laha anei kēia?

ʻAʻole, ʻaʻole he maʻi lele ʻo Pemphigus Vulgaris. ʻAʻole hiki iā ʻoe ke hoʻolaha iā ia i kekahi. No laila, ʻaʻohe mea e hopohopo ai.

Pehea ʻoe e ʻike ai i kēia?

E nānā mua kāu kauka iā ʻoe a nīnau e pili ana i kāu mau hōʻailona. E nīnau lākou e pili ana i kou mōʻaukala olakino a inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like. A laila, e hana paha lākou i kekahi mau hoʻokolohua e hōʻoia i ke kūlana.

He aha nā hoʻokolohua e hana ʻia nei?

No ka hōʻoia ʻana i ka maʻi, hiki i kāu kauka ke hana i kahi biopsy ʻili . Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka ʻili i hoʻopilikia ʻia, mai kahi paha i loaʻa ai nā pehu, a nānā iā ia ma lalo o kahi microscope. Hiki paha i kēia ke komo pū me kahi hoʻāʻo kūikawā i kapa ʻia he hoʻāʻo immunofluorescence.

ʻO kekahi hoʻāʻo he hoʻāʻo koko . Nānā kēia i nā antibodies i loko o kou koko e hoʻoulu ai i kāu mau hōʻailona.

He aha nā lāʻau lapaʻau?

ʻO ka mālama ʻana no ka pemphigus vulgaris e kālele ana i ka kaohi ʻana i nā hōʻailona a me ka pale ʻana i nā pilikia e like me ka maʻi . Hiki ke ʻokoʻa nā koho lapaʻau mai kēlā kanaka a kēia kanaka. Hiki iā lākou ke komo pū me:

  • Inā he maʻi, e hāʻawi iā ia i ka lāʻau.
  • Inā he mau lāʻau lapaʻau e like me ke kumu o nā hōʻailona, ​​​​e hoʻōki i ka lawe ʻana iā lākou.
  • Ke hoʻohana nei i nā lāʻau lapaʻau, nā kirīmi, a me nā ʻaila e ho'ōla i nā ʻeha a hōʻemi i ka ʻeha.
  • E mālama pono i nā ʻeha a me nā pehu, e like me kāu e mālama ai i kahi kuni a ʻeha paha.
  • Inā ʻaʻole hiki iā ʻoe ke ʻai ma muli o nā ʻeha waha, ʻo ka ʻai ʻana i kahi meaʻai palaka, ʻai ʻole, a i ʻole kekahi manawa meaʻai IV, hiki ke kōkua i ka pale ʻana i ka ʻai ʻole.
  • Ke hoʻohana nei i ka lāʻau hoʻomāmā e hōʻemi i ka ʻeha o nā pehu waha.

He aha nā lāʻau lapaʻau no ka hoʻohana ʻana iā Pemphigus Vulgaris?

Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia e hōʻemi i nā hōʻailona, ​​​​pale i nā ʻōhū, a mālama paha i nā maʻi:

  • ʻO nā Corticosteroids, i hoʻopili ʻia i ka ʻili a i lawe ʻia paha ma ka waha, kōkua i ka hoʻēmi ʻana i ka mumū.
  • Nā lāʻau hoʻopau i ka ʻōnaehana pale . ʻO nā laʻana e komo pū me ka azathioprine, cyclosporine, mycophenolate, cyclophosphamide, methotrexate, a i ʻole rituximab. Hana kēia mau mea ma ka hōʻemi ʻana i ka hana o ka ʻōnaehana pale a me ke kāohi ʻana iā ia mai ka hoʻouka ʻana i nā ʻāpana olakino.
  • Nā lāʻau antibiotic a i ʻole antifungal. Hāʻawi ʻia kēia mau mea inā he maʻi.

Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?

ʻAʻole like nā lāʻau lapaʻau a pau, no laila hiki ke loaʻa nā hopena ʻaoʻao ma muli o ke ʻano o ka lāʻau lapaʻau a kāu kauka i kuhikuhi ai. Ma mua o ka hoʻomaka ʻana i kahi lāʻau lapaʻau hou, pono ʻoe e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, nā mea hoʻohui āu e lawe nei, a me nā maʻi āpau āu e loaʻa ai. E nānā kāu kauka i kou kūlana a me ka holomua o kāu lāʻau lapaʻau. Hiki iā ia ke hana i nā hoʻāʻo koko a mimi paha e nānā i nā hopena ʻaoʻao.

He aha kāu e ʻai ai a inu ai i kēia maʻi?

Hiki ke paʻakikī ka ʻai ʻana a me ka inu ʻana i ka wā e loaʻa ai iā ʻoe ʻo Pemphigus Vulgaris, ʻoiai inā he mau pehu a me nā ʻeha i loko o kou waha . No laila, e koho i nā meaʻai palupalu, wai, a me nā meaʻai ʻaʻole ʻōniʻoniʻo . ʻAʻole ʻeha kēia mau mea no nā ʻeha. E pale i nā meaʻai ʻakika, ʻala, a me nā meaʻai ʻōniʻoniʻo (e.g., lemona, ʻalani, chili, ʻuala palai).

Inā ʻaʻole hiki iā ʻoe ke ʻai a inu paha, e ʻike koke i ke kauka.

ʻEhia ka manawa e ʻoi aku ai koʻu maikaʻi ma hope o ka hoʻomaka ʻana o ka lāʻau lapaʻau?

ʻOkoʻa ka manawa ho'ōla mai kēlā kanaka a kēia kanaka. ʻO ka maʻamau, hiki ke hala i kekahi mau pule ma hope o ka hoʻomaka ʻana o ka lāʻau no nā pehu hou e oki ai ke kūkulu ʻana . Ma hope o kēlā, hiki ke hala i kekahi mau mahina no ka ho'ōla ʻana o kou ʻili.

He maʻi mau loa ʻo Pemphigus vulgaris, ʻo ia hoʻi, hiki ke hoʻi hou mai nā hōʻailona ma hope o ka mālama ʻia ʻana.

Hiki ke pale ʻia ka Pemphigus Vulgaris?

No ka mea, ʻaʻole ʻike ʻia ke kumu pololei, ʻaʻohe ala e pale aku ai iā Pemphigus Vulgaris. Eia nō naʻe, hiki i ka lāʻau lapaʻau ke hōʻemi i nā hōʻailona.

He aha ka mea e hana inā loaʻa iaʻu ʻo Pemphigus Vulgaris?

Me ka mālama ʻana, hiki iā ʻoe ke kāohi i ka pemphigus vulgaris. ʻAʻole pinepine kēia ʻano e hoʻopilikia i kou ola. Eia nō naʻe, inā koʻikoʻi nā hōʻailona, ​​​​hiki iā lākou ke hoʻopau iā ʻoe no kekahi manawa. ʻO ke ʻano kēia he mea paʻakikī paha ke hana i kāu mau hana o kēlā me kēia lā a i ʻole e hele i ka hana. ʻAʻole hiki i kekahi poʻe ke hiamoe maikaʻi a hōʻemi paha i ke kaumaha inā ʻaʻole hiki iā lākou ke ʻai pono ma muli o nā ʻeha waha.

He mea kākaʻikahi nā ʻōpala ke ho'ōla ʻia nā pehu. Eia nō naʻe, inā pohā kahi ʻeha a paʻakikī ke ho'ōla, hiki ke waiho i nā ʻōpala a i ʻole nā ​​māka i hoʻololi ʻia ke kala ma ka ʻili.

Inā ʻaʻole mālama ʻia, hiki i nā hōʻailona ke laha ma ke kino a alakaʻi i nā pilikia e hoʻoweliweli i ke ola (e.g., ka ʻai ʻole, ka maloʻo ʻana o ka wai, ka sepsis - he maʻi koʻikoʻi). ʻO ka pilikia koʻikoʻi loa o ka pemphigus vulgaris i mālama ʻole ʻia he maʻi koʻikoʻi, mālama ʻole ʻia.

ʻAʻohe lāʻau lapaʻau no Pemphigus Vulgaris. Ke hoʻomau nei ka noiʻi ʻana i ke kumu a me nā lāʻau lapaʻau hou.

Pehea ka lōʻihi o kēia kūlana?

He maʻi lōʻihi (mau) ʻo Pemphigus Vulgaris, no laila hiki iā ʻoe ke ʻike i nā hōʻailona i kou ola a pau. Hoʻomaka pinepine nā hōʻailona ma waena o 40 a me 60 mau makahiki. Hiki i nā hōʻailona ke hele mai a hele (flare-ups). Hiki i ka lāʻau lapaʻau ke kōkua i ka hōʻemi ʻana i kāu mau hōʻailona.

Pehea lā wau e mālama ai iaʻu iho?

Hiki iā ʻoe ke mālama iā ʻoe iho ma ka home a hoʻokele i nā hōʻailona o Pemphigus Vulgaris ma ka hana ʻana i kēia mau mea:

  • E ʻai i ka meaʻai palupalu, palupalu, a wai hoʻi ke loaʻa iā ʻoe nā ʻeha waha.
  • E mālama i kou mau pehu a me kou mau ʻeha, e like me kou mālama ʻana i kahi ʻoki a i ʻole ke kuni.
  • E ʻaʻahu i nā lole pale a hoʻohana i ka sunscreen e pale i kou ʻili mai nā kukuna UV ʻino o ka lā.
  • E hoʻohana i nā kopa a me nā lotion ʻala ʻole e palupalu i kou ʻili.

Āhea wau e ʻike ai i ke kauka?

Pono ʻoe e ʻike i ke kauka inā loaʻa iā ʻoe kēia mau hōʻailona:

  • Inā ʻaʻole e ola nā ʻeha.
  • Inā he mau pehu ma luna o kahi ʻāpana nui o ke kino.
  • Inā e kahe ana nā pehu ʻeha i kahi wai melemele a keʻokeʻo paha, a inā paha e kū mai ana kahi ʻili melemele a puni lākou (he mau hōʻailona paha kēia o ka maʻi).
  • Inā he pehu i loko a puni paha o nā pehu.
  • Inā paʻakikī ke ʻai a me ka inu.
  • Inā loaʻa iā ʻoe nā hōʻailona e like me ke kuni, ka ʻūhā, a me ka ʻehaʻeha o nā ʻiʻo.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

Ke hele ʻoe e ʻike i ke kauka, hiki iā ʻoe ke nīnau i nā nīnau e like me kēia:

  • He aha ke ʻano o ka lāʻau lapaʻau āu e paipai nei?
  • Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
  • Pehea e hiki ai iaʻu ke pale aku i nā maʻi?
  • Pehea e hiki ai iaʻu ke mālama i koʻu mau ʻeha ma ka home?

He aha ka ʻokoʻa ma waena o Pemphigus Vulgaris a me Bullous Pemphigoid?

ʻO Pemphigus Vulgaris a me Bullous Pemphigoid nā maʻi autoimmune e hoʻopilikia i kou ʻili. Hoʻopilikia pinepine nā mea ʻelua i nā poʻe ma luna o 65 mau makahiki. Eia nō naʻe, ʻo ka ʻokoʻa nui ma waena o nā maʻi ʻelua e pili ana i nā ʻeha e kū mai ana a me ke kumu .

Hoʻokumu ʻo Pemphigus vulgaris i nā ʻūlū liʻiliʻi piha i ka wai ma kou ʻili a me nā membrane mucous, e like me kou waha.

ʻO ka bullous pemphigoid ke kumu o ka ʻili ʻānai, piʻi, a ʻulaʻula i nā kiko ma ka ʻili i kapa ʻia he hive-like welts . Uhi pinepine ʻia kēia mau kiko me nā pehu paʻakikī a ʻaʻole i haki.

E lawe i ka leka i ka home

He maʻi ʻili lōʻihi ka Pemphigus Vulgaris e mau ana no ke ola holoʻokoʻa. Hiki ke ʻoluʻolu ʻole nā ​​hōʻailona a hiki ke hoʻoulu i nā ʻeha ʻili a me ka waha. ʻO ka mea nui loa, ʻo ia ka ʻai pono ʻana a pale i nā hemahema meaʻai ke loaʻa iā ʻoe kēia maʻi . E kamaʻilio me kāu kauka e pili ana i nā koho lapaʻau maikaʻi loa no kāu mau hōʻailona. Mai hopohopo, ʻo ka mea nui loa, ʻo ia ka makaʻala a loaʻa ka lāʻau kūpono.


pemphigus vulgaris, maʻi ʻili, pehu, ʻōpū waha, autoimmune, pale ʻana, maʻi ʻili

Frequently Asked Questions (FAQ)

He aha nā lāʻau lapaʻau no ka hoʻohana ʻana iā Pemphigus Vulgaris?

Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia e hōʻemi i nā hōʻailona, ​​​​pale i nā ʻōhū, a mālama paha i nā maʻi:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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