Loaʻa iā ʻoe i kekahi manawa nā pehu ʻeha a me nā ʻeha ma kou kino, ʻoi aku hoʻi i loko o kou waha? Poha maʻalahi lākou a paʻakikī ke ʻai a inu paha? A laila he mea nui paha kēia iā ʻoe. Kāhea mākou i kēia maʻi ʻo Pemphigus Vulgaris. Mai hopohopo, e kamaʻilio maʻalahi kākou e pili ana.
He aha ka maʻi ʻo Pemphigus Vulgaris?
I ka ʻōlelo maʻalahi, ʻo Pemphigus Vulgaris kahi maʻi i hoʻokumu ʻia e kahi hana hewa i loko o kāu ʻōnaehana pale . Kāhea mākou i kēia he maʻi autoimmune. ʻO ke kuleana o kā mākou ʻōnaehana pale, ʻo ia ke pale iā mākou mai nā germs haole, bacteria, a me nā virus. Ua like ia me kahi pūʻali koa e pale ana i kahi ʻāina. Eia nō naʻe, ma Pemphigus Vulgaris, hoʻouka hewa kāu ʻōnaehana pale ponoʻī i kāu mau ʻili olakino a me nā membrane mucous. ʻO nā membrane mucous nā uhi palupalu a pulu e hoʻopili ana i loko o kou waha, ihu, puʻu, ala hanu, ala ʻai, ala mimi, a me ke ala genital.
ʻO kēia hoʻouka kaua ke kumu o nā pehu e hana ʻia ma ka ʻili a me nā membrane mucous. ʻO ka pinepine, ʻo ka poʻe me Pemphigus Vulgaris e loaʻa mua nā pehu i loko o ka waha . He palupalu loa kēia mau pehu a pohā maʻalahi. A laila lilo lākou i mau ʻeha ʻeha.
ʻO Pemphigus vulgaris ke ʻano maʻamau o ka pemphigus.
Pehea ka maʻamau o kēia? ʻO wai ka mea i loaʻa pinepine?
He maʻi laha ʻole ʻo Pemphigus Vulgaris. ʻOiai hiki ke hoʻopilikia i kekahi, hoʻopilikia pinepine ia i ka poʻe ma luna o 40 mau makahiki. He mea laha ʻole loa ia i nā pēpē a me nā keiki.
Pehea ka hopena o Pemphigus Vulgaris i koʻu kino?
Hoʻomaka pinepine nā hōʻailona o Pemphigus Vulgaris i loko o kou waha . Hoʻokumu ʻia nā pehu ʻeha ma laila, e paʻakikī ai ka ʻai ʻana a me ka inu ʻana. E noʻonoʻo he mau ʻeha ʻeha ma kou waha a puni. ʻAʻole hiki iā ʻoe ke nānā aku i kāu meaʻai punahele no ka mea he ʻeha a ʻā. He pilikia kekahi poʻe i ka inu ʻana i ka wai.
Ma hope o ka hoʻopilikia ʻana i nā membrane mucous o ka waha, hiki i nā hōʻailona ke laha i ka ʻili ma nā wahi ʻē aʻe o kou kino. He lahilahi loa kēia mau pehu, no laila e pohā maʻalahi lākou. Ke pohā nā pehu, hiki iā lākou ke hoʻokahe i ka wai, a i kekahi manawa e puka mai ka pus. A laila lilo kēia mau wahi i mau ʻeha hāmama.
He aha nā hōʻailona o kēia?
ʻAʻole like nā hōʻailona o ka maʻi Pemphigus Vulgaris i nā kānaka a pau, a hiki ke ʻokoʻa ko lākou koʻikoʻi mai kēlā kanaka a kēia kanaka . ʻO nā hōʻailona maʻamau:
- ʻIke ʻia kahi pehu piha i ka wai. He apo ʻulaʻula paha kēia a puni, a he keʻokeʻo poni māmā paha ke kikowaena.
- Poha maʻalahi nā pehu, e kahe ana ka wai maopopo a i ʻole ke koko paha.
- Hiki ke hana ʻia kahi ʻōpala a unahi paha ma luna a puni paha o ka pehu.
- Ke ʻili nei ka ʻili ma luna a puni paha o ka pehu.
- Ke pahū ka pehu, hana ʻia nā ʻeha hāmama.
- Aia ka ʻeha nui i loko a puni nā pehu.
Mai hoʻopā i nā pehu - hiki iā lākou ke lilo i maʻi!
Mai ʻānai a ʻōʻili paha i kou mau pehu, no ka mea hiki i kēia ke lilo i mau ʻeha hāmama a alakaʻi maʻalahi i nā maʻi. Hiki i nā hōʻailona o kahi maʻi ke komo pū me:
- Ke puka mai nei kahi kahe e like me ka pus keʻokeʻo a melemele paha mai loko mai o ka pehu.
- Ua pehu ka pehu a ʻeha loa ke ʻano.
- Hoʻokumu ʻia kahi ʻili melemele ma luna a i ʻole a puni ka pehu.
- Pehu a hoʻonui ʻia ka ʻili a puni ka pehu.
- ʻAʻole e ho'ōla ana ka pehu.
E hoʻomanaʻo, inā loaʻa iā ʻoe nā hōʻailona e like me kēia, pono ʻoe e ʻike koke i ke kauka.
Ma hea e ʻike ʻia ai nā hōʻailona?
Hoʻopilikia nā hōʻailona o Pemphigus Vulgaris i kou ʻili a me nā membrane mucous. ʻO nā wahi maʻamau e ʻike ʻia ai nā hōʻailona :
- Waha a me ka puʻu
- Ihu
- Nā maka
- Wahi ʻōpū kāne `(genitals)`
- Umauma
- Ma waho
- Nā lima a me nā wāwae
- Iwi poʻo
He aha ke kumu o Pemphigus Vulgaris?
ʻAʻole i ʻike ʻia ke kumu maoli o Pemphigus Vulgaris .
E like me kā mākou i kūkākūkā ai ma mua, he maʻi autoimmune kēia, kahi e kuhi hewa ai nā antibodies o kāu ʻōnaehana pale - nā protein e pale aku i kou kino mai nā germs, bacteria, a me nā mea ʻē aʻe - i kāu mau cell olakino ponoʻī a hoʻouka iā lākou me he mea lā he poʻe komo hewa lākou. ʻO kēia hoʻouka ʻana i nā cell olakino ke kumu o nā hōʻailona o ka pehu ʻana ma ka ʻili a me nā membrane mucous.
Hiki ke hana ʻia kēia kūlana e kekahi mau lāʻau lapaʻau?
ʻAʻole pinepine loa, hiki i kou kino ke pane maikaʻi ʻole i kekahi mau lāʻau lapaʻau a hana i nā hōʻailona o ka pemphigus vulgaris. ʻO kekahi o kēia mau lāʻau lapaʻau:
- Nā mea hoʻopaʻa ACE: ʻO kēia nā lāʻau lapaʻau i hāʻawi ʻia no ke koko kiʻekiʻe.
- Nā 'Chelating agents': He mau lāʻau lapaʻau kēia e wehe ai i kekahi mau mea mai ke koko.
- Nā lāʻau lapaʻau
- Nā lāʻau anti-inflammatory nonsteroidal (NSAIDs)
He mea laha anei kēia?
ʻAʻole, ʻaʻole he maʻi lele ʻo Pemphigus Vulgaris. ʻAʻole hiki iā ʻoe ke hoʻolaha iā ia i kekahi. No laila, ʻaʻohe mea e hopohopo ai.
Pehea ʻoe e ʻike ai i kēia?
E nānā mua kāu kauka iā ʻoe a nīnau e pili ana i kāu mau hōʻailona. E nīnau lākou e pili ana i kou mōʻaukala olakino a inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like. A laila, e hana paha lākou i kekahi mau hoʻokolohua e hōʻoia i ke kūlana.
He aha nā hoʻokolohua e hana ʻia nei?
No ka hōʻoia ʻana i ka maʻi, hiki i kāu kauka ke hana i kahi biopsy ʻili . Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka ʻili i hoʻopilikia ʻia, mai kahi paha i loaʻa ai nā pehu, a nānā iā ia ma lalo o kahi microscope. Hiki paha i kēia ke komo pū me kahi hoʻāʻo kūikawā i kapa ʻia he hoʻāʻo immunofluorescence.
ʻO kekahi hoʻāʻo he hoʻāʻo koko . Nānā kēia i nā antibodies i loko o kou koko e hoʻoulu ai i kāu mau hōʻailona.
He aha nā lāʻau lapaʻau?
ʻO ka mālama ʻana no ka pemphigus vulgaris e kālele ana i ka kaohi ʻana i nā hōʻailona a me ka pale ʻana i nā pilikia e like me ka maʻi . Hiki ke ʻokoʻa nā koho lapaʻau mai kēlā kanaka a kēia kanaka. Hiki iā lākou ke komo pū me:
- Inā he maʻi, e hāʻawi iā ia i ka lāʻau.
- Inā he mau lāʻau lapaʻau e like me ke kumu o nā hōʻailona, e hoʻōki i ka lawe ʻana iā lākou.
- Ke hoʻohana nei i nā lāʻau lapaʻau, nā kirīmi, a me nā ʻaila e ho'ōla i nā ʻeha a hōʻemi i ka ʻeha.
- E mālama pono i nā ʻeha a me nā pehu, e like me kāu e mālama ai i kahi kuni a ʻeha paha.
- Inā ʻaʻole hiki iā ʻoe ke ʻai ma muli o nā ʻeha waha, ʻo ka ʻai ʻana i kahi meaʻai palaka, ʻai ʻole, a i ʻole kekahi manawa meaʻai IV, hiki ke kōkua i ka pale ʻana i ka ʻai ʻole.
- Ke hoʻohana nei i ka lāʻau hoʻomāmā e hōʻemi i ka ʻeha o nā pehu waha.
He aha nā lāʻau lapaʻau no ka hoʻohana ʻana iā Pemphigus Vulgaris?
Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me kēia e hōʻemi i nā hōʻailona, pale i nā ʻōhū, a mālama paha i nā maʻi:
- ʻO nā Corticosteroids, i hoʻopili ʻia i ka ʻili a i lawe ʻia paha ma ka waha, kōkua i ka hoʻēmi ʻana i ka mumū.
- Nā lāʻau hoʻopau i ka ʻōnaehana pale . ʻO nā laʻana e komo pū me ka azathioprine, cyclosporine, mycophenolate, cyclophosphamide, methotrexate, a i ʻole rituximab. Hana kēia mau mea ma ka hōʻemi ʻana i ka hana o ka ʻōnaehana pale a me ke kāohi ʻana iā ia mai ka hoʻouka ʻana i nā ʻāpana olakino.
- Nā lāʻau antibiotic a i ʻole antifungal. Hāʻawi ʻia kēia mau mea inā he maʻi.
Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
ʻAʻole like nā lāʻau lapaʻau a pau, no laila hiki ke loaʻa nā hopena ʻaoʻao ma muli o ke ʻano o ka lāʻau lapaʻau a kāu kauka i kuhikuhi ai. Ma mua o ka hoʻomaka ʻana i kahi lāʻau lapaʻau hou, pono ʻoe e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, nā mea hoʻohui āu e lawe nei, a me nā maʻi āpau āu e loaʻa ai. E nānā kāu kauka i kou kūlana a me ka holomua o kāu lāʻau lapaʻau. Hiki iā ia ke hana i nā hoʻāʻo koko a mimi paha e nānā i nā hopena ʻaoʻao.
He aha kāu e ʻai ai a inu ai i kēia maʻi?
Hiki ke paʻakikī ka ʻai ʻana a me ka inu ʻana i ka wā e loaʻa ai iā ʻoe ʻo Pemphigus Vulgaris, ʻoiai inā he mau pehu a me nā ʻeha i loko o kou waha . No laila, e koho i nā meaʻai palupalu, wai, a me nā meaʻai ʻaʻole ʻōniʻoniʻo . ʻAʻole ʻeha kēia mau mea no nā ʻeha. E pale i nā meaʻai ʻakika, ʻala, a me nā meaʻai ʻōniʻoniʻo (e.g., lemona, ʻalani, chili, ʻuala palai).
Inā ʻaʻole hiki iā ʻoe ke ʻai a inu paha, e ʻike koke i ke kauka.
ʻEhia ka manawa e ʻoi aku ai koʻu maikaʻi ma hope o ka hoʻomaka ʻana o ka lāʻau lapaʻau?
ʻOkoʻa ka manawa ho'ōla mai kēlā kanaka a kēia kanaka. ʻO ka maʻamau, hiki ke hala i kekahi mau pule ma hope o ka hoʻomaka ʻana o ka lāʻau no nā pehu hou e oki ai ke kūkulu ʻana . Ma hope o kēlā, hiki ke hala i kekahi mau mahina no ka ho'ōla ʻana o kou ʻili.
He maʻi mau loa ʻo Pemphigus vulgaris, ʻo ia hoʻi, hiki ke hoʻi hou mai nā hōʻailona ma hope o ka mālama ʻia ʻana.
Hiki ke pale ʻia ka Pemphigus Vulgaris?
No ka mea, ʻaʻole ʻike ʻia ke kumu pololei, ʻaʻohe ala e pale aku ai iā Pemphigus Vulgaris. Eia nō naʻe, hiki i ka lāʻau lapaʻau ke hōʻemi i nā hōʻailona.
He aha ka mea e hana inā loaʻa iaʻu ʻo Pemphigus Vulgaris?
Me ka mālama ʻana, hiki iā ʻoe ke kāohi i ka pemphigus vulgaris. ʻAʻole pinepine kēia ʻano e hoʻopilikia i kou ola. Eia nō naʻe, inā koʻikoʻi nā hōʻailona, hiki iā lākou ke hoʻopau iā ʻoe no kekahi manawa. ʻO ke ʻano kēia he mea paʻakikī paha ke hana i kāu mau hana o kēlā me kēia lā a i ʻole e hele i ka hana. ʻAʻole hiki i kekahi poʻe ke hiamoe maikaʻi a hōʻemi paha i ke kaumaha inā ʻaʻole hiki iā lākou ke ʻai pono ma muli o nā ʻeha waha.
He mea kākaʻikahi nā ʻōpala ke ho'ōla ʻia nā pehu. Eia nō naʻe, inā pohā kahi ʻeha a paʻakikī ke ho'ōla, hiki ke waiho i nā ʻōpala a i ʻole nā māka i hoʻololi ʻia ke kala ma ka ʻili.
Inā ʻaʻole mālama ʻia, hiki i nā hōʻailona ke laha ma ke kino a alakaʻi i nā pilikia e hoʻoweliweli i ke ola (e.g., ka ʻai ʻole, ka maloʻo ʻana o ka wai, ka sepsis - he maʻi koʻikoʻi). ʻO ka pilikia koʻikoʻi loa o ka pemphigus vulgaris i mālama ʻole ʻia he maʻi koʻikoʻi, mālama ʻole ʻia.
ʻAʻohe lāʻau lapaʻau no Pemphigus Vulgaris. Ke hoʻomau nei ka noiʻi ʻana i ke kumu a me nā lāʻau lapaʻau hou.
Pehea ka lōʻihi o kēia kūlana?
He maʻi lōʻihi (mau) ʻo Pemphigus Vulgaris, no laila hiki iā ʻoe ke ʻike i nā hōʻailona i kou ola a pau. Hoʻomaka pinepine nā hōʻailona ma waena o 40 a me 60 mau makahiki. Hiki i nā hōʻailona ke hele mai a hele (flare-ups). Hiki i ka lāʻau lapaʻau ke kōkua i ka hōʻemi ʻana i kāu mau hōʻailona.
Pehea lā wau e mālama ai iaʻu iho?
Hiki iā ʻoe ke mālama iā ʻoe iho ma ka home a hoʻokele i nā hōʻailona o Pemphigus Vulgaris ma ka hana ʻana i kēia mau mea:
- E ʻai i ka meaʻai palupalu, palupalu, a wai hoʻi ke loaʻa iā ʻoe nā ʻeha waha.
- E mālama i kou mau pehu a me kou mau ʻeha, e like me kou mālama ʻana i kahi ʻoki a i ʻole ke kuni.
- E ʻaʻahu i nā lole pale a hoʻohana i ka sunscreen e pale i kou ʻili mai nā kukuna UV ʻino o ka lā.
- E hoʻohana i nā kopa a me nā lotion ʻala ʻole e palupalu i kou ʻili.
Āhea wau e ʻike ai i ke kauka?
Pono ʻoe e ʻike i ke kauka inā loaʻa iā ʻoe kēia mau hōʻailona:
- Inā ʻaʻole e ola nā ʻeha.
- Inā he mau pehu ma luna o kahi ʻāpana nui o ke kino.
- Inā e kahe ana nā pehu ʻeha i kahi wai melemele a keʻokeʻo paha, a inā paha e kū mai ana kahi ʻili melemele a puni lākou (he mau hōʻailona paha kēia o ka maʻi).
- Inā he pehu i loko a puni paha o nā pehu.
- Inā paʻakikī ke ʻai a me ka inu.
- Inā loaʻa iā ʻoe nā hōʻailona e like me ke kuni, ka ʻūhā, a me ka ʻehaʻeha o nā ʻiʻo.
He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?
Ke hele ʻoe e ʻike i ke kauka, hiki iā ʻoe ke nīnau i nā nīnau e like me kēia:
- He aha ke ʻano o ka lāʻau lapaʻau āu e paipai nei?
- Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
- Pehea e hiki ai iaʻu ke pale aku i nā maʻi?
- Pehea e hiki ai iaʻu ke mālama i koʻu mau ʻeha ma ka home?
He aha ka ʻokoʻa ma waena o Pemphigus Vulgaris a me Bullous Pemphigoid?
ʻO Pemphigus Vulgaris a me Bullous Pemphigoid nā maʻi autoimmune e hoʻopilikia i kou ʻili. Hoʻopilikia pinepine nā mea ʻelua i nā poʻe ma luna o 65 mau makahiki. Eia nō naʻe, ʻo ka ʻokoʻa nui ma waena o nā maʻi ʻelua e pili ana i nā ʻeha e kū mai ana a me ke kumu .
Hoʻokumu ʻo Pemphigus vulgaris i nā ʻūlū liʻiliʻi piha i ka wai ma kou ʻili a me nā membrane mucous, e like me kou waha.
ʻO ka bullous pemphigoid ke kumu o ka ʻili ʻānai, piʻi, a ʻulaʻula i nā kiko ma ka ʻili i kapa ʻia he hive-like welts . Uhi pinepine ʻia kēia mau kiko me nā pehu paʻakikī a ʻaʻole i haki.
E lawe i ka leka i ka home
He maʻi ʻili lōʻihi ka Pemphigus Vulgaris e mau ana no ke ola holoʻokoʻa. Hiki ke ʻoluʻolu ʻole nā hōʻailona a hiki ke hoʻoulu i nā ʻeha ʻili a me ka waha. ʻO ka mea nui loa, ʻo ia ka ʻai pono ʻana a pale i nā hemahema meaʻai ke loaʻa iā ʻoe kēia maʻi . E kamaʻilio me kāu kauka e pili ana i nā koho lapaʻau maikaʻi loa no kāu mau hōʻailona. Mai hopohopo, ʻo ka mea nui loa, ʻo ia ka makaʻala a loaʻa ka lāʻau kūpono.
pemphigus vulgaris, maʻi ʻili, pehu, ʻōpū waha, autoimmune, pale ʻana, maʻi ʻili











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