He aha ka Sneddon Syndrome? Loaʻa iā ʻoe nā kiko e like me kēia ma kou ʻili? E kamaʻilio kākou!

Ua ʻike anei ʻoe he mau kiko poni ko kekahi poʻe ma ko lākou ʻili, ʻoi aku hoʻi ma ko lākou mau lālā, ma ke ʻano like me ka ʻupena? I kekahi manawa hoʻopiʻi pū lākou i ka poniuniu a me ke poʻo ʻeha. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi laha ʻole nona nā hōʻailona like, akā ʻaʻohe mea e kamaʻilio nui e pili ana i ia mea. Ua kapa ʻia kēia ʻo Sneddon Syndrome.

He aha ka Sneddon Syndrome? I ka pōkole...

I ka ʻōlelo maʻalahi, ʻo Sneddon Syndrome kahi maʻi e hoʻopilikia ana i nā kīʻaha koko liʻiliʻi a me waena i loko o kou kino. E noʻonoʻo i kēia mau kīʻaha koko e like me nā paipu e lawe ana i ka wai. I loko o kēia maʻi, ʻo ka papa laumania o nā cell i loko o kou mau kīʻaha koko, i kapa ʻia ʻo endothelium i ka lāʻau lapaʻau, e ulu wikiwiki a ʻoi aku ma mua o ka mea e pono ai. He aha ka mea e hana ai? Hoʻemi kēia mau cell keu i ka hakahaka i loko o nā kīʻaha koko, e like me ka wā e paʻa ai ka lepo i loko o kahi paipu, lilo ia i mea paʻakikī no ka wai e kahe. ʻO kēia ke kumu o ke kahe ʻana o ke koko e ālai ʻia.

He kūlana kēia e pono e kiaʻi ʻia no kekahi manawa, no ka mea, hiki ke lilo i mea ʻino aʻe i ka hala ʻana o ka manawa. ʻO ka poʻe me kēia kūlana, ʻoi aku ka nui o ka pilikia o nā ʻūpā koko. Hiki iā lākou ke hoʻomohala i nā pilikia ʻili a me nā pilikia neurological. I kekahi manawa ua kapa ʻia ʻo Sneddon-Champion syndrome. ʻO kekahi inoa ʻē aʻe ʻo livedo reticularis racemosa. Hiki i kēia kūlana ke hana i nā hahau a me nā hoʻouka ischemic transient (TIAs) i kekahi poʻe.

Pehea ka maʻamau o kēia ʻano? ʻO wai ka mea maʻamau loa i waena o lākou?

ʻO ka ʻoiaʻiʻo, he maʻi laha ʻole ka Sneddon Syndrome. Ma ke ʻano helu, ua manaʻo ʻia he ʻehā wale nō kānaka i loko o hoʻokahi miliona e loaʻa ana i kēlā me kēia makahiki. ʻO ia hoʻi ma kahi o hoʻokahi i loko o ʻelua a me ka hapa haneli tausani.

Eia kekahi, ʻoi aku ka maʻamau o ke ʻano i nā wahine ma mua o nā kāne. Ma kahi o 80% o ka poʻe me ka maʻi Sneddon he mau wahine. ʻIke pinepine ʻia lākou me ke ʻano ma kahi o 40 mau makahiki.

He aha nā hōʻailona o kēia? Pehea ʻoe e ʻike ai?

Hiki i ke kanaka me ka Sneddon Syndrome ke ʻike i nā ʻano hōʻailona like ʻole. Eia naʻe, ʻaʻole ʻike ʻia kēia mau hōʻailona a pau i ka manawa hoʻokahi. Hiki ke ʻike ʻia kekahi mau hōʻailona i nā makahiki ma hope o ka hoʻomaka ʻana o nā pilikia neurological. A i ʻole hiki i kekahi poʻe ke ʻike mua i nā pilikia maka a i ʻole nā ​​​​​​ʻeha poʻo. Eia kekahi o nā hōʻailona:

• He ʻano e like me ka ʻupena ma ka ʻili:ʻO kēia ka hōʻailona mua a ka poʻe he nui e ʻike ai. Hoʻomohala ka ʻili i kahi moʻo o nā kiko ʻulaʻula-poni, e like me nā ʻupena lawaiʻa a i ʻole nā ​​​​​​kikona ma kekahi mau nahesa. ʻAʻole kēia he mea ʻeha. Inā ʻike ʻia kēia mau kiko ma kou mau lima a me kou mau wāwae, ʻike ʻia i ke anu, a nalowale i ka wā e mahana ai ʻoe, ua kapa ʻia ʻo livedo reticularis. Eia nō naʻe, inā ʻike ʻia kēia ʻano ma kou umauma, ʻōpū, a i ʻole nā ​​​​​​puʻupuʻu, a ʻaʻole nalo ʻoiai ke mahana ʻoe, ua kapa ʻia ʻo livedo racemosa.
• ʻEha poʻo: Hiki ke loaʻa pinepine, i kekahi manawa ʻeha poʻo nui.
• Pōniuniu: He manaʻo o ka wili ʻana.
• Nā hahau a me nā TIA: E like me ka mea i ʻōlelo ʻia ma mua, ʻo ia kekahi o nā mea koʻikoʻi loa.
• Nā loli i ke ʻano a me ka noʻonoʻo: Aia paha he mau loli i kou ʻano, ke ʻano o kou noʻonoʻo ʻana, a me kou hiki ke hoʻomanaʻo.
• Nā pilikia puʻupaʻa: ʻAʻole kēia i maʻamau, akā hiki i kekahi poʻe ke loaʻa nā pilikia puʻupaʻa.

ʻO ka mea nui loa, inā loaʻa iā ʻoe kekahi a ʻelua paha o kēia mau hōʻailona, ​​​​ʻoiai inā he ʻeha poʻo a me ka poniuniu kou me ke ʻano ʻili e like me ka mesh, pono ʻoe e ʻike i ke kauka no ka ʻōlelo aʻo.

No ke aha i loaʻa ai ka Sneddon Syndrome? He aha ke kumu?

He mea kēia i hiki ʻole i nā kauka ke hoʻomaopopo. ʻAʻole i loaʻa ke kumu kikoʻī o ka Sneddon Syndrome. ʻO ia ke kumu i kapa ʻia ai he idiopathic, ʻo ia hoʻi, ʻaʻole ʻike ʻia ke kumu. Eia nō naʻe, no ka mea ua ʻike ʻia kēia maʻi e holo i loko o kekahi mau ʻohana, ua manaʻo ʻia he ʻāpana genetic paha .

Eia kekahi, i kekahi mau hihia, hiki ke hana pū ʻia ka maʻi Sneddon me nā kūlana autoimmune ʻē aʻe . ʻO kahi maʻi autoimmune he kūlana wale nō ia e hoʻouka ai ka ʻōnaehana pale o ko mākou kino i nā cell o ko mākou kino ponoʻī. Inā loaʻa iā ʻoe ka maʻi Sneddon, hiki ke pili pū me kekahi o kēia mau kūlana:

• Lupus
• ʻO ka maʻi Antiphospholipid
• ʻO ka maʻi o Behçet
• Maʻi pili pili i hui pū ʻia

Pehea e ʻike ʻia ai kēia? He aha nā hoʻokolohua e hana ʻia ai?

Inā kānalua kāu kauka he Sneddon Syndrome kou ma muli o kāu mau hōʻailona, ​​e kauoha lākou i kekahi mau hoʻokolohua like ʻole. E nānā kēia mau hoʻokolohua i:

• Kou koko: E nānā i nā hōʻailona o nā maʻi autoimmune a me nā pilikia o ke kāpili ʻana o ke koko.
• Kou puʻuwai: E nānā i ke kahe ʻana o ke koko ma kou puʻuwai a me nā kīʻaha koko.
• Kou lolo:E nānā inā ua hōʻino ʻia ka lolo. Hiki ke kumu o ka hahau ʻana.
• Kou ʻili: Lawe ʻia kahi ʻāpana ʻili liʻiliʻi a nānā ʻia (biopsy ʻili) e ʻike inā he mau loli cell i ʻike ʻia e kēia maʻi.

Hiki i kēia mau hoʻokolohua ke komo pū me nā hoʻokolohua kiʻi kūikawā . Eia kekahi laʻana:

• Nā scan MRI (kiʻi resonance magnetic - nā scan MRI)
• ʻO ke kiʻi CT `(tomography i helu ʻia - nā kiʻi CT)`
• ʻO Angiograms (kahi X-ray kūikawā e nānā i ke kūlana o nā kīʻaha koko)

Hiki i nā kauka ke hōʻoia pololei i kēia maʻi ma hope o ka hana ʻana i kēia mau hoʻokolohua āpau.

Pehea e mālama ʻia ai? (Lāʻau Lapaʻau) He aha nā koho?

ʻAʻole maopopo loa ke ala maikaʻi loa e mālama ai i ka Sneddon Syndrome. ʻO kekahi kumu no kēia, he kakaikahi ka poʻe me ke kūlana a he mea paʻakikī ke loaʻa ka poʻe lawa e hana i nā hoʻokolohua lapaʻau nui.

Eia nō naʻe, aia nā koho lapaʻau like ʻole ma muli o nā hōʻailona o ka maʻi. Eia kekahi laʻana, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me:

• Nā lāʻau anticoagulant a i ʻole antiplatelet: Pale kēia i ke kāpili ʻana o ke koko a hoʻomaʻamaʻa i ke kahe koko.
• Nā Vasodilators: No ka laʻana, nifedipine. Hoʻonui kēia i nā kīʻaha koko a hoʻonui i ke kahe koko. Hāʻawi pinepine kēia i ka hōʻoluʻolu mai nā hōʻailona ʻili.
• Nā mea hoʻopaʻa i ka enzyme hoʻololi-angiotensin (ACE inhibitors): Kōkua kēia i ka hoʻōki ʻana i ka ulu ʻana o kēlā mau cell endothelial i ʻōlelo ʻia ma mua.

He mea nui: Inā loaʻa iā ʻoe ka maʻi Sneddon, pono ʻoe e pale loa i ka puhipaka a me ka hoʻohana ʻana i nā pila hoʻomalu hānau i loaʻa ka estrogen. Hiki i kēia mau mea ke hoʻonui i ka ʻino o ke kūlana.

Aia kekahi ala e pale aku ai i kēia maʻi?

ʻO ka mea pōʻino, ma muli o ka ʻike o kēia manawa, ʻaʻohe ala e pale aku ai i ka Sneddon Syndrome. No ka mea, ʻaʻole ʻike ʻia ke kumu pololei, he paʻakikī ke ʻōlelo pehea e pale aku ai.

He aha ka mea e hiki mai ana inā hoʻomau kēia kūlana? (Wānana) He aha kā mākou e manaʻo ai no ka wā e hiki mai ana?

I nā hihia he nui, hoʻololi ka Sneddon Syndrome i ka ʻōnaehana nerve. No ka laʻana , hiki ke ulu mālie ka nalowale o ka hoʻomanaʻo a me ka paʻakikī o ka ʻōlelo ʻana i ka hala ʻana o ka manawa. I kekahi mau hihia, hiki ke ʻike ʻia ka poʻe me Sneddon Syndrome me ka dementia hoʻomaka mua. No laila he mea nui e makaʻala i kēia mau hōʻailona.

Aia anei kahi lāʻau lapaʻau piha?

Wahi a ka ʻike lapaʻau o kēia manawa, ʻo Sneddon SyndromeʻAʻole i loaʻa kahi "lāʻau lapaʻau" piha. ʻO ka pahuhopu o nā lāʻau lapaʻau ke kāohi i nā hōʻailona a hoʻāʻo e pale i ka maʻi mai ka ʻino ʻana.

Āhea ʻoe e ʻimi ai i ke aʻo lapaʻau?

Inā loaʻa iā ʻoe nā hōʻailona o ka Sneddon Syndrome, e like me ke ʻano ʻili e like me ka mesh, ka ʻeha poʻo, a me ka poniuniu, e ʻike koke i ke kauka. Mai hoʻokaʻulua, ʻoiai inā loaʻa iā ʻoe nā hōʻailona ʻē aʻe me nā kiko ʻili.

Inā ua ʻike mua ʻia ʻoe me ka maʻi Sneddon, inā loaʻa iā ʻoe nā hōʻailona hou, a inā manaʻo ʻoe e ʻoi aku ka ʻino o kāu mau hōʻailona, ​​e hoʻomaopopo koke i kāu kauka.

Eia kekahi, inā ʻike ʻoe i kekahi mau hōʻailona o ka hahau ʻana, mai hoʻokaʻulua. E kelepona koke i ka 911 (ma Sri Lanka, 1990 Suwaseriya Ambulance Service) a i ʻole e hele i ka keʻena pilikia o ka haukapila kokoke loa. Hiki i nā hōʻailona o ka hahau ʻana ke komo pū me:

• ʻEha poʻo koʻikoʻi koke.
• Nā pilikia ʻike (e like me ka nalowale o ka ʻike ma kekahi maka, ka pohihihi o nā maka ʻelua).
• Ka maneʻo a nāwaliwali paha ma kekahi ʻaoʻao a i ʻole nā ​​ʻaoʻao ʻelua o ke kino.
• Ka paʻakikī o ka hele wāwae.
• Ka paʻakikī i ka ʻōlelo ʻana a i ʻole ka hoʻomaopopo ʻana i ka mea a haʻi e ʻōlelo nei.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He maʻi laha ʻole a he maʻi koʻikoʻi paha ka Sneddon Syndrome. Eia nō naʻe, inā ua ʻike ʻia ʻoe me kēia maʻi, e hahai pono i nā ʻōlelo a kāu kauka. E lawe i kāu lāʻau lapaʻau i ka manawa kūpono, e mālama i kāu mau manawa hoʻopaʻa, a mai poina i nā papa hana hoʻāʻo.

Hiki iā ʻoe ke kōkua iā ʻoe iho ma ka lawe ʻana i kahi nohona olakino no ka puʻuwai. ʻO ia hoʻi ka ʻai ʻana i ka meaʻai kaulike, ka hoʻoikaika kino, a me ka pale ʻana i ka puhipaka a me ka kaohi hānau ʻana me ka estrogen. Hiki i kēia mau mea ke kōkua nui i ka kaohi ʻana i kou kūlana. Mai hopohopo, hiki iā ʻoe ke ola me kēia kūlana me ka mālama lapaʻau kūpono a me nā hoʻololi nohona.

ʻO ka maʻi Sneddon, ka maʻi o ke kīʻaha koko, nā kiko ʻili, ka hahau ʻana, ka neuropathy, ka livedo reticularis, nā ʻūpā koko