Ke polū koke nei kāu pēpē? He Tetralogy o Fallot paha ia.

Ua makaʻu paha ʻoe i ka wā e polū koke ai kāu keiki liʻiliʻi? A i ʻole he paʻakikī iā ia ke hanu i ka wā e hānai waiū ana, e uē ana, a i ʻole e huli ana? He mea maʻamau no kekahi makuahine a makua paha ke makaʻu i ka ʻike ʻana i nā mea e like me kēia. I kēia lā, ke kamaʻilio nei mākou e pili ana iā Tetralogy of Fallot , kahi maʻi puʻuwai hānau e hiki ai ke hana i nā hōʻailona e like me kēia. ʻOiai paha he paʻakikī iki ka inoa, e wehewehe maʻalahi kākou.

He aha maoli ka Tetralogy o Fallot?

I ka ʻōlelo maʻalahi, ʻo Tetralogy of Fallot kahi hui pū ʻana o nā kīnā puʻuwai ʻehā i loaʻa i ka wā hānau. Ua kapa ʻia hoʻi ia he maʻi puʻuwai hānau. He pilikia ia e kū mai ana i ka wā o ka ulu ʻana o ka puʻuwai i ka wā e ulu ana ka pēpē i loko o ka ʻōpū. ʻO kēia ke kumu o ke koko waiwai i ka oxygen (koko ʻulaʻula) e hui pū me ke koko nele i ka oxygen (koko polū). A laila hoʻoneʻe ʻia kēia koko i hui ʻia e ka puʻuwai i ke kino. ʻO ka hopena, ʻaʻole lawa ka oxygen i nā ʻōpū o ke kino. I ka lāʻau lapaʻau, kapa mākou i kēia maʻi he hypoxemia . I mea e maopopo ai i kēia, e nānā kākou i ke ʻano o ka hana ʻana o ka puʻuwai olakino.

Pehea e hana ai ka puʻuwai olakino

E noʻonoʻo e like ko kākou puʻuwai me kahi hale ʻehā keʻena. Aia ʻelua keʻena ma ka papahele luna (atria) a me ʻelua keʻena nui ma ka papahele haʻahaʻa (ventricles). Aia nā kiwikā ma waena o kēia mau keʻena, e like me nā puka. Ua hoʻokaʻawale ʻia nā ʻaoʻao ʻākau a me ka hema o ka puʻuwai e kahi paia (septum). 1. ʻAoʻao ʻākau: Komo ke koko polū nele i ka oxygen o ke kino i ka atrium ʻākau ma o ka vena cava luna a me ka vena cava lalo. 2. Mai laila mai, hele ke koko ma o kahi kiwikā (tricuspid valve) i loko o ka ventricle ʻākau. 3. Mai ka ventricle ʻākau mai, hoʻopuka ʻia kēia koko polū ma o kekahi kiwikā ʻē aʻe (pulmonic valve) i loko o ke aʻa nui (pulmonary artery) e hele ana i nā māmā. 4. I loko o nā māmā: Hoʻopiha hou ʻia kēia koko me ka oxygen, a lilo i koko ʻulaʻula maʻemaʻe. 5. ʻAoʻao hema: Hoʻi kēia koko ʻulaʻula waiwai i ka oxygen i ka atrium hema o ka puʻuwai. 6. Mai laila mai, hele ia ma o kahi kiwikā (mitral valve) i loko o ka ventricle hema. 7. ʻO ka hope loa, ua hoʻopuka ʻia kēia koko ʻulaʻula maʻemaʻe mai ka ventricle hema ma o ke aʻa nui loa o ke kino (aorta) i ke kino holoʻokoʻa. Penei ke ala e loaʻa ai i ko kākou mau kino ka oxygen e pono ai lākou e ola.

ʻO nā hemahema ʻehā e kū mai ana ma Tetralogy of Fallot (ʻO ka "Tetralogy")

I loko o ka puʻuwai o kahi pēpē me Tetralogy of Fallot, ʻehā mau kīnā nui e hoʻololi ai i ke kaʻina hana maʻamau a mākou i kūkākūkā ai.

He aha ke kumu o kēia kūlana?

ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia. He kīnā ia e kū mai ana i ka wā e hoʻokumu ʻia ai nā ʻāpana puʻuwai i ka wā mua o ka ulu ʻana o ka pēpē i loko o ka ʻōpū. ʻAʻole ia he hewa nau, ʻaʻole hoʻi he mea āu i hana ai i ka wā hāpai. No laila, mai manaʻo hewa no ia mea.

Loaʻa i kāu pēpē kēia mau hōʻailona pū kekahi?

ʻO ka hapa nui o nā keiki me Tetralogy o Fallot e hōʻike i nā hōʻailona i loko o ka makahiki mua o ke ola.

• Polū (Cyanosis):ʻO kēia ka hōʻailona nui. Loaʻa i nā lehelehe, ke alelo, ka ʻili, a me nā kui o ke pēpē ke kala polū a ʻulaʻula paha.
• "Nā Kilokilo Tet / Hypercyanosis": He mea nui loa kēia. Ke uē kahi pēpē, inu waiū, hoʻāʻo e hele i ka lua, a ala aʻe paha i ke kakahiaka, hiki iā lākou ke lilo i polū hohonu, paʻakikī ka hanu ʻana, a lilo i mea hoʻomaha loa. I kekahi manawa hiki iā lākou ke nalowale ka ʻike. Hiki i kēia kūlana ke mau mai kekahi mau minuke a i kekahi mau hola.
• Paʻakikī ka hanu ʻana : Luhi koke ka pēpē a hiamoe ma hope o ka holo ʻana a me ka pāʻani ʻana.
• Kūlou: Ke luhi ke keiki liʻiliʻi i ka pāʻani ʻana, e noho koke lākou i lalo me ko lākou mau kuli i huki ʻia i luna i ko lākou umauma (kūlou). Hoʻonui kēia i ka nui o ke koko e hele ana i ko lākou mau māmā, e maʻalahi ai ka hanu ʻana .
• Ka holomua ʻole o ka ulu ʻana: ʻOi aku ka lohi o ka piʻi ʻana o ke kaumaha o ka pēpē, ka ulu ʻana, a me ka ulu ʻana ma mua o nā keiki ʻē aʻe.

Āhea ʻoe e ʻimi ai i ke aʻo lapaʻau?

Mai poina i ke keʻena lapaʻau mahina o kāu pēpē. Hiki i ke kauka ke ʻike i kēia mau kūlana i ka nānā ʻana i kāu pēpē. Inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona, ​​e ʻike koke i ke kauka.

• Inā polū ka ʻili a me nā lehelehe o ka pēpē.
• Inā pilikia ʻoe i ka hanu ʻana .
• Inā luhi ʻoe i ka wā e hānai waiū ana a i ʻole e uē ana.
• Inā manaʻo ʻoe e lohi ana kou ulu ʻana.

Inā loaʻa nā pilikia ma lalo nei, e lawe koke i ke kanaka i ka haukapila kokoke loa ʻo Emergency Department (ETU):

• Kilokilo Tet
• He mea paʻakikī loa ka hanu ʻana.
• Nā hopu ʻana
• Ka mae ʻana
• Luhi nui a nāwaliwali paha

Pehea e ʻike ʻia ai ka maʻi? (Nā hoʻāʻo a me ke kuhikuhi ʻana)

E nānā kāu kauka i ke pēpē, e hoʻolohe i ka puʻuwai o ka naʻau, a inā he kānalua, e kuhikuhi iā ʻoe no kekahi mau hoʻokolohua.

• ʻO ke kiʻi X-ray o ka umauma: Nānā kēia i ke ʻano o ka puʻuwai. I ka Tetralogy o Fallot, ʻike ʻia paha ka puʻuwai "ʻano kāmaʻa" no ka mea ua hoʻonui ʻia ka ventricle ʻākau.
• Electrocardiogram ( ECG ): He hoʻāʻo ʻeha ʻole e ana i ka hana uila o ka puʻuwai.
• ʻEchocardiogram (Echo):ʻO kēia ka hoʻāʻo koʻikoʻi a pololei loa. Ua like ia me kahi scan. Hiki iā ia ke ʻike maopopo i nā mea āpau i loko o ka puʻuwai, e like me nā keʻena, nā valves, nā lua ( VSD ), a me ka haiki ʻana (PS).
• Ka Catheterization o ka Puʻuwai: I kekahi mau hihia, hana ʻia kēia hoʻāʻo ma mua o ke ʻoki ʻana e ana i ke kaomi o ka puʻuwai a me nā pae oxygen, a e nānā pono i ke ʻano o nā aa koko. Ma kēia hoʻāʻo, hoʻokomo ʻia kahi ʻōmole liʻiliʻi ma o kahi aa koko ma ka ʻūhā i ka puʻuwai.

He aha nā lāʻau lapaʻau?

ʻO ke ʻoki kino wale nō ke ʻano lapaʻau mau loa no Tetralogy of Fallot.

He aha kāu e hana ai inā loaʻa iā ʻoe kahi "Tet Spell"?

Inā lilo koke kāu pēpē i polū loa, he mea nui loa ia e noho mālie . 1. E kau i ka pēpē ma kona kua, me nā kuli i huki ʻia i ka umauma (kūlana kuli-a-umauma) . 2. E lawe koke i ka pēpē i ka haukapila. Ma ka haukapila, e hāʻawi ʻia ka pēpē i ka oxygen a me nā lāʻau lapaʻau e like me ka propranolol e kāohi i nā "tet spell".

ʻoki kino

ʻO ka manawa o ke ʻoki ʻana ma muli o ke koʻikoʻi o nā hōʻailona o ka pēpē. Hana pinepine ʻia ke ʻoki ʻana i loko o nā makahiki ʻelua mua o ke ola.

• ʻO ke ʻoki kino palliative (Blalock-Taussig shunt): He liʻiliʻi loa a nāwaliwali paha kekahi mau pēpē a ʻaʻole hiki ke kū i ke ʻoki kino piha. I ia mau hihia, hana ʻia kahi pilina liʻiliʻi e like me ka paipu ma waena o kahi aʻa i loko o ke kino a me kahi aʻa i loko o ka māmā e hoʻonui i ka nui o ke koko e hele ana i nā māmā. Hiki i kēia ke kōkua i ka pēpē e nui iki a ikaika.
• ʻO ke ʻoki kino hoʻoponopono piha: Ma kēia, ua pani ʻia ka lua i loko o ka puʻuwai (VSD) me kahi ʻāpana, a ua hoʻonui ʻia ke alahaka haiki i nā māmā (PS). Ma hope o kēia ʻoki kino, hoʻi ke kahe o ke koko i loko o ka puʻuwai i ka maʻamau.

Me ka holomua o ka ʻenehana lapaʻau i kēia lā, ua holomua nui kēia ʻoki kino.

Ma hope o ke ʻoki kino...

Ma hope o ke ʻoki ʻana i ka holomua, hiki i ka hapa nui o nā keiki ke ola maʻamau me ka ʻole o nā hōʻailona a i ʻole nā ​​​​palena. Hiki iā lākou ke hele i ke kula, pāʻani, hana i ka wā e hiki mai ana, a mare. Eia nō naʻe, ma hope o ke ʻoki ʻana, he mea nui e loaʻa ka nānā mau ʻana me ke kauka i ko lākou ola a pau. I kekahi manawa, hiki ke loli i ka puʻuwai puʻuwai (arrhythmias), no laila he mea nui e loaʻa nā nānā mau. tetralogy o fallot, maʻi puʻuwai, pediatrics, pēpē polū, cyanosis, tet spell, kīnā hānau, kīnā puʻuwai hānau, lua i loko o ka puʻuwai, VSD