Hiki iā ʻoe ke noʻonoʻo i nā kīʻaha koko e lawe ana i ke koko mai ko kākou puʻuwai a i ko kākou mau māmā e emi mālie ana, e hoʻonui nui ana i ke koko? Ua like ia me ke kaomi ʻana i kahi paipu wai a piʻi ka wikiwiki o ka wai. ʻO kēia ka mea a mākou e kapa nei ʻo ' Pulmonary Arterial Hypertension' a i ʻole 'PAH' i ka lāʻau lapaʻau. He ʻano ʻokoʻa iki kēia mai ke koko kiʻekiʻe maʻamau a pono e nānā pono ʻia. Hiki i kēia ke hana i nā hōʻailona e like me ka pōkole o ka hanu, ka ʻeha o ka umauma, a me ka luhi nui. No laila i kēia lā e kamaʻilio mākou e pili ana i kahi lāʻau kūikawā i hoʻohana ʻia e mālama ai i kēia ʻano, ʻo ia ka inikini Treprostinil.
He aha ke ʻano lāʻau lapaʻau ʻo Treprostinil?
I ka ʻōlelo maʻalahi, ʻo Treprostinil (inoa inoa: Remodulin) kahi lāʻau lapaʻau i hāʻawi ʻia i nā poʻe me ka maʻi hypertension arterial pulmonary (PAH) aʻu i ʻōlelo ai ma mua. Hana kēia lāʻau lapaʻau ma ka hoʻonui iki ʻana i nā kīʻaha koko i haiki ʻia, e maʻalahi ai ke kahe ʻana o ke koko. Hoʻemi kēia i ka ukana hana ma ka puʻuwai a kōkua i ka kaohi ʻana i nā hōʻailona. Hoʻomaʻalahi hoʻi ia i ka hana ʻana i nā hana o kēlā me kēia lā. He lāʻau lapaʻau koʻikoʻi loa kēia e kōkua ai i ka hoʻomaikaʻi ʻana i ke ʻano o ke ola.
Hiki i kāu kauka ke kuhikuhi i kēia lāʻau lapaʻau no nā kūlana ʻē aʻe, no laila inā he mau nīnau kāu e pili ana i kēia, e ʻoluʻolu e nīnau i kāu kauka.
Nā mea e haʻi aku i kāu kauka ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau
Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui loa ia e hāʻawi i kāu kauka i kahi wehewehe piha o kou kūlana olakino. E hōʻoia e haʻi i kēia mau mea:
- Maʻi puʻupaʻa: Inā loaʻa iā ʻoe kekahi maʻi e pili ana i ka puʻupaʻa.
- Maʻi akepaʻa: Inā he pilikia me ka hana akepaʻa.
- Nā maʻi ʻaleka: E hōʻoia e haʻi i kāu kauka inā ua loaʻa iā ʻoe kahi maʻi ʻaleka iā Treprostinil, Epoprostenol, a i ʻole kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, a mea hoʻoluʻu paha.
- Hāpai: Inā hāpai ʻoe, e ho'āʻo ana e hāpai, a hānai waiū paha, pono ʻoe e kamaʻilio me kāu kauka ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau.
Pehea e pono ai iaʻu ke hoʻohana i kēia lāʻau lapaʻau?
ʻAʻole kēia e like me ka pila a i ʻole ka capsule a mākou e lawe mau ai. Hāʻawi ʻia ka inikini Treprostinil i loko o kou kino ma o kahi pamu liʻiliʻi e holo mau ana (infusion hoʻomau) . Komo ka lāʻau lapaʻau i loko o kou kino ma o kahi ʻōmole lahilahi, i kapa ʻia he catheter, i hoʻopili ʻia i kēia pamu. Hiki ke hana ʻia kēia ma nā ʻano ʻelua:
1. Subcutaneous: Hoʻokomo ʻia ke catheter ma lalo o ka ʻili a hāʻawi ʻia ka lāʻau lapaʻau.
2. Ma o kahi aa koko (Intravenous):Hoʻokomo pololei ʻia ke catheter i loko o kahi kīʻaha koko (vein) a lawelawe ʻia ka lāʻau lapaʻau.
E hāʻawi ʻia ʻoe i ke aʻo piha loa ma ka haukapila no ka hoʻohana ʻana i kēia, pehea e hoʻomākaukau ai i ka pamu, a pehea e hoʻokomo ai i ka catheter. He mea nui loa e hahai pono i nā ʻōlelo kuhikuhi i hāʻawi ʻia e ke kauka a me nā limahana kahu maʻi .
He mea nui loa: Mai ho'ōki i ka lawe ʻana i kēia lāʻau lapaʻau no kekahi kumu me ka ʻole o ke kūkākūkā ʻana me kāu hui lapaʻau. ʻO ka hoʻōki koke ʻana iā ia hiki ke hoʻonui i kou kūlana.
He aha kāu e hana ai me nā nila a me nā syringe i hoʻohana ʻia?
Mai hoʻolei i nā nila a me nā syringe i hoʻohana ʻia i loko o ka ʻōpala. Pono e waiho ʻia i loko o kahi pahu kūikawā (pahu ʻoi) i hāʻawi ʻia. Inā ʻaʻohe āu, e noi i kāu kauka a i ʻole ka haukapila no hoʻokahi.
Pono anei e hāʻawi ʻia kēia lāʻau lapaʻau i nā keiki?
Pono paha nā keiki i ka mālama kūikawā i ka hāʻawi ʻana i kēia lāʻau lapaʻau, no laila he mea nui e kūkākūkā i kēia me ke kauka pediatric no ka ʻōlelo aʻo.
He aha inā lawe nui wau i ka lāʻau lapaʻau?
Inā manaʻo ʻoe ua lawe nui ʻoe i ka lāʻau lapaʻau, e kāhea koke aku i ke Kikowaena ʻIke Poisons Lahui ma ka Halemai Lahui ʻo Colombo . A i ʻole e hele i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa.
Nā lāʻau ʻē aʻe e launa pū me kēia lāʻau (Nā Hana Lāʻau)
Hiki i nā lāʻau lapaʻau ʻē aʻe āu e lawe nei ke launa pū me Treprostinil, no laila e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei (me nā huaora, nā lāʻau lapaʻau lāʻau, a me nā mea hoʻohui).
| ʻAno lāʻau lapaʻau | Nā mea e makaʻala ai |
|---|---|
| ʻO kekahi mau lāʻau lapaʻau no ke koko kiʻekiʻe | Ke hui pū ʻia kēia mau mea me Treprostinil, e hāʻule paha ke koko i lalo loa. |
| Mea hoʻohuihui koko | Nā laʻana: Nā lāʻau lapaʻau e like me Warfarin, Enoxaparin, Dabigatran, Apixaban. Hiki i kēia ke hoʻonui i ka pilikia o ke kahe ʻana o ke koko. |
| Nā lāʻau lapaʻau | Hiki ke hoʻohaʻahaʻa i ke koko. |
| Nā lāʻau lapaʻau ʻē aʻe | Hiki i nā lāʻau lapaʻau e like me Gemfibrozil lāua ʻo Rifampin ke hoʻopilikia i ka pono o kēia lāʻau lapaʻau. |
Nā mea e hoʻomanaʻo ai i ka wā e lawe ai i ka lāʻau lapaʻau
- Nā nānā maʻamau: E hoʻomau i ka launa pū me kāu kauka i nā manawa a pau e nānā i ka holomua o kou kūlana. E hele pinepine i nā keʻena lapaʻau.
- ʻIli a puni ke catheter: E nānā pinepine i ka ʻili a puni ke catheter. Inā he ʻulaʻula ʻē, ʻeha, pehu, a i ʻole ka wai e like me ka pus, e hoʻomaopopo koke i kāu hui mālama ola. He hōʻailona paha kēia o ka maʻi.
- Inā e ʻoi aku ka ʻino o kou kūlana: I kekahi manawa e ʻoi aku ka ʻino o kou kūlana ma hope o ka lawe ʻana i kēia lāʻau lapaʻau. Inā manaʻo ʻoe i kēia ʻano, e like me ka paʻakikī o ka hanu ʻana a i ʻole ka ʻeha o ka umauma, e kāhea koke i kāu kauka. Pono paha e hoʻololi ʻia kāu mahele lāʻau.
Nā hopena ʻaoʻao e hiki mai ana ma muli o ka lāʻau lapaʻau
E like me nā lāʻau lapaʻau āpau, hiki iā Treprostinil ke hana i nā hopena ʻaoʻao. He koʻikoʻi kekahi o kēia mau mea, aʻo kekahi he mea maʻamau.
| Ka hoʻokaʻawale ʻana o nā hopena ʻaoʻao | |
|---|---|
| Nā hopena ʻaoʻao e pono e hōʻike koke ʻia i kāu kauka | |
| Nā hopena maʻi e like me ka ʻili ʻili, ka ʻūlū, ka hives | Ka pehu ʻana o ka maka, nā lehelehe, a i ʻole ke alelo |
| Paʻakikī ka hanu ʻana | ʻEha umauma |
| Ka wikiwiki, ke kuʻi ʻana, a i ʻole ka puʻuwai puʻuwai kūpono ʻole | Ka luaʻi, ka poniuniu, a me ka hāʻule ʻana |
| Kuni a i ʻole ke anu | ʻEha, ʻeha, a pehu paha ma kahi i inikini ʻia |
| ʻEha, ʻeha, a nalowale paha ka manaʻo ma nā lima a me nā wāwae | Ka nāwaliwali a luhi paha maʻamau ʻole |
| Nā hopena ʻaoʻao ʻaʻole i koʻikoʻi pinepine, akā pono e hōʻike ʻia i ke kauka inā hoʻomau lākou | |
| ʻEha iwi a ʻauwae paha | Ka maʻi pākī |
| Ka holoi ʻana | ʻEha poʻo |
| Ka luaʻi, ka luaʻi | |
Pehea e mālama ai i ka lāʻau lapaʻau?
No ka mālama ʻana i ka maikaʻi o ka lāʻau lapaʻau, he mea nui loa ia e mālama pono.
- E mālama ʻia mai nā keiki a me nā holoholona.
- Nā ʻōmole i wehe ʻole ʻia: E mālama ma kahi mahana ma waena o 15 a me 25 degere Celsius.
- Ma hope o ka wehe ʻana i kahi ʻōmole: Ma hope o ka lawe ʻana i ka mahele mua o ka lāʻau lapaʻau, pono e hoʻohana ʻia ka ʻōmole i loko o 30 mau lā.
- Lāʻau lapaʻau i pau ka lāʻau: Mai hoʻohana no kekahi kumu ma hope o ka lā pau.
- Nā lāʻau lapaʻau i loko o ka pamu:
- Inā hāʻawi ʻia ma lalo o ka ʻili: Hiki ke hoʻohana ʻia ka lāʻau lapaʻau i loko o hoʻokahi syringe a hiki i 72 mau hola. Ma hope o 72 mau hola, e hoʻolei i ke koena o ka lāʻau.
- Inā hāʻawi ʻia ma ke ʻano intravenous: Hiki ke hoʻohana ʻia ka lāʻau lapaʻau i loko o hoʻokahi syringe a hiki i 48 mau hola. E hoʻolei i ke koena o ka lāʻau lapaʻau ma hope o 48 mau hola.
Leka Lawe-Home
- He lāʻau lapaʻau koʻikoʻi ʻo Treprostinil no ka kaohi ʻana i ke koko kiʻekiʻe o ke aʻa pulmonary (PAH). Pono e hoʻohana wale ʻia e like me ke kuhikuhi a kāu kauka.
- Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, e haʻi i kāu kauka e pili ana i kou mau kūlana olakino a me nā lāʻau lapaʻau ʻē aʻe āu e lawe nei.
- Mai ho'ōki i ka lawe ʻana i kāu lāʻau lapaʻau me ke aʻo ʻole ʻia e ke kauka no kekahi kumu. Hiki ke lilo i mea weliweli loa.
- E makaʻala mau i nā hopena ʻino e like me ka ʻulaʻula, ka ʻeha, a me ka pehu ʻana ma kahi i inikini ʻia, a me ka ʻeha o ka umauma a me ka paʻakikī o ka hanu ʻana. Inā ʻike ʻoe i kekahi o kēia mau mea, e hoʻomaopopo koke i kāu kauka.
- He mea nui loa e mālama pono i nā lāʻau lapaʻau a hoʻolei aku i nā nila i hoʻohana ʻia me ka palekana.











💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo