Ua ʻike kākou a pau ʻaʻole like ke koko i loko o ko kākou kino me ka wai, akā, he wai me kahi mānoanoa. Akā, e noʻonoʻo, he aha ka mea e hana ai inā lilo kēia koko i ʻoi aku ka mānoanoa ma mua o ka maʻamau, e like me ka lepo mānoanoa? Lilo ia i mea paʻakikī no kēia koko mānoanoa ke neʻe ma waena o nā kīʻaha koko maikaʻi ma loko o ko kākou kino. Ua like ia me ka lepo mānoanoa e paʻa ana i loko o kahi paipu. Ma kēia ʻano, mānoanoa ke koko e like me ka waiū niu, a ua pilikia ke kahe ʻana o ke koko i loko o ke kino, ʻo ia ka mea a kākou e kapa nei he Hyperviscosity Syndrome i ka lāʻau lapaʻau. ʻAʻole kēia he mea liʻiliʻi wale nō, akā, i kekahi manawa he kūlana weliweli loa ia, e hoʻoweliweli ana i ke ola. E kamaʻilio maʻalahi kākou e pili ana i kēia, ma ke ʻano hiki iā ʻoe ke hoʻomaopopo.
No ke aha i mānoanoa koke ai ke koko?
ʻO ka mea mua e hoʻomaopopo ai, ʻaʻole he maʻi ka Hyperviscosity Syndrome. He hōʻailona ia o kekahi maʻi ʻē aʻe. E like me ka ʻū ʻana he hōʻailona ia o ke anu a i ʻole ka maʻi pneumonia. ʻO ka mānoanoa o ke koko ke kumu nui ʻia e ka nui o nā ʻano ʻano hunaola a i ʻole nā protein i loko o ke koko.
I ka ʻōlelo maʻalahi, inā piʻi ka nui o nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, nā platelets, a i ʻole nā protein serum i loko o ke koko i kahi ʻano ʻē, mānoanoa ke koko.
Aia ma ka papa ma lalo nei kekahi o nā kūlana olakino nui e hiki ai ke hoʻoulu i kēia ʻano.
| Nā kūlana e hiki ai ke hoʻoulu i ke koko | He wehewehe maʻalahi |
|---|---|
| ʻO ka Macroglobulinemia o Waldenström (WB) | ʻO kēia ke kumu maʻamau o ka hyperviscosity. He ʻano maʻi koko kēia e kū mai ana i loko o ka iwi iwi a me nā ʻiʻo lymphatic. Hoʻokumu ʻia ia e ka hana nui ʻana o kahi protein ʻē, ka mea e hoʻomānoanoa ai ke koko. |
| ʻO ka Myeloma lehulehu | He ʻano maʻi ʻaʻai kēia e hoʻopilikia ai i nā pūnaewele plasma. ʻO nā protein ʻano ʻē i hana ʻia e nā pūnaewele kanesa ke kumu o ka mānoanoa o ke koko. |
| ʻO ka Polycythemia Rubra Vera | He maʻi kēia o ka iwi iwi. Ma kēia ʻano, hana ʻia nā hunaola koko ʻulaʻula ma ke ʻano i kāohi ʻole ʻia. I ka piʻi ʻana o ka nui o nā hunaola koko ʻulaʻula, piʻi nui nō hoʻi ka mānoanoa o ke koko. |
| Leukemia | I loko o ka maʻi leukemia, kahi maʻi ʻaʻai koko, aia ka nui o ka hana ʻana o nā hunaola koko keʻokeʻo. Hiki ke ʻano ʻē kēia mau hunaola. Hiki i kēia ke kumu e ālai ʻia ai nā kīʻaha koko a mānoanoa ke koko. |
| Nā maʻi pili o ka ʻiʻo | Hiki ke loaʻa ke kāpili ʻana o ke koko i kekahi manawa i nā maʻi e like me ka rheumatoid arthritis, akā he mea kakaikahi loa kēia. |
| Nā kumu kakaikahi ʻē aʻe | Aia paha kekahi mau kumu ʻē aʻe, e like me ka cryoglobulinaemia (kahi maʻi e hoʻoulu ai i ka mumū o nā kīʻaha koko), ka hypoxia mau (nele mau o ka oxygen), a me kekahi mau lāʻau lapaʻau maʻi kanesa (Retinoic acid therapy). |
Pehea kou manaʻo ke mānoanoa kou koko? He aha nā hōʻailona?
E noʻonoʻo e pili ana i ia mea, ʻo kēlā me kēia ʻāpana o ko kākou kino, mai ka lolo a i nā wēlau o ko kākou mau manamana lima, ua lawe ʻia e ke koko, e lawe ana i ka oxygen a me nā meaʻai. No laila, ke ālai ʻia kēia kahe koko, ʻaʻole loaʻa i kēlā mau ʻāpana ka mea e pono ai. ʻO ia ke kumu e ʻike ʻia ai nā hōʻailona. Hiki ke ʻokoʻa kēia mau hōʻailona mai kēlā kanaka a kēia kanaka, a hiki nō hoʻi ke ʻokoʻa ma muli o ka maʻi mua i hoʻomānoanoa ai ke koko.
Eia kekahi o nā hōʻailona i ʻike pinepine ʻia:
Nā hōʻailona e hoʻopilikia ana i ka lolo a me ka ʻōnaehana nerve
Hiki ke hoʻopilikia nui ʻia ka lolo e ke kahe koko i hoʻopilikia ʻia.
- ʻEha poʻo nui a me ka poʻo hina
- Nā pilikia ʻike: ʻike maka pōwehiwehi, ʻike pālua, i kekahi manawa nalowale koke ka ʻike
- Nā pilikia lohe: emi a nalowale paha ka lohe
- Nā ʻōhūhū
- Luhi nui a me ka hiamoe (Lethargy)
Nā hōʻailona e pili ana i ke kahe koko
Ke mānoanoa ke koko, ua hoʻopilikia ʻia ke kaohi palupalu o ke kahe ʻana o ke koko, a hiki ke alakaʻi i ke kahe koko i manaʻo ʻole ʻia.
- ʻEha maʻalahi
- Ke kahe koko ʻana o ka mucosal (ke kahe koko o ka ihu, nā ʻāʻī)
- ʻO ke kahe koko ʻē aʻe (e.g., ke koko i loko o ka ʻōpala)
Nā hōʻailona koʻikoʻi ʻē aʻe
Hōʻike kēia mau mea ua hōʻino ʻia nā ʻōkana nui o ke kino.
- Ke koko kiʻekiʻe (Hypertension)
- Ka hāʻule ʻana o ka puʻuwai: ʻeha o ka umauma, pōkole o ka hanu
- Ka hāʻule ʻana o ka puʻupaʻa
- Nā ʻūpā koko (Thrombosis)
- Ka maʻi koʻikoʻi (Sepsis)
Inā loaʻa iā ʻoe a i ʻole kekahi āu i ʻike ai kekahi o kēia mau hōʻailona, he mea nui loa e ʻike koke i ke kauka me ka hoʻokaʻulua ʻole.
Pehea e mālama ai i kēia maʻi weliweli?
He pilikia olakino ka Hyperviscosity Syndrome no ka mea, inā ʻaʻole mālama ʻia, hiki iā ia ke hoʻopau i nā ʻōpū koʻikoʻi e like me ka lolo, ka puʻuwai, a me nā puʻupaʻa i ka oxygen, e alakaʻi ana i ka hōʻino mau loa a i ʻole ka hāʻule ʻana. No laila, he mea nui ka mālama koke ʻana.
ʻO ka maʻamau, ʻelua pae ka hoʻolālā lapaʻau.
1. Lapaʻau koke, pōkole
ʻO ka hana mua, ʻo ia ke kāohi i nā hōʻailona a hoʻemi koke i ka mānoanoa o ke koko. ʻO kekahi o nā lāʻau lapaʻau i hoʻohana pinepine ʻia no kēia ʻo Plasmapheresis .
He hana like ka Plasmapheresis me ka hoʻomaʻemaʻe koko. Lawe ʻia kahi liʻiliʻi o kou koko mai kou kino, hoʻoili ʻia ma o kahi mīkini kūikawā, a hoʻokaʻawale ʻia a lawe ʻia ka plasma, nona nā protein keu e hoʻoulu ai i kou koko e kulu. A laila hui pū ʻia nā hunaola koko ʻulaʻula a keʻokeʻo olakino me kahi wai pani a hoʻihoʻi ʻia i kou kino.
Hiki i kēia ke hōʻemi koke i ke kāpili ʻana o ke koko a hoʻōki i ka hōʻino ʻana o nā ʻōkana. Eia nō naʻe, na kāu hui lapaʻau e hoʻoholo inā kūpono kēia lāʻau no nā mea āpau a inā he mea pono.
2. Ka lāʻau lapaʻau lōʻihi (ka mālama ʻana i ka maʻi kumu)
Ma hope o ka hoʻēmi ʻana i ka mānoanoa o ke koko, ʻo ka mea nui aʻe, ʻo ia ka mālama ʻana i ka maʻi mua nāna i hoʻokumu . No ka mea, inā ʻaʻole mālama ʻia kēlā maʻi, hiki i ke koko ke mānoanoa hou.
- Inā he maʻi kanesa e like me Multiple Myeloma a i ʻole Leukemia ke kumu, hāʻawi ʻia nā lāʻau lapaʻau anti-cancer e like me ka chemotherapy .
- Inā he polycythaemia ke kumu, hāʻawi ʻia ka lāʻau e wehe i nā hunaola koko ʻulaʻula keu a hōʻemi paha i kā lākou hana ʻana.
- Inā he maʻi ʻē aʻe ia, e ʻōlelo nā kauka i nā lāʻau lapaʻau kūikawā no ia.
No kēia, e hui pū kahi hui o nā kauka, me nā hematologists, oncologists, a me nā nephrologists, e hoʻomohala i ka hoʻolālā lapaʻau maikaʻi loa nāu.
Leka Lawe-Home
- ʻO ka Hyperviscosity Syndrome kahi kūlana e mānoanoa ai ke koko e like me ka ʻaila niu, e ālai ana i ke kahe o ke koko i loko o ke kino.
- ʻAʻole kēia he maʻi ʻokoʻa. He hōʻailona ia o kekahi maʻi koʻikoʻi ʻē aʻe, e like me ke kanesa koko.
- Mai hoʻowahāwahā i nā hōʻailona e like me ke poʻo ʻeha nui, nā loli o ka ʻike, ke kahe koko ʻē, a i ʻole ka luhi nui.
- He pilikia olakino kēia. E ʻike koke i kāu kauka ke ʻike ʻoe i nā hōʻailona. Inā pono, e hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila.
- ʻO ka mālama ʻana e pili ana i nā hana koke e hōʻemi i ka mānoanoa o ke koko (e like me ka plasmapheresis) a me ka mālama ʻana i ka maʻi kumu.











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