Ke luhi nei ʻoe i kekahi manawa a ʻaʻole hiki iā ʻoe ke hana i kekahi mea liʻiliʻi loa? A i ʻole loaʻa iā ʻoe nā palapū polū ma kou kino me ka ʻole o ka pā ʻana i kekahi mea? Manaʻo paha ʻoe e maʻi pinepine ana ʻoe, e like me ke anu a i ʻole ka maʻi palū? ʻO kekahi kumu ma hope o kēia, ʻo ia ka emi ʻana o nā ʻano nui ʻekolu o nā hunaola koko. I ka lāʻau lapaʻau, kapa mākou i kēia ʻano he pancytopenia . Mai hopohopo, ʻaʻole kēia he maʻi, akā he hōʻailona o kekahi ʻano maʻi ʻē aʻe. E hoʻomaopopo pono kākou i kēia.
Nā ʻano o nā pūnaewele i loko o ko kākou koko a me kā lākou mau hana
I mea e hoʻomaopopo ai i kēia, pono mua kākou e ʻike e pili ana i nā koa nui ʻekolu i loko o ko kākou koko. Hoʻopuka ʻia kēia mau hunaola koko i loko o ka iwi ʻiʻo, kahi ʻāpana huʻahuʻa o ko kākou mau iwi.
Nā Kelepona Koko ʻUlaʻula
ʻO kēia nā pūnaewele e lawe ana i ka oxygen ma o ko kākou kino. Ke hanu kākou, hopu kēia mau pūnaewele koko ʻulaʻula i ka oxygen e komo mai ana i loko o ko kākou mau māmā a hāʻawi iā ia i kēlā me kēia pūnaewele i loko o ko kākou kino. Kōkua pū lākou i ka lawe ʻana i ke kalapona ʻokikene i hana ʻia i loko o nā pūnaewele i hoʻi i nā māmā a i waho. ʻO kēia mau pūnaewele ka mea e hāʻawi i ko kākou koko i kona kala ʻulaʻula.
Nā Kelepona Koko Keʻokeʻo
ʻO kēia ka pūʻali koa o ko mākou kino. E like me nā koa e pale aku ana i ka ʻāina. Mālama kēia mau hunaola koko keʻokeʻo iā mākou mai nā maʻi ma o ka ʻimi ʻana, hoʻouka ʻana, a me ka luku ʻana i nā ʻenemi o waho e like me nā maʻi a me nā bacteria e komo i loko o ko mākou kino.
Nā Platelets
ʻO kēia nā ʻāpana liʻiliʻi loa o ko kākou koko. Ua like lākou me nā pāpili liʻiliʻi ma ko kākou kino. Ke ʻeha kākou i kekahi wahi a hoʻomaka ke kahe ʻana o ke koko, ʻo kēia mau platelets nā mea e holo wikiwiki mai ana a pili pū e sila i ka ʻeha a hoʻōki i ke kahe ʻana o ke koko. Kāhea pū mākou i kēia he clotting koko.
No laila, ʻo ka pancytopenia, e like me kaʻu i ʻōlelo ai ma mua, he emi like ʻana o kēia mau ʻano cell koʻikoʻi ʻekolu. I ka pololei, he hui pū ʻana ia o ʻekolu mau maʻi koko:
* Anemia: Ka emi ʻana o nā hunaola koko ʻulaʻula.
* Leukopenia: Ka emi ʻana o nā hunaola koko keʻokeʻo.
* Thrombocytopenia: Ka emi ʻana o ka helu platelet.
He aha nā hōʻailona o ka pancytopenia?
ʻO nā hōʻailona o ka pancytopenia nā hōʻailona maoli i hoʻokumu ʻia e ka emi ʻana o nā ʻano ʻekolu o nā cell i ʻōlelo ʻia ma luna. I kekahi manawa, ʻaʻohe hōʻailona iki. E nānā kākou i nā hōʻailona e hiki ke kū mai ma lalo o kēlā me kēia o kēia mau kūlana.
| Ua emi ka helu o nā ʻāpana koko (inoa lapaʻau) | Nā hōʻailona maʻamau |
|---|---|
| Ua emi nā hunaola koko ʻulaʻula (Anemia) |
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| Ua emi nā hunaola koko keʻokeʻo (Leukopenia) |
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| Helu platelet haʻahaʻa (Thrombocytopenia) |
|
| Nā hōʻailona koʻikoʻi e pono ai ke kōkua koke ʻana o ke kauka a i ʻole e hele i ka ETU (Emergency Treatment Unit) | |
| |
He aha nā kumu o ka pancytopenia?
Nui nā kumu o ka pancytopenia. I kekahi manawa, ma hope o ka pau ʻana o nā hoʻokolohua āpau, aia nā hihia kahi i hiki ʻole ai ke loaʻa ke kumu . Kāhea mākou i kēia ʻo 'Idiopathic Pancytopenia'. Akā eia kekahi o nā kumu maʻamau:
- Nā maʻi e pili ana i ka iwi ʻiwi:Nā maʻi i hiki ʻole ai i ka iwi iwi ke hana i nā hunaola koko olakino kūpono. Eia kekahi laʻana, he maʻi i kapa ʻia ʻo 'Aplastic Anemia'.
- Kanesa: ʻO nā maʻi ʻaʻai koko a iwi paha, e like me ka leukemia a me ka lymphoma, e pālahalaha i ka iwi a hoʻopilikia i ka hana ʻana o nā ʻāpana olakino. Manaʻo ka poʻe he nui he leukemia ka pancytopenia. ʻAʻole, ʻaʻole ia. Akā ʻo ka leukemia ke kumu nui o ka pancytopenia.
- Nā lāʻau lapaʻau no ke kanesa: Hiki i ka chemotherapy a me ka radiation ke luku ʻaʻole wale i nā hunaola kanesa, akā, i nā hunaola koko olakino hoʻi e māhele koke ana.
- Nā maʻi viral: Hiki ke hana ʻia kēia ʻano e kekahi mau maʻi viral koʻikoʻi, e like me ka HIV, Hepatitis C, a me Mononucleosis.
- Nā maʻi Autoimmune: I kekahi manawa hoʻomaka hewa ka ʻōnaehana pale ponoʻī o ko mākou kino e hoʻouka i ko mākou mau hunaola koko olakino ponoʻī. ʻO Lupus kahi laʻana maikaʻi o kēia.
- Kekahi mau lāʻau lapaʻau: ʻOiai he mea kakaikahi, hiki ke loaʻa kēia ʻano ma ke ʻano he hopena ʻaoʻao o nā lāʻau lapaʻau e like me kekahi mau antibiotics a me nā lāʻau koko kiʻekiʻe. Mai ho'ōki i ka lawe ʻana i kekahi lāʻau lapaʻau me ka ʻole o ke kūkākūkā ʻana me kāu kauka.
- Ka ʻike ʻia ʻana i nā mea ʻawahia: ʻO ka ʻike ʻia ʻana i nā kemika e like me ka arsenic, benzene, a i ʻole ka radiation hiki ke hōʻino i ka iwi iwi.
- ʻO ka maʻi ate a me ka inu nui ʻana i ka waiʻona: ʻO nā maʻi e like me ka cirrhosis o ke akepaʻa hiki ke hoʻonui i ka spleen a hoʻopaʻa ʻia a luku ʻia nā hunaola koko.
- Nā hemahema meaʻai: Ma kekahi mau ʻāina, ʻo ka nele o nā meaʻai e like me ka huaora B12 a i ʻole folate kekahi kumu o kēia ʻano.
Pehea e ʻike ai i kēia maʻi?
Ke ʻike ʻoe i ke kauka, e nīnau mua ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, e nīnau e pili ana i kou mōʻaukala ʻohana o nā maʻi, a nānā iā ʻoe. Inā kānalua ʻia ka pancytopenia, hiki iā ia ke kauoha i kekahi mau hoʻokolohua, e like me:
- Helu Koko Piha (FBC): Hiki i kēia ke nānā pono i ka nui o nā hunaola ʻulaʻula, nā hunaola keʻokeʻo, a me nā platelet i loko o kou koko.
- ʻO ka Smear Koko Peripheral: Ua nānā ʻia kahi hāpana koko ma lalo o kahi microscope e ʻike ai inā he ʻano ʻē ke ʻano a me ke ʻano o nā cell.
- Biopsy Iwi ʻAoʻao: ʻO kēia ka hoʻāʻo paʻa loa. Lawe ʻia kahi ʻāpana liʻiliʻi o ka iwi ʻaoʻao mai kahi e like me ka iwi ʻūhā ma lalo o ka anesthesia a nānā ʻia e ʻike inā he maʻi i loko o ka iwi ʻaoʻao.
- Nā hoʻokolohua ʻē aʻe: Eia kekahi, hiki ke hana ʻia nā hoʻokolohua e like me nā pae huaora, ka hana ate, a me nā hoʻokolohua no nā maʻi e ʻike ai i ke kumu.
Pehea e mālama ʻia ai ka pancytopenia?
ʻO ka mea nui e hoʻomanaʻo ai, ʻo ia kēia: ʻO ka mālama ʻana no ka pancytopenia e pili ana i ke kūlana kumu i hoʻokumu ai. E hoʻāʻo mua nā kauka e ʻimi i ke kumu a mālama iā ia.
- Inā he hemahema meaʻai ke kumu, hiki ke hoʻoponopono ʻia me ka ʻai kūpono a me nā mea hoʻopihapiha wikamina.
- Inā he lāʻau lapaʻau ke kumu, e hoʻōki ke kauka i kēlā lāʻau lapaʻau a kuhikuhi i kekahi lāʻau lapaʻau kūpono ʻē aʻe.
- Inā ma muli o kahi maʻi , e mālama ʻia kēlā maʻi.
- Inā he maʻi autoimmune ke kumu, hāʻawi ʻia nā lāʻau lapaʻau e kāohi ana i ka ʻōnaehana pale.
ʻOiai e mālama ana i ke kumu kumu, hoʻohana ʻia nā lāʻau lapaʻau e like me kēia e mālama i ka pancytopenia:
- Nā Hoʻoili Koko: Inā haʻahaʻa loa ka helu o nā hunaola koko ʻulaʻula a i ʻole nā platelet, hāʻawi ʻia ke koko mai nā kumu o waho e hoʻihoʻi koke iā ia.
- Nā lāʻau hoʻouluulu iwi: Hāʻawi ʻia nā inikini e kōkua i ka iwi iwi e hana i nā hunaola koko hou aʻe.
- Hoʻoili Kelepona Kumu a i ʻole ka Iwi Moa: I kekahi mau hihia koʻikoʻi, wehe ʻia ka iwi iwi maʻi a hoʻololi ʻia me ka iwi iwi olakino.
Leka Lawe-Home
- ʻAʻole he maʻi ka Pancytopenia, akā he kūlana i hoʻokumu ʻia e ka emi ʻana o nā ʻano nui ʻekolu o nā cell i loko o kou koko (ʻulaʻula, keʻokeʻo, a me nā platelets).
- He hōʻailona pinepine kēia o kekahi maʻi ʻē aʻe, no laila ʻo ka mea nui ka ʻimi ʻana i ke kumu.
- Inā loaʻa iā ʻoe nā hōʻailona e like me ka luhi hiki ʻole ke hoʻomanawanui, nā ʻehaʻeha pinepine, a me ka maʻi pinepine, mai hoʻowahāwahā iā lākou a e ʻike i ke kauka kūpono.
- Ke ʻike ʻia ke kumu kūpono a mālama ʻia, hiki ke hoʻomalu pinepine ʻia a hoʻōla loa ʻia paha kēia ʻano. No laila, mai hopohopo.
- Mai hoʻomaka a hoʻōki paha i ka lāʻau lapaʻau ma kāu iho. E hahai mau i nā ʻōlelo a kāu kauka.











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